Reactome | ATP [mitochondrial matrix]

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ATP [mitochondrial matrix] Show undefined attributes

compartment	[Compartment:5460] mitochondrial matrix
componentOf	[Complex:R-GGA-164835] ATPase:ATP [mitochondrial inner membrane] - Gallus gallus
consumedByEvent	[Reaction:R-GGA-373134] succinate + CoASH + ATP <=> succinylCoA + ADP + Pi - Gallus gallus [Reaction:R-CEL-9611218] YRDC synthesizes threonylcarbamoyladenylate - Caenorhabditis elegans [Reaction:R-DME-9611218] YRDC synthesizes threonylcarbamoyladenylate - Drosophila melanogaster [Reaction:R-GGA-9611218] YRDC synthesizes threonylcarbamoyladenylate - Gallus gallus [Reaction:R-XTR-9611218] YRDC synthesizes threonylcarbamoyladenylate - Xenopus tropicalis [Reaction:R-DRE-9611218] YRDC synthesizes threonylcarbamoyladenylate - Danio rerio [Reaction:R-SSC-9611218] YRDC synthesizes threonylcarbamoyladenylate - Sus scrofa [Reaction:R-BTA-9611218] YRDC synthesizes threonylcarbamoyladenylate - Bos taurus [Reaction:R-CFA-9611218] YRDC synthesizes threonylcarbamoyladenylate - Canis familiaris [Reaction:R-RNO-9611218] YRDC synthesizes threonylcarbamoyladenylate - Rattus norvegicus [Reaction:R-MMU-9611218] YRDC synthesizes threonylcarbamoyladenylate - Mus musculus [Reaction:R-HSA-9611218] YRDC synthesizes threonylcarbamoyladenylate - Homo sapiens [BlackBoxEvent:R-SCE-9838004] LONP1 degrades mitochondrial inner membrane proteins - Saccharomyces cerevisiae [BlackBoxEvent:R-SPO-9838004] LONP1 degrades mitochondrial inner membrane proteins - Schizosaccharomyces pombe [BlackBoxEvent:R-DDI-9838004] LONP1 degrades mitochondrial inner membrane proteins - Dictyostelium discoideum [BlackBoxEvent:R-CEL-9838004] LONP1 degrades mitochondrial inner membrane proteins - Caenorhabditis elegans [BlackBoxEvent:R-DME-9838004] LONP1 degrades mitochondrial inner membrane proteins - Drosophila melanogaster [BlackBoxEvent:R-GGA-9838004] LONP1 degrades mitochondrial inner membrane proteins - Gallus gallus [BlackBoxEvent:R-DRE-9838004] LONP1 degrades mitochondrial inner membrane proteins - Danio rerio [BlackBoxEvent:R-SSC-9838004] LONP1 degrades mitochondrial inner membrane proteins - Sus scrofa [BlackBoxEvent:R-BTA-9838004] LONP1 degrades mitochondrial inner membrane proteins - Bos taurus [BlackBoxEvent:R-CFA-9838004] LONP1 degrades mitochondrial inner membrane proteins - Canis familiaris [BlackBoxEvent:R-RNO-9838004] LONP1 degrades mitochondrial inner membrane proteins - Rattus norvegicus [BlackBoxEvent:R-MMU-9838004] LONP1 degrades mitochondrial inner membrane proteins - Mus musculus [BlackBoxEvent:R-HSA-9838004] LONP1 degrades mitochondrial inner membrane proteins - Homo sapiens [Reaction:R-MMU-8875095] Slc27a3 ligates CoA to VLCFA - Mus musculus [Reaction:R-HSA-8875077] SLC27A3 ligates CoA-SH to VLCFA - Homo sapiens [Reaction:R-GGA-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA - Gallus gallus [Reaction:R-XTR-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA - Xenopus tropicalis [Reaction:R-DRE-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA - Danio rerio [Reaction:R-SSC-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA - Sus scrofa [Reaction:R-BTA-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA - Bos taurus [Reaction:R-CFA-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA - Canis familiaris [Reaction:R-RNO-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA - Rattus norvegicus [Reaction:R-MMU-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA - Mus musculus [Reaction:R-HSA-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA - Homo sapiens [FailedReaction:R-HSA-9912480] BCKDK loss-of-function mutations do not phosphorylate BCKDH - Homo sapiens [FailedReaction:R-HSA-9912480] BCKDK loss-of-function mutations do not phosphorylate BCKDH - Homo sapiens [Reaction:R-PFA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Plasmodium falciparum [Reaction:R-SCE-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Saccharomyces cerevisiae [Reaction:R-SPO-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Schizosaccharomyces pombe [Reaction:R-DDI-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Dictyostelium discoideum [Reaction:R-GGA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Gallus gallus [Reaction:R-XTR-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Xenopus tropicalis [Reaction:R-DRE-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Danio rerio [Reaction:R-SSC-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Sus scrofa [Reaction:R-BTA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Bos taurus [Reaction:R-CFA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Canis familiaris [Reaction:R-RNO-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Rattus norvegicus [Reaction:R-MMU-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Mus musculus [Reaction:R-HSA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] - Homo sapiens [FailedReaction:R-HSA-3322125] Defective MMAB does not transfer adenosyl group from ATP to B12s - Homo sapiens [Reaction:R-XTR-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane - Xenopus tropicalis [Reaction:R-DRE-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane - Danio rerio [Reaction:R-SSC-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane - Sus scrofa [Reaction:R-BTA-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane - Bos taurus [Reaction:R-CFA-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane - Canis familiaris [Reaction:R-RNO-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane - Rattus norvegicus [Reaction:R-MMU-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane - Mus musculus [Reaction:R-HSA-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane - Homo sapiens [Reaction:R-PFA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Plasmodium falciparum [Reaction:R-SCE-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Saccharomyces cerevisiae [Reaction:R-SPO-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Schizosaccharomyces pombe [Reaction:R-DDI-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Dictyostelium discoideum [Reaction:R-CEL-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Caenorhabditis elegans [Reaction:R-DME-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Drosophila melanogaster [Reaction:R-GGA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Gallus gallus [Reaction:R-XTR-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Xenopus tropicalis [Reaction:R-DRE-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Danio rerio [Reaction:R-SSC-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Sus scrofa [Reaction:R-BTA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Bos taurus [Reaction:R-CFA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Canis familiaris [Reaction:R-MMU-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Mus musculus [Reaction:R-HSA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Homo sapiens [Reaction:R-RNO-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane - Rattus norvegicus [Reaction:R-SCE-70501] PC carboxylates PYR to OA - Saccharomyces cerevisiae [Reaction:R-SPO-70501] PC carboxylates PYR to OA - Schizosaccharomyces pombe [Reaction:R-CEL-70501] PC carboxylates PYR to OA - Caenorhabditis elegans [Reaction:R-DME-70501] PC carboxylates PYR to OA - Drosophila melanogaster [Reaction:R-XTR-70501] PC carboxylates PYR to OA - Xenopus tropicalis [Reaction:R-SSC-70501] PC carboxylates PYR to OA - Sus scrofa [Reaction:R-HSA-70501] PC carboxylates PYR to OA - Homo sapiens [Reaction:R-DRE-70501] PC carboxylates PYR to OA - Danio rerio [Reaction:R-MMU-70501] PC carboxylates PYR to OA - Mus musculus [Reaction:R-HSA-3159253] MMAB adenosylates cob(I)alamin - Homo sapiens [Reaction:R-HSA-3159253] MMAB adenosylates cob(I)alamin - Homo sapiens [Reaction:R-MMU-3159253] MMAB adenosylates cob(I)alamin - Mus musculus [Reaction:R-MMU-3159253] MMAB adenosylates cob(I)alamin - Mus musculus [Reaction:R-RNO-3159253] MMAB adenosylates cob(I)alamin - Rattus norvegicus [Reaction:R-RNO-3159253] MMAB adenosylates cob(I)alamin - Rattus norvegicus [Reaction:R-CFA-3159253] MMAB adenosylates cob(I)alamin - Canis familiaris [Reaction:R-CFA-3159253] MMAB adenosylates cob(I)alamin - Canis familiaris [Reaction:R-BTA-3159253] MMAB adenosylates cob(I)alamin - Bos taurus [Reaction:R-BTA-3159253] MMAB adenosylates cob(I)alamin - Bos taurus [Reaction:R-SSC-3159253] MMAB adenosylates cob(I)alamin - Sus scrofa [Reaction:R-SSC-3159253] MMAB adenosylates cob(I)alamin - Sus scrofa [Reaction:R-DRE-3159253] MMAB adenosylates cob(I)alamin - Danio rerio [Reaction:R-DRE-3159253] MMAB adenosylates cob(I)alamin - Danio rerio [Reaction:R-XTR-3159253] MMAB adenosylates cob(I)alamin - Xenopus tropicalis [Reaction:R-XTR-3159253] MMAB adenosylates cob(I)alamin - Xenopus tropicalis [Reaction:R-GGA-3159253] MMAB adenosylates cob(I)alamin - Gallus gallus [Reaction:R-GGA-3159253] MMAB adenosylates cob(I)alamin - Gallus gallus [Reaction:R-CEL-3159253] MMAB adenosylates cob(I)alamin - Caenorhabditis elegans [Reaction:R-CEL-3159253] MMAB adenosylates cob(I)alamin - Caenorhabditis elegans [Reaction:R-DDI-3159253] MMAB adenosylates cob(I)alamin - Dictyostelium discoideum [Reaction:R-DDI-3159253] MMAB adenosylates cob(I)alamin - Dictyostelium discoideum [Reaction:R-RNO-70501] PC carboxylates PYR to OA - Rattus norvegicus [Reaction:R-CFA-70501] PC carboxylates PYR to OA - Canis familiaris [Reaction:R-BTA-70501] PC carboxylates PYR to OA - Bos taurus [Reaction:R-HSA-9836927] SUPV3L1 unwinds double-stranded mitochondiral RNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA - Homo sapiens [BlackBoxEvent:R-PFA-9839105] AFG3L2 degrades mitochondrial matrix proteins - Plasmodium falciparum [BlackBoxEvent:R-SCE-9839105] AFG3L2 degrades mitochondrial matrix proteins - Saccharomyces cerevisiae [BlackBoxEvent:R-SPO-9839105] AFG3L2 degrades mitochondrial matrix proteins - Schizosaccharomyces pombe [BlackBoxEvent:R-DDI-9839105] AFG3L2 degrades mitochondrial matrix proteins - Dictyostelium discoideum [BlackBoxEvent:R-CEL-9839105] AFG3L2 degrades mitochondrial matrix proteins - Caenorhabditis elegans [BlackBoxEvent:R-DME-9839105] AFG3L2 degrades mitochondrial matrix proteins - Drosophila melanogaster [BlackBoxEvent:R-GGA-9839105] AFG3L2 degrades mitochondrial matrix proteins - Gallus gallus [BlackBoxEvent:R-XTR-9839105] AFG3L2 degrades mitochondrial