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What is Reactome ?
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Digital Preservation
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H2O [mitochondrial matrix]
Stable Identifier
R-ALL-113521
Type
Chemical Compound [SimpleEntity]
Compartment
mitochondrial matrix
Synonyms
water
Icon
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Plasmodium falciparum
Rattus norvegicus
Saccharomyces cerevisiae
Schizosaccharomyces pombe
Sus scrofa
Xenopus tropicalis
Expand all
Cellular responses to stimuli (Bos taurus)
Cellular responses to stress (Bos taurus)
Cellular response to chemical stress (Bos taurus)
Cytoprotection by HMOX1 (Bos taurus)
Electron transfer from reduced cytochrome c to molecular oxygen (Bos taurus)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Bos taurus)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Bos taurus)
H2O [mitochondrial matrix]
NUDT2 hydrolyses GP4G to GTP, GMP (Bos taurus)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Bos taurus)
H2O [mitochondrial matrix]
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Bos taurus)
H2O [mitochondrial matrix]
Mitochondrial unfolded protein response (UPRmt) (Bos taurus)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Bos taurus)
H2O [mitochondrial matrix]
DNA Repair (Bos taurus)
Base Excision Repair (Bos taurus)
Resolution of Abasic Sites (AP sites) (Bos taurus)
Resolution of AP sites via the multiple-nucleotide patch replacement pathway (Bos taurus)
POLB-Dependent Long Patch Base Excision Repair (Bos taurus)
ADPRHL2 hydrolyses poly(ADP-ribose) (Bos taurus)
H2O [mitochondrial matrix]
Extracellular matrix organization (Bos taurus)
Degradation of the extracellular matrix (Bos taurus)
Collagen degradation (Bos taurus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Bos taurus)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Bos taurus)
RNA Polymerase II Transcription (Bos taurus)
Generic Transcription Pathway (Bos taurus)
Transcriptional Regulation by TP53 (Bos taurus)
TP53 Regulates Metabolic Genes (Bos taurus)
Electron transfer from reduced cytochrome c to molecular oxygen (Bos taurus)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Bos taurus)
H2O [mitochondrial matrix]
Metabolism (Bos taurus)
Aerobic respiration and respiratory electron transport (Bos taurus)
Citric acid cycle (TCA cycle) (Bos taurus)
CS acetylates OA to citrate (Bos taurus)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Bos taurus)
H2O [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Bos taurus)
ATPase synthesizes ATP (Bos taurus)
H2O [mitochondrial matrix]
Pyruvate metabolism (Bos taurus)
Regulation of pyruvate metabolism (Bos taurus)
Regulation of pyruvate dehydrogenase (PDH) complex (Bos taurus)
PDP1,2 dephosphorylate p-lipo-PDH (Bos taurus)
H2O [mitochondrial matrix]
SIRT4 cleaves lipoyl from DLAT (Bos taurus)
H2O [mitochondrial matrix]
Respiratory electron transport (Bos taurus)
Electron transfer from reduced cytochrome c to molecular oxygen (Bos taurus)
H2O [mitochondrial matrix]
Biological oxidations (Bos taurus)
Phase I - Functionalization of compounds (Bos taurus)
Cytochrome P450 - arranged by substrate type (Bos taurus)
Endogenous sterols (Bos taurus)
CYP11A1 cleaves 20a,22b-DHCHOL (Bos taurus)
H2O [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Bos taurus)
H2O [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Bos taurus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Bos taurus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Bos taurus)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Bos taurus)
H2O [mitochondrial matrix]
Vitamins (Bos taurus)
CYP24A1 24-hydroxylates CTL (Bos taurus)
H2O [mitochondrial matrix]
Ethanol oxidation (Bos taurus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Bos taurus)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Bos taurus)
H2O [mitochondrial matrix]
Phase II - Conjugation of compounds (Bos taurus)
Glucuronidation (Bos taurus)
ABHD10 hydrolyses MPAG (Bos taurus)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Bos taurus)
Branched-chain amino acid catabolism (Bos taurus)
ECHS1 hydrates methacrylyl-CoA (Bos taurus)
H2O [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Bos taurus)
H2O [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Bos taurus)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Bos taurus)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Bos taurus)
H2O [mitochondrial matrix]
Choline catabolism (Bos taurus)
ALDH7A1 oxidises BETALD to BET (Bos taurus)
H2O [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Bos taurus)
H2O [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Bos taurus)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Bos taurus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Bos taurus)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Bos taurus)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Bos taurus)
H2O [mitochondrial matrix]
Lysine catabolism (Bos taurus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Bos taurus)
H2O [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Bos taurus)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Bos taurus)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Bos taurus)
H2O [mitochondrial matrix]
Proline catabolism (Bos taurus)
ALDH4A1 oxidises L-GluSS to Glu (Bos taurus)
H2O [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-5COOH (Bos taurus)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Bos taurus)
Degradation of cysteine and homocysteine (Bos taurus)
Sulfide oxidation to sulfate (Bos taurus)
Persulfide sulfur is dioxygenated (Bos taurus)
H2O [mitochondrial matrix]
Sulfite is oxidized to sulfate (Bos taurus)
H2O [mitochondrial matrix]
Urea cycle (Bos taurus)
arginine + H2O => ornithine + urea [ARG2] (Bos taurus)
H2O [mitochondrial matrix]
Metabolism of lipids (Bos taurus)
Fatty acid metabolism (Bos taurus)
Mitochondrial Fatty Acid Beta-Oxidation (Bos taurus)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Bos taurus)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Bos taurus)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Bos taurus)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Bos taurus)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Bos taurus)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Bos taurus)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Bos taurus)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Bos taurus)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Bos taurus)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Bos taurus)
H2O [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Bos taurus)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Bos taurus)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Bos taurus)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Bos taurus)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Bos taurus)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Bos taurus)
H2O [mitochondrial matrix]
Metabolism of steroids (Bos taurus)
Bile acid and bile salt metabolism (Bos taurus)
Synthesis of bile acids and bile salts (Bos taurus)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Bos taurus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Bos taurus)
H2O [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Bos taurus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Bos taurus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Bos taurus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Bos taurus)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Bos taurus)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Bos taurus)
CYP27A1 27-hydroxylates CHOL (Bos taurus)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Bos taurus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Bos taurus)
H2O [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Bos taurus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Bos taurus)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Bos taurus)
H2O [mitochondrial matrix]
Metabolism of steroid hormones (Bos taurus)
Glucocorticoid biosynthesis (Bos taurus)
CYP11B1 oxidises 11DCORT (Bos taurus)
H2O [mitochondrial matrix]
Mineralocorticoid biosynthesis (Bos taurus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Bos taurus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Bos taurus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Bos taurus)
H2O [mitochondrial matrix]
Pregnenolone biosynthesis (Bos taurus)
CYP11A1 cleaves 20a,22b-DHCHOL (Bos taurus)
H2O [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Bos taurus)
H2O [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Bos taurus)
H2O [mitochondrial matrix]
Phospholipid metabolism (Bos taurus)
Glycerophospholipid biosynthesis (Bos taurus)
Acyl chain remodeling of CL (Bos taurus)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Bos taurus)
H2O [mitochondrial matrix]
Acyl chain remodelling of PG (Bos taurus)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Bos taurus)
H2O [mitochondrial matrix]
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Bos taurus)
H2O [mitochondrial matrix]
Synthesis of PA (Bos taurus)
ACP6 hydrolyses MYS-LPA (Bos taurus)
H2O [mitochondrial matrix]
Synthesis of PE (Bos taurus)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Bos taurus)
H2O [mitochondrial matrix]
Metabolism of nucleotides (Bos taurus)
Interconversion of nucleotide di- and triphosphates (Bos taurus)
NUDT13 hydrolyses AP6A to AP4 and ADP (Bos taurus)
H2O [mitochondrial matrix]
Nucleotide catabolism (Bos taurus)
Purine catabolism (Bos taurus)
Phosphate bond hydrolysis by NUDT proteins (Bos taurus)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Bos taurus)
H2O [mitochondrial matrix]
Pyrimidine catabolism (Bos taurus)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Bos taurus)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Bos taurus)
Heme biosynthesis (Bos taurus)
COX10 transforms heme to heme O (Bos taurus)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Bos taurus)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Bos taurus)
Metabolism of cofactors (Bos taurus)
Ubiquinol biosynthesis (Bos taurus)
COQ6 hydroxylates DHB (Bos taurus)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Bos taurus)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Bos taurus)
Metabolism of folate and pterines (Bos taurus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Bos taurus)
H2O [mitochondrial matrix]
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Bos taurus)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Bos taurus)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Bos taurus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Bos taurus)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Bos taurus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Bos taurus)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Bos taurus)
H2O [mitochondrial matrix]
Metabolism of proteins (Bos taurus)
Mitochondrial protein degradation (Bos taurus)
AFG3L2 degrades mitochondrial inner membrane proteins (Bos taurus)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Bos taurus)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Bos taurus)
H2O [mitochondrial matrix]
CLPXP degrades mitochondrial matrix proteins (Bos taurus)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Bos taurus)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Bos taurus)
H2O [mitochondrial matrix]
Translation (Bos taurus)
tRNA Aminoacylation (Bos taurus)
Mitochondrial tRNA aminoacylation (Bos taurus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Bos taurus)
H2O [mitochondrial matrix]
Muscle contraction (Bos taurus)
Smooth Muscle Contraction (Bos taurus)
ALDH2 transforms GTN to NO (Bos taurus)
H2O [mitochondrial matrix]
Neuronal System (Bos taurus)
Transmission across Chemical Synapses (Bos taurus)
Neurotransmitter release cycle (Bos taurus)
GABA synthesis, release, reuptake and degradation (Bos taurus)
Degradation of GABA (Bos taurus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Bos taurus)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Bos taurus)
glutamine + H2O => glutamate + NH4+ (GLS) (Bos taurus)
H2O [mitochondrial matrix]
Programmed Cell Death (Bos taurus)
Apoptosis (Bos taurus)
Regulation of Apoptosis (Bos taurus)
OMA1 hydrolyses OPA1 (Bos taurus)
H2O [mitochondrial matrix]
Transport of small molecules (Bos taurus)
ABC-family proteins mediated transport (Bos taurus)
Mitochondrial ABC transporters (Bos taurus)
ABC7, mABC1 and mABC2 mediate heme transport (Bos taurus)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Caenorhabditis elegans)
Cellular responses to stress (Caenorhabditis elegans)
Cellular response to chemical stress (Caenorhabditis elegans)
Detoxification of Reactive Oxygen Species (Caenorhabditis elegans)
NUDT2 hydrolyses GP4G to GTP, GMP (Caenorhabditis elegans)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Extracellular matrix organization (Caenorhabditis elegans)
Degradation of the extracellular matrix (Caenorhabditis elegans)
Collagen degradation (Caenorhabditis elegans)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Caenorhabditis elegans)
RNA Polymerase II Transcription (Caenorhabditis elegans)
Generic Transcription Pathway (Caenorhabditis elegans)
Transcriptional Regulation by TP53 (Caenorhabditis elegans)
TP53 Regulates Metabolic Genes (Caenorhabditis elegans)
glutamine + H2O => glutamate + NH4+ (GLS) (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Metabolism (Caenorhabditis elegans)
Aerobic respiration and respiratory electron transport (Caenorhabditis elegans)
Citric acid cycle (TCA cycle) (Caenorhabditis elegans)
CS acetylates OA to citrate (Caenorhabditis elegans)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Caenorhabditis elegans)
ATPase synthesizes ATP (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Pyruvate metabolism (Caenorhabditis elegans)
Regulation of pyruvate metabolism (Caenorhabditis elegans)
Regulation of pyruvate dehydrogenase (PDH) complex (Caenorhabditis elegans)
PDP1,2 dephosphorylate p-lipo-PDH (Caenorhabditis elegans)
H2O [mitochondrial matrix]
SIRT4 cleaves lipoyl from DLAT (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Biological oxidations (Caenorhabditis elegans)
Phase I - Functionalization of compounds (Caenorhabditis elegans)
Ethanol oxidation (Caenorhabditis elegans)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Caenorhabditis elegans)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Caenorhabditis elegans)
Branched-chain amino acid catabolism (Caenorhabditis elegans)
ECHS1 hydrates methacrylyl-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Choline catabolism (Caenorhabditis elegans)
ALDH7A1 oxidises BETALD to BET (Caenorhabditis elegans)
H2O [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Caenorhabditis elegans)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Caenorhabditis elegans)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Caenorhabditis elegans)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Lysine catabolism (Caenorhabditis elegans)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Caenorhabditis elegans)
H2O [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Caenorhabditis elegans)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Caenorhabditis elegans)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Proline catabolism (Caenorhabditis elegans)
PRODH2 oxidises HPRO to 1PYR-5COOH (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Caenorhabditis elegans)
Degradation of cysteine and homocysteine (Caenorhabditis elegans)
Sulfide oxidation to sulfate (Caenorhabditis elegans)
Persulfide sulfur is dioxygenated (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Sulfite is oxidized to sulfate (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Urea cycle (Caenorhabditis elegans)
arginine + H2O => ornithine + urea [ARG2] (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Metabolism of lipids (Caenorhabditis elegans)
Fatty acid metabolism (Caenorhabditis elegans)
Mitochondrial Fatty Acid Beta-Oxidation (Caenorhabditis elegans)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Caenorhabditis elegans)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Caenorhabditis elegans)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Caenorhabditis elegans)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Caenorhabditis elegans)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Caenorhabditis elegans)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Caenorhabditis elegans)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Caenorhabditis elegans)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Caenorhabditis elegans)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Phospholipid metabolism (Caenorhabditis elegans)
Glycerophospholipid biosynthesis (Caenorhabditis elegans)
Synthesis of PA (Caenorhabditis elegans)
ACP6 hydrolyses MYS-LPA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Synthesis of PE (Caenorhabditis elegans)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Metabolism of nucleotides (Caenorhabditis elegans)
Nucleotide catabolism (Caenorhabditis elegans)
Purine catabolism (Caenorhabditis elegans)
Phosphate bond hydrolysis by NUDT proteins (Caenorhabditis elegans)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Caenorhabditis elegans)
Heme biosynthesis (Caenorhabditis elegans)
COX10 transforms heme to heme O (Caenorhabditis elegans)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Caenorhabditis elegans)
Metabolism of cofactors (Caenorhabditis elegans)
Ubiquinol biosynthesis (Caenorhabditis elegans)
COQ6 hydroxylates DHB (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Caenorhabditis elegans)
Metabolism of folate and pterines (Caenorhabditis elegans)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Caenorhabditis elegans)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Caenorhabditis elegans)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Metabolism of proteins (Caenorhabditis elegans)
Mitochondrial protein degradation (Caenorhabditis elegans)
AFG3L2 degrades mitochondrial inner membrane proteins (Caenorhabditis elegans)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Caenorhabditis elegans)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Caenorhabditis elegans)
H2O [mitochondrial matrix]
CLPXP degrades mitochondrial matrix proteins (Caenorhabditis elegans)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Caenorhabditis elegans)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Translation (Caenorhabditis elegans)
tRNA Aminoacylation (Caenorhabditis elegans)
Mitochondrial tRNA aminoacylation (Caenorhabditis elegans)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Muscle contraction (Caenorhabditis elegans)
Smooth Muscle Contraction (Caenorhabditis elegans)
ALDH2 transforms GTN to NO (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Neuronal System (Caenorhabditis elegans)
Transmission across Chemical Synapses (Caenorhabditis elegans)
Neurotransmitter release cycle (Caenorhabditis elegans)
GABA synthesis, release, reuptake and degradation (Caenorhabditis elegans)
Degradation of GABA (Caenorhabditis elegans)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Caenorhabditis elegans)
glutamine + H2O => glutamate + NH4+ (GLS) (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Transport of small molecules (Caenorhabditis elegans)
ABC-family proteins mediated transport (Caenorhabditis elegans)
Mitochondrial ABC transporters (Caenorhabditis elegans)
ABC7, mABC1 and mABC2 mediate heme transport (Caenorhabditis elegans)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Canis familiaris)
Cellular responses to stress (Canis familiaris)
Cellular response to chemical stress (Canis familiaris)
Cytoprotection by HMOX1 (Canis familiaris)
Electron transfer from reduced cytochrome c to molecular oxygen (Canis familiaris)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Canis familiaris)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Canis familiaris)
H2O [mitochondrial matrix]
NUDT2 hydrolyses GP4G to GTP, GMP (Canis familiaris)
H2O [mitochondrial matrix]
Mitochondrial unfolded protein response (UPRmt) (Canis familiaris)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Canis familiaris)
H2O [mitochondrial matrix]
Extracellular matrix organization (Canis familiaris)
Degradation of the extracellular matrix (Canis familiaris)
Collagen degradation (Canis familiaris)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Canis familiaris)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Canis familiaris)
RNA Polymerase II Transcription (Canis familiaris)
Generic Transcription Pathway (Canis familiaris)
Transcriptional Regulation by TP53 (Canis familiaris)
TP53 Regulates Metabolic Genes (Canis familiaris)
Electron transfer from reduced cytochrome c to molecular oxygen (Canis familiaris)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism (Canis familiaris)
Aerobic respiration and respiratory electron transport (Canis familiaris)
Citric acid cycle (TCA cycle) (Canis familiaris)
CS acetylates OA to citrate (Canis familiaris)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Canis familiaris)
H2O [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Canis familiaris)
ATPase synthesizes ATP (Canis familiaris)
H2O [mitochondrial matrix]
Pyruvate metabolism (Canis familiaris)
Regulation of pyruvate metabolism (Canis familiaris)
Regulation of pyruvate dehydrogenase (PDH) complex (Canis familiaris)
PDP1,2 dephosphorylate p-lipo-PDH (Canis familiaris)
H2O [mitochondrial matrix]
SIRT4 cleaves lipoyl from DLAT (Canis familiaris)
H2O [mitochondrial matrix]
Respiratory electron transport (Canis familiaris)
Electron transfer from reduced cytochrome c to molecular oxygen (Canis familiaris)
H2O [mitochondrial matrix]
Biological oxidations (Canis familiaris)
Phase I - Functionalization of compounds (Canis familiaris)
Cytochrome P450 - arranged by substrate type (Canis familiaris)
Endogenous sterols (Canis familiaris)
CYP11A1 cleaves 20a,22b-DHCHOL (Canis familiaris)
H2O [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Canis familiaris)
H2O [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Canis familiaris)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Canis familiaris)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Canis familiaris)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Canis familiaris)
H2O [mitochondrial matrix]
Vitamins (Canis familiaris)
CYP24A1 24-hydroxylates CTL (Canis familiaris)
H2O [mitochondrial matrix]
Ethanol oxidation (Canis familiaris)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Canis familiaris)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Canis familiaris)
H2O [mitochondrial matrix]
Phase II - Conjugation of compounds (Canis familiaris)
Glucuronidation (Canis familiaris)
ABHD10 hydrolyses MPAG (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Canis familiaris)
Branched-chain amino acid catabolism (Canis familiaris)
ECHS1 hydrates methacrylyl-CoA (Canis familiaris)
H2O [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Canis familiaris)
H2O [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Canis familiaris)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Canis familiaris)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Canis familiaris)
H2O [mitochondrial matrix]
Choline catabolism (Canis familiaris)
ALDH7A1 oxidises BETALD to BET (Canis familiaris)
H2O [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Canis familiaris)
