Mitochondrial 3-hydroxyisobutyryl-CoA hydrolase (HIBCH) catalyzes the hydrolysis of beta-hydroxyisobutyryl-CoA to form beta-hydroxyisobutyrate (3-hydroxy-2-methylpropanoate) and CoA (Hawes et al. 1996).
Hawes, JW, Jaskiewicz, J, Shimomura, Y, Huang, B, Bunting, J, Harper, ET, Harris, RA
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