matrix proteins - Xenopus tropicalis [BlackBoxEvent:R-DRE-9839105] AFG3L2 degrades mitochondrial matrix proteins - Danio rerio [BlackBoxEvent:R-SSC-9839105] AFG3L2 degrades mitochondrial matrix proteins - Sus scrofa [BlackBoxEvent:R-BTA-9839105] AFG3L2 degrades mitochondrial matrix proteins - Bos taurus [BlackBoxEvent:R-CFA-9839105] AFG3L2 degrades mitochondrial matrix proteins - Canis familiaris [BlackBoxEvent:R-RNO-9839105] AFG3L2 degrades mitochondrial matrix proteins - Rattus norvegicus [BlackBoxEvent:R-MMU-9839105] AFG3L2 degrades mitochondrial matrix proteins - Mus musculus [BlackBoxEvent:R-HSA-9839105] AFG3L2 degrades mitochondrial matrix proteins - Homo sapiens [BlackBoxEvent:R-SCE-9838081] LONP1 degrades mitochondrial matrix proteins - Saccharomyces cerevisiae [BlackBoxEvent:R-SPO-9838081] LONP1 degrades mitochondrial matrix proteins - Schizosaccharomyces pombe [BlackBoxEvent:R-DDI-9838081] LONP1 degrades mitochondrial matrix proteins - Dictyostelium discoideum [BlackBoxEvent:R-CEL-9838081] LONP1 degrades mitochondrial matrix proteins - Caenorhabditis elegans [BlackBoxEvent:R-DME-9838081] LONP1 degrades mitochondrial matrix proteins - Drosophila melanogaster [BlackBoxEvent:R-GGA-9838081] LONP1 degrades mitochondrial matrix proteins - Gallus gallus [BlackBoxEvent:R-DRE-9838081] LONP1 degrades mitochondrial matrix proteins - Danio rerio [BlackBoxEvent:R-SSC-9838081] LONP1 degrades mitochondrial matrix proteins - Sus scrofa [BlackBoxEvent:R-BTA-9838081] LONP1 degrades mitochondrial matrix proteins - Bos taurus [BlackBoxEvent:R-CFA-9838081] LONP1 degrades mitochondrial matrix proteins - Canis familiaris [BlackBoxEvent:R-RNO-9838081] LONP1 degrades mitochondrial matrix proteins - Rattus norvegicus [BlackBoxEvent:R-MMU-9838081] LONP1 degrades mitochondrial matrix proteins - Mus musculus [BlackBoxEvent:R-HSA-9838081] LONP1 degrades mitochondrial matrix proteins - Homo sapiens [BlackBoxEvent:R-CEL-9838289] CLPXP degrades mitochondrial matrix proteins - Caenorhabditis elegans [BlackBoxEvent:R-DME-9838289] CLPXP degrades mitochondrial matrix proteins - Drosophila melanogaster [BlackBoxEvent:R-XTR-9838289] CLPXP degrades mitochondrial matrix proteins - Xenopus tropicalis [BlackBoxEvent:R-DRE-9838289] CLPXP degrades mitochondrial matrix proteins - Danio rerio [BlackBoxEvent:R-SSC-9838289] CLPXP degrades mitochondrial matrix proteins - Sus scrofa [BlackBoxEvent:R-BTA-9838289] CLPXP degrades mitochondrial matrix proteins - Bos taurus [BlackBoxEvent:R-CFA-9838289] CLPXP degrades mitochondrial matrix proteins - Canis familiaris [BlackBoxEvent:R-RNO-9838289] CLPXP degrades mitochondrial matrix proteins - Rattus norvegicus [BlackBoxEvent:R-MMU-9838289] CLPXP degrades mitochondrial matrix proteins - Mus musculus [BlackBoxEvent:R-HSA-9838289] CLPXP degrades mitochondrial matrix proteins - Homo sapiens [Reaction:R-PFA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Plasmodium falciparum [Reaction:R-PFA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Plasmodium falciparum [Reaction:R-PFA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Plasmodium falciparum [Reaction:R-PFA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Plasmodium falciparum [Reaction:R-SCE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Saccharomyces cerevisiae [Reaction:R-SCE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Saccharomyces cerevisiae [Reaction:R-SCE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Saccharomyces cerevisiae [Reaction:R-SCE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Saccharomyces cerevisiae [Reaction:R-SPO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Schizosaccharomyces pombe [Reaction:R-SPO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Schizosaccharomyces pombe [Reaction:R-SPO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Schizosaccharomyces pombe [Reaction:R-SPO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Schizosaccharomyces pombe [Reaction:R-DDI-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Dictyostelium discoideum [Reaction:R-DDI-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Dictyostelium discoideum [Reaction:R-DDI-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Dictyostelium discoideum [Reaction:R-DDI-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Dictyostelium discoideum [Reaction:R-CEL-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Caenorhabditis elegans [Reaction:R-CEL-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Caenorhabditis elegans [Reaction:R-CEL-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Caenorhabditis elegans [Reaction:R-CEL-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Caenorhabditis elegans [Reaction:R-DME-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Drosophila melanogaster [Reaction:R-DME-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Drosophila melanogaster [Reaction:R-DME-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Drosophila melanogaster [Reaction:R-DME-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Drosophila melanogaster [Reaction:R-XTR-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Xenopus tropicalis [Reaction:R-XTR-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Xenopus tropicalis [Reaction:R-XTR-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Xenopus tropicalis [Reaction:R-XTR-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Xenopus tropicalis [Reaction:R-DRE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Danio rerio [Reaction:R-DRE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Danio rerio [Reaction:R-DRE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Danio rerio [Reaction:R-DRE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Danio rerio [Reaction:R-SSC-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Sus scrofa [Reaction:R-SSC-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Sus scrofa [Reaction:R-SSC-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Sus scrofa [Reaction:R-SSC-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Sus scrofa [Reaction:R-BTA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Bos taurus [Reaction:R-BTA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Bos taurus [Reaction:R-BTA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Bos taurus [Reaction:R-BTA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Bos taurus [Reaction:R-RNO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Rattus norvegicus [Reaction:R-RNO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Rattus norvegicus [Reaction:R-RNO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Rattus norvegicus [Reaction:R-RNO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Rattus norvegicus [Reaction:R-MMU-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Mus musculus [Reaction:R-MMU-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Mus musculus [Reaction:R-MMU-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Mus musculus [Reaction:R-MMU-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Mus musculus [Reaction:R-HSA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Homo sapiens [Reaction:R-HSA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Homo sapiens [Reaction:R-HSA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Homo sapiens [Reaction:R-HSA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix - Homo sapiens [BlackBoxEvent:R-CEL-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Caenorhabditis elegans [BlackBoxEvent:R-DME-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Drosophila melanogaster [BlackBoxEvent:R-GGA-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Gallus gallus [BlackBoxEvent:R-DRE-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Danio rerio [BlackBoxEvent:R-SSC-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Sus scrofa [BlackBoxEvent:R-BTA-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Bos taurus [BlackBoxEvent:R-CFA-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Canis familiaris [BlackBoxEvent:R-RNO-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Rattus norvegicus [BlackBoxEvent:R-MMU-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Mus musculus [BlackBoxEvent:R-HSA-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) - Homo sapiens [Reaction:R-DDI-5696007] ACSF3 ligates CoA-SH to VLCFA - Dictyostelium discoideum [Reaction:R-DME-5696007] ACSF3 ligates CoA-SH to VLCFA - Drosophila melanogaster [Reaction:R-DRE-5696007] ACSF3 ligates CoA-SH to VLCFA - Danio rerio [Reaction:R-SSC-5696007] ACSF3 ligates CoA-SH to VLCFA - Sus scrofa [Reaction:R-BTA-5696007] ACSF3 ligates CoA-SH to VLCFA - Bos taurus [Reaction:R-RNO-5696007] ACSF3 ligates CoA-SH to VLCFA - Rattus norvegicus [Reaction:R-MMU-5696007] ACSF3 ligates CoA-SH to VLCFA - Mus musculus [Reaction:R-HSA-5696007] ACSF3 ligates CoA-SH to VLCFA - Homo sapiens [Reaction:R-DDI-8875071] ACSS3 ligates CoA to CH3COO- - Dictyostelium discoideum [Reaction:R-DME-8875071] ACSS3 ligates CoA to CH3COO- - Drosophila melanogaster [Reaction:R-GGA-8875071] ACSS3 ligates CoA to CH3COO- - Gallus gallus [Reaction:R-XTR-8875071] ACSS3 ligates CoA to CH3COO- - Xenopus tropicalis [Reaction:R-SSC-8875071] ACSS3 ligates CoA to CH3COO- - Sus scrofa [Reaction:R-BTA-8875071] ACSS3 ligates CoA to CH3COO- - Bos taurus [Reaction:R-CFA-8875071] ACSS3 ligates CoA to CH3COO- - Canis familiaris [Reaction:R-RNO-8875071] ACSS3 ligates CoA to CH3COO- - Rattus norvegicus [Reaction:R-MMU-8875071] ACSS3 ligates CoA to CH3COO- - Mus musculus [Reaction:R-HSA-8875071] ACSS3 ligates CoA to CH3COO- - Homo sapiens [BlackBoxEvent:R-CEL-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Caenorhabditis elegans [BlackBoxEvent:R-DME-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Drosophila melanogaster [BlackBoxEvent:R-GGA-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Gallus gallus [BlackBoxEvent:R-XTR-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Xenopus tropicalis [BlackBoxEvent:R-DRE-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Danio rerio [BlackBoxEvent:R-SSC-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Sus scrofa [BlackBoxEvent:R-BTA-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Bos taurus [BlackBoxEvent:R-CFA-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Canis familiaris [BlackBoxEvent:R-RNO-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Rattus norvegicus [BlackBoxEvent:R-MMU-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Mus