H2O [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Canis familiaris)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Canis familiaris)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Canis familiaris)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Canis familiaris)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Canis familiaris)
H2O [mitochondrial matrix]
Lysine catabolism (Canis familiaris)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Canis familiaris)
H2O [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Canis familiaris)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Canis familiaris)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Canis familiaris)
H2O [mitochondrial matrix]
Proline catabolism (Canis familiaris)
ALDH4A1 oxidises L-GluSS to Glu (Canis familiaris)
H2O [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-5COOH (Canis familiaris)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Canis familiaris)
Degradation of cysteine and homocysteine (Canis familiaris)
Sulfide oxidation to sulfate (Canis familiaris)
Persulfide sulfur is dioxygenated (Canis familiaris)
H2O [mitochondrial matrix]
Sulfite is oxidized to sulfate (Canis familiaris)
H2O [mitochondrial matrix]
Urea cycle (Canis familiaris)
arginine + H2O => ornithine + urea [ARG2] (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism of lipids (Canis familiaris)
Fatty acid metabolism (Canis familiaris)
Fatty acyl-CoA biosynthesis (Canis familiaris)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Canis familiaris)
H2O [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Canis familiaris)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Canis familiaris)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Canis familiaris)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Canis familiaris)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Canis familiaris)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Canis familiaris)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Canis familiaris)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Canis familiaris)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Canis familiaris)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Canis familiaris)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Canis familiaris)
H2O [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Canis familiaris)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Canis familiaris)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Canis familiaris)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Canis familiaris)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Canis familiaris)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism of steroids (Canis familiaris)
Bile acid and bile salt metabolism (Canis familiaris)
Synthesis of bile acids and bile salts (Canis familiaris)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Canis familiaris)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Canis familiaris)
H2O [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Canis familiaris)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Canis familiaris)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Canis familiaris)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Canis familiaris)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Canis familiaris)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Canis familiaris)
CYP27A1 27-hydroxylates CHOL (Canis familiaris)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Canis familiaris)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Canis familiaris)
H2O [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Canis familiaris)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Canis familiaris)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism of steroid hormones (Canis familiaris)
Glucocorticoid biosynthesis (Canis familiaris)
CYP11B1 oxidises 11DCORT (Canis familiaris)
H2O [mitochondrial matrix]
Mineralocorticoid biosynthesis (Canis familiaris)
CYP11B2 18-hydroxylates CORST to 18HCORST (Canis familiaris)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Canis familiaris)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Canis familiaris)
H2O [mitochondrial matrix]
Pregnenolone biosynthesis (Canis familiaris)
CYP11A1 cleaves 20a,22b-DHCHOL (Canis familiaris)
H2O [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Canis familiaris)
H2O [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Canis familiaris)
H2O [mitochondrial matrix]
Phospholipid metabolism (Canis familiaris)
Glycerophospholipid biosynthesis (Canis familiaris)
Acyl chain remodeling of CL (Canis familiaris)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Canis familiaris)
H2O [mitochondrial matrix]
Acyl chain remodelling of PG (Canis familiaris)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Canis familiaris)
H2O [mitochondrial matrix]
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Canis familiaris)
H2O [mitochondrial matrix]
Synthesis of PA (Canis familiaris)
ACP6 hydrolyses MYS-LPA (Canis familiaris)
H2O [mitochondrial matrix]
Synthesis of PE (Canis familiaris)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism of nucleotides (Canis familiaris)
Interconversion of nucleotide di- and triphosphates (Canis familiaris)
NUDT13 hydrolyses AP6A to AP4 and ADP (Canis familiaris)
H2O [mitochondrial matrix]
Nucleotide catabolism (Canis familiaris)
Purine catabolism (Canis familiaris)
Phosphate bond hydrolysis by NUDT proteins (Canis familiaris)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Canis familiaris)
H2O [mitochondrial matrix]
Pyrimidine catabolism (Canis familiaris)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Canis familiaris)
Heme biosynthesis (Canis familiaris)
COX10 transforms heme to heme O (Canis familiaris)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Canis familiaris)
Metabolism of cofactors (Canis familiaris)
Ubiquinol biosynthesis (Canis familiaris)
COQ6 hydroxylates DHB (Canis familiaris)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Canis familiaris)
Metabolism of folate and pterines (Canis familiaris)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Canis familiaris)
H2O [mitochondrial matrix]
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Canis familiaris)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Canis familiaris)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Canis familiaris)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Canis familiaris)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Canis familiaris)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Canis familiaris)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Canis familiaris)
H2O [mitochondrial matrix]
Metabolism of proteins (Canis familiaris)
Mitochondrial protein degradation (Canis familiaris)
AFG3L2 degrades mitochondrial inner membrane proteins (Canis familiaris)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Canis familiaris)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Canis familiaris)
H2O [mitochondrial matrix]
CLPXP degrades mitochondrial matrix proteins (Canis familiaris)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Canis familiaris)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Canis familiaris)
H2O [mitochondrial matrix]
Translation (Canis familiaris)
tRNA Aminoacylation (Canis familiaris)
Mitochondrial tRNA aminoacylation (Canis familiaris)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Canis familiaris)
H2O [mitochondrial matrix]
Muscle contraction (Canis familiaris)
Smooth Muscle Contraction (Canis familiaris)
ALDH2 transforms GTN to NO (Canis familiaris)
H2O [mitochondrial matrix]
Neuronal System (Canis familiaris)
Transmission across Chemical Synapses (Canis familiaris)
Neurotransmitter release cycle (Canis familiaris)
GABA synthesis, release, reuptake and degradation (Canis familiaris)
Degradation of GABA (Canis familiaris)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Canis familiaris)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Canis familiaris)
glutamine + H2O => glutamate + NH4+ (GLS) (Canis familiaris)
H2O [mitochondrial matrix]
Programmed Cell Death (Canis familiaris)
Apoptosis (Canis familiaris)
Regulation of Apoptosis (Canis familiaris)
OMA1 hydrolyses OPA1 (Canis familiaris)
H2O [mitochondrial matrix]
Transport of small molecules (Canis familiaris)
ABC-family proteins mediated transport (Canis familiaris)
Mitochondrial ABC transporters (Canis familiaris)
ABC7, mABC1 and mABC2 mediate heme transport (Canis familiaris)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Danio rerio)
Cellular responses to stress (Danio rerio)
Cellular response to chemical stress (Danio rerio)
Cytoprotection by HMOX1 (Danio rerio)
Electron transfer from reduced cytochrome c to molecular oxygen (Danio rerio)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Danio rerio)
NUDT2 hydrolyses GP4G to GTP, GMP (Danio rerio)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Danio rerio)
H2O [mitochondrial matrix]
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Danio rerio)
H2O [mitochondrial matrix]
DNA Repair (Danio rerio)
Base Excision Repair (Danio rerio)
Resolution of Abasic Sites (AP sites) (Danio rerio)
Resolution of AP sites via the multiple-nucleotide patch replacement pathway (Danio rerio)
POLB-Dependent Long Patch Base Excision Repair (Danio rerio)
ADPRHL2 hydrolyses poly(ADP-ribose) (Danio rerio)
H2O [mitochondrial matrix]
Extracellular matrix organization (Danio rerio)
Degradation of the extracellular matrix (Danio rerio)
Collagen degradation (Danio rerio)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Danio rerio)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Danio rerio)
RNA Polymerase II Transcription (Danio rerio)
Generic Transcription Pathway (Danio rerio)
Transcriptional Regulation by TP53 (Danio rerio)
TP53 Regulates Metabolic Genes (Danio rerio)
Electron transfer from reduced cytochrome c to molecular oxygen (Danio rerio)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Danio rerio)
H2O [mitochondrial matrix]
Metabolism (Danio rerio)
Aerobic respiration and respiratory electron transport (Danio rerio)
Citric acid cycle (TCA cycle) (Danio rerio)
CS acetylates OA to citrate (Danio rerio)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Danio rerio)
H2O [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Danio rerio)
ATPase synthesizes ATP (Danio rerio)
H2O [mitochondrial matrix]
Pyruvate metabolism (Danio rerio)
Regulation of pyruvate metabolism (Danio rerio)
Regulation of pyruvate dehydrogenase (PDH) complex (Danio rerio)
SIRT4 cleaves lipoyl from DLAT (Danio rerio)
H2O [mitochondrial matrix]
Respiratory electron transport (Danio rerio)
Electron transfer from reduced cytochrome c to molecular oxygen (Danio rerio)
H2O [mitochondrial matrix]
Biological oxidations (Danio rerio)
Phase I - Functionalization of compounds (Danio rerio)
Cytochrome P450 - arranged by substrate type (Danio rerio)
Endogenous sterols (Danio rerio)
CYP11A1 cleaves 20a,22b-DHCHOL (Danio rerio)
H2O [mitochondrial matrix]
Vitamins (Danio rerio)
CYP24A1 24-hydroxylates CTL (Danio rerio)
H2O [mitochondrial matrix]
Ethanol oxidation (Danio rerio)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Danio rerio)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Danio rerio)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Danio rerio)
Branched-chain amino acid catabolism (Danio rerio)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Danio rerio)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Danio rerio)
H2O [mitochondrial matrix]
Choline catabolism (Danio rerio)
ALDH7A1 oxidises BETALD to BET (Danio rerio)
H2O [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Danio rerio)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Danio rerio)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Danio rerio)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Danio rerio)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Danio rerio)
H2O [mitochondrial matrix]
Lysine catabolism (Danio rerio)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Danio rerio)
H2O [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Danio rerio)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Danio rerio)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Danio rerio)
H2O [mitochondrial matrix]
Proline catabolism (Danio rerio)
ALDH4A1 oxidises L-GluSS to Glu (Danio rerio)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Danio rerio)
Degradation of cysteine and homocysteine (Danio rerio)
Sulfide oxidation to sulfate (Danio rerio)
Persulfide sulfur is dioxygenated (Danio rerio)
H2O [mitochondrial matrix]
Urea cycle (Danio rerio)
arginine + H2O => ornithine + urea [ARG2] (Danio rerio)
H2O [mitochondrial matrix]
Metabolism of lipids (Danio rerio)
Fatty acid metabolism (Danio rerio)
Mitochondrial Fatty Acid Beta-Oxidation (Danio rerio)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Danio rerio)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Danio rerio)
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Danio rerio)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Danio rerio)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Danio rerio)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Danio rerio)
H2O [mitochondrial matrix]
Metabolism of steroids (Danio rerio)
Metabolism of steroid hormones (Danio rerio)
Pregnenolone biosynthesis (Danio rerio)
CYP11A1 cleaves 20a,22b-DHCHOL (Danio rerio)
H2O [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Danio rerio)
H2O [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Danio rerio)
H2O [mitochondrial matrix]
Phospholipid metabolism (Danio rerio)
Glycerophospholipid biosynthesis (Danio rerio)
Acyl chain remodeling of CL (Danio rerio)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Danio rerio)
H2O [mitochondrial matrix]
Synthesis of PA (Danio rerio)
ACP6 hydrolyses MYS-LPA (Danio rerio)
H2O [mitochondrial matrix]
Synthesis of PE (Danio rerio)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Danio rerio)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Danio rerio)
Metabolism of cofactors (Danio rerio)
Ubiquinol biosynthesis (Danio rerio)
COQ6 hydroxylates DHB (Danio rerio)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Danio rerio)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Danio rerio)
Metabolism of folate and pterines (Danio rerio)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Danio rerio)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Danio rerio)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Danio rerio)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Danio rerio)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Danio rerio)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Danio rerio)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Danio rerio)
H2O [mitochondrial matrix]
Metabolism of proteins (Danio rerio)
Mitochondrial protein degradation (Danio rerio)
AFG3L2 degrades mitochondrial inner membrane proteins (Danio rerio)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Danio rerio)
H2O [mitochondrial matrix]
Translation (Danio rerio)
tRNA Aminoacylation (Danio rerio)
Mitochondrial tRNA aminoacylation (Danio rerio)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Danio rerio)
H2O [mitochondrial matrix]
Muscle contraction (Danio rerio)
Smooth Muscle Contraction (Danio rerio)
ALDH2 transforms GTN to NO (Danio rerio)
H2O [mitochondrial matrix]
Neuronal System (Danio rerio)
Transmission across Chemical Synapses (Danio rerio)
Neurotransmitter release cycle (Danio rerio)
Glutamate Neurotransmitter Release Cycle (Danio rerio)
glutamine + H2O => glutamate + NH4+ (GLS) (Danio rerio)
H2O [mitochondrial matrix]
Programmed Cell Death (Danio rerio)
Apoptosis (Danio rerio)
Regulation of Apoptosis (Danio rerio)
OMA1 hydrolyses OPA1 (Danio rerio)
H2O [mitochondrial matrix]
Transport of small molecules (Danio rerio)
ABC-family proteins mediated transport (Danio rerio)
Mitochondrial ABC transporters (Danio rerio)
ABC7, mABC1 and mABC2 mediate heme transport (Danio rerio)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Dictyostelium discoideum)
Cellular responses to stress (Dictyostelium discoideum)
Cellular response to chemical stress (Dictyostelium discoideum)
Detoxification of Reactive Oxygen Species (Dictyostelium discoideum)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Dictyostelium discoideum)
H2O [mitochondrial matrix]
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Metabolism (Dictyostelium discoideum)
Aerobic respiration and respiratory electron transport (Dictyostelium discoideum)
Citric acid cycle (TCA cycle) (Dictyostelium discoideum)
CS acetylates OA to citrate (Dictyostelium discoideum)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Biological oxidations (Dictyostelium discoideum)
Phase I - Functionalization of compounds (Dictyostelium discoideum)
Ethanol oxidation (Dictyostelium discoideum)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Dictyostelium discoideum)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Dictyostelium discoideum)
Branched-chain amino acid catabolism (Dictyostelium discoideum)
ECHS1 hydrates methacrylyl-CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Choline catabolism (Dictyostelium discoideum)
ALDH7A1 oxidises BETALD to BET (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Dictyostelium discoideum)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Dictyostelium discoideum)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Lysine catabolism (Dictyostelium discoideum)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Dictyostelium discoideum)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Dictyostelium discoideum)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Proline catabolism (Dictyostelium discoideum)
PRODH2 oxidises HPRO to 1PYR-5COOH (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Dictyostelium discoideum)
Degradation of cysteine and homocysteine (Dictyostelium discoideum)
Sulfide oxidation to sulfate (Dictyostelium discoideum)
Sulfite is oxidized to sulfate (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Urea cycle (Dictyostelium discoideum)
arginine + H2O => ornithine + urea [ARG2] (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Metabolism of lipids (Dictyostelium discoideum)
Fatty acid metabolism (Dictyostelium discoideum)
Fatty acyl-CoA biosynthesis (Dictyostelium discoideum)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Dictyostelium discoideum)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Dictyostelium discoideum)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Dictyostelium discoideum)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Dictyostelium discoideum)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Dictyostelium discoideum)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Dictyostelium discoideum)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Dictyostelium discoideum)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Phospholipid metabolism (Dictyostelium discoideum)
Glycerophospholipid biosynthesis (Dictyostelium discoideum)
Synthesis of PA (Dictyostelium discoideum)
ACP6 hydrolyses MYS-LPA (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Dictyostelium discoideum)
Heme biosynthesis (Dictyostelium discoideum)
COX10 transforms heme to heme O (Dictyostelium discoideum)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Dictyostelium discoideum)
Metabolism of cofactors (Dictyostelium discoideum)
Ubiquinol biosynthesis (Dictyostelium discoideum)
COQ6 hydroxylates DHB (Dictyostelium discoideum)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Dictyostelium discoideum)
Metabolism of folate and pterines (Dictyostelium discoideum)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Dictyostelium discoideum)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Dictyostelium discoideum)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Metabolism of proteins (Dictyostelium discoideum)
Mitochondrial protein degradation (Dictyostelium discoideum)
AFG3L2 degrades mitochondrial inner membrane proteins (Dictyostelium discoideum)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Dictyostelium discoideum)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Dictyostelium discoideum)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Translation (Dictyostelium discoideum)
tRNA Aminoacylation (Dictyostelium discoideum)
Mitochondrial tRNA aminoacylation (Dictyostelium discoideum)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Muscle contraction (Dictyostelium discoideum)
Smooth Muscle Contraction (Dictyostelium discoideum)
ALDH2 transforms GTN to NO (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Programmed Cell Death (Dictyostelium discoideum)
Apoptosis (Dictyostelium discoideum)
Regulation of Apoptosis (Dictyostelium discoideum)
OMA1 hydrolyses OPA1 (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Transport of small molecules (Dictyostelium discoideum)
ABC-family proteins mediated transport (Dictyostelium discoideum)
Mitochondrial ABC transporters (Dictyostelium discoideum)
ABC7, mABC1 and mABC2 mediate heme transport (Dictyostelium discoideum)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Drosophila melanogaster)
Cellular responses to stress (Drosophila melanogaster)
Cellular response to chemical stress (Drosophila melanogaster)
Cytoprotection by HMOX1 (Drosophila melanogaster)
Electron transfer from reduced cytochrome c to molecular oxygen (Drosophila melanogaster)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Drosophila melanogaster)
NUDT2 hydrolyses GP4G to GTP, GMP (Drosophila melanogaster)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Drosophila melanogaster)
H2O [mitochondrial matrix]
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Drosophila melanogaster)
H2O [mitochondrial matrix]
Extracellular matrix organization (Drosophila melanogaster)
Degradation of the extracellular matrix (Drosophila melanogaster)
Collagen degradation (Drosophila melanogaster)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Drosophila melanogaster)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Drosophila melanogaster)
RNA Polymerase II Transcription (Drosophila melanogaster)
Generic Transcription Pathway (Drosophila melanogaster)
Transcriptional Regulation by TP53 (Drosophila melanogaster)
TP53 Regulates Metabolic Genes (Drosophila melanogaster)
Electron transfer from reduced cytochrome c to molecular oxygen (Drosophila melanogaster)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Drosophila melanogaster)
H2O [mitochondrial matrix]
Metabolism (Drosophila melanogaster)
Aerobic respiration and respiratory electron transport (Drosophila melanogaster)
Citric acid cycle (TCA cycle) (Drosophila melanogaster)
CS acetylates OA to citrate (Drosophila melanogaster)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Drosophila melanogaster)
H2O [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Drosophila melanogaster)
ATPase synthesizes ATP (Drosophila melanogaster)
H2O [mitochondrial matrix]
Pyruvate metabolism (Drosophila melanogaster)
Regulation of pyruvate metabolism (Drosophila melanogaster)
Regulation of pyruvate dehydrogenase (PDH) complex (Drosophila melanogaster)
PDP1,2 dephosphorylate p-lipo-PDH (Drosophila melanogaster)
H2O [mitochondrial matrix]
SIRT4 cleaves lipoyl from DLAT (Drosophila melanogaster)
H2O [mitochondrial matrix]
Respiratory electron transport (Drosophila melanogaster)
Electron transfer from reduced cytochrome c to molecular oxygen (Drosophila melanogaster)
H2O [mitochondrial matrix]
Biological oxidations (Drosophila melanogaster)
Phase I - Functionalization of compounds (Drosophila melanogaster)
Ethanol oxidation (Drosophila melanogaster)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Drosophila melanogaster)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Drosophila melanogaster)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Drosophila melanogaster)
Branched-chain amino acid catabolism (Drosophila melanogaster)
ECHS1 hydrates methacrylyl-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Drosophila melanogaster)
H2O [mitochondrial matrix]
Choline catabolism (Drosophila melanogaster)
ALDH7A1 oxidises BETALD to BET (Drosophila melanogaster)
H2O [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Drosophila melanogaster)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Drosophila melanogaster)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Drosophila melanogaster)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Drosophila melanogaster)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Drosophila melanogaster)
H2O [mitochondrial matrix]
Lysine catabolism (Drosophila melanogaster)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Drosophila melanogaster)
H2O [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Drosophila melanogaster)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Drosophila melanogaster)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Drosophila melanogaster)
H2O [mitochondrial matrix]
Proline catabolism (Drosophila melanogaster)
PRODH2 oxidises HPRO to 1PYR-5COOH (Drosophila melanogaster)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Drosophila melanogaster)
Degradation of cysteine and homocysteine (Drosophila melanogaster)
Sulfide oxidation to sulfate (Drosophila melanogaster)
Persulfide sulfur is dioxygenated (Drosophila melanogaster)
H2O [mitochondrial matrix]
Sulfite is oxidized to sulfate (Drosophila melanogaster)
H2O [mitochondrial matrix]
Urea cycle (Drosophila melanogaster)
arginine + H2O => ornithine + urea [ARG2] (Drosophila melanogaster)
H2O [mitochondrial matrix]
Metabolism of lipids (Drosophila melanogaster)
Fatty acid metabolism (Drosophila melanogaster)
Fatty acyl-CoA biosynthesis (Drosophila melanogaster)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Drosophila melanogaster)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Drosophila melanogaster)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Drosophila melanogaster)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Drosophila melanogaster)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Drosophila melanogaster)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Drosophila melanogaster)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Drosophila melanogaster)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Drosophila melanogaster)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Drosophila melanogaster)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Phospholipid metabolism (Drosophila melanogaster)
Glycerophospholipid biosynthesis (Drosophila melanogaster)
Synthesis of PE (Drosophila melanogaster)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Metabolism of nucleotides (Drosophila melanogaster)
Nucleotide catabolism (Drosophila melanogaster)
Purine catabolism (Drosophila melanogaster)
Phosphate bond hydrolysis by NUDT proteins (Drosophila melanogaster)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Drosophila melanogaster)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Drosophila melanogaster)
Heme biosynthesis (Drosophila melanogaster)
COX10 transforms heme to heme O (Drosophila melanogaster)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Drosophila melanogaster)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Drosophila melanogaster)
Metabolism of cofactors (Drosophila melanogaster)
Ubiquinol biosynthesis (Drosophila melanogaster)
COQ6 hydroxylates DHB (Drosophila melanogaster)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Drosophila melanogaster)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Drosophila melanogaster)
Metabolism of folate and pterines (Drosophila melanogaster)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Drosophila melanogaster)
H2O [mitochondrial matrix]
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Drosophila melanogaster)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Drosophila melanogaster)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Drosophila melanogaster)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Drosophila melanogaster)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Drosophila melanogaster)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Drosophila melanogaster)
H2O [mitochondrial matrix]
Metabolism of proteins (Drosophila melanogaster)
Mitochondrial protein degradation (Drosophila melanogaster)
AFG3L2 degrades mitochondrial inner membrane proteins (Drosophila melanogaster)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Drosophila melanogaster)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Drosophila melanogaster)
H2O [mitochondrial matrix]
CLPXP degrades mitochondrial matrix proteins (Drosophila melanogaster)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Drosophila melanogaster)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Drosophila melanogaster)
H2O [mitochondrial matrix]
Translation (Drosophila melanogaster)
tRNA Aminoacylation (Drosophila melanogaster)
Mitochondrial tRNA aminoacylation (Drosophila melanogaster)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Drosophila melanogaster)
H2O [mitochondrial matrix]
Muscle contraction (Drosophila melanogaster)
Smooth Muscle Contraction (Drosophila melanogaster)
ALDH2 transforms GTN to NO (Drosophila melanogaster)
H2O [mitochondrial matrix]
Neuronal System (Drosophila melanogaster)
Transmission across Chemical Synapses (Drosophila melanogaster)
Neurotransmitter release cycle (Drosophila melanogaster)
GABA synthesis, release, reuptake and degradation (Drosophila melanogaster)
Degradation of GABA (Drosophila melanogaster)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Drosophila melanogaster)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Drosophila melanogaster)
glutamine + H2O => glutamate + NH4+ (GLS) (Drosophila melanogaster)
H2O [mitochondrial matrix]
Transport of small molecules (Drosophila melanogaster)
ABC-family proteins mediated transport (Drosophila melanogaster)
Mitochondrial ABC transporters (Drosophila melanogaster)
ABC7, mABC1 and mABC2 mediate heme transport (Drosophila melanogaster)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Gallus gallus)
Cellular responses to stress (Gallus gallus)
Cellular response to chemical stress (Gallus gallus)
Cytoprotection by HMOX1 (Gallus gallus)
Electron transfer from reduced cytochrome c to molecular oxygen (Gallus gallus)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Gallus gallus)
NUDT2 hydrolyses GP4G to GTP, GMP (Gallus gallus)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Gallus gallus)
H2O [mitochondrial matrix]
Mitochondrial unfolded protein response (UPRmt) (Gallus gallus)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Gallus gallus)
H2O [mitochondrial matrix]
DNA Repair (Gallus gallus)
Base Excision Repair (Gallus gallus)
Resolution of Abasic Sites (AP sites) (Gallus gallus)
Resolution of AP sites via the multiple-nucleotide patch replacement pathway (Gallus gallus)
POLB-Dependent Long Patch Base Excision Repair (Gallus gallus)
ADPRHL2 hydrolyses poly(ADP-ribose) (Gallus gallus)
H2O [mitochondrial matrix]
Extracellular matrix organization (Gallus gallus)
Degradation of the extracellular matrix (Gallus gallus)
Collagen degradation (Gallus gallus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Gallus gallus)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Gallus gallus)
RNA Polymerase II Transcription (Gallus gallus)
Generic Transcription Pathway (Gallus gallus)
Transcriptional Regulation by TP53 (Gallus gallus)
TP53 Regulates Metabolic Genes (Gallus gallus)
Electron transfer from reduced cytochrome c to molecular oxygen (Gallus gallus)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Gallus gallus)
H2O [mitochondrial matrix]
Metabolism (Gallus gallus)
Amino acid metabolism (Gallus gallus)
Arginine metabolism (Gallus gallus)
arginine + H2O => ornithine + urea (Gallus gallus)
H2O [mitochondrial matrix]
The tricarboxylic acid cycle (Gallus gallus)
acetyl-CoA + H2O + oxaloacetate => citrate + CoA (Gallus gallus)
H2O [mitochondrial matrix]
fumarate + H2O <=> malate (Gallus gallus)
H2O [mitochondrial matrix]
malate <=> fumarate + H2O (Gallus gallus)
H2O [mitochondrial matrix]
Metabolism of proteins (Gallus gallus)
Mitochondrial protein degradation (Gallus gallus)
AFG3L2 degrades mitochondrial inner membrane proteins (Gallus gallus)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Gallus gallus)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Gallus gallus)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Gallus gallus)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Gallus gallus)
H2O [mitochondrial matrix]
Translation (Gallus gallus)
tRNA Aminoacylation (Gallus gallus)
Mitochondrial tRNA aminoacylation (Gallus gallus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Gallus gallus)
H2O [mitochondrial matrix]
Muscle contraction (Gallus gallus)
Smooth Muscle Contraction (Gallus gallus)
ALDH2 transforms GTN to NO (Gallus gallus)
H2O [mitochondrial matrix]
Neuronal System (Gallus gallus)
Transmission across Chemical Synapses (Gallus gallus)
Neurotransmitter release cycle (Gallus gallus)
GABA synthesis, release, reuptake and degradation (Gallus gallus)
Degradation of GABA (Gallus gallus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Gallus gallus)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Gallus gallus)
glutamine + H2O => glutamate + NH4+ (GLS) (Gallus gallus)
H2O [mitochondrial matrix]
Programmed Cell Death (Gallus gallus)
Apoptosis (Gallus gallus)
Regulation of Apoptosis (Gallus gallus)
OMA1 hydrolyses OPA1 (Gallus gallus)
H2O [mitochondrial matrix]
Transport of small molecules (Gallus gallus)
ABC-family proteins mediated transport (Gallus gallus)
Mitochondrial ABC transporters (Gallus gallus)
ABC7, mABC1 and mABC2 mediate heme transport (Gallus gallus)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Homo sapiens)
Cellular responses to stress (Homo sapiens)
Cellular response to chemical stress (Homo sapiens)
Cytoprotection by HMOX1 (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Homo sapiens)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Homo sapiens)
H2O [mitochondrial matrix]
NUDT2 hydrolyses GP4G to GTP, GMP (Homo sapiens)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Homo sapiens)
H2O [mitochondrial matrix]
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Homo sapiens)
H2O [mitochondrial matrix]
Mitochondrial unfolded protein response (UPRmt) (Homo sapiens)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Homo sapiens)
H2O [mitochondrial matrix]
DNA Repair (Homo sapiens)
Base Excision Repair (Homo sapiens)
Resolution of Abasic Sites (AP sites) (Homo sapiens)
Resolution of AP sites via the multiple-nucleotide patch replacement pathway (Homo sapiens)
POLB-Dependent Long Patch Base Excision Repair (Homo sapiens)
ADPRHL2 hydrolyses poly(ADP-ribose) (Homo sapiens)
H2O [mitochondrial matrix]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of branched-chain amino acid catabolism (Homo sapiens)
3-hydroxyisobutyryl-CoA hydrolase deficiency (Homo sapiens)
HIBCH mutants don't synthesize beta-hydroxyisobutyrate (Homo sapiens)
H2O [mitochondrial matrix]
3-methylglutaconic aciduria (Homo sapiens)
AUH mutants don't synthesize 3-hydroxy-methylglutaryl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Maple Syrup Urine Disease (Homo sapiens)
H139Hfs13* PPM1K causes a mild variant of MSUD (Homo sapiens)
H139Hfs13* PPM1K does not dephosphorylate BCKDH (Homo sapiens)
H2O [mitochondrial matrix]
Mitochondrial short-chain enoyl-CoA hydratase deficiency 1 (Homo sapiens)
ECHS1 mutants don't synthesize beta-hydroxyisobutyryl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Extracellular matrix organization (Homo sapiens)
Degradation of the extracellular matrix (Homo sapiens)
Collagen degradation (Homo sapiens)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Homo sapiens)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Homo sapiens)
RNA Polymerase II Transcription (Homo sapiens)
Generic Transcription Pathway (Homo sapiens)
Transcriptional Regulation by TP53 (Homo sapiens)
TP53 Regulates Metabolic Genes (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Citric acid cycle (TCA cycle) (Homo sapiens)
CS acetylates OA to citrate (Homo sapiens)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Homo sapiens)
H2O [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Homo sapiens)
ATPase synthesizes ATP (Homo sapiens)
H2O [mitochondrial matrix]
Pyruvate metabolism (Homo sapiens)
Mitochondrial H2O2 decarboxylates PYR to acetate (Homo sapiens)
H2O [mitochondrial matrix]
Regulation of pyruvate metabolism (Homo sapiens)
Regulation of pyruvate dehydrogenase (PDH) complex (Homo sapiens)
GS-MCA spontaneously hydrolyzes (Homo sapiens)
H2O [mitochondrial matrix]
PDP1,2 dephosphorylate p-lipo-PDH (Homo sapiens)
H2O [mitochondrial matrix]
SIRT4 cleaves lipoyl from DLAT (Homo sapiens)
H2O [mitochondrial matrix]
Respiratory electron transport (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
H2O [mitochondrial matrix]
Biological oxidations (Homo sapiens)
Phase I - Functionalization of compounds (Homo sapiens)
Cytochrome P450 - arranged by substrate type (Homo sapiens)
Endogenous sterols (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
H2O [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Homo sapiens)
H2O [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Homo sapiens)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Homo sapiens)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Homo sapiens)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Homo sapiens)
H2O [mitochondrial matrix]
Vitamins (Homo sapiens)
CYP24A1 24-hydroxylates CTL (Homo sapiens)
H2O [mitochondrial matrix]
Ethanol oxidation (Homo sapiens)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Homo sapiens)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Homo sapiens)
H2O [mitochondrial matrix]
Phase II - Conjugation of compounds (Homo sapiens)
Glucuronidation (Homo sapiens)
ABHD10 hydrolyses MPAG (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Homo sapiens)
Branched-chain amino acid catabolism (Homo sapiens)
ECHS1 hydrates methacrylyl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Homo sapiens)
H2O [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Homo sapiens)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Homo sapiens)
H2O [mitochondrial matrix]
tiglyl-CoA + H2O <=> alpha-methyl-beta-hydroxybutyryl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Choline catabolism (Homo sapiens)
ALDH7A1 oxidises BETALD to BET (Homo sapiens)
H2O [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Homo sapiens)
H2O [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Homo sapiens)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Homo sapiens)
L-glutamate gamma-semialdehyde <=> L-1-pyrroline-5-carboxylate (Homo sapiens)
H2O [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Homo sapiens)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Homo sapiens)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Homo sapiens)
H2O [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Homo sapiens)
Spontaneous hydrolysis of 1-pyrroline-3-hydroxy-5-carboxylate to 4-OH-L-glutamate semialdehyde (Homo sapiens)
H2O [mitochondrial matrix]
Lysine catabolism (Homo sapiens)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Homo sapiens)
H2O [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Homo sapiens)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Homo sapiens)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Homo sapiens)
H2O [mitochondrial matrix]
Proline catabolism (Homo sapiens)
1PYR-5COOH spontaneously hydrolyses to L-GluSS (Homo sapiens)
H2O [mitochondrial matrix]
ALDH4A1 oxidises L-GluSS to Glu (Homo sapiens)
H2O [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-5COOH (Homo sapiens)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Homo sapiens)
Degradation of cysteine and homocysteine (Homo sapiens)
Sulfide oxidation to sulfate (Homo sapiens)
Persulfide sulfur is dioxygenated (Homo sapiens)
H2O [mitochondrial matrix]
Sulfite is oxidized to sulfate (Homo sapiens)
H2O [mitochondrial matrix]
Tryptophan catabolism (Homo sapiens)
4-(2-aminophenyl)-2,4-dioxobutanoate => kynurenic acid + H2O [mitochondrial] (Homo sapiens)
H2O [mitochondrial matrix]
Urea cycle (Homo sapiens)
arginine + H2O => ornithine + urea [ARG2] (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Fatty acyl-CoA biosynthesis (Homo sapiens)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Homo sapiens)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Homo sapiens)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Homo sapiens)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Homo sapiens)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Homo sapiens)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Homo sapiens)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Homo sapiens)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Homo sapiens)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Homo sapiens)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Homo sapiens)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Homo sapiens)
Linoleoyl-CoA is converted to cis,cis-3,6- dodecadienoyl-CoA by three cycles of beta-oxidation (Homo sapiens)
H2O [mitochondrial matrix]
Trans,cis-lauro-2,6-dienoyl-CoA is converted to cis,cis-3,6- 4-cis-decenoyl-CoA by one cycle of beta-oxidation (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of steroids (Homo sapiens)
Bile acid and bile salt metabolism (Homo sapiens)
Synthesis of bile acids and bile salts (Homo sapiens)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Homo sapiens)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Homo sapiens)
H2O [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Homo sapiens)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Homo sapiens)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Homo sapiens)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Homo sapiens)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Homo sapiens)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Homo sapiens)
CYP27A1 27-hydroxylates CHOL (Homo sapiens)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Homo sapiens)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Homo sapiens)
H2O [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Homo sapiens)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Homo sapiens)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of steroid hormones (Homo sapiens)
Glucocorticoid biosynthesis (Homo sapiens)
CYP11B1 oxidises 11DCORT (Homo sapiens)
H2O [mitochondrial matrix]
Mineralocorticoid biosynthesis (Homo sapiens)
CYP11B2 18-hydroxylates CORST to 18HCORST (Homo sapiens)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Homo sapiens)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Homo sapiens)
H2O [mitochondrial matrix]
Pregnenolone biosynthesis (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
H2O [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Homo sapiens)
H2O [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Homo sapiens)
H2O [mitochondrial matrix]
Phospholipid metabolism (Homo sapiens)
Glycerophospholipid biosynthesis (Homo sapiens)
Acyl chain remodeling of CL (Homo sapiens)
CL is hydrolyzed to MLCL by PLA2G6 (IM) (Homo sapiens)
H2O [mitochondrial matrix]
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Homo sapiens)
H2O [mitochondrial matrix]
Acyl chain remodelling of PG (Homo sapiens)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Homo sapiens)
H2O [mitochondrial matrix]
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Homo sapiens)
H2O [mitochondrial matrix]
Synthesis of PA (Homo sapiens)
ACP6 hydrolyses MYS-LPA (Homo sapiens)
H2O [mitochondrial matrix]
Synthesis of PE (Homo sapiens)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Homo sapiens)
H2O [mitochondrial matrix]
Synthesis of PG (Homo sapiens)
PTPMT1 dephosphorylates PGP to PG (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of nucleotides (Homo sapiens)
Interconversion of nucleotide di- and triphosphates (Homo sapiens)
NUDT13 hydrolyses AP6A to AP4 and ADP (Homo sapiens)
H2O [mitochondrial matrix]
Nucleotide catabolism (Homo sapiens)
Purine catabolism (Homo sapiens)
Phosphate bond hydrolysis by NUDT proteins (Homo sapiens)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Homo sapiens)
H2O [mitochondrial matrix]
Pyrimidine catabolism (Homo sapiens)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Homo sapiens)
Heme biosynthesis (Homo sapiens)
COX10 transforms heme to heme O (Homo sapiens)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
COQ6 hydroxylates DHB (Homo sapiens)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Homo sapiens)
H2O [mitochondrial matrix]
Unknown dehydrogenase oxidizes 4-HBz (Homo sapiens)
H2O [mitochondrial matrix]
Unknown enzyme hydroxylates DMPhOH (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Homo sapiens)
Metabolism of folate and pterines (Homo sapiens)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Homo sapiens)
H2O [mitochondrial matrix]
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Homo sapiens)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Homo sapiens)
H2O [mitochondrial matrix]
Vitamin B5 (pantothenate) metabolism (Homo sapiens)
NUDT8 hydrolyzes CoA-SH to PPANT (Homo sapiens)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Homo sapiens)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Homo sapiens)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Homo sapiens)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Homo sapiens)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of RNA (Homo sapiens)
Mitochondrial RNA degradation (Homo sapiens)
REXO2 hydrolyzes 4-5 nucleotide RNAs to ribonucleotides (Homo sapiens)
H2O [mitochondrial matrix]
SUPV3L1:PNPT1 hydrolyzes mitochondrial RNA to yield 4-5 nucleotide oligoribonucleotides (Homo sapiens)
H2O [mitochondrial matrix]
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
AFG3L2 degrades mitochondrial inner membrane proteins (Homo sapiens)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Homo sapiens)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Homo sapiens)
H2O [mitochondrial matrix]
CLPXP degrades mitochondrial matrix proteins (Homo sapiens)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Homo sapiens)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Homo sapiens)
H2O [mitochondrial matrix]
Translation (Homo sapiens)
tRNA Aminoacylation (Homo sapiens)
Mitochondrial tRNA aminoacylation (Homo sapiens)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Homo sapiens)
H2O [mitochondrial matrix]
Muscle contraction (Homo sapiens)
Smooth Muscle Contraction (Homo sapiens)
ALDH2 transforms GTN to NO (Homo sapiens)
H2O [mitochondrial matrix]
Neuronal System (Homo sapiens)
Transmission across Chemical Synapses (Homo sapiens)
Neurotransmitter release cycle (Homo sapiens)
GABA synthesis, release, reuptake and degradation (Homo sapiens)
Degradation of GABA (Homo sapiens)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Homo sapiens)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Homo sapiens)
glutamine + H2O => glutamate + NH4+ (GLS) (Homo sapiens)
H2O [mitochondrial matrix]