musculus [Reaction:R-DME-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Drosophila melanogaster [Reaction:R-GGA-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Gallus gallus [Reaction:R-XTR-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Xenopus tropicalis [Reaction:R-DRE-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Danio rerio [Reaction:R-SSC-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Sus scrofa [Reaction:R-BTA-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Bos taurus [Reaction:R-CFA-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Canis familiaris [Reaction:R-RNO-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Rattus norvegicus [Reaction:R-MMU-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Mus musculus [BlackBoxEvent:R-HSA-9915448] POLRMT polymerizes R-loop RNA - Homo sapiens [Reaction:R-HSA-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork - Homo sapiens [BlackBoxEvent:R-HSA-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication - Homo sapiens [Reaction:R-HSA-9914903] LIG3 (Ligase III) ligates nascent mitochondrial DNA strands - Homo sapiens [FailedReaction:R-HSA-9909466] MCCC mutants don't synthesize beta-methylglutaconyl-CoA - Homo sapiens [FailedReaction:R-HSA-9955543] CPS1 variants don't synthesize carbamoyl phosphate - Homo sapiens [FailedReaction:R-HSA-9955543] CPS1 variants don't synthesize carbamoyl phosphate - Homo sapiens [Reaction:R-SCE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Saccharomyces cerevisiae [Reaction:R-SCE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Saccharomyces cerevisiae [Reaction:R-SCE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Saccharomyces cerevisiae [Reaction:R-SCE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Saccharomyces cerevisiae [Reaction:R-SCE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Saccharomyces cerevisiae [Reaction:R-SCE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Saccharomyces cerevisiae [Reaction:R-SPO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Schizosaccharomyces pombe [Reaction:R-SPO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Schizosaccharomyces pombe [Reaction:R-SPO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Schizosaccharomyces pombe [Reaction:R-SPO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Schizosaccharomyces pombe [Reaction:R-SPO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Schizosaccharomyces pombe [Reaction:R-SPO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Schizosaccharomyces pombe [Reaction:R-DDI-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Dictyostelium discoideum [Reaction:R-DDI-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Dictyostelium discoideum [Reaction:R-DDI-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Dictyostelium discoideum [Reaction:R-DDI-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Dictyostelium discoideum [Reaction:R-DDI-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Dictyostelium discoideum [Reaction:R-DDI-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Dictyostelium discoideum [Reaction:R-CEL-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Caenorhabditis elegans [Reaction:R-CEL-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Caenorhabditis elegans [Reaction:R-CEL-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Caenorhabditis elegans [Reaction:R-CEL-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Caenorhabditis elegans [Reaction:R-CEL-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Caenorhabditis elegans [Reaction:R-CEL-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Caenorhabditis elegans [Reaction:R-DME-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Drosophila melanogaster [Reaction:R-DME-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Drosophila melanogaster [Reaction:R-DME-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Drosophila melanogaster [Reaction:R-DME-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Drosophila melanogaster [Reaction:R-DME-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Drosophila melanogaster [Reaction:R-DME-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Drosophila melanogaster [Reaction:R-GGA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Gallus gallus [Reaction:R-GGA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Gallus gallus [Reaction:R-GGA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Gallus gallus [Reaction:R-GGA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Gallus gallus [Reaction:R-GGA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Gallus gallus [Reaction:R-GGA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Gallus gallus [Reaction:R-XTR-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Xenopus tropicalis [Reaction:R-XTR-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Xenopus tropicalis [Reaction:R-XTR-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Xenopus tropicalis [Reaction:R-XTR-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Xenopus tropicalis [Reaction:R-XTR-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Xenopus tropicalis [Reaction:R-XTR-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Xenopus tropicalis [Reaction:R-DRE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Danio rerio [Reaction:R-DRE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Danio rerio [Reaction:R-DRE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Danio rerio [Reaction:R-DRE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Danio rerio [Reaction:R-DRE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Danio rerio [Reaction:R-DRE-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Danio rerio [Reaction:R-SSC-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Sus scrofa [Reaction:R-SSC-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Sus scrofa [Reaction:R-SSC-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Sus scrofa [Reaction:R-SSC-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Sus scrofa [Reaction:R-SSC-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Sus scrofa [Reaction:R-SSC-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Sus scrofa [Reaction:R-BTA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Bos taurus [Reaction:R-BTA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Bos taurus [Reaction:R-BTA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Bos taurus [Reaction:R-BTA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Bos taurus [Reaction:R-BTA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Bos taurus [Reaction:R-BTA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Bos taurus [Reaction:R-CFA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Canis familiaris [Reaction:R-CFA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Canis familiaris [Reaction:R-CFA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Canis familiaris [Reaction:R-CFA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Canis familiaris [Reaction:R-CFA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Canis familiaris [Reaction:R-CFA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Canis familiaris [Reaction:R-RNO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Rattus norvegicus [Reaction:R-RNO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Rattus norvegicus [Reaction:R-RNO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Rattus norvegicus [Reaction:R-RNO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Rattus norvegicus [Reaction:R-RNO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Rattus norvegicus [Reaction:R-RNO-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Rattus norvegicus [Reaction:R-MMU-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Mus musculus [Reaction:R-MMU-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Mus musculus [Reaction:R-MMU-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Mus musculus [Reaction:R-MMU-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Mus musculus [Reaction:R-MMU-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Mus musculus [Reaction:R-MMU-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Mus musculus [Reaction:R-HSA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Homo sapiens [Reaction:R-HSA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Homo sapiens [Reaction:R-HSA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Homo sapiens [Reaction:R-HSA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Homo sapiens [Reaction:R-HSA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Homo sapiens [Reaction:R-HSA-200682] Mitochondrial FPGS-1 transforms THF to THFPG - Homo sapiens [Reaction:R-GGA-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate - Gallus gallus [Reaction:R-XTR-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate - Xenopus tropicalis [Reaction:R-DRE-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate - Danio rerio [Reaction:R-SSC-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate - Sus scrofa [Reaction:R-BTA-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate - Bos taurus [Reaction:R-CFA-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate - Canis familiaris [Reaction:R-RNO-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate - Rattus norvegicus [Reaction:R-MMU-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate - Mus musculus [Reaction:R-HSA-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate - Homo sapiens [Reaction:R-GGA-159567] ACSM2B-like proteins transform ST to ST-CoA - Gallus gallus [Reaction:R-XTR-159567] ACSM2B-like proteins transform ST to ST-CoA - Xenopus tropicalis [Reaction:R-DRE-159567] ACSM2B-like proteins transform ST to ST-CoA - Danio rerio [Reaction:R-SSC-159567] ACSM2B-like proteins transform ST to ST-CoA - Sus scrofa [Reaction:R-BTA-159567] ACSM2B-like proteins transform ST to ST-CoA - Bos taurus [Reaction:R-CFA-159567] ACSM2B-like proteins transform ST to ST-CoA - Canis familiaris [Reaction:R-RNO-159567] ACSM2B-like proteins transform ST to ST-CoA - Rattus norvegicus [Reaction:R-MMU-159567] ACSM2B-like proteins transform ST to ST-CoA - Mus musculus [Reaction:R-HSA-159567] ACSM2B-like proteins transform ST to ST-CoA - Homo sapiens [Reaction:R-GGA-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate - Gallus gallus [Reaction:R-XTR-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate - Xenopus tropicalis [Reaction:R-DRE-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate - Danio rerio [Reaction:R-SSC-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate - Sus scrofa [Reaction:R-BTA-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate - Bos taurus [Reaction:R-CFA-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate - Canis familiaris [Reaction:R-RNO-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate - Rattus norvegicus [Reaction:R-MMU-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate - Mus musculus [Reaction:R-HSA-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate - Homo sapiens [Reaction:R-GGA-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs - Gallus gallus [Reaction:R-XTR-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs - Xenopus tropicalis [Reaction:R-DRE-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs - Danio rerio [Reaction:R-SSC-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs - Sus scrofa [Reaction:R-BTA-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs - Bos taurus [Reaction:R-CFA-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs - Canis familiaris [Reaction:R-RNO-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs - Rattus norvegicus [Reaction:R-HSA-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs - Homo sapiens [Reaction:R-MMU-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs - Mus musculus [Reaction:R-PFA-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Plasmodium falciparum [Reaction:R-SCE-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Saccharomyces cerevisiae [Reaction:R-SPO-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Schizosaccharomyces pombe [Reaction:R-DDI-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Dictyostelium discoideum [Reaction:R-CEL-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Caenorhabditis elegans [Reaction:R-DME-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Drosophila melanogaster [Reaction:R-XTR-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Xenopus tropicalis [Reaction:R-DRE-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Danio rerio [Reaction:R-SSC-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Sus scrofa [Reaction:R-BTA-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Bos taurus [Reaction:R-CFA-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Canis familiaris [Reaction:R-HSA-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Homo sapiens [Reaction:R-MMU-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) - Mus musculus [Reaction:R-PFA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Plasmodium falciparum [Reaction:R-SCE-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Saccharomyces cerevisiae [Reaction:R-DDI-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Dictyostelium discoideum [Reaction:R-CEL-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Caenorhabditis elegans [Reaction:R-DME-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Drosophila melanogaster [Reaction:R-GGA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Gallus gallus [Reaction:R-XTR-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Xenopus tropicalis [Reaction:R-DRE-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Danio rerio [Reaction:R-SSC-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Sus scrofa [Reaction:R-BTA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Bos taurus [Reaction:R-CFA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Canis familiaris [Reaction:R-RNO-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Rattus norvegicus [Reaction:R-HSA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Homo sapiens [Reaction:R-MMU-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs - Mus musculus [Reaction:R-DDI-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Dictyostelium discoideum [Reaction:R-DME-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Drosophila melanogaster [Reaction:R-GGA-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Gallus gallus [Reaction:R-XTR-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Xenopus tropicalis [Reaction:R-DRE-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Danio rerio [Reaction:R-SSC-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Sus scrofa [Reaction:R-BTA-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Bos taurus [Reaction:R-CFA-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Canis familiaris [Reaction:R-RNO-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Rattus norvegicus [Reaction:R-HSA-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Homo sapiens [Reaction:R-MMU-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] - Mus musculus [Reaction:R-DDI-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Dictyostelium discoideum [Reaction:R-GGA-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Gallus gallus [Reaction:R-XTR-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Xenopus tropicalis [Reaction:R-DRE-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Danio rerio [Reaction:R-SSC-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Sus scrofa [Reaction:R-BTA-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Bos taurus [Reaction:R-CFA-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Canis familiaris [Reaction:R-RNO-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Rattus norvegicus [Reaction:R-HSA-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Homo sapiens [Reaction:R-MMU-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) - Mus musculus [Reaction:R-SCE-1252253] TIM23 PAM complex translocates proteins from the mitochondrial intermembrane space to the mitochondrial matrix - Saccharomyces cerevisiae [Reaction:R-HSA-1299475] TIMM23 PAM translocates proteins from the mitochondrial intermembrane space to the mitochondrial matrix - Homo sapiens [Reaction:R-PFA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Plasmodium falciparum [Reaction:R-SCE-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Saccharomyces cerevisiae [Reaction:R-SPO-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Schizosaccharomyces pombe [Reaction:R-DDI-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Dictyostelium discoideum [Reaction:R-CEL-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Caenorhabditis elegans [Reaction:R-DME-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Drosophila melanogaster [Reaction:R-GGA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Gallus gallus [Reaction:R-XTR-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Xenopus tropicalis [Reaction:R-DRE-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Danio rerio [Reaction:R-SSC-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Sus scrofa [Reaction:R-BTA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Bos taurus [Reaction:R-CFA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Canis familiaris [Reaction:R-MMU-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Mus musculus [Reaction:R-HSA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Homo sapiens [Reaction:R-RNO-6806967] CARKD dehydrates S-NAD(P)HX to NADPH - Rattus norvegicus [Reaction:R-SCE-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Saccharomyces cerevisiae [Reaction:R-SPO-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Schizosaccharomyces pombe [Reaction:R-DDI-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Dictyostelium discoideum [Reaction:R-CEL-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Caenorhabditis elegans [Reaction:R-DME-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Drosophila melanogaster [Reaction:R-GGA-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Gallus gallus [Reaction:R-DRE-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Danio rerio [Reaction:R-SSC-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Sus scrofa [Reaction:R-BTA-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Bos taurus [Reaction:R-CFA-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Canis familiaris [Reaction:R-MMU-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Mus musculus [Reaction:R-HSA-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Homo sapiens [Reaction:R-RNO-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD - Rattus norvegicus [Reaction:R-PFA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Plasmodium falciparum [Reaction:R-CEL-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Caenorhabditis elegans [Reaction:R-DME-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Drosophila melanogaster [Reaction:R-GGA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Gallus gallus [Reaction:R-XTR-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Xenopus tropicalis [Reaction:R-SSC-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Sus scrofa [Reaction:R-BTA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Bos taurus [Reaction:R-CFA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Canis familiaris [Reaction:R-MMU-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Mus musculus [Reaction:R-HSA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Homo sapiens [Reaction:R-RNO-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ - Rattus norvegicus [Reaction:R-CEL-5696004] ACSF2 ligates CoA-SH to MCFA - Caenorhabditis elegans [Reaction:R-DME-5696004] ACSF2 ligates CoA-SH to MCFA - Drosophila melanogaster [Reaction:R-GGA-5696004] ACSF2 ligates CoA-SH to MCFA - Gallus gallus [Reaction:R-XTR-5696004] ACSF2 ligates CoA-SH to MCFA - Xenopus tropicalis [Reaction:R-DRE-5696004] ACSF2 ligates CoA-SH to MCFA - Danio rerio [Reaction:R-SSC-5696004] ACSF2 ligates CoA-SH to MCFA - Sus scrofa [Reaction:R-BTA-5696004] ACSF2 ligates CoA-SH to MCFA - Bos taurus [Reaction:R-RNO-5696004] ACSF2 ligates CoA-SH to MCFA - Rattus norvegicus [Reaction:R-MMU-5696004] ACSF2 ligates CoA-SH to MCFA - Mus musculus [Reaction:R-HSA-5696004] ACSF2 ligates CoA-SH to MCFA - Homo sapiens [Reaction:R-CFA-5696004] ACSF2 ligates CoA-SH to MCFA - Canis familiaris [Reaction:R-DDI-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Dictyostelium discoideum [Reaction:R-CEL-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Caenorhabditis elegans [Reaction:R-DME-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Drosophila melanogaster [Reaction:R-GGA-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Gallus gallus [Reaction:R-XTR-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Xenopus