Programmed Cell Death (Homo sapiens)
Apoptosis (Homo sapiens)
Regulation of Apoptosis (Homo sapiens)
OMA1 hydrolyses OPA1 (Homo sapiens)
H2O [mitochondrial matrix]
Protein localization (Homo sapiens)
Mitochondrial protein import (Homo sapiens)
MPP cleaves targeting peptide (presequence) of inner membrane precursors (Homo sapiens)
H2O [mitochondrial matrix]
MPP cleaves targeting peptide (presequence) of matrix precursors (Homo sapiens)
H2O [mitochondrial matrix]
Transport of small molecules (Homo sapiens)
ABC-family proteins mediated transport (Homo sapiens)
Mitochondrial ABC transporters (Homo sapiens)
ABC7, mABC1 and mABC2 mediate heme transport (Homo sapiens)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Mus musculus)
Cellular responses to stress (Mus musculus)
Cellular response to chemical stress (Mus musculus)
Cytoprotection by HMOX1 (Mus musculus)
Electron transfer from reduced cytochrome c to molecular oxygen (Mus musculus)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Mus musculus)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Mus musculus)
H2O [mitochondrial matrix]
NUDT2 hydrolyses GP4G to GTP, GMP (Mus musculus)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Mus musculus)
H2O [mitochondrial matrix]
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Mus musculus)
H2O [mitochondrial matrix]
Mitochondrial unfolded protein response (UPRmt) (Mus musculus)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Mus musculus)
H2O [mitochondrial matrix]
DNA Repair (Mus musculus)
Base Excision Repair (Mus musculus)
Resolution of Abasic Sites (AP sites) (Mus musculus)
Resolution of AP sites via the multiple-nucleotide patch replacement pathway (Mus musculus)
POLB-Dependent Long Patch Base Excision Repair (Mus musculus)
ADPRHL2 hydrolyses poly(ADP-ribose) (Mus musculus)
H2O [mitochondrial matrix]
Extracellular matrix organization (Mus musculus)
Degradation of the extracellular matrix (Mus musculus)
Collagen degradation (Mus musculus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Mus musculus)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Mus musculus)
RNA Polymerase II Transcription (Mus musculus)
Generic Transcription Pathway (Mus musculus)
Transcriptional Regulation by TP53 (Mus musculus)
TP53 Regulates Metabolic Genes (Mus musculus)
Electron transfer from reduced cytochrome c to molecular oxygen (Mus musculus)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Mus musculus)
H2O [mitochondrial matrix]
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Citric acid cycle (TCA cycle) (Mus musculus)
CS acetylates OA to citrate (Mus musculus)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Mus musculus)
H2O [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Mus musculus)
ATPase synthesizes ATP (Mus musculus)
H2O [mitochondrial matrix]
Pyruvate metabolism (Mus musculus)
Regulation of pyruvate metabolism (Mus musculus)
Regulation of pyruvate dehydrogenase (PDH) complex (Mus musculus)
PDP1,2 dephosphorylate p-lipo-PDH (Mus musculus)
H2O [mitochondrial matrix]
SIRT4 cleaves lipoyl from DLAT (Mus musculus)
H2O [mitochondrial matrix]
Respiratory electron transport (Mus musculus)
Electron transfer from reduced cytochrome c to molecular oxygen (Mus musculus)
H2O [mitochondrial matrix]
Biological oxidations (Mus musculus)
Phase I - Functionalization of compounds (Mus musculus)
Cytochrome P450 - arranged by substrate type (Mus musculus)
Endogenous sterols (Mus musculus)
CYP11A1 cleaves 20a,22b-DHCHOL (Mus musculus)
H2O [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Mus musculus)
H2O [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Mus musculus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Mus musculus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Mus musculus)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Mus musculus)
H2O [mitochondrial matrix]
Vitamins (Mus musculus)
CYP24A1 24-hydroxylates CTL (Mus musculus)
H2O [mitochondrial matrix]
Ethanol oxidation (Mus musculus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Mus musculus)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Mus musculus)
H2O [mitochondrial matrix]
Phase II - Conjugation of compounds (Mus musculus)
Glucuronidation (Mus musculus)
ABHD10 hydrolyses MPAG (Mus musculus)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Mus musculus)
Branched-chain amino acid catabolism (Mus musculus)
ECHS1 hydrates methacrylyl-CoA (Mus musculus)
H2O [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Mus musculus)
H2O [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Mus musculus)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Mus musculus)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Mus musculus)
H2O [mitochondrial matrix]
Choline catabolism (Mus musculus)
ALDH7A1 oxidises BETALD to BET (Mus musculus)
H2O [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Mus musculus)
H2O [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Mus musculus)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Mus musculus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Mus musculus)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Mus musculus)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Mus musculus)
H2O [mitochondrial matrix]
Lysine catabolism (Mus musculus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Mus musculus)
H2O [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Mus musculus)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Mus musculus)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Mus musculus)
H2O [mitochondrial matrix]
Proline catabolism (Mus musculus)
ALDH4A1 oxidises L-GluSS to Glu (Mus musculus)
H2O [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-5COOH (Mus musculus)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Mus musculus)
Degradation of cysteine and homocysteine (Mus musculus)
Sulfide oxidation to sulfate (Mus musculus)
Persulfide sulfur is dioxygenated (Mus musculus)
H2O [mitochondrial matrix]
Sulfite is oxidized to sulfate (Mus musculus)
H2O [mitochondrial matrix]
Urea cycle (Mus musculus)
arginine + H2O => ornithine + urea [ARG2] (Mus musculus)
H2O [mitochondrial matrix]
Metabolism of lipids (Mus musculus)
Fatty acid metabolism (Mus musculus)
Mitochondrial Fatty Acid Beta-Oxidation (Mus musculus)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Mus musculus)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Mus musculus)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Mus musculus)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Mus musculus)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Mus musculus)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Mus musculus)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Mus musculus)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Mus musculus)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Mus musculus)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Mus musculus)
H2O [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Mus musculus)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Mus musculus)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Mus musculus)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Mus musculus)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Mus musculus)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Mus musculus)
H2O [mitochondrial matrix]
Metabolism of steroids (Mus musculus)
Bile acid and bile salt metabolism (Mus musculus)
Synthesis of bile acids and bile salts (Mus musculus)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Mus musculus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Mus musculus)
H2O [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Mus musculus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Mus musculus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Mus musculus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Mus musculus)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Mus musculus)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Mus musculus)
CYP27A1 27-hydroxylates CHOL (Mus musculus)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Mus musculus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Mus musculus)
H2O [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Mus musculus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Mus musculus)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Mus musculus)
H2O [mitochondrial matrix]
Metabolism of steroid hormones (Mus musculus)
Glucocorticoid biosynthesis (Mus musculus)
CYP11B1 oxidises 11DCORT (Mus musculus)
H2O [mitochondrial matrix]
Mineralocorticoid biosynthesis (Mus musculus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Mus musculus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Mus musculus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Mus musculus)
H2O [mitochondrial matrix]
Pregnenolone biosynthesis (Mus musculus)
CYP11A1 cleaves 20a,22b-DHCHOL (Mus musculus)
H2O [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Mus musculus)
H2O [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Mus musculus)
H2O [mitochondrial matrix]
Phospholipid metabolism (Mus musculus)
Glycerophospholipid biosynthesis (Mus musculus)
Acyl chain remodeling of CL (Mus musculus)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Mus musculus)
H2O [mitochondrial matrix]
Acyl chain remodelling of PG (Mus musculus)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Mus musculus)
H2O [mitochondrial matrix]
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Mus musculus)
H2O [mitochondrial matrix]
Synthesis of PA (Mus musculus)
ACP6 hydrolyses MYS-LPA (Mus musculus)
H2O [mitochondrial matrix]
Synthesis of PE (Mus musculus)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Mus musculus)
H2O [mitochondrial matrix]
Metabolism of nucleotides (Mus musculus)
Interconversion of nucleotide di- and triphosphates (Mus musculus)
NUDT13 hydrolyses AP6A to AP4 and ADP (Mus musculus)
H2O [mitochondrial matrix]
Nucleotide catabolism (Mus musculus)
Purine catabolism (Mus musculus)
Phosphate bond hydrolysis by NUDT proteins (Mus musculus)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Mus musculus)
H2O [mitochondrial matrix]
Pyrimidine catabolism (Mus musculus)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Mus musculus)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Mus musculus)
Heme biosynthesis (Mus musculus)
COX10 transforms heme to heme O (Mus musculus)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Mus musculus)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Mus musculus)
Metabolism of cofactors (Mus musculus)
Ubiquinol biosynthesis (Mus musculus)
COQ6 hydroxylates DHB (Mus musculus)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Mus musculus)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Mus musculus)
Metabolism of folate and pterines (Mus musculus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Mus musculus)
H2O [mitochondrial matrix]
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Mus musculus)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Mus musculus)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Mus musculus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Mus musculus)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Mus musculus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Mus musculus)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Mus musculus)
H2O [mitochondrial matrix]
Metabolism of proteins (Mus musculus)
Mitochondrial protein degradation (Mus musculus)
AFG3L2 degrades mitochondrial inner membrane proteins (Mus musculus)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Mus musculus)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Mus musculus)
H2O [mitochondrial matrix]
CLPXP degrades mitochondrial matrix proteins (Mus musculus)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Mus musculus)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Mus musculus)
H2O [mitochondrial matrix]
Translation (Mus musculus)
tRNA Aminoacylation (Mus musculus)
Mitochondrial tRNA aminoacylation (Mus musculus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Mus musculus)
H2O [mitochondrial matrix]
Muscle contraction (Mus musculus)
Smooth Muscle Contraction (Mus musculus)
ALDH2 transforms GTN to NO (Mus musculus)
H2O [mitochondrial matrix]
Neuronal System (Mus musculus)
Transmission across Chemical Synapses (Mus musculus)
Neurotransmitter release cycle (Mus musculus)
GABA synthesis, release, reuptake and degradation (Mus musculus)
Degradation of GABA (Mus musculus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Mus musculus)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Mus musculus)
glutamine + H2O => glutamate + NH4+ (GLS) (Mus musculus)
H2O [mitochondrial matrix]
Programmed Cell Death (Mus musculus)
Apoptosis (Mus musculus)
Regulation of Apoptosis (Mus musculus)
OMA1 hydrolyses OPA1 (Mus musculus)
H2O [mitochondrial matrix]
Transport of small molecules (Mus musculus)
ABC-family proteins mediated transport (Mus musculus)
Mitochondrial ABC transporters (Mus musculus)
ABC7, mABC1 and mABC2 mediate heme transport (Mus musculus)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Plasmodium falciparum)
Cellular responses to stress (Plasmodium falciparum)
Cellular response to chemical stress (Plasmodium falciparum)
Detoxification of Reactive Oxygen Species (Plasmodium falciparum)
NUDT2 hydrolyses GP4G to GTP, GMP (Plasmodium falciparum)
H2O [mitochondrial matrix]
Metabolism (Plasmodium falciparum)
Aerobic respiration and respiratory electron transport (Plasmodium falciparum)
Citric acid cycle (TCA cycle) (Plasmodium falciparum)
CS acetylates OA to citrate (Plasmodium falciparum)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Plasmodium falciparum)
Branched-chain amino acid catabolism (Plasmodium falciparum)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Plasmodium falciparum)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Plasmodium falciparum)
H2O [mitochondrial matrix]
Urea cycle (Plasmodium falciparum)
arginine + H2O => ornithine + urea [ARG2] (Plasmodium falciparum)
H2O [mitochondrial matrix]
Metabolism of lipids (Plasmodium falciparum)
Fatty acid metabolism (Plasmodium falciparum)
Mitochondrial Fatty Acid Beta-Oxidation (Plasmodium falciparum)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Plasmodium falciparum)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Plasmodium falciparum)
Heme biosynthesis (Plasmodium falciparum)
COX10 transforms heme to heme O (Plasmodium falciparum)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Plasmodium falciparum)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Plasmodium falciparum)
Metabolism of water-soluble vitamins and cofactors (Plasmodium falciparum)
Metabolism of folate and pterines (Plasmodium falciparum)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Plasmodium falciparum)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Plasmodium falciparum)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Plasmodium falciparum)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Plasmodium falciparum)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Plasmodium falciparum)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Plasmodium falciparum)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Plasmodium falciparum)
H2O [mitochondrial matrix]
Metabolism of proteins (Plasmodium falciparum)
Mitochondrial protein degradation (Plasmodium falciparum)
AFG3L2 degrades mitochondrial matrix proteins (Plasmodium falciparum)
H2O [mitochondrial matrix]
Translation (Plasmodium falciparum)
tRNA Aminoacylation (Plasmodium falciparum)
Mitochondrial tRNA aminoacylation (Plasmodium falciparum)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Plasmodium falciparum)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Rattus norvegicus)
Cellular responses to stress (Rattus norvegicus)
Cellular response to chemical stress (Rattus norvegicus)
Cytoprotection by HMOX1 (Rattus norvegicus)
Electron transfer from reduced cytochrome c to molecular oxygen (Rattus norvegicus)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Rattus norvegicus)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Rattus norvegicus)
H2O [mitochondrial matrix]
NUDT2 hydrolyses GP4G to GTP, GMP (Rattus norvegicus)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Rattus norvegicus)
H2O [mitochondrial matrix]
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Rattus norvegicus)
H2O [mitochondrial matrix]
Mitochondrial unfolded protein response (UPRmt) (Rattus norvegicus)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Rattus norvegicus)
H2O [mitochondrial matrix]
DNA Repair (Rattus norvegicus)
Base Excision Repair (Rattus norvegicus)
Resolution of Abasic Sites (AP sites) (Rattus norvegicus)
Resolution of AP sites via the multiple-nucleotide patch replacement pathway (Rattus norvegicus)
POLB-Dependent Long Patch Base Excision Repair (Rattus norvegicus)
ADPRHL2 hydrolyses poly(ADP-ribose) (Rattus norvegicus)
H2O [mitochondrial matrix]
Extracellular matrix organization (Rattus norvegicus)
Degradation of the extracellular matrix (Rattus norvegicus)
Collagen degradation (Rattus norvegicus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Rattus norvegicus)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Rattus norvegicus)
RNA Polymerase II Transcription (Rattus norvegicus)
Generic Transcription Pathway (Rattus norvegicus)
Transcriptional Regulation by TP53 (Rattus norvegicus)
TP53 Regulates Metabolic Genes (Rattus norvegicus)
Electron transfer from reduced cytochrome c to molecular oxygen (Rattus norvegicus)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism (Rattus norvegicus)
Aerobic respiration and respiratory electron transport (Rattus norvegicus)
Citric acid cycle (TCA cycle) (Rattus norvegicus)
CS acetylates OA to citrate (Rattus norvegicus)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Rattus norvegicus)
H2O [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Rattus norvegicus)
ATPase synthesizes ATP (Rattus norvegicus)
H2O [mitochondrial matrix]
Pyruvate metabolism (Rattus norvegicus)
Regulation of pyruvate metabolism (Rattus norvegicus)
Regulation of pyruvate dehydrogenase (PDH) complex (Rattus norvegicus)
PDP1,2 dephosphorylate p-lipo-PDH (Rattus norvegicus)
H2O [mitochondrial matrix]
SIRT4 cleaves lipoyl from DLAT (Rattus norvegicus)
H2O [mitochondrial matrix]
Respiratory electron transport (Rattus norvegicus)
Electron transfer from reduced cytochrome c to molecular oxygen (Rattus norvegicus)
H2O [mitochondrial matrix]
Biological oxidations (Rattus norvegicus)
Phase I - Functionalization of compounds (Rattus norvegicus)
Cytochrome P450 - arranged by substrate type (Rattus norvegicus)
Endogenous sterols (Rattus norvegicus)
CYP11A1 cleaves 20a,22b-DHCHOL (Rattus norvegicus)
H2O [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Rattus norvegicus)
H2O [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Rattus norvegicus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Rattus norvegicus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Rattus norvegicus)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Rattus norvegicus)
H2O [mitochondrial matrix]
Vitamins (Rattus norvegicus)
CYP24A1 24-hydroxylates CTL (Rattus norvegicus)
H2O [mitochondrial matrix]
Ethanol oxidation (Rattus norvegicus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Rattus norvegicus)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Rattus norvegicus)
H2O [mitochondrial matrix]
Phase II - Conjugation of compounds (Rattus norvegicus)
Glucuronidation (Rattus norvegicus)
ABHD10 hydrolyses MPAG (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Rattus norvegicus)
Branched-chain amino acid catabolism (Rattus norvegicus)
ECHS1 hydrates methacrylyl-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Rattus norvegicus)
H2O [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Rattus norvegicus)
H2O [mitochondrial matrix]
Choline catabolism (Rattus norvegicus)
ALDH7A1 oxidises BETALD to BET (Rattus norvegicus)
H2O [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Rattus norvegicus)
H2O [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Rattus norvegicus)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Rattus norvegicus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Rattus norvegicus)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Rattus norvegicus)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Rattus norvegicus)
H2O [mitochondrial matrix]
Lysine catabolism (Rattus norvegicus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Rattus norvegicus)
H2O [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Rattus norvegicus)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Rattus norvegicus)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Rattus norvegicus)
H2O [mitochondrial matrix]
Proline catabolism (Rattus norvegicus)
ALDH4A1 oxidises L-GluSS to Glu (Rattus norvegicus)
H2O [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-5COOH (Rattus norvegicus)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Rattus norvegicus)
Degradation of cysteine and homocysteine (Rattus norvegicus)
Sulfide oxidation to sulfate (Rattus norvegicus)
Persulfide sulfur is dioxygenated (Rattus norvegicus)
H2O [mitochondrial matrix]
Sulfite is oxidized to sulfate (Rattus norvegicus)
H2O [mitochondrial matrix]
Urea cycle (Rattus norvegicus)
arginine + H2O => ornithine + urea [ARG2] (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism of lipids (Rattus norvegicus)
Fatty acid metabolism (Rattus norvegicus)
Fatty acyl-CoA biosynthesis (Rattus norvegicus)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Rattus norvegicus)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Rattus norvegicus)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Rattus norvegicus)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Rattus norvegicus)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Rattus norvegicus)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Rattus norvegicus)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Rattus norvegicus)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Rattus norvegicus)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Rattus norvegicus)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism of steroids (Rattus norvegicus)
Bile acid and bile salt metabolism (Rattus norvegicus)
Synthesis of bile acids and bile salts (Rattus norvegicus)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Rattus norvegicus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Rattus norvegicus)
H2O [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Rattus norvegicus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Rattus norvegicus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Rattus norvegicus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Rattus norvegicus)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Rattus norvegicus)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Rattus norvegicus)
CYP27A1 27-hydroxylates CHOL (Rattus norvegicus)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Rattus norvegicus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Rattus norvegicus)
H2O [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Rattus norvegicus)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Rattus norvegicus)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism of steroid hormones (Rattus norvegicus)
Glucocorticoid biosynthesis (Rattus norvegicus)
CYP11B1 oxidises 11DCORT (Rattus norvegicus)
H2O [mitochondrial matrix]
Mineralocorticoid biosynthesis (Rattus norvegicus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Rattus norvegicus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Rattus norvegicus)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Rattus norvegicus)
H2O [mitochondrial matrix]
Pregnenolone biosynthesis (Rattus norvegicus)
CYP11A1 cleaves 20a,22b-DHCHOL (Rattus norvegicus)
H2O [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Rattus norvegicus)
H2O [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Rattus norvegicus)
H2O [mitochondrial matrix]
Phospholipid metabolism (Rattus norvegicus)
Glycerophospholipid biosynthesis (Rattus norvegicus)
Acyl chain remodeling of CL (Rattus norvegicus)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Rattus norvegicus)
H2O [mitochondrial matrix]
Acyl chain remodelling of PG (Rattus norvegicus)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Rattus norvegicus)
H2O [mitochondrial matrix]
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Rattus norvegicus)
H2O [mitochondrial matrix]
Synthesis of PA (Rattus norvegicus)
ACP6 hydrolyses MYS-LPA (Rattus norvegicus)
H2O [mitochondrial matrix]
Synthesis of PE (Rattus norvegicus)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism of nucleotides (Rattus norvegicus)
Interconversion of nucleotide di- and triphosphates (Rattus norvegicus)
NUDT13 hydrolyses AP6A to AP4 and ADP (Rattus norvegicus)
H2O [mitochondrial matrix]
Nucleotide catabolism (Rattus norvegicus)
Purine catabolism (Rattus norvegicus)
Phosphate bond hydrolysis by NUDT proteins (Rattus norvegicus)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Rattus norvegicus)
H2O [mitochondrial matrix]
Pyrimidine catabolism (Rattus norvegicus)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Rattus norvegicus)
Heme biosynthesis (Rattus norvegicus)
COX10 transforms heme to heme O (Rattus norvegicus)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Rattus norvegicus)
Metabolism of cofactors (Rattus norvegicus)
Ubiquinol biosynthesis (Rattus norvegicus)
COQ6 hydroxylates DHB (Rattus norvegicus)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Rattus norvegicus)
Metabolism of folate and pterines (Rattus norvegicus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Rattus norvegicus)
H2O [mitochondrial matrix]
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Rattus norvegicus)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Rattus norvegicus)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Rattus norvegicus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Rattus norvegicus)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Rattus norvegicus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Rattus norvegicus)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism of proteins (Rattus norvegicus)
Mitochondrial protein degradation (Rattus norvegicus)
AFG3L2 degrades mitochondrial inner membrane proteins (Rattus norvegicus)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Rattus norvegicus)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Rattus norvegicus)
H2O [mitochondrial matrix]
CLPXP degrades mitochondrial matrix proteins (Rattus norvegicus)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Rattus norvegicus)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Rattus norvegicus)
H2O [mitochondrial matrix]
Translation (Rattus norvegicus)
tRNA Aminoacylation (Rattus norvegicus)
Mitochondrial tRNA aminoacylation (Rattus norvegicus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Rattus norvegicus)
H2O [mitochondrial matrix]
Muscle contraction (Rattus norvegicus)
Smooth Muscle Contraction (Rattus norvegicus)
ALDH2 transforms GTN to NO (Rattus norvegicus)
H2O [mitochondrial matrix]
Neuronal System (Rattus norvegicus)
Transmission across Chemical Synapses (Rattus norvegicus)
Neurotransmitter release cycle (Rattus norvegicus)
GABA synthesis, release, reuptake and degradation (Rattus norvegicus)
Degradation of GABA (Rattus norvegicus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Rattus norvegicus)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Rattus norvegicus)
glutamine + H2O => glutamate + NH4+ (GLS) (Rattus norvegicus)
H2O [mitochondrial matrix]
Programmed Cell Death (Rattus norvegicus)
Apoptosis (Rattus norvegicus)
Regulation of Apoptosis (Rattus norvegicus)
OMA1 hydrolyses OPA1 (Rattus norvegicus)
H2O [mitochondrial matrix]
Transport of small molecules (Rattus norvegicus)
ABC-family proteins mediated transport (Rattus norvegicus)
Mitochondrial ABC transporters (Rattus norvegicus)
ABC7, mABC1 and mABC2 mediate heme transport (Rattus norvegicus)
H2O [mitochondrial matrix]
Metabolism (Saccharomyces cerevisiae)
Aerobic respiration and respiratory electron transport (Saccharomyces cerevisiae)
Citric acid cycle (TCA cycle) (Saccharomyces cerevisiae)
CS acetylates OA to citrate (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Biological oxidations (Saccharomyces cerevisiae)
Phase I - Functionalization of compounds (Saccharomyces cerevisiae)
Ethanol oxidation (Saccharomyces cerevisiae)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Saccharomyces cerevisiae)
Branched-chain amino acid catabolism (Saccharomyces cerevisiae)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Lysine catabolism (Saccharomyces cerevisiae)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Proline catabolism (Saccharomyces cerevisiae)
PRODH2 oxidises HPRO to 1PYR-5COOH (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Urea cycle (Saccharomyces cerevisiae)
arginine + H2O => ornithine + urea [ARG2] (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Metabolism of lipids (Saccharomyces cerevisiae)
Phospholipid metabolism (Saccharomyces cerevisiae)
Glycerophospholipid biosynthesis (Saccharomyces cerevisiae)
Acyl chain remodeling of CL (Saccharomyces cerevisiae)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Acyl chain remodelling of PG (Saccharomyces cerevisiae)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Saccharomyces cerevisiae)
Heme biosynthesis (Saccharomyces cerevisiae)
COX10 transforms heme to heme O (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Saccharomyces cerevisiae)
Metabolism of cofactors (Saccharomyces cerevisiae)
Ubiquinol biosynthesis (Saccharomyces cerevisiae)
COQ6 hydroxylates DHB (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Saccharomyces cerevisiae)
Metabolism of folate and pterines (Saccharomyces cerevisiae)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Saccharomyces cerevisiae)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Metabolism of proteins (Saccharomyces cerevisiae)
Mitochondrial protein degradation (Saccharomyces cerevisiae)
AFG3L2 degrades mitochondrial inner membrane proteins (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Translation (Saccharomyces cerevisiae)
tRNA Aminoacylation (Saccharomyces cerevisiae)
Mitochondrial tRNA aminoacylation (Saccharomyces cerevisiae)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Muscle contraction (Saccharomyces cerevisiae)
Smooth Muscle Contraction (Saccharomyces cerevisiae)
ALDH2 transforms GTN to NO (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Neuronal System (Saccharomyces cerevisiae)
Transmission across Chemical Synapses (Saccharomyces cerevisiae)
Neurotransmitter release cycle (Saccharomyces cerevisiae)
GABA synthesis, release, reuptake and degradation (Saccharomyces cerevisiae)
Degradation of GABA (Saccharomyces cerevisiae)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Programmed Cell Death (Saccharomyces cerevisiae)
Apoptosis (Saccharomyces cerevisiae)
Regulation of Apoptosis (Saccharomyces cerevisiae)
OMA1 hydrolyses OPA1 (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Transport of small molecules (Saccharomyces cerevisiae)
ABC-family proteins mediated transport (Saccharomyces cerevisiae)
Mitochondrial ABC transporters (Saccharomyces cerevisiae)
ABC7, mABC1 and mABC2 mediate heme transport (Saccharomyces cerevisiae)
H2O [mitochondrial matrix]
Metabolism (Schizosaccharomyces pombe)
Aerobic respiration and respiratory electron transport (Schizosaccharomyces pombe)
Citric acid cycle (TCA cycle) (Schizosaccharomyces pombe)
CS acetylates OA to citrate (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Biological oxidations (Schizosaccharomyces pombe)
Phase I - Functionalization of compounds (Schizosaccharomyces pombe)
Ethanol oxidation (Schizosaccharomyces pombe)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Schizosaccharomyces pombe)
Branched-chain amino acid catabolism (Schizosaccharomyces pombe)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Lysine catabolism (Schizosaccharomyces pombe)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Proline catabolism (Schizosaccharomyces pombe)
PRODH2 oxidises HPRO to 1PYR-5COOH (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Urea cycle (Schizosaccharomyces pombe)
arginine + H2O => ornithine + urea [ARG2] (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Metabolism of lipids (Schizosaccharomyces pombe)
Phospholipid metabolism (Schizosaccharomyces pombe)
Glycerophospholipid biosynthesis (Schizosaccharomyces pombe)
Acyl chain remodeling of CL (Schizosaccharomyces pombe)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Acyl chain remodelling of PG (Schizosaccharomyces pombe)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Synthesis of PA (Schizosaccharomyces pombe)
ACP6 hydrolyses MYS-LPA (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Schizosaccharomyces pombe)
Heme biosynthesis (Schizosaccharomyces pombe)
COX10 transforms heme to heme O (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Schizosaccharomyces pombe)
Metabolism of cofactors (Schizosaccharomyces pombe)
Ubiquinol biosynthesis (Schizosaccharomyces pombe)
COQ6 hydroxylates DHB (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Schizosaccharomyces pombe)
Metabolism of folate and pterines (Schizosaccharomyces pombe)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Schizosaccharomyces pombe)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Metabolism of proteins (Schizosaccharomyces pombe)
Mitochondrial protein degradation (Schizosaccharomyces pombe)
AFG3L2 degrades mitochondrial inner membrane proteins (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Translation (Schizosaccharomyces pombe)
tRNA Aminoacylation (Schizosaccharomyces pombe)
Mitochondrial tRNA aminoacylation (Schizosaccharomyces pombe)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Muscle contraction (Schizosaccharomyces pombe)
Smooth Muscle Contraction (Schizosaccharomyces pombe)
ALDH2 transforms GTN to NO (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Neuronal System (Schizosaccharomyces pombe)
Transmission across Chemical Synapses (Schizosaccharomyces pombe)
Neurotransmitter release cycle (Schizosaccharomyces pombe)
GABA synthesis, release, reuptake and degradation (Schizosaccharomyces pombe)
Degradation of GABA (Schizosaccharomyces pombe)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Programmed Cell Death (Schizosaccharomyces pombe)
Apoptosis (Schizosaccharomyces pombe)
Regulation of Apoptosis (Schizosaccharomyces pombe)
OMA1 hydrolyses OPA1 (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Transport of small molecules (Schizosaccharomyces pombe)
ABC-family proteins mediated transport (Schizosaccharomyces pombe)
Mitochondrial ABC transporters (Schizosaccharomyces pombe)
ABC7, mABC1 and mABC2 mediate heme transport (Schizosaccharomyces pombe)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Sus scrofa)
Cellular responses to stress (Sus scrofa)
Cellular response to chemical stress (Sus scrofa)
Cytoprotection by HMOX1 (Sus scrofa)
Electron transfer from reduced cytochrome c to molecular oxygen (Sus scrofa)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Sus scrofa)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Sus scrofa)
H2O [mitochondrial matrix]
NUDT2 hydrolyses GP4G to GTP, GMP (Sus scrofa)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Sus scrofa)
H2O [mitochondrial matrix]
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Sus scrofa)
H2O [mitochondrial matrix]
Mitochondrial unfolded protein response (UPRmt) (Sus scrofa)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Sus scrofa)
H2O [mitochondrial matrix]
DNA Repair (Sus scrofa)
Base Excision Repair (Sus scrofa)
Resolution of Abasic Sites (AP sites) (Sus scrofa)
Resolution of AP sites via the multiple-nucleotide patch replacement pathway (Sus scrofa)
POLB-Dependent Long Patch Base Excision Repair (Sus scrofa)
ADPRHL2 hydrolyses poly(ADP-ribose) (Sus scrofa)
H2O [mitochondrial matrix]
Extracellular matrix organization (Sus scrofa)
Degradation of the extracellular matrix (Sus scrofa)
Collagen degradation (Sus scrofa)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Sus scrofa)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Sus scrofa)
RNA Polymerase II Transcription (Sus scrofa)
Generic Transcription Pathway (Sus scrofa)
Transcriptional Regulation by TP53 (Sus scrofa)
TP53 Regulates Metabolic Genes (Sus scrofa)
Electron transfer from reduced cytochrome c to molecular oxygen (Sus scrofa)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism (Sus scrofa)
Aerobic respiration and respiratory electron transport (Sus scrofa)
Citric acid cycle (TCA cycle) (Sus scrofa)
CS acetylates OA to citrate (Sus scrofa)
H2O [mitochondrial matrix]
FH tetramer hydrates fumarate to L-malate (Sus scrofa)
H2O [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Sus scrofa)
ATPase synthesizes ATP (Sus scrofa)
H2O [mitochondrial matrix]
Pyruvate metabolism (Sus scrofa)
Regulation of pyruvate metabolism (Sus scrofa)
Regulation of pyruvate dehydrogenase (PDH) complex (Sus scrofa)
PDP1,2 dephosphorylate p-lipo-PDH (Sus scrofa)
H2O [mitochondrial matrix]
SIRT4 cleaves lipoyl from DLAT (Sus scrofa)
H2O [mitochondrial matrix]
Respiratory electron transport (Sus scrofa)
Electron transfer from reduced cytochrome c to molecular oxygen (Sus scrofa)
H2O [mitochondrial matrix]
Biological oxidations (Sus scrofa)
Phase I - Functionalization of compounds (Sus scrofa)
Cytochrome P450 - arranged by substrate type (Sus scrofa)
Endogenous sterols (Sus scrofa)
CYP11A1 cleaves 20a,22b-DHCHOL (Sus scrofa)
H2O [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Sus scrofa)
H2O [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Sus scrofa)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Sus scrofa)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Sus scrofa)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Sus scrofa)
H2O [mitochondrial matrix]
Vitamins (Sus scrofa)
CYP24A1 24-hydroxylates CTL (Sus scrofa)
H2O [mitochondrial matrix]
Ethanol oxidation (Sus scrofa)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Sus scrofa)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Sus scrofa)
H2O [mitochondrial matrix]
Phase II - Conjugation of compounds (Sus scrofa)
Glucuronidation (Sus scrofa)
ABHD10 hydrolyses MPAG (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Sus scrofa)
Branched-chain amino acid catabolism (Sus scrofa)
ECHS1 hydrates methacrylyl-CoA (Sus scrofa)
H2O [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Sus scrofa)
H2O [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Sus scrofa)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Sus scrofa)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Sus scrofa)
H2O [mitochondrial matrix]
Choline catabolism (Sus scrofa)
ALDH7A1 oxidises BETALD to BET (Sus scrofa)
H2O [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Sus scrofa)
H2O [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Sus scrofa)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Sus scrofa)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Sus scrofa)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Sus scrofa)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Sus scrofa)
H2O [mitochondrial matrix]
Lysine catabolism (Sus scrofa)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Sus scrofa)
H2O [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Sus scrofa)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Sus scrofa)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Sus scrofa)
H2O [mitochondrial matrix]
Proline catabolism (Sus scrofa)
ALDH4A1 oxidises L-GluSS to Glu (Sus scrofa)
H2O [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-5COOH (Sus scrofa)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Sus scrofa)
Degradation of cysteine and homocysteine (Sus scrofa)
Sulfide oxidation to sulfate (Sus scrofa)
Persulfide sulfur is dioxygenated (Sus scrofa)
H2O [mitochondrial matrix]
Sulfite is oxidized to sulfate (Sus scrofa)
H2O [mitochondrial matrix]
Urea cycle (Sus scrofa)
arginine + H2O => ornithine + urea [ARG2] (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism of lipids (Sus scrofa)
Fatty acid metabolism (Sus scrofa)
Fatty acyl-CoA biosynthesis (Sus scrofa)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Sus scrofa)
H2O [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Sus scrofa)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Sus scrofa)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Sus scrofa)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Sus scrofa)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Sus scrofa)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Sus scrofa)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Sus scrofa)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Sus scrofa)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Sus scrofa)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Sus scrofa)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Sus scrofa)
H2O [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Sus scrofa)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Sus scrofa)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Sus scrofa)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Sus scrofa)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Sus scrofa)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism of steroids (Sus scrofa)
Bile acid and bile salt metabolism (Sus scrofa)
Synthesis of bile acids and bile salts (Sus scrofa)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Sus scrofa)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Sus scrofa)
H2O [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Sus scrofa)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Sus scrofa)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Sus scrofa)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Sus scrofa)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Sus scrofa)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Sus scrofa)
CYP27A1 27-hydroxylates CHOL (Sus scrofa)
H2O [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Sus scrofa)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Sus scrofa)
H2O [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Sus scrofa)
H2O [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Sus scrofa)
H2O [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism of steroid hormones (Sus scrofa)
Glucocorticoid biosynthesis (Sus scrofa)
CYP11B1 oxidises 11DCORT (Sus scrofa)
H2O [mitochondrial matrix]
Mineralocorticoid biosynthesis (Sus scrofa)
CYP11B2 18-hydroxylates CORST to 18HCORST (Sus scrofa)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Sus scrofa)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Sus scrofa)
H2O [mitochondrial matrix]
Pregnenolone biosynthesis (Sus scrofa)
CYP11A1 cleaves 20a,22b-DHCHOL (Sus scrofa)
H2O [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Sus scrofa)
H2O [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Sus scrofa)
H2O [mitochondrial matrix]
Phospholipid metabolism (Sus scrofa)
Glycerophospholipid biosynthesis (Sus scrofa)
Acyl chain remodeling of CL (Sus scrofa)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Sus scrofa)
H2O [mitochondrial matrix]
Acyl chain remodelling of PG (Sus scrofa)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Sus scrofa)
H2O [mitochondrial matrix]
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Sus scrofa)
H2O [mitochondrial matrix]
Synthesis of PA (Sus scrofa)
ACP6 hydrolyses MYS-LPA (Sus scrofa)
H2O [mitochondrial matrix]
Synthesis of PE (Sus scrofa)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism of nucleotides (Sus scrofa)
Interconversion of nucleotide di- and triphosphates (Sus scrofa)
NUDT13 hydrolyses AP6A to AP4 and ADP (Sus scrofa)
H2O [mitochondrial matrix]
Nucleotide catabolism (Sus scrofa)
Purine catabolism (Sus scrofa)
Phosphate bond hydrolysis by NUDT proteins (Sus scrofa)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Sus scrofa)
H2O [mitochondrial matrix]
Pyrimidine catabolism (Sus scrofa)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Sus scrofa)
Heme biosynthesis (Sus scrofa)
COX10 transforms heme to heme O (Sus scrofa)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Sus scrofa)
Metabolism of cofactors (Sus scrofa)
Ubiquinol biosynthesis (Sus scrofa)
COQ6 hydroxylates DHB (Sus scrofa)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Sus scrofa)
Metabolism of folate and pterines (Sus scrofa)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Sus scrofa)
H2O [mitochondrial matrix]
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Sus scrofa)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Sus scrofa)
H2O [mitochondrial matrix]
Pyrophosphate hydrolysis (Sus scrofa)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Sus scrofa)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Sus scrofa)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Sus scrofa)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Sus scrofa)
H2O [mitochondrial matrix]
Metabolism of proteins (Sus scrofa)
Mitochondrial protein degradation (Sus scrofa)
AFG3L2 degrades mitochondrial inner membrane proteins (Sus scrofa)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Sus scrofa)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Sus scrofa)
H2O [mitochondrial matrix]
CLPXP degrades mitochondrial matrix proteins (Sus scrofa)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial inner membrane proteins (Sus scrofa)
H2O [mitochondrial matrix]
LONP1 degrades mitochondrial matrix proteins (Sus scrofa)
H2O [mitochondrial matrix]
Translation (Sus scrofa)
tRNA Aminoacylation (Sus scrofa)
Mitochondrial tRNA aminoacylation (Sus scrofa)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Sus scrofa)
H2O [mitochondrial matrix]
Muscle contraction (Sus scrofa)
Smooth Muscle Contraction (Sus scrofa)
ALDH2 transforms GTN to NO (Sus scrofa)
H2O [mitochondrial matrix]
Neuronal System (Sus scrofa)
Transmission across Chemical Synapses (Sus scrofa)
Neurotransmitter release cycle (Sus scrofa)
GABA synthesis, release, reuptake and degradation (Sus scrofa)
Degradation of GABA (Sus scrofa)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Sus scrofa)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Sus scrofa)
glutamine + H2O => glutamate + NH4+ (GLS) (Sus scrofa)
H2O [mitochondrial matrix]
Programmed Cell Death (Sus scrofa)
Apoptosis (Sus scrofa)
Regulation of Apoptosis (Sus scrofa)
OMA1 hydrolyses OPA1 (Sus scrofa)
H2O [mitochondrial matrix]
Transport of small molecules (Sus scrofa)
ABC-family proteins mediated transport (Sus scrofa)
Mitochondrial ABC transporters (Sus scrofa)
ABC7, mABC1 and mABC2 mediate heme transport (Sus scrofa)
H2O [mitochondrial matrix]
Cellular responses to stimuli (Xenopus tropicalis)
Cellular responses to stress (Xenopus tropicalis)
Cellular response to chemical stress (Xenopus tropicalis)
Cytoprotection by HMOX1 (Xenopus tropicalis)
Electron transfer from reduced cytochrome c to molecular oxygen (Xenopus tropicalis)
H2O [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Xenopus tropicalis)