tropicalis [Reaction:R-SSC-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Sus scrofa [Reaction:R-BTA-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Bos taurus [Reaction:R-CFA-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Canis familiaris [Reaction:R-RNO-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Rattus norvegicus [Reaction:R-MMU-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Mus musculus [Reaction:R-HSA-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Homo sapiens [Reaction:R-DRE-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) - Danio rerio [Reaction:R-CEL-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Caenorhabditis elegans [Reaction:R-DME-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Drosophila melanogaster [Reaction:R-SCE-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Saccharomyces cerevisiae [Reaction:R-SPO-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Schizosaccharomyces pombe [Reaction:R-RNO-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Rattus norvegicus [Reaction:R-GGA-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Gallus gallus [Reaction:R-XTR-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Xenopus tropicalis [Reaction:R-SSC-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Sus scrofa [Reaction:R-BTA-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Bos taurus [Reaction:R-CFA-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Canis familiaris [Reaction:R-MMU-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Mus musculus [Reaction:R-HSA-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] - Homo sapiens [Reaction:R-SPO-203946] PDK isozymes phosphorylate PDHC subunit E1 - Schizosaccharomyces pombe [Reaction:R-SPO-203946] PDK isozymes phosphorylate PDHC subunit E1 - Schizosaccharomyces pombe [Reaction:R-GGA-203946] PDK isozymes phosphorylate PDHC subunit E1 - Gallus gallus [Reaction:R-GGA-203946] PDK isozymes phosphorylate PDHC subunit E1 - Gallus gallus [Reaction:R-CEL-203946] PDK isozymes phosphorylate PDHC subunit E1 - Caenorhabditis elegans [Reaction:R-CEL-203946] PDK isozymes phosphorylate PDHC subunit E1 - Caenorhabditis elegans [Reaction:R-DME-203946] PDK isozymes phosphorylate PDHC subunit E1 - Drosophila melanogaster [Reaction:R-DME-203946] PDK isozymes phosphorylate PDHC subunit E1 - Drosophila melanogaster [Reaction:R-XTR-203946] PDK isozymes phosphorylate PDHC subunit E1 - Xenopus tropicalis [Reaction:R-XTR-203946] PDK isozymes phosphorylate PDHC subunit E1 - Xenopus tropicalis [Reaction:R-BTA-203946] PDK isozymes phosphorylate PDHC subunit E1 - Bos taurus [Reaction:R-BTA-203946] PDK isozymes phosphorylate PDHC subunit E1 - Bos taurus [Reaction:R-CFA-203946] PDK isozymes phosphorylate PDHC subunit E1 - Canis familiaris [Reaction:R-CFA-203946] PDK isozymes phosphorylate PDHC subunit E1 - Canis familiaris [Reaction:R-RNO-203946] PDK isozymes phosphorylate PDHC subunit E1 - Rattus norvegicus [Reaction:R-RNO-203946] PDK isozymes phosphorylate PDHC subunit E1 - Rattus norvegicus [Reaction:R-MMU-203946] PDK isozymes phosphorylate PDHC subunit E1 - Mus musculus [Reaction:R-MMU-203946] PDK isozymes phosphorylate PDHC subunit E1 - Mus musculus [Reaction:R-SSC-203946] PDK isozymes phosphorylate PDHC subunit E1 - Sus scrofa [Reaction:R-SSC-203946] PDK isozymes phosphorylate PDHC subunit E1 - Sus scrofa [Reaction:R-HSA-203946] PDK isozymes phosphorylate PDHC subunit E1 - Homo sapiens [Reaction:R-HSA-203946] PDK isozymes phosphorylate PDHC subunit E1 - Homo sapiens [Reaction:R-DRE-203946] PDK isozymes phosphorylate PDHC subunit E1 - Danio rerio [Reaction:R-DRE-203946] PDK isozymes phosphorylate PDHC subunit E1 - Danio rerio [Reaction:R-HSA-8875013] ACSM3,ACSM6 ligate CoA to BUT - Homo sapiens [Reaction:R-MMU-8875039] Acsm3 ligates CoA to BUT - Mus musculus [Reaction:R-HSA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Homo sapiens [Reaction:R-HSA-5693148] BCKDK phosphorylates BCKDH - Homo sapiens [Reaction:R-HSA-5693148] BCKDK phosphorylates BCKDH - Homo sapiens [Reaction:R-MMU-5693148] BCKDK phosphorylates BCKDH - Mus musculus [Reaction:R-MMU-5693148] BCKDK phosphorylates BCKDH - Mus musculus [Reaction:R-RNO-5693148] BCKDK phosphorylates BCKDH - Rattus norvegicus [Reaction:R-RNO-5693148] BCKDK phosphorylates BCKDH - Rattus norvegicus [Reaction:R-CFA-5693148] BCKDK phosphorylates BCKDH - Canis familiaris [Reaction:R-CFA-5693148] BCKDK phosphorylates BCKDH - Canis familiaris [Reaction:R-BTA-5693148] BCKDK phosphorylates BCKDH - Bos taurus [Reaction:R-BTA-5693148] BCKDK phosphorylates BCKDH - Bos taurus [Reaction:R-SSC-5693148] BCKDK phosphorylates BCKDH - Sus scrofa [Reaction:R-SSC-5693148] BCKDK phosphorylates BCKDH - Sus scrofa [Reaction:R-DRE-5693148] BCKDK phosphorylates BCKDH - Danio rerio [Reaction:R-DRE-5693148] BCKDK phosphorylates BCKDH - Danio rerio [Reaction:R-XTR-5693148] BCKDK phosphorylates BCKDH - Xenopus tropicalis [Reaction:R-XTR-5693148] BCKDK phosphorylates BCKDH - Xenopus tropicalis [Reaction:R-GGA-5693148] BCKDK phosphorylates BCKDH - Gallus gallus [Reaction:R-GGA-5693148] BCKDK phosphorylates BCKDH - Gallus gallus [Reaction:R-MMU-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Mus musculus [Reaction:R-RNO-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Rattus norvegicus [Reaction:R-CFA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Canis familiaris [Reaction:R-BTA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Bos taurus [Reaction:R-DRE-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Danio rerio [Reaction:R-XTR-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Xenopus tropicalis [Reaction:R-GGA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Gallus gallus [Reaction:R-CEL-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Caenorhabditis elegans [Reaction:R-DDI-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate - Dictyostelium discoideum [Reaction:R-GGA-353154] pyruvate + CO2 + ATP => oxaloacetate + ADP + orthophosphate - Gallus gallus [Reaction:R-HSA-6786881] TRNT1 polymerizes CCA at the 3' end of pre-tRNA - Homo sapiens [Reaction:R-HSA-380216] glutamate + tRNA(Glu) + ATP => Glu-tRNA(Glu) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380222] tryptophan + tRNA(Trp) + ATP => Trp-tRNA(Trp) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380158] cysteine + tRNA(Cys) + ATP => Cys-tRNA(Cys) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380157] methionine + tRNA(Met) + ATP => Met-tRNA(Met) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380176] isoleucine + tRNA(Ile) + ATP => Ile-tRNA(Ile) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380240] glycine + tRNA(Gly) + ATP => Gly-tRNA(Gly) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380241] glutamine + tRNA(Glu) + ATP => Glu-tRNA(Glu) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380177] alanine + tRNA(Ala) + ATP => Ala-tRNA(Ala) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380234] histidine + tRNA(His) + ATP => His-tRNA(His) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380203] phenylalanine + tRNA(Phe) + ATP => Phe-tRNA(Phe) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380200] leucine + tRNA(Leu) + ATP => Leu-tRNA(Leu) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380201] threonine + tRNA(Thr) + ATP => Thr-tRNA(Thr) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380233] lysine + tRNA(Lys) + ATP => Lys-tRNA(Lys) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380239] serine + tRNA(Ser) + ATP => Ser-tRNA(Ser) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380227] asparagine + tRNA(Asn) + ATP => Asn-tRNA(Asn) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380224] arginine + tRNA(Arg) + ATP => Arg-tRNA(Arg) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380198] proline + tRNA(Pro) + ATP => Pro-tRNA(Pro) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380170] tyrosine + tRNA(Tyr) + ATP => Tyr-tRNA(Tyr) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380199] valine + tRNA(Val) + ATP => Val-tRNA(Val) + AMP + pyrophosphate - Homo sapiens [Reaction:R-HSA-380229] aspartate + tRNA(Asp) + ATP => Asp-tRNA(Asp) + AMP + pyrophosphate - Homo sapiens [BlackBoxEvent:R-SCE-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Saccharomyces cerevisiae [BlackBoxEvent:R-SPO-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Schizosaccharomyces pombe [BlackBoxEvent:R-DDI-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Dictyostelium discoideum [BlackBoxEvent:R-CEL-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Caenorhabditis elegans [BlackBoxEvent:R-DME-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Drosophila melanogaster [BlackBoxEvent:R-GGA-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Gallus gallus [BlackBoxEvent:R-XTR-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Xenopus tropicalis [BlackBoxEvent:R-DRE-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Danio rerio [BlackBoxEvent:R-SSC-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Sus scrofa [BlackBoxEvent:R-BTA-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Bos taurus [BlackBoxEvent:R-CFA-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Canis familiaris [BlackBoxEvent:R-RNO-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Rattus norvegicus [BlackBoxEvent:R-MMU-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Mus musculus [BlackBoxEvent:R-HSA-9839113] AFG3L2 degrades mitochondrial inner membrane proteins - Homo sapiens [Reaction:R-PFA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Plasmodium falciparum [Reaction:R-SCE-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Saccharomyces cerevisiae [Reaction:R-SPO-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Schizosaccharomyces pombe [Reaction:R-DDI-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Dictyostelium discoideum [Reaction:R-CEL-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Caenorhabditis elegans [Reaction:R-DME-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Drosophila melanogaster [Reaction:R-GGA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Gallus gallus [Reaction:R-XTR-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Xenopus tropicalis [Reaction:R-DRE-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Danio rerio [Reaction:R-SSC-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Sus scrofa [Reaction:R-BTA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Bos taurus [Reaction:R-CFA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Canis familiaris [Reaction:R-RNO-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Rattus norvegicus [Reaction:R-MMU-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Mus musculus [Reaction:R-HSA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF - Homo sapiens [Reaction:R-SCE-382560] ABC7, mABC1 and mABC2 mediate heme transport - Saccharomyces cerevisiae [Reaction:R-SPO-382560] ABC7, mABC1 and mABC2 mediate heme transport - Schizosaccharomyces pombe [Reaction:R-DDI-382560] ABC7, mABC1 and mABC2 mediate heme transport - Dictyostelium discoideum [Reaction:R-CEL-382560] ABC7, mABC1 and mABC2 mediate heme transport - Caenorhabditis elegans [Reaction:R-DME-382560] ABC7, mABC1 and mABC2 mediate heme transport - Drosophila melanogaster [Reaction:R-GGA-382560] ABC7, mABC1 and mABC2 mediate heme transport - Gallus gallus [Reaction:R-XTR-382560] ABC7, mABC1 and mABC2 mediate heme transport - Xenopus tropicalis [Reaction:R-DRE-382560] ABC7, mABC1 and mABC2 mediate heme transport - Danio rerio [Reaction:R-SSC-382560] ABC7, mABC1 and mABC2 mediate heme transport - Sus scrofa [Reaction:R-BTA-382560] ABC7, mABC1 and mABC2 mediate heme transport - Bos taurus [Reaction:R-CFA-382560] ABC7, mABC1 and mABC2 mediate heme transport - Canis familiaris [Reaction:R-RNO-382560] ABC7, mABC1 and mABC2 mediate heme transport - Rattus norvegicus [Reaction:R-MMU-382560] ABC7, mABC1 and mABC2 mediate heme transport - Mus musculus [Reaction:R-HSA-382560] ABC7, mABC1 and mABC2 mediate heme transport - Homo sapiens [Reaction:R-SCE-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Saccharomyces cerevisiae [Reaction:R-SCE-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Saccharomyces cerevisiae [Reaction:R-SPO-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Schizosaccharomyces pombe [Reaction:R-SPO-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Schizosaccharomyces pombe [Reaction:R-GGA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Gallus gallus [Reaction:R-GGA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Gallus gallus [Reaction:R-XTR-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Xenopus tropicalis [Reaction:R-XTR-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Xenopus tropicalis [Reaction:R-SSC-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Sus scrofa [Reaction:R-SSC-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Sus scrofa [Reaction:R-BTA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Bos taurus [Reaction:R-BTA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Bos taurus [Reaction:R-CFA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Canis familiaris [Reaction:R-CFA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Canis familiaris [Reaction:R-RNO-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Rattus norvegicus [Reaction:R-RNO-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Rattus norvegicus [Reaction:R-MMU-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Mus musculus [Reaction:R-MMU-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Mus musculus [Reaction:R-HSA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Homo sapiens [Reaction:R-HSA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] - Homo sapiens
created	[InstanceEdit:113517] Schmidt, EE, 2004-06-09 05:19:12
crossReference	[DatabaseIdentifier:29359] COMPOUND:C00002
dbId	113593
deleted	[Deleted:9655303] Deletion of instance: 8938081
displayName	ATP [mitochondrial matrix]
inDisease	false
maxDepth	1
modified	[InstanceEdit:9655330] D'Eustachio, Peter, 2019-07-24
name	ATP Adenosine 5'-triphosphate ATP(4-)
negativelyRegulates	[NegativeRegulation:R-HSA-9012284] Negative regulation by 'ATP [mitochondrial matrix]' [NegativeRegulation:9853611] Negative regulation by 'ATP [mitochondrial matrix]'
positivelyRegulates	[PositiveRegulation:9987148] Positive regulation by 'ATP [mitochondrial matrix]' [PositiveRegulation:9853679] Positive regulation by 'ATP [mitochondrial matrix]'
producedByEvent	[Reaction:R-PFA-70997] SUCLG1/A2 cleaves succinyl-CoA - Plasmodium falciparum [Reaction:R-XTR-70997] SUCLG1/A2 cleaves succinyl-CoA - Xenopus tropicalis [Reaction:R-SSC-70997] SUCLG1/A2 cleaves succinyl-CoA - Sus scrofa [Reaction:R-BTA-70997] SUCLG1/A2 cleaves succinyl-CoA - Bos taurus [Reaction:R-DDI-70997] SUCLG1/A2 cleaves succinyl-CoA - Dictyostelium discoideum [Reaction:R-SCE-70997] SUCLG1/A2 cleaves succinyl-CoA - Saccharomyces cerevisiae [Reaction:R-SPO-70997] SUCLG1/A2 cleaves succinyl-CoA - Schizosaccharomyces pombe [Reaction:R-CEL-70997] SUCLG1/A2 cleaves succinyl-CoA - Caenorhabditis elegans [Reaction:R-GGA-70997] SUCLG1/A2 cleaves succinyl-CoA - Gallus gallus [Reaction:R-DME-70997] SUCLG1/A2 cleaves succinyl-CoA - Drosophila melanogaster [Reaction:R-MMU-70997] SUCLG1/A2 cleaves succinyl-CoA - Mus musculus [Reaction:R-HSA-70997] SUCLG1/A2 cleaves succinyl-CoA - Homo sapiens [Reaction:R-RNO-70997] SUCLG1/A2 cleaves succinyl-CoA - Rattus norvegicus [Reaction:R-CFA-70997] SUCLG1/A2 cleaves succinyl-CoA - Canis familiaris [Reaction:R-DRE-70997] SUCLG1/A2 cleaves succinyl-CoA - Danio rerio [Reaction:R-PFA-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Plasmodium falciparum [Reaction:R-SCE-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Saccharomyces cerevisiae [Reaction:R-SPO-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Schizosaccharomyces pombe [Reaction:R-DDI-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Dictyostelium discoideum [Reaction:R-CEL-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Caenorhabditis elegans [Reaction:R-DME-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Drosophila melanogaster [Reaction:R-XTR-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Xenopus tropicalis [Reaction:R-DRE-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Danio rerio [Reaction:R-SSC-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Sus scrofa [Reaction:R-BTA-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Bos taurus [Reaction:R-CFA-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Canis familiaris [Reaction:R-MMU-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Mus musculus [Reaction:R-HSA-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) - Homo sapiens [Reaction:R-CEL-164834] Enzyme-bound ATP is released - Caenorhabditis elegans [Reaction:R-DME-164834] Enzyme-bound ATP is released - Drosophila melanogaster [Reaction:R-GGA-164834] Enzyme-bound ATP is released - Gallus gallus [Reaction:R-DRE-164834] Enzyme-bound ATP is released - Danio rerio [Reaction:R-SSC-164834] Enzyme-bound ATP is released - Sus scrofa [Reaction:R-BTA-164834] Enzyme-bound ATP is released - Bos taurus [Reaction:R-CFA-164834] Enzyme-bound ATP is released - Canis familiaris [Reaction:R-MMU-164834] Enzyme-bound ATP is released - Mus musculus [Reaction:R-HSA-164834] Enzyme-bound ATP is released - Homo sapiens [Reaction:R-RNO-164834] Enzyme-bound ATP is released - Rattus norvegicus [Reaction:R-DDI-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Dictyostelium discoideum [Reaction:R-CEL-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Caenorhabditis elegans [Reaction:R-DME-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Drosophila melanogaster [Reaction:R-GGA-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Gallus gallus [Reaction:R-XTR-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Xenopus tropicalis [Reaction:R-DRE-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Danio rerio [Reaction:R-SSC-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Sus scrofa [Reaction:R-BTA-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Bos taurus [Reaction:R-CFA-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Canis familiaris [Reaction:R-RNO-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Rattus norvegicus [Reaction:R-MMU-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Mus musculus [Reaction:R-HSA-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) - Homo sapiens [Reaction:R-GGA-372977] succinylCoA + ADP + Pi <=> succinate + CoASH + ATP - Gallus gallus [Reaction:R-PFA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Plasmodium falciparum [Reaction:R-SCE-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Saccharomyces cerevisiae [Reaction:R-SPO-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Schizosaccharomyces pombe [Reaction:R-DDI-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Dictyostelium discoideum [Reaction:R-CEL-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Caenorhabditis elegans [Reaction:R-DME-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Drosophila melanogaster [Reaction:R-GGA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Gallus gallus [Reaction:R-XTR-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Xenopus tropicalis [Reaction:R-DRE-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Danio rerio [Reaction:R-SSC-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Sus scrofa [Reaction:R-BTA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Bos taurus [Reaction:R-CFA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Canis familiaris [Reaction:R-RNO-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Rattus norvegicus [Reaction:R-MMU-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Mus musculus [Reaction:R-HSA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF - Homo sapiens
referenceEntity	[ReferenceMolecule:chebi:30616] ATP(4-) [ChEBI:30616]
referenceType	ReferenceMolecule
schemaClass	SimpleEntity
stId	R-ALL-113593
updateTrackers	[UpdateTracker:9900714] Update Tracker - [SimpleEntity:113593] ATP [mitochondrial matrix] - v70:[addName, add_removeReferenceEntity]

Referrals

(hasComponent)	[Complex:R-GGA-164835] ATPase:ATP [mitochondrial inner membrane] [Complex:R-CFA-164835] ATPase:ATP [mitochondrial inner membrane] [Complex:R-MMU-164835] ATPase:ATP [mitochondrial inner membrane] [Complex:R-SSC-164835] ATPase:ATP [mitochondrial inner membrane] [Complex:R-BTA-164835] ATPase:ATP [mitochondrial inner membrane] [Complex:R-DME-164835] ATPase:ATP [mitochondrial inner membrane] [Complex:R-DRE-164835] ATPase:ATP [mitochondrial inner membrane] [Complex:R-CEL-164835] ATPase:ATP [mitochondrial inner membrane] [Complex:R-HSA-164835] ATPase:ATP [mitochondrial inner membrane] [Complex:R-RNO-164835] ATPase:ATP [mitochondrial inner membrane]