NUDT2 hydrolyses GP4G to GTP, GMP (Xenopus tropicalis)
H2O [mitochondrial matrix]
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Xenopus tropicalis)
H2O [mitochondrial matrix]
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Xenopus tropicalis)
H2O [mitochondrial matrix]
DNA Repair (Xenopus tropicalis)
Base Excision Repair (Xenopus tropicalis)
Resolution of Abasic Sites (AP sites) (Xenopus tropicalis)
Resolution of AP sites via the multiple-nucleotide patch replacement pathway (Xenopus tropicalis)
POLB-Dependent Long Patch Base Excision Repair (Xenopus tropicalis)
ADPRHL2 hydrolyses poly(ADP-ribose) (Xenopus tropicalis)
H2O [mitochondrial matrix]
Gene expression (Transcription) (Xenopus tropicalis)
RNA Polymerase II Transcription (Xenopus tropicalis)
Generic Transcription Pathway (Xenopus tropicalis)
Transcriptional Regulation by TP53 (Xenopus tropicalis)
TP53 Regulates Metabolic Genes (Xenopus tropicalis)
Electron transfer from reduced cytochrome c to molecular oxygen (Xenopus tropicalis)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Xenopus tropicalis)
H2O [mitochondrial matrix]
Metabolism (Xenopus tropicalis)
Aerobic respiration and respiratory electron transport (Xenopus tropicalis)
Citric acid cycle (TCA cycle) (Xenopus tropicalis)
CS acetylates OA to citrate (Xenopus tropicalis)
H2O [mitochondrial matrix]
Pyruvate metabolism (Xenopus tropicalis)
Regulation of pyruvate metabolism (Xenopus tropicalis)
Regulation of pyruvate dehydrogenase (PDH) complex (Xenopus tropicalis)
SIRT4 cleaves lipoyl from DLAT (Xenopus tropicalis)
H2O [mitochondrial matrix]
Respiratory electron transport (Xenopus tropicalis)
Electron transfer from reduced cytochrome c to molecular oxygen (Xenopus tropicalis)
H2O [mitochondrial matrix]
Biological oxidations (Xenopus tropicalis)
Phase I - Functionalization of compounds (Xenopus tropicalis)
Cytochrome P450 - arranged by substrate type (Xenopus tropicalis)
Endogenous sterols (Xenopus tropicalis)
CYP11A1 cleaves 20a,22b-DHCHOL (Xenopus tropicalis)
H2O [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Xenopus tropicalis)
H2O [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Xenopus tropicalis)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Xenopus tropicalis)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Xenopus tropicalis)
H2O [mitochondrial matrix]
Ethanol oxidation (Xenopus tropicalis)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Xenopus tropicalis)
H2O [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Xenopus tropicalis)
H2O [mitochondrial matrix]
Phase II - Conjugation of compounds (Xenopus tropicalis)
Glucuronidation (Xenopus tropicalis)
ABHD10 hydrolyses MPAG (Xenopus tropicalis)
H2O [mitochondrial matrix]
Metabolism of amino acids and derivatives (Xenopus tropicalis)
Branched-chain amino acid catabolism (Xenopus tropicalis)
ECHS1 hydrates methacrylyl-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Xenopus tropicalis)
H2O [mitochondrial matrix]
Choline catabolism (Xenopus tropicalis)
ALDH7A1 oxidises BETALD to BET (Xenopus tropicalis)
H2O [mitochondrial matrix]
Glutamate and glutamine metabolism (Xenopus tropicalis)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Xenopus tropicalis)
H2O [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Xenopus tropicalis)
H2O [mitochondrial matrix]
glutamine + H2O => glutamate + NH4+ (GLS) (Xenopus tropicalis)
H2O [mitochondrial matrix]
Lysine catabolism (Xenopus tropicalis)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Xenopus tropicalis)
H2O [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Xenopus tropicalis)
H2O [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Xenopus tropicalis)
H2O [mitochondrial matrix]
Proline catabolism (Xenopus tropicalis)
ALDH4A1 oxidises L-GluSS to Glu (Xenopus tropicalis)
H2O [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-5COOH (Xenopus tropicalis)
H2O [mitochondrial matrix]
Sulfur amino acid metabolism (Xenopus tropicalis)
Degradation of cysteine and homocysteine (Xenopus tropicalis)
Sulfide oxidation to sulfate (Xenopus tropicalis)
Persulfide sulfur is dioxygenated (Xenopus tropicalis)
H2O [mitochondrial matrix]
Sulfite is oxidized to sulfate (Xenopus tropicalis)
H2O [mitochondrial matrix]
Urea cycle (Xenopus tropicalis)
arginine + H2O => ornithine + urea [ARG2] (Xenopus tropicalis)
H2O [mitochondrial matrix]
Metabolism of lipids (Xenopus tropicalis)
Fatty acid metabolism (Xenopus tropicalis)
Mitochondrial Fatty Acid Beta-Oxidation (Xenopus tropicalis)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Xenopus tropicalis)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Xenopus tropicalis)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Xenopus tropicalis)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Xenopus tropicalis)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Xenopus tropicalis)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Xenopus tropicalis)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Xenopus tropicalis)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Xenopus tropicalis)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Metabolism of steroids (Xenopus tropicalis)
Metabolism of steroid hormones (Xenopus tropicalis)
Glucocorticoid biosynthesis (Xenopus tropicalis)
CYP11B1 oxidises 11DCORT (Xenopus tropicalis)
H2O [mitochondrial matrix]
Mineralocorticoid biosynthesis (Xenopus tropicalis)
CYP11B2 18-hydroxylates CORST to 18HCORST (Xenopus tropicalis)
H2O [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Xenopus tropicalis)
H2O [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Xenopus tropicalis)
H2O [mitochondrial matrix]
Pregnenolone biosynthesis (Xenopus tropicalis)
CYP11A1 cleaves 20a,22b-DHCHOL (Xenopus tropicalis)
H2O [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Xenopus tropicalis)
H2O [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Xenopus tropicalis)
H2O [mitochondrial matrix]
Phospholipid metabolism (Xenopus tropicalis)
Glycerophospholipid biosynthesis (Xenopus tropicalis)
Acyl chain remodeling of CL (Xenopus tropicalis)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Xenopus tropicalis)
H2O [mitochondrial matrix]
Acyl chain remodelling of PG (Xenopus tropicalis)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Xenopus tropicalis)
H2O [mitochondrial matrix]
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Xenopus tropicalis)
H2O [mitochondrial matrix]
Synthesis of PA (Xenopus tropicalis)
ACP6 hydrolyses MYS-LPA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Synthesis of PE (Xenopus tropicalis)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Metabolism of nucleotides (Xenopus tropicalis)
Interconversion of nucleotide di- and triphosphates (Xenopus tropicalis)
NUDT13 hydrolyses AP6A to AP4 and ADP (Xenopus tropicalis)
H2O [mitochondrial matrix]
Nucleotide catabolism (Xenopus tropicalis)
Purine catabolism (Xenopus tropicalis)
Phosphate bond hydrolysis by NUDT proteins (Xenopus tropicalis)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Xenopus tropicalis)
H2O [mitochondrial matrix]
Pyrimidine catabolism (Xenopus tropicalis)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Xenopus tropicalis)
H2O [mitochondrial matrix]
Metabolism of porphyrins (Xenopus tropicalis)
Heme biosynthesis (Xenopus tropicalis)
COX10 transforms heme to heme O (Xenopus tropicalis)
H2O [mitochondrial matrix]
COX15 transforms heme O to heme A (Xenopus tropicalis)
H2O [mitochondrial matrix]
Metabolism of vitamins and cofactors (Xenopus tropicalis)
Metabolism of cofactors (Xenopus tropicalis)
Ubiquinol biosynthesis (Xenopus tropicalis)
COQ6 hydroxylates DHB (Xenopus tropicalis)
H2O [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Xenopus tropicalis)
H2O [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Xenopus tropicalis)
Metabolism of folate and pterines (Xenopus tropicalis)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Xenopus tropicalis)
H2O [mitochondrial matrix]
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Xenopus tropicalis)
H2O [mitochondrial matrix]
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Xenopus tropicalis)
H2O [mitochondrial matrix]
Reversible hydration of carbon dioxide (Xenopus tropicalis)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Xenopus tropicalis)
H2O [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Xenopus tropicalis)
H2O [mitochondrial matrix]
Metabolism of proteins (Xenopus tropicalis)
Mitochondrial protein degradation (Xenopus tropicalis)
AFG3L2 degrades mitochondrial inner membrane proteins (Xenopus tropicalis)
H2O [mitochondrial matrix]
AFG3L2 degrades mitochondrial matrix proteins (Xenopus tropicalis)
H2O [mitochondrial matrix]
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Xenopus tropicalis)
H2O [mitochondrial matrix]
CLPXP degrades mitochondrial matrix proteins (Xenopus tropicalis)
H2O [mitochondrial matrix]
Muscle contraction (Xenopus tropicalis)
Smooth Muscle Contraction (Xenopus tropicalis)
ALDH2 transforms GTN to NO (Xenopus tropicalis)
H2O [mitochondrial matrix]
Neuronal System (Xenopus tropicalis)
Transmission across Chemical Synapses (Xenopus tropicalis)
Neurotransmitter release cycle (Xenopus tropicalis)
GABA synthesis, release, reuptake and degradation (Xenopus tropicalis)
Degradation of GABA (Xenopus tropicalis)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Xenopus tropicalis)
H2O [mitochondrial matrix]
Glutamate Neurotransmitter Release Cycle (Xenopus tropicalis)
glutamine + H2O => glutamate + NH4+ (GLS) (Xenopus tropicalis)
H2O [mitochondrial matrix]
Programmed Cell Death (Xenopus tropicalis)
Apoptosis (Xenopus tropicalis)
Regulation of Apoptosis (Xenopus tropicalis)
OMA1 hydrolyses OPA1 (Xenopus tropicalis)
H2O [mitochondrial matrix]
Transport of small molecules (Xenopus tropicalis)
ABC-family proteins mediated transport (Xenopus tropicalis)
Mitochondrial ABC transporters (Xenopus tropicalis)
ABC7, mABC1 and mABC2 mediate heme transport (Xenopus tropicalis)
H2O [mitochondrial matrix]
External Reference Information
External Reference
water [ChEBI:15377]
Participates
as an input of
arginine + H2O => ornithine + urea (Gallus gallus)
acetyl-CoA + H2O + oxaloacetate => citrate + CoA (Gallus gallus)
fumarate + H2O <=> malate (Gallus gallus)
SUPV3L1:PNPT1 hydrolyzes mitochondrial RNA to yield 4-5 nucleotide oligoribonucleotides (Homo sapiens)
REXO2 hydrolyzes 4-5 nucleotide RNAs to ribonucleotides (Homo sapiens)
AFG3L2 degrades mitochondrial inner membrane proteins (Saccharomyces cerevisiae)
AFG3L2 degrades mitochondrial inner membrane proteins (Schizosaccharomyces pombe)
AFG3L2 degrades mitochondrial inner membrane proteins (Dictyostelium discoideum)
AFG3L2 degrades mitochondrial inner membrane proteins (Caenorhabditis elegans)
AFG3L2 degrades mitochondrial inner membrane proteins (Drosophila melanogaster)
AFG3L2 degrades mitochondrial inner membrane proteins (Gallus gallus)
AFG3L2 degrades mitochondrial inner membrane proteins (Xenopus tropicalis)
AFG3L2 degrades mitochondrial inner membrane proteins (Danio rerio)
AFG3L2 degrades mitochondrial inner membrane proteins (Sus scrofa)
AFG3L2 degrades mitochondrial inner membrane proteins (Bos taurus)
AFG3L2 degrades mitochondrial inner membrane proteins (Canis familiaris)
AFG3L2 degrades mitochondrial inner membrane proteins (Rattus norvegicus)
AFG3L2 degrades mitochondrial inner membrane proteins (Mus musculus)
AFG3L2 degrades mitochondrial inner membrane proteins (Homo sapiens)
AFG3L2 degrades mitochondrial matrix proteins (Plasmodium falciparum)
AFG3L2 degrades mitochondrial matrix proteins (Saccharomyces cerevisiae)
AFG3L2 degrades mitochondrial matrix proteins (Schizosaccharomyces pombe)
AFG3L2 degrades mitochondrial matrix proteins (Dictyostelium discoideum)
AFG3L2 degrades mitochondrial matrix proteins (Caenorhabditis elegans)
AFG3L2 degrades mitochondrial matrix proteins (Drosophila melanogaster)
AFG3L2 degrades mitochondrial matrix proteins (Gallus gallus)
AFG3L2 degrades mitochondrial matrix proteins (Xenopus tropicalis)
AFG3L2 degrades mitochondrial matrix proteins (Danio rerio)
AFG3L2 degrades mitochondrial matrix proteins (Sus scrofa)
AFG3L2 degrades mitochondrial matrix proteins (Bos taurus)
AFG3L2 degrades mitochondrial matrix proteins (Canis familiaris)
AFG3L2 degrades mitochondrial matrix proteins (Rattus norvegicus)
AFG3L2 degrades mitochondrial matrix proteins (Mus musculus)
AFG3L2 degrades mitochondrial matrix proteins (Homo sapiens)
LONP1 degrades mitochondrial matrix proteins (Saccharomyces cerevisiae)
LONP1 degrades mitochondrial matrix proteins (Schizosaccharomyces pombe)
LONP1 degrades mitochondrial matrix proteins (Dictyostelium discoideum)
LONP1 degrades mitochondrial matrix proteins (Caenorhabditis elegans)
LONP1 degrades mitochondrial matrix proteins (Drosophila melanogaster)
LONP1 degrades mitochondrial matrix proteins (Gallus gallus)
LONP1 degrades mitochondrial matrix proteins (Sus scrofa)
LONP1 degrades mitochondrial matrix proteins (Bos taurus)
LONP1 degrades mitochondrial matrix proteins (Canis familiaris)
LONP1 degrades mitochondrial matrix proteins (Rattus norvegicus)
LONP1 degrades mitochondrial matrix proteins (Mus musculus)
LONP1 degrades mitochondrial matrix proteins (Homo sapiens)
CLPXP degrades mitochondrial matrix proteins (Caenorhabditis elegans)
CLPXP degrades mitochondrial matrix proteins (Drosophila melanogaster)
CLPXP degrades mitochondrial matrix proteins (Xenopus tropicalis)
CLPXP degrades mitochondrial matrix proteins (Sus scrofa)
CLPXP degrades mitochondrial matrix proteins (Bos taurus)
CLPXP degrades mitochondrial matrix proteins (Canis familiaris)
CLPXP degrades mitochondrial matrix proteins (Rattus norvegicus)
CLPXP degrades mitochondrial matrix proteins (Mus musculus)
CLPXP degrades mitochondrial matrix proteins (Homo sapiens)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Caenorhabditis elegans)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Drosophila melanogaster)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Gallus gallus)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Xenopus tropicalis)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Sus scrofa)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Bos taurus)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Canis familiaris)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Rattus norvegicus)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Mus musculus)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Homo sapiens)
LONP1 degrades mitochondrial inner membrane proteins (Saccharomyces cerevisiae)
LONP1 degrades mitochondrial inner membrane proteins (Schizosaccharomyces pombe)
LONP1 degrades mitochondrial inner membrane proteins (Dictyostelium discoideum)
LONP1 degrades mitochondrial inner membrane proteins (Caenorhabditis elegans)
LONP1 degrades mitochondrial inner membrane proteins (Drosophila melanogaster)
LONP1 degrades mitochondrial inner membrane proteins (Gallus gallus)
LONP1 degrades mitochondrial inner membrane proteins (Sus scrofa)
LONP1 degrades mitochondrial inner membrane proteins (Bos taurus)
LONP1 degrades mitochondrial inner membrane proteins (Canis familiaris)
LONP1 degrades mitochondrial inner membrane proteins (Rattus norvegicus)
LONP1 degrades mitochondrial inner membrane proteins (Mus musculus)
LONP1 degrades mitochondrial inner membrane proteins (Homo sapiens)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Xenopus tropicalis)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Canis familiaris)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Saccharomyces cerevisiae)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Saccharomyces cerevisiae)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Schizosaccharomyces pombe)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Schizosaccharomyces pombe)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Gallus gallus)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Gallus gallus)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Xenopus tropicalis)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Sus scrofa)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Sus scrofa)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Bos taurus)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Bos taurus)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Canis familiaris)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Rattus norvegicus)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Rattus norvegicus)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Mus musculus)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Mus musculus)
PG is hydrolyzed to 1-acyl LPG by PLA2G4B (IM) (Homo sapiens)
PG is hydrolysed to 2-acyl LPG by PLA2G4B (IM) (Homo sapiens)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Caenorhabditis elegans)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Drosophila melanogaster)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Gallus gallus)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Xenopus tropicalis)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Danio rerio)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Sus scrofa)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Bos taurus)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Canis familiaris)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Rattus norvegicus)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Mus musculus)
PXLP-K278-ETNPPL tetramer hydrolyses PETA (Homo sapiens)
ACP6 hydrolyses MYS-LPA (Schizosaccharomyces pombe)
ACP6 hydrolyses MYS-LPA (Dictyostelium discoideum)
ACP6 hydrolyses MYS-LPA (Caenorhabditis elegans)
ACP6 hydrolyses MYS-LPA (Gallus gallus)
ACP6 hydrolyses MYS-LPA (Xenopus tropicalis)
ACP6 hydrolyses MYS-LPA (Danio rerio)
ACP6 hydrolyses MYS-LPA (Sus scrofa)
ACP6 hydrolyses MYS-LPA (Bos taurus)
ACP6 hydrolyses MYS-LPA (Canis familiaris)
ACP6 hydrolyses MYS-LPA (Rattus norvegicus)
ACP6 hydrolyses MYS-LPA (Mus musculus)
ACP6 hydrolyses MYS-LPA (Homo sapiens)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Plasmodium falciparum)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Caenorhabditis elegans)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Drosophila melanogaster)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Gallus gallus)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Xenopus tropicalis)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Danio rerio)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Sus scrofa)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Bos taurus)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Canis familiaris)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Rattus norvegicus)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Mus musculus)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Homo sapiens)
ADPRHL2 hydrolyses poly(ADP-ribose) (Gallus gallus)
ADPRHL2 hydrolyses poly(ADP-ribose) (Xenopus tropicalis)
ADPRHL2 hydrolyses poly(ADP-ribose) (Danio rerio)
ADPRHL2 hydrolyses poly(ADP-ribose) (Sus scrofa)
ADPRHL2 hydrolyses poly(ADP-ribose) (Bos taurus)
ADPRHL2 hydrolyses poly(ADP-ribose) (Rattus norvegicus)
ADPRHL2 hydrolyses poly(ADP-ribose) (Mus musculus)
ADPRHL2 hydrolyses poly(ADP-ribose) (Homo sapiens)
H139Hfs13* PPM1K does not dephosphorylate BCKDH (Homo sapiens)
ECHS1 mutants don't synthesize beta-hydroxyisobutyryl-CoA (Homo sapiens)
HIBCH mutants don't synthesize beta-hydroxyisobutyrate (Homo sapiens)
AUH mutants don't synthesize 3-hydroxy-methylglutaryl-CoA (Homo sapiens)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Saccharomyces cerevisiae)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Schizosaccharomyces pombe)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Dictyostelium discoideum)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Caenorhabditis elegans)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Drosophila melanogaster)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Xenopus tropicalis)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Danio rerio)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Sus scrofa)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Bos taurus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Canis familiaris)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Rattus norvegicus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Mus musculus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Homo sapiens)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Saccharomyces cerevisiae)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Schizosaccharomyces pombe)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Dictyostelium discoideum)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Caenorhabditis elegans)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Drosophila melanogaster)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Gallus gallus)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Xenopus tropicalis)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Danio rerio)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Sus scrofa)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Bos taurus)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Canis familiaris)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Rattus norvegicus)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Mus musculus)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Homo sapiens)
Nudt8 hydrolyzes CoA-SH to PPANT (Mus musculus)
NUDT8 hydrolyzes CoA-SH to PPANT (Homo sapiens)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Plasmodium falciparum)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Dictyostelium discoideum)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Xenopus tropicalis)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Danio rerio)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Sus scrofa)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Bos taurus)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Canis familiaris)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Rattus norvegicus)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Mus musculus)
PXLP-K280-SHMT2 tetramer transfers CH2OH group to Gly to form L-Ser (Homo sapiens)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Plasmodium falciparum)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Saccharomyces cerevisiae)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Schizosaccharomyces pombe)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Dictyostelium discoideum)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Drosophila melanogaster)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Gallus gallus)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Xenopus tropicalis)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Danio rerio)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Sus scrofa)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Bos taurus)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Canis familiaris)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Rattus norvegicus)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Mus musculus)
MTHFD2, D2L oxidise 5,10-methenyl-THF to 10-formyl-THF (Homo sapiens)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Caenorhabditis elegans)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Drosophila melanogaster)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Gallus gallus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Xenopus tropicalis)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Sus scrofa)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Bos taurus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Canis familiaris)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Rattus norvegicus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Mus musculus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Homo sapiens)
ABHD10 hydrolyses MPAG (Gallus gallus)
ABHD10 hydrolyses MPAG (Xenopus tropicalis)
ABHD10 hydrolyses MPAG (Sus scrofa)
ABHD10 hydrolyses MPAG (Bos taurus)
ABHD10 hydrolyses MPAG (Canis familiaris)
ABHD10 hydrolyses MPAG (Rattus norvegicus)
ABHD10 hydrolyses MPAG (Mus musculus)
ABHD10 hydrolyses MPAG (Homo sapiens)
ABC7, mABC1 and mABC2 mediate heme transport (Saccharomyces cerevisiae)
ABC7, mABC1 and mABC2 mediate heme transport (Schizosaccharomyces pombe)
ABC7, mABC1 and mABC2 mediate heme transport (Dictyostelium discoideum)
ABC7, mABC1 and mABC2 mediate heme transport (Caenorhabditis elegans)
ABC7, mABC1 and mABC2 mediate heme transport (Drosophila melanogaster)
ABC7, mABC1 and mABC2 mediate heme transport (Gallus gallus)
ABC7, mABC1 and mABC2 mediate heme transport (Xenopus tropicalis)
ABC7, mABC1 and mABC2 mediate heme transport (Danio rerio)
ABC7, mABC1 and mABC2 mediate heme transport (Sus scrofa)
ABC7, mABC1 and mABC2 mediate heme transport (Bos taurus)
ABC7, mABC1 and mABC2 mediate heme transport (Canis familiaris)
ABC7, mABC1 and mABC2 mediate heme transport (Rattus norvegicus)
ABC7, mABC1 and mABC2 mediate heme transport (Mus musculus)
ABC7, mABC1 and mABC2 mediate heme transport (Homo sapiens)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Gallus gallus)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Sus scrofa)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Bos taurus)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Canis familiaris)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Rattus norvegicus)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Mus musculus)
SIRT3 deacetylates Ac-K272,K290-FOXO3 (Homo sapiens)
ALDH4A1 oxidises L-GluSS to Glu (Gallus gallus)
ALDH4A1 oxidises L-GluSS to Glu (Xenopus tropicalis)
ALDH4A1 oxidises L-GluSS to Glu (Danio rerio)
ALDH4A1 oxidises L-GluSS to Glu (Bos taurus)
ALDH4A1 oxidises L-GluSS to Glu (Canis familiaris)
ALDH4A1 oxidises L-GluSS to Glu (Rattus norvegicus)
ALDH4A1 oxidises L-GluSS to Glu (Mus musculus)
ALDH4A1 oxidises L-GluSS to Glu (Homo sapiens)
ALDH4A1 oxidises L-GluSS to Glu (Sus scrofa)
SARDH:FAD oxidatively demethylates SARC to Gly (Drosophila melanogaster)
SARDH:FAD oxidatively demethylates SARC to Gly (Gallus gallus)
SARDH:FAD oxidatively demethylates SARC to Gly (Danio rerio)
SARDH:FAD oxidatively demethylates SARC to Gly (Bos taurus)
SARDH:FAD oxidatively demethylates SARC to Gly (Canis familiaris)
SARDH:FAD oxidatively demethylates SARC to Gly (Rattus norvegicus)
SARDH:FAD oxidatively demethylates SARC to Gly (Mus musculus)
SARDH:FAD oxidatively demethylates SARC to Gly (Homo sapiens)
SARDH:FAD oxidatively demethylates SARC to Gly (Sus scrofa)
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Caenorhabditis elegans)
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Gallus gallus)
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Bos taurus)
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Canis familiaris)
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Rattus norvegicus)
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Mus musculus)
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Homo sapiens)
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Sus scrofa)
arginine + H2O => ornithine + urea [ARG2] (Plasmodium falciparum)
arginine + H2O => ornithine + urea [ARG2] (Saccharomyces cerevisiae)
arginine + H2O => ornithine + urea [ARG2] (Schizosaccharomyces pombe)
arginine + H2O => ornithine + urea [ARG2] (Dictyostelium discoideum)
arginine + H2O => ornithine + urea [ARG2] (Caenorhabditis elegans)
arginine + H2O => ornithine + urea [ARG2] (Drosophila melanogaster)
arginine + H2O => ornithine + urea [ARG2] (Gallus gallus)
arginine + H2O => ornithine + urea [ARG2] (Xenopus tropicalis)
arginine + H2O => ornithine + urea [ARG2] (Danio rerio)
arginine + H2O => ornithine + urea [ARG2] (Bos taurus)
arginine + H2O => ornithine + urea [ARG2] (Canis familiaris)
arginine + H2O => ornithine + urea [ARG2] (Rattus norvegicus)
arginine + H2O => ornithine + urea [ARG2] (Mus musculus)
arginine + H2O => ornithine + urea [ARG2] (Homo sapiens)
arginine + H2O => ornithine + urea [ARG2] (Sus scrofa)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Dictyostelium discoideum)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Caenorhabditis elegans)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Drosophila melanogaster)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Gallus gallus)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Xenopus tropicalis)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Danio rerio)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Sus scrofa)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Canis familiaris)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Rattus norvegicus)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Mus musculus)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Homo sapiens)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Bos taurus)
ALDH7A1 oxidises BETALD to BET (Dictyostelium discoideum)
ALDH7A1 oxidises BETALD to BET (Caenorhabditis elegans)
ALDH7A1 oxidises BETALD to BET (Drosophila melanogaster)
ALDH7A1 oxidises BETALD to BET (Gallus gallus)
ALDH7A1 oxidises BETALD to BET (Xenopus tropicalis)
ALDH7A1 oxidises BETALD to BET (Danio rerio)
ALDH7A1 oxidises BETALD to BET (Sus scrofa)
ALDH7A1 oxidises BETALD to BET (Bos taurus)
ALDH7A1 oxidises BETALD to BET (Canis familiaris)
ALDH7A1 oxidises BETALD to BET (Rattus norvegicus)
ALDH7A1 oxidises BETALD to BET (Mus musculus)
ALDH7A1 oxidises BETALD to BET (Homo sapiens)
MPP cleaves targeting peptide (presequence) of inner membrane precursors (Homo sapiens)
MPP cleaves targeting peptide (presequence) of matrix precursors (Homo sapiens)
COX15 transforms heme O to heme A (Plasmodium falciparum)
COX15 transforms heme O to heme A (Saccharomyces cerevisiae)
COX15 transforms heme O to heme A (Schizosaccharomyces pombe)
COX15 transforms heme O to heme A (Dictyostelium discoideum)
COX15 transforms heme O to heme A (Caenorhabditis elegans)
COX15 transforms heme O to heme A (Drosophila melanogaster)
COX15 transforms heme O to heme A (Gallus gallus)
COX15 transforms heme O to heme A (Xenopus tropicalis)
COX15 transforms heme O to heme A (Sus scrofa)
COX15 transforms heme O to heme A (Canis familiaris)
COX15 transforms heme O to heme A (Rattus norvegicus)
COX15 transforms heme O to heme A (Mus musculus)
COX15 transforms heme O to heme A (Homo sapiens)
COX10 transforms heme to heme O (Plasmodium falciparum)
COX10 transforms heme to heme O (Saccharomyces cerevisiae)
COX10 transforms heme to heme O (Schizosaccharomyces pombe)
COX10 transforms heme to heme O (Dictyostelium discoideum)
COX10 transforms heme to heme O (Caenorhabditis elegans)
COX10 transforms heme to heme O (Drosophila melanogaster)
COX10 transforms heme to heme O (Gallus gallus)
COX10 transforms heme to heme O (Xenopus tropicalis)
COX10 transforms heme to heme O (Sus scrofa)
COX10 transforms heme to heme O (Canis familiaris)
COX10 transforms heme to heme O (Rattus norvegicus)
COX10 transforms heme to heme O (Mus musculus)
COX10 transforms heme to heme O (Homo sapiens)
COX10 transforms heme to heme O (Bos taurus)
COX15 transforms heme O to heme A (Bos taurus)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Plasmodium falciparum)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Dictyostelium discoideum)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Caenorhabditis elegans)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Drosophila melanogaster)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Gallus gallus)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Xenopus tropicalis)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Sus scrofa)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Bos taurus)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Rattus norvegicus)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Mus musculus)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Homo sapiens)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Canis familiaris)
Sulfite is oxidized to sulfate (Dictyostelium discoideum)
Sulfite is oxidized to sulfate (Caenorhabditis elegans)
Sulfite is oxidized to sulfate (Drosophila melanogaster)
Sulfite is oxidized to sulfate (Gallus gallus)
Sulfite is oxidized to sulfate (Xenopus tropicalis)
Sulfite is oxidized to sulfate (Sus scrofa)
Sulfite is oxidized to sulfate (Bos taurus)
Sulfite is oxidized to sulfate (Canis familiaris)
Sulfite is oxidized to sulfate (Rattus norvegicus)
Sulfite is oxidized to sulfate (Mus musculus)
Persulfide sulfur is dioxygenated (Caenorhabditis elegans)
Persulfide sulfur is dioxygenated (Drosophila melanogaster)
Persulfide sulfur is dioxygenated (Xenopus tropicalis)
Persulfide sulfur is dioxygenated (Danio rerio)
Persulfide sulfur is dioxygenated (Sus scrofa)
Persulfide sulfur is dioxygenated (Bos taurus)
Persulfide sulfur is dioxygenated (Canis familiaris)
Persulfide sulfur is dioxygenated (Rattus norvegicus)
Persulfide sulfur is dioxygenated (Mus musculus)
Persulfide sulfur is dioxygenated (Homo sapiens)
Sulfite is oxidized to sulfate (Homo sapiens)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Plasmodium falciparum)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Dictyostelium discoideum)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Caenorhabditis elegans)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Drosophila melanogaster)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Gallus gallus)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Xenopus tropicalis)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Danio rerio)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Sus scrofa)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Bos taurus)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Canis familiaris)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Rattus norvegicus)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Mus musculus)
ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA (Homo sapiens)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Dictyostelium discoideum)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Caenorhabditis elegans)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Drosophila melanogaster)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Xenopus tropicalis)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Sus scrofa)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Bos taurus)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Canis familiaris)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Rattus norvegicus)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Mus musculus)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Homo sapiens)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Dictyostelium discoideum)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Caenorhabditis elegans)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Drosophila melanogaster)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Xenopus tropicalis)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Sus scrofa)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Bos taurus)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Canis familiaris)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Rattus norvegicus)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Mus musculus)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Homo sapiens)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Dictyostelium discoideum)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Caenorhabditis elegans)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Drosophila melanogaster)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Xenopus tropicalis)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Sus scrofa)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Bos taurus)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Canis familiaris)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Rattus norvegicus)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Mus musculus)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Homo sapiens)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Dictyostelium discoideum)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Caenorhabditis elegans)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Drosophila melanogaster)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Xenopus tropicalis)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Sus scrofa)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Bos taurus)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Canis familiaris)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Rattus norvegicus)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Mus musculus)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Homo sapiens)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Dictyostelium discoideum)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Caenorhabditis elegans)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Drosophila melanogaster)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Xenopus tropicalis)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Sus scrofa)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Bos taurus)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Canis familiaris)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Rattus norvegicus)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Mus musculus)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Caenorhabditis elegans)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Drosophila melanogaster)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Gallus gallus)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Xenopus tropicalis)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Danio rerio)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Sus scrofa)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Bos taurus)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Canis familiaris)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Rattus norvegicus)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Mus musculus)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Caenorhabditis elegans)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Drosophila melanogaster)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Gallus gallus)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Xenopus tropicalis)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Danio rerio)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Sus scrofa)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Bos taurus)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Canis familiaris)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Rattus norvegicus)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Mus musculus)
trans-Hexadec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxyhexadecanoyl-CoA (Homo sapiens)
trans-Tetradec-2-enoyl-CoA+H2O<=>(S)-3-Hydroxytetradecanoyl-CoA (Homo sapiens)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Homo sapiens)
Linoleoyl-CoA is converted to cis,cis-3,6- dodecadienoyl-CoA by three cycles of beta-oxidation (Homo sapiens)
Trans,cis-lauro-2,6-dienoyl-CoA is converted to cis,cis-3,6- 4-cis-decenoyl-CoA by one cycle of beta-oxidation (Homo sapiens)
SIRT4 cleaves lipoyl from DLAT (Caenorhabditis elegans)
SIRT4 cleaves lipoyl from DLAT (Drosophila melanogaster)
SIRT4 cleaves lipoyl from DLAT (Gallus gallus)
SIRT4 cleaves lipoyl from DLAT (Xenopus tropicalis)
SIRT4 cleaves lipoyl from DLAT (Danio rerio)
SIRT4 cleaves lipoyl from DLAT (Sus scrofa)
SIRT4 cleaves lipoyl from DLAT (Bos taurus)
SIRT4 cleaves lipoyl from DLAT (Canis familiaris)
SIRT4 cleaves lipoyl from DLAT (Rattus norvegicus)
SIRT4 cleaves lipoyl from DLAT (Mus musculus)
SIRT4 cleaves lipoyl from DLAT (Homo sapiens)
NUDT13 hydrolyses AP6A to AP4 and ADP (Gallus gallus)
NUDT13 hydrolyses AP6A to AP4 and ADP (Xenopus tropicalis)
NUDT13 hydrolyses AP6A to AP4 and ADP (Sus scrofa)
NUDT13 hydrolyses AP6A to AP4 and ADP (Bos taurus)
NUDT13 hydrolyses AP6A to AP4 and ADP (Canis familiaris)
NUDT13 hydrolyses AP6A to AP4 and ADP (Rattus norvegicus)
NUDT13 hydrolyses AP6A to AP4 and ADP (Mus musculus)
NUDT13 hydrolyses AP6A to AP4 and ADP (Homo sapiens)
1PYR-5COOH spontaneously hydrolyses to L-GluSS (Homo sapiens)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Plasmodium falciparum)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Saccharomyces cerevisiae)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Dictyostelium discoideum)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Caenorhabditis elegans)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Drosophila melanogaster)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Gallus gallus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Danio rerio)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Sus scrofa)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Bos taurus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Canis familiaris)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Rattus norvegicus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Mus musculus)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Homo sapiens)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Schizosaccharomyces pombe)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Caenorhabditis elegans)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Drosophila melanogaster)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Gallus gallus)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Xenopus tropicalis)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Sus scrofa)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Bos taurus)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Canis familiaris)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Rattus norvegicus)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Mus musculus)
Mitochondrial NUDT9 hydrolyses ADP-ribose to R5P and AMP (Homo sapiens)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Gallus gallus)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Xenopus tropicalis)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Sus scrofa)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Bos taurus)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Canis familiaris)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Rattus norvegicus)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Mus musculus)
TMP, (d)UMP, uridine 2' monophosphate, or uridine 3'-monophosphate + H2O => thymidine, deoxyuridine, or uridine + orthophosphate [NT5M] (Homo sapiens)
NUDT2 hydrolyses GP4G to GTP, GMP (Plasmodium falciparum)
NUDT2 hydrolyses GP4G to GTP, GMP (Caenorhabditis elegans)
NUDT2 hydrolyses GP4G to GTP, GMP (Drosophila melanogaster)
NUDT2 hydrolyses GP4G to GTP, GMP (Gallus gallus)
NUDT2 hydrolyses GP4G to GTP, GMP (Xenopus tropicalis)
NUDT2 hydrolyses GP4G to GTP, GMP (Danio rerio)
NUDT2 hydrolyses GP4G to GTP, GMP (Sus scrofa)
NUDT2 hydrolyses GP4G to GTP, GMP (Bos taurus)
NUDT2 hydrolyses GP4G to GTP, GMP (Canis familiaris)
NUDT2 hydrolyses GP4G to GTP, GMP (Rattus norvegicus)
NUDT2 hydrolyses GP4G to GTP, GMP (Mus musculus)
NUDT2 hydrolyses GP4G to GTP, GMP (Homo sapiens)
GS-MCA spontaneously hydrolyzes (Homo sapiens)
Spontaneous hydrolysis of 1-pyrroline-3-hydroxy-5-carboxylate to 4-OH-L-glutamate semialdehyde (Homo sapiens)
Unknown dehydrogenase oxidizes 4-HBz (Homo sapiens)
glutamine + H2O => glutamate + NH4+ (GLS) (Caenorhabditis elegans)
glutamine + H2O => glutamate + NH4+ (GLS) (Drosophila melanogaster)
glutamine + H2O => glutamate + NH4+ (GLS) (Gallus gallus)
glutamine + H2O => glutamate + NH4+ (GLS) (Xenopus tropicalis)
glutamine + H2O => glutamate + NH4+ (GLS) (Danio rerio)
glutamine + H2O => glutamate + NH4+ (GLS) (Sus scrofa)
glutamine + H2O => glutamate + NH4+ (GLS) (Bos taurus)
glutamine + H2O => glutamate + NH4+ (GLS) (Canis familiaris)
glutamine + H2O => glutamate + NH4+ (GLS) (Rattus norvegicus)
glutamine + H2O => glutamate + NH4+ (GLS) (Mus musculus)
glutamine + H2O => glutamate + NH4+ (GLS) (Homo sapiens)
OMA1 hydrolyses OPA1 (Saccharomyces cerevisiae)
OMA1 hydrolyses OPA1 (Schizosaccharomyces pombe)
OMA1 hydrolyses OPA1 (Dictyostelium discoideum)
OMA1 hydrolyses OPA1 (Gallus gallus)
OMA1 hydrolyses OPA1 (Xenopus tropicalis)
OMA1 hydrolyses OPA1 (Danio rerio)
OMA1 hydrolyses OPA1 (Sus scrofa)
OMA1 hydrolyses OPA1 (Bos taurus)
OMA1 hydrolyses OPA1 (Canis familiaris)
OMA1 hydrolyses OPA1 (Rattus norvegicus)
OMA1 hydrolyses OPA1 (Mus musculus)
OMA1 hydrolyses OPA1 (Homo sapiens)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Dictyostelium discoideum)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Caenorhabditis elegans)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Drosophila melanogaster)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Gallus gallus)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Xenopus tropicalis)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Danio rerio)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Sus scrofa)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Bos taurus)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Canis familiaris)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Rattus norvegicus)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Mus musculus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Caenorhabditis elegans)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Drosophila melanogaster)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Gallus gallus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Danio rerio)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Sus scrofa)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Bos taurus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Canis familiaris)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Rattus norvegicus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Mus musculus)
PXLP-K278-PHYKPL tetramer hydrolyses 5PHL (Homo sapiens)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Saccharomyces cerevisiae)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Schizosaccharomyces pombe)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Dictyostelium discoideum)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Caenorhabditis elegans)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Drosophila melanogaster)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Danio rerio)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Bos taurus)
FH tetramer hydrates fumarate to L-malate (Dictyostelium discoideum)
PDP1,2 dephosphorylate p-lipo-PDH (Gallus gallus)
PDP1,2 dephosphorylate p-lipo-PDH (Sus scrofa)
FH tetramer hydrates fumarate to L-malate (Saccharomyces cerevisiae)
CS acetylates OA to citrate (Saccharomyces cerevisiae)
CS acetylates OA to citrate (Schizosaccharomyces pombe)
FH tetramer hydrates fumarate to L-malate (Schizosaccharomyces pombe)
CS acetylates OA to citrate (Plasmodium falciparum)
CS acetylates OA to citrate (Dictyostelium discoideum)
PDP1,2 dephosphorylate p-lipo-PDH (Caenorhabditis elegans)
FH tetramer hydrates fumarate to L-malate (Caenorhabditis elegans)
CS acetylates OA to citrate (Caenorhabditis elegans)
PDP1,2 dephosphorylate p-lipo-PDH (Drosophila melanogaster)
FH tetramer hydrates fumarate to L-malate (Drosophila melanogaster)
CS acetylates OA to citrate (Drosophila melanogaster)
FH tetramer hydrates fumarate to L-malate (Gallus gallus)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Gallus gallus)
CS acetylates OA to citrate (Gallus gallus)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Xenopus tropicalis)
CS acetylates OA to citrate (Xenopus tropicalis)
FH tetramer hydrates fumarate to L-malate (Danio rerio)
CS acetylates OA to citrate (Danio rerio)
FH tetramer hydrates fumarate to L-malate (Rattus norvegicus)
CS acetylates OA to citrate (Rattus norvegicus)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Sus scrofa)
CS acetylates OA to citrate (Sus scrofa)
FH tetramer hydrates fumarate to L-malate (Sus scrofa)
PDP1,2 dephosphorylate p-lipo-PDH (Bos taurus)
PDP1,2 dephosphorylate p-lipo-PDH (Canis familiaris)
PDP1,2 dephosphorylate p-lipo-PDH (Homo sapiens)
PDP1,2 dephosphorylate p-lipo-PDH (Mus musculus)
CS acetylates OA to citrate (Mus musculus)
FH tetramer hydrates fumarate to L-malate (Mus musculus)
CS acetylates OA to citrate (Homo sapiens)
tiglyl-CoA + H2O <=> alpha-methyl-beta-hydroxybutyryl-CoA (Homo sapiens)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Dictyostelium discoideum)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Caenorhabditis elegans)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Drosophila melanogaster)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Gallus gallus)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Xenopus tropicalis)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Danio rerio)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Sus scrofa)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Bos taurus)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Canis familiaris)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Rattus norvegicus)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Mus musculus)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Plasmodium falciparum)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Saccharomyces cerevisiae)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Schizosaccharomyces pombe)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Dictyostelium discoideum)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Caenorhabditis elegans)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Drosophila melanogaster)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Gallus gallus)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Danio rerio)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Sus scrofa)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Bos taurus)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Canis familiaris)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Rattus norvegicus)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Mus musculus)
ECHS1 hydrates methacrylyl-CoA (Dictyostelium discoideum)
ECHS1 hydrates methacrylyl-CoA (Caenorhabditis elegans)
ECHS1 hydrates methacrylyl-CoA (Drosophila melanogaster)
ECHS1 hydrates methacrylyl-CoA (Xenopus tropicalis)
ECHS1 hydrates methacrylyl-CoA (Sus scrofa)
ECHS1 hydrates methacrylyl-CoA (Bos taurus)
ECHS1 hydrates methacrylyl-CoA (Canis familiaris)
ECHS1 hydrates methacrylyl-CoA (Rattus norvegicus)
ECHS1 hydrates methacrylyl-CoA (Mus musculus)
PPM1K dephosphorylates p-BCKDH (Gallus gallus)
PPM1K dephosphorylates p-BCKDH (Sus scrofa)
PPM1K dephosphorylates p-BCKDH (Bos taurus)
PPM1K dephosphorylates p-BCKDH (Canis familiaris)
PPM1K dephosphorylates p-BCKDH (Rattus norvegicus)
PPM1K dephosphorylates p-BCKDH (Mus musculus)
PPM1K dephosphorylates p-BCKDH (Homo sapiens)
CL is hydrolyzed to MLCL by PLA2G6 (IM) (Homo sapiens)
PTPMT1 dephosphorylates PGP to PG (Homo sapiens)
Ptpmt1 dephosphorylates PGP to PG (Mus musculus)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Homo sapiens)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Mus musculus)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Rattus norvegicus)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Canis familiaris)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Bos taurus)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Sus scrofa)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Danio rerio)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Xenopus tropicalis)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Gallus gallus)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Schizosaccharomyces pombe)
MLCL is hydrolyzed to DLCL by PLA2G4A (IM) (Saccharomyces cerevisiae)
CL is hydrolyzed to MLCL by Pla2g6 (IM) (Rattus norvegicus)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Canis familiaris)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Homo sapiens)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Homo sapiens)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Mus musculus)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Rattus norvegicus)
PDP1,2 dephosphorylate p-lipo-PDH (Rattus norvegicus)
FH tetramer hydrates fumarate to L-malate (Bos taurus)
CS acetylates OA to citrate (Bos taurus)
FH tetramer hydrates fumarate to L-malate (Canis familiaris)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Canis familiaris)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Homo sapiens)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Mus musculus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Rattus norvegicus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Bos taurus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Sus scrofa)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Xenopus tropicalis)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Gallus gallus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Drosophila melanogaster)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Caenorhabditis elegans)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Schizosaccharomyces pombe)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Saccharomyces cerevisiae)
CS acetylates OA to citrate (Canis familiaris)
FH tetramer hydrates fumarate to L-malate (Homo sapiens)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Homo sapiens)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Homo sapiens)
ECHS1 hydrates methacrylyl-CoA (Homo sapiens)
as an output of
malate <=> fumarate + H2O (Gallus gallus)
ALDH2 transforms GTN to NO (Saccharomyces cerevisiae)
ALDH2 transforms GTN to NO (Schizosaccharomyces pombe)
ALDH2 transforms GTN to NO (Dictyostelium discoideum)
ALDH2 transforms GTN to NO (Caenorhabditis elegans)
ALDH2 transforms GTN to NO (Drosophila melanogaster)
ALDH2 transforms GTN to NO (Gallus gallus)
ALDH2 transforms GTN to NO (Xenopus tropicalis)
ALDH2 transforms GTN to NO (Danio rerio)
ALDH2 transforms GTN to NO (Sus scrofa)
ALDH2 transforms GTN to NO (Bos taurus)
ALDH2 transforms GTN to NO (Canis familiaris)
ALDH2 transforms GTN to NO (Rattus norvegicus)
ALDH2 transforms GTN to NO (Mus musculus)
ALDH2 transforms GTN to NO (Homo sapiens)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Plasmodium falciparum)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Caenorhabditis elegans)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Drosophila melanogaster)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Gallus gallus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Xenopus tropicalis)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Danio rerio)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Sus scrofa)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Bos taurus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Canis familiaris)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Rattus norvegicus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Mus musculus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Homo sapiens)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Sus scrofa)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Bos taurus)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Canis familiaris)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Rattus norvegicus)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Mus musculus)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Homo sapiens)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Sus scrofa)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Bos taurus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Canis familiaris)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Rattus norvegicus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Mus musculus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Sus scrofa)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Bos taurus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Canis familiaris)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Rattus norvegicus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Mus musculus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Sus scrofa)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Bos taurus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Canis familiaris)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Rattus norvegicus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Mus musculus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Homo sapiens)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Homo sapiens)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Homo sapiens)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Sus scrofa)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Bos taurus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Canis familiaris)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Rattus norvegicus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Mus musculus)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Sus scrofa)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Bos taurus)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Canis familiaris)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Rattus norvegicus)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Mus musculus)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Homo sapiens)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Homo sapiens)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Sus scrofa)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Bos taurus)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Canis familiaris)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Rattus norvegicus)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Mus musculus)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Sus scrofa)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Bos taurus)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Canis familiaris)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Rattus norvegicus)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Mus musculus)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Homo sapiens)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Homo sapiens)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Sus scrofa)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Bos taurus)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Canis familiaris)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Rattus norvegicus)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Mus musculus)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Homo sapiens)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Sus scrofa)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Bos taurus)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Canis familiaris)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Rattus norvegicus)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Mus musculus)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Homo sapiens)
CYP24A1 24-hydroxylates CTL (Danio rerio)
CYP24A1 24-hydroxylates CTL (Sus scrofa)
CYP24A1 24-hydroxylates CTL (Bos taurus)
CYP24A1 24-hydroxylates CTL (Canis familiaris)
CYP24A1 24-hydroxylates CTL (Rattus norvegicus)
CYP24A1 24-hydroxylates CTL (Mus musculus)
CYP24A1 24-hydroxylates CTL (Homo sapiens)
CYP27A1 27-hydroxylates CHOL (Sus scrofa)
CYP27A1 27-hydroxylates CHOL (Bos taurus)
CYP27A1 27-hydroxylates CHOL (Canis familiaris)
CYP27A1 27-hydroxylates CHOL (Rattus norvegicus)
CYP27A1 27-hydroxylates CHOL (Mus musculus)
CYP27A1 27-hydroxylates CHOL (Homo sapiens)
CYP11B2 oxidises 18HCORST to ALDO (Xenopus tropicalis)
CYP11B2 oxidises 18HCORST to ALDO (Sus scrofa)
CYP11B2 oxidises 18HCORST to ALDO (Bos taurus)
CYP11B2 oxidises 18HCORST to ALDO (Canis familiaris)
CYP11B2 oxidises 18HCORST to ALDO (Rattus norvegicus)
CYP11B2 oxidises 18HCORST to ALDO (Mus musculus)
CYP11B2 oxidises 18HCORST to ALDO (Homo sapiens)
CYP11B2 18-hydroxylates CORST to 18HCORST (Xenopus tropicalis)
CYP11B2 18-hydroxylates CORST to 18HCORST (Sus scrofa)
CYP11B2 18-hydroxylates CORST to 18HCORST (Bos taurus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Canis familiaris)
CYP11B2 18-hydroxylates CORST to 18HCORST (Rattus norvegicus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Mus musculus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Homo sapiens)
CYP11B2 oxidises 11DCORST to CORST (Xenopus tropicalis)
CYP11B2 oxidises 11DCORST to CORST (Sus scrofa)
CYP11B2 oxidises 11DCORST to CORST (Bos taurus)
CYP11B2 oxidises 11DCORST to CORST (Canis familiaris)
CYP11B2 oxidises 11DCORST to CORST (Rattus norvegicus)
CYP11B2 oxidises 11DCORST to CORST (Mus musculus)
CYP11B2 oxidises 11DCORST to CORST (Homo sapiens)
CYP11B1 oxidises 11DCORT (Xenopus tropicalis)
CYP11B1 oxidises 11DCORT (Sus scrofa)
CYP11B1 oxidises 11DCORT (Bos taurus)
CYP11B1 oxidises 11DCORT (Canis familiaris)
CYP11B1 oxidises 11DCORT (Rattus norvegicus)
CYP11B1 oxidises 11DCORT (Mus musculus)
CYP11B1 oxidises 11DCORT (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Gallus gallus)
CYP11A1 cleaves 20a,22b-DHCHOL (Xenopus tropicalis)
CYP11A1 cleaves 20a,22b-DHCHOL (Danio rerio)
CYP11A1 cleaves 20a,22b-DHCHOL (Sus scrofa)
CYP11A1 cleaves 20a,22b-DHCHOL (Bos taurus)
CYP11A1 cleaves 20a,22b-DHCHOL (Canis familiaris)
CYP11A1 cleaves 20a,22b-DHCHOL (Rattus norvegicus)
CYP11A1 cleaves 20a,22b-DHCHOL (Mus musculus)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Gallus gallus)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Xenopus tropicalis)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Danio rerio)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Sus scrofa)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Bos taurus)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Canis familiaris)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Rattus norvegicus)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Mus musculus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Gallus gallus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Xenopus tropicalis)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Danio rerio)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Sus scrofa)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Bos taurus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Canis familiaris)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Rattus norvegicus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Mus musculus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Homo sapiens)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
4-(2-aminophenyl)-2,4-dioxobutanoate => kynurenic acid + H2O [mitochondrial] (Homo sapiens)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Dictyostelium discoideum)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Caenorhabditis elegans)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Drosophila melanogaster)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Gallus gallus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Xenopus tropicalis)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Danio rerio)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Sus scrofa)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Bos taurus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Canis familiaris)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Rattus norvegicus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Mus musculus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Homo sapiens)
Mitochondrial H2O2 decarboxylates PYR to acetate (Homo sapiens)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Dictyostelium discoideum)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Drosophila melanogaster)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Gallus gallus)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Sus scrofa)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Canis familiaris)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Rattus norvegicus)
RPP14 (HTD2) dehydrates 3HA-CoA to t2E-CoA (Homo sapiens)
ATPase synthesizes ATP (Caenorhabditis elegans)
ATPase synthesizes ATP (Drosophila melanogaster)
ATPase synthesizes ATP (Gallus gallus)
ATPase synthesizes ATP (Danio rerio)
ATPase synthesizes ATP (Sus scrofa)
ATPase synthesizes ATP (Bos taurus)
ATPase synthesizes ATP (Canis familiaris)
ATPase synthesizes ATP (Rattus norvegicus)
ATPase synthesizes ATP (Homo sapiens)
ATPase synthesizes ATP (Mus musculus)
Electron transfer from reduced cytochrome c to molecular oxygen (Drosophila melanogaster)
Electron transfer from reduced cytochrome c to molecular oxygen (Gallus gallus)
Electron transfer from reduced cytochrome c to molecular oxygen (Xenopus tropicalis)
Electron transfer from reduced cytochrome c to molecular oxygen (Danio rerio)
Electron transfer from reduced cytochrome c to molecular oxygen (Sus scrofa)
Electron transfer from reduced cytochrome c to molecular oxygen (Bos taurus)
Electron transfer from reduced cytochrome c to molecular oxygen (Canis familiaris)
Electron transfer from reduced cytochrome c to molecular oxygen (Rattus norvegicus)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Mus musculus)
PRODH2 oxidises HPRO to 1PYR-5COOH (Saccharomyces cerevisiae)
PRODH2 oxidises HPRO to 1PYR-5COOH (Schizosaccharomyces pombe)
PRODH2 oxidises HPRO to 1PYR-5COOH (Dictyostelium discoideum)
PRODH2 oxidises HPRO to 1PYR-5COOH (Caenorhabditis elegans)
PRODH2 oxidises HPRO to 1PYR-5COOH (Drosophila melanogaster)
PRODH2 oxidises HPRO to 1PYR-5COOH (Xenopus tropicalis)
PRODH2 oxidises HPRO to 1PYR-5COOH (Sus scrofa)
PRODH2 oxidises HPRO to 1PYR-5COOH (Bos taurus)
PRODH2 oxidises HPRO to 1PYR-5COOH (Canis familiaris)
PRODH2 oxidises HPRO to 1PYR-5COOH (Rattus norvegicus)
PRODH2 oxidises HPRO to 1PYR-5COOH (Mus musculus)
PRODH2 oxidises HPRO to 1PYR-5COOH (Homo sapiens)
L-glutamate gamma-semialdehyde <=> L-1-pyrroline-5-carboxylate (Homo sapiens)
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Dictyostelium discoideum)
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Drosophila melanogaster)
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Xenopus tropicalis)
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Danio rerio)
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Sus scrofa)
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Bos taurus)
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Rattus norvegicus)
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Mus musculus)
PRDX5 reduces peroxynitrite to nitrite using TXN2 (Homo sapiens)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Dictyostelium discoideum)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Xenopus tropicalis)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Danio rerio)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Sus scrofa)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Caenorhabditis elegans)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Drosophila melanogaster)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Gallus gallus)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Bos taurus)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Rattus norvegicus)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Mus musculus)
PRDX3,5 catalyze TXN2 reduced + H2O2 => TXN2 oxidized + 2H2O (Homo sapiens)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Sus scrofa)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Bos taurus)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Canis familiaris)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Rattus norvegicus)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Mus musculus)
GPX1 catalyzes 2 glutathione, reduced + H2O2 => glutathione, oxidized + 2 H2O (Homo sapiens)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Saccharomyces cerevisiae)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Schizosaccharomyces pombe)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Dictyostelium discoideum)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Drosophila melanogaster)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Gallus gallus)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Xenopus tropicalis)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Sus scrofa)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Bos taurus)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Canis familiaris)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Rattus norvegicus)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Mus musculus)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Homo sapiens)
HMPhOH is hydroxylated to MDMQ6H2 by HMPhOH monooxygenase (Saccharomyces cerevisiae)
Unknown enzyme hydroxylates DMPhOH (Homo sapiens)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Danio rerio)
COQ6 hydroxylates DHB (Saccharomyces cerevisiae)
COQ6 hydroxylates DHB (Schizosaccharomyces pombe)
COQ6 hydroxylates DHB (Dictyostelium discoideum)
COQ6 hydroxylates DHB (Caenorhabditis elegans)
COQ6 hydroxylates DHB (Drosophila melanogaster)
COQ6 hydroxylates DHB (Gallus gallus)
COQ6 hydroxylates DHB (Xenopus tropicalis)
COQ6 hydroxylates DHB (Sus scrofa)
COQ6 hydroxylates DHB (Bos taurus)
COQ6 hydroxylates DHB (Canis familiaris)
COQ6 hydroxylates DHB (Rattus norvegicus)
COQ6 hydroxylates DHB (Mus musculus)
COQ6 hydroxylates DHB (Homo sapiens)
COQ6 hydroxylates DHB (Danio rerio)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Saccharomyces cerevisiae)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Schizosaccharomyces pombe)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Dictyostelium discoideum)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Caenorhabditis elegans)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Drosophila melanogaster)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Danio rerio)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Bos taurus)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Gallus gallus)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Xenopus tropicalis)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Sus scrofa)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Canis familiaris)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Homo sapiens)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Mus musculus)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Rattus norvegicus)
Other forms of this molecule
H2O [cytoplasm]
H2O [lipid droplet]
H2O [early endosome]
H2O [multivesicular body lumen]
H2O [phagocytic vesicle lumen]
H2O [melanosome lumen]
H2O [secretory granule lumen]
H2O [lysosomal lumen]
H2O [endoplasmic reticulum quality control compartment]
H2O [endocytic vesicle lumen]
H2O [Golgi lumen]
H2O [endoplasmic reticulum lumen]
H2O [peroxisomal matrix]
H2O [mitochondrial intermembrane space]
H2O [extracellular region]
H2O [nucleoplasm]
H2O [cytosol]
Cross References
COMPOUND
C00001
PubChem Substance
8145132
HMDB Metabolite
HMDB0002111
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