(input)	[Reaction:R-GGA-353154] pyruvate + CO2 + ATP => oxaloacetate + ADP + orthophosphate [Reaction:R-GGA-373134] succinate + CoASH + ATP <=> succinylCoA + ADP + Pi [Reaction:R-CEL-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-DME-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-GGA-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-XTR-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-DRE-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-SSC-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-BTA-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-CFA-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-RNO-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-MMU-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-HSA-9611218] YRDC synthesizes threonylcarbamoyladenylate [Reaction:R-HSA-6786881] TRNT1 polymerizes CCA at the 3' end of pre-tRNA [Reaction:R-HSA-9836927] SUPV3L1 unwinds double-stranded mitochondiral RNA [Reaction:R-HSA-9936998] MTPAP polyadenylates mitochondrial mRNA [Reaction:R-HSA-380216] glutamate + tRNA(Glu) + ATP => Glu-tRNA(Glu) + AMP + pyrophosphate [Reaction:R-HSA-380222] tryptophan + tRNA(Trp) + ATP => Trp-tRNA(Trp) + AMP + pyrophosphate [Reaction:R-HSA-380158] cysteine + tRNA(Cys) + ATP => Cys-tRNA(Cys) + AMP + pyrophosphate [Reaction:R-HSA-380157] methionine + tRNA(Met) + ATP => Met-tRNA(Met) + AMP + pyrophosphate [Reaction:R-HSA-380176] isoleucine + tRNA(Ile) + ATP => Ile-tRNA(Ile) + AMP + pyrophosphate [Reaction:R-HSA-380240] glycine + tRNA(Gly) + ATP => Gly-tRNA(Gly) + AMP + pyrophosphate [Reaction:R-HSA-380241] glutamine + tRNA(Glu) + ATP => Glu-tRNA(Glu) + AMP + pyrophosphate [Reaction:R-HSA-380177] alanine + tRNA(Ala) + ATP => Ala-tRNA(Ala) + AMP + pyrophosphate [Reaction:R-HSA-380234] histidine + tRNA(His) + ATP => His-tRNA(His) + AMP + pyrophosphate [Reaction:R-HSA-380203] phenylalanine + tRNA(Phe) + ATP => Phe-tRNA(Phe) + AMP + pyrophosphate [Reaction:R-HSA-380200] leucine + tRNA(Leu) + ATP => Leu-tRNA(Leu) + AMP + pyrophosphate [Reaction:R-HSA-380201] threonine + tRNA(Thr) + ATP => Thr-tRNA(Thr) + AMP + pyrophosphate [Reaction:R-HSA-380233] lysine + tRNA(Lys) + ATP => Lys-tRNA(Lys) + AMP + pyrophosphate [Reaction:R-HSA-380239] serine + tRNA(Ser) + ATP => Ser-tRNA(Ser) + AMP + pyrophosphate [Reaction:R-HSA-380227] asparagine + tRNA(Asn) + ATP => Asn-tRNA(Asn) + AMP + pyrophosphate [Reaction:R-HSA-380224] arginine + tRNA(Arg) + ATP => Arg-tRNA(Arg) + AMP + pyrophosphate [Reaction:R-HSA-380198] proline + tRNA(Pro) + ATP => Pro-tRNA(Pro) + AMP + pyrophosphate [Reaction:R-HSA-380170] tyrosine + tRNA(Tyr) + ATP => Tyr-tRNA(Tyr) + AMP + pyrophosphate [Reaction:R-HSA-380199] valine + tRNA(Val) + ATP => Val-tRNA(Val) + AMP + pyrophosphate [Reaction:R-HSA-380229] aspartate + tRNA(Asp) + ATP => Asp-tRNA(Asp) + AMP + pyrophosphate [BlackBoxEvent:R-SCE-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-SPO-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-DDI-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-CEL-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-DME-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-GGA-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-XTR-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-DRE-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-SSC-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-BTA-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-CFA-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-RNO-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-MMU-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-HSA-9839113] AFG3L2 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-PFA-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-SCE-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-SPO-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-DDI-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-CEL-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-DME-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-GGA-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-XTR-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-DRE-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-SSC-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-BTA-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-CFA-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-RNO-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-MMU-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-HSA-9839105] AFG3L2 degrades mitochondrial matrix proteins [BlackBoxEvent:R-SCE-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-SPO-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-DDI-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-CEL-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-DME-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-GGA-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-DRE-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-SSC-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-BTA-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-CFA-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-RNO-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-MMU-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-HSA-9838081] LONP1 degrades mitochondrial matrix proteins [BlackBoxEvent:R-CEL-9838289] CLPXP degrades mitochondrial matrix proteins [BlackBoxEvent:R-DME-9838289] CLPXP degrades mitochondrial matrix proteins [BlackBoxEvent:R-XTR-9838289] CLPXP degrades mitochondrial matrix proteins [BlackBoxEvent:R-DRE-9838289] CLPXP degrades mitochondrial matrix proteins [BlackBoxEvent:R-SSC-9838289] CLPXP degrades mitochondrial matrix proteins [BlackBoxEvent:R-BTA-9838289] CLPXP degrades mitochondrial matrix proteins [BlackBoxEvent:R-CFA-9838289] CLPXP degrades mitochondrial matrix proteins [BlackBoxEvent:R-RNO-9838289] CLPXP degrades mitochondrial matrix proteins [BlackBoxEvent:R-MMU-9838289] CLPXP degrades mitochondrial matrix proteins [BlackBoxEvent:R-HSA-9838289] CLPXP degrades mitochondrial matrix proteins [Reaction:R-PFA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-SCE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-SPO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-DDI-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-CEL-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-DME-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-XTR-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-DRE-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-SSC-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-BTA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-RNO-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-MMU-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [Reaction:R-HSA-9838321] PRKACA phosphorylates TFAM in the mitochondrial matrix [BlackBoxEvent:R-CEL-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-DME-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-GGA-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-DRE-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-SSC-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-BTA-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-CFA-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-RNO-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-MMU-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-HSA-9839059] AFG3L2:SPG7 degrades SMDT1 (EMRE) [BlackBoxEvent:R-SCE-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-SPO-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-DDI-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-CEL-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-DME-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-GGA-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-DRE-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-SSC-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-BTA-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-CFA-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-RNO-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-MMU-9838004] LONP1 degrades mitochondrial inner membrane proteins [BlackBoxEvent:R-HSA-9838004] LONP1 degrades mitochondrial inner membrane proteins [Reaction:R-MMU-8875095] Slc27a3 ligates CoA to VLCFA [Reaction:R-HSA-8875077] SLC27A3 ligates CoA-SH to VLCFA [Reaction:R-DDI-5696007] ACSF3 ligates CoA-SH to VLCFA [Reaction:R-DME-5696007] ACSF3 ligates CoA-SH to VLCFA [Reaction:R-DRE-5696007] ACSF3 ligates CoA-SH to VLCFA [Reaction:R-SSC-5696007] ACSF3 ligates CoA-SH to VLCFA [Reaction:R-BTA-5696007] ACSF3 ligates CoA-SH to VLCFA [Reaction:R-RNO-5696007] ACSF3 ligates CoA-SH to VLCFA [Reaction:R-MMU-5696007] ACSF3 ligates CoA-SH to VLCFA [Reaction:R-HSA-5696007] ACSF3 ligates CoA-SH to VLCFA [Reaction:R-DDI-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-DME-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-GGA-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-XTR-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-SSC-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-BTA-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-CFA-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-RNO-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-MMU-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-HSA-8875071] ACSS3 ligates CoA to CH3COO- [Reaction:R-GGA-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA [Reaction:R-XTR-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA [Reaction:R-DRE-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA [Reaction:R-SSC-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA [Reaction:R-BTA-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA [Reaction:R-CFA-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA [Reaction:R-RNO-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA [Reaction:R-MMU-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA [Reaction:R-HSA-9749971] ACSM2B-like proteins transform 2,5-DHBA to 2,5-DHB-CoA [BlackBoxEvent:R-CEL-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [BlackBoxEvent:R-DME-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [BlackBoxEvent:R-GGA-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [BlackBoxEvent:R-XTR-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [BlackBoxEvent:R-DRE-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [BlackBoxEvent:R-SSC-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [BlackBoxEvent:R-BTA-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [BlackBoxEvent:R-CFA-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [BlackBoxEvent:R-RNO-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [BlackBoxEvent:R-MMU-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [Reaction:R-DME-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [Reaction:R-GGA-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [Reaction:R-XTR-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [Reaction:R-DRE-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [Reaction:R-SSC-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [Reaction:R-BTA-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [Reaction:R-CFA-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [Reaction:R-RNO-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [Reaction:R-MMU-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [BlackBoxEvent:R-HSA-9915448] POLRMT polymerizes R-loop RNA [Reaction:R-HSA-9914438] TWNK (PEO1) unwinds double-stranded mitochondrial DNA at the replication fork [BlackBoxEvent:R-HSA-9914409] POLRMT polymerizes RNA primer for mitochondrial L strand replication [Reaction:R-HSA-9914903] LIG3 (Ligase III) ligates nascent mitochondrial DNA strands [FailedReaction:R-HSA-9909466] MCCC mutants don't synthesize beta-methylglutaconyl-CoA [FailedReaction:R-HSA-9912480] BCKDK loss-of-function mutations do not phosphorylate BCKDH [FailedReaction:R-HSA-9955543] CPS1 variants don't synthesize carbamoyl phosphate [Reaction:R-PFA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-SCE-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-SPO-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-DDI-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-GGA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-XTR-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-DRE-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-SSC-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-BTA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-CFA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-RNO-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-MMU-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [Reaction:R-HSA-449911] acetate + CoA + ATP => acetyl-CoA + AMP + pyrophosphate [mitochondrial] [FailedReaction:R-HSA-3322125] Defective MMAB does not transfer adenosyl group from ATP to B12s [Reaction:R-SCE-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-SPO-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-DDI-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-CEL-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-DME-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-GGA-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-XTR-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-DRE-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-SSC-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-BTA-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-CFA-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-RNO-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-MMU-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-HSA-200682] Mitochondrial FPGS-1 transforms THF to THFPG [Reaction:R-PFA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-SCE-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-SPO-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-DDI-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-CEL-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-DME-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-GGA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-XTR-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-DRE-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-SSC-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-BTA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-CFA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-RNO-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-MMU-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-HSA-5696839] MTHFD1L dimer ligates HCOOH to THF to form 10-formyl-THF [Reaction:R-GGA-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate [Reaction:R-XTR-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate [Reaction:R-DRE-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate [Reaction:R-SSC-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate [Reaction:R-BTA-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate [Reaction:R-CFA-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate [Reaction:R-RNO-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate [Reaction:R-MMU-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate [Reaction:R-HSA-159443] benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate [Reaction:R-GGA-159567] ACSM2B-like proteins transform ST to ST-CoA [Reaction:R-XTR-159567] ACSM2B-like proteins transform ST to ST-CoA [Reaction:R-DRE-159567] ACSM2B-like proteins transform ST to ST-CoA [Reaction:R-SSC-159567] ACSM2B-like proteins transform ST to ST-CoA [Reaction:R-BTA-159567] ACSM2B-like proteins transform ST to ST-CoA [Reaction:R-CFA-159567] ACSM2B-like proteins transform ST to ST-CoA [Reaction:R-RNO-159567] ACSM2B-like proteins transform ST to ST-CoA [Reaction:R-MMU-159567] ACSM2B-like proteins transform ST to ST-CoA [Reaction:R-HSA-159567] ACSM2B-like proteins transform ST to ST-CoA [Reaction:R-GGA-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate [Reaction:R-XTR-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate [Reaction:R-DRE-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate [Reaction:R-SSC-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate [Reaction:R-BTA-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate [Reaction:R-CFA-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate [Reaction:R-RNO-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate [Reaction:R-MMU-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate [Reaction:R-HSA-177157] phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate [Reaction:R-XTR-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane [Reaction:R-DRE-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane [Reaction:R-SSC-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane [Reaction:R-BTA-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane [Reaction:R-CFA-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane [Reaction:R-RNO-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane [Reaction:R-MMU-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane [Reaction:R-HSA-5672027] ARL2:GTP:ARL2BP:SLC25A4 dimer exchanges ATP for ADP across the mitochondrial inner membrane [Reaction:R-SCE-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-SPO-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-DDI-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-CEL-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-DME-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-GGA-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-XTR-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-DRE-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-SSC-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-BTA-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-CFA-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-RNO-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-MMU-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-HSA-382560] ABC7, mABC1 and mABC2 mediate heme transport [Reaction:R-GGA-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs [Reaction:R-XTR-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs [Reaction:R-DRE-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs [Reaction:R-SSC-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs [Reaction:R-BTA-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs [Reaction:R-CFA-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs [Reaction:R-RNO-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs [Reaction:R-HSA-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs [Reaction:R-MMU-9605496] NME6 phosphorylates (d)NDPs to (d)NTPs [Reaction:R-PFA-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-SCE-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-SPO-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-DDI-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-CEL-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-DME-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-XTR-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-DRE-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-SSC-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-BTA-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-CFA-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-HSA-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-MMU-482804] (d)NDP + ATP <=> (d)NTP + ADP (NME4) [Reaction:R-PFA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-SCE-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-DDI-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-CEL-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-DME-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-GGA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-XTR-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-DRE-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-SSC-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-BTA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-CFA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-RNO-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-HSA-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-MMU-6788798] AK4 phosphorylates (d)NMPs to (d)NDPs [Reaction:R-DDI-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-DME-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-GGA-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-XTR-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-DRE-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-SSC-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-BTA-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-CFA-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-RNO-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-HSA-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-MMU-109759] deoxycytidine, thymidine, or deoxyuridine + ATP => dCMP, TMP, or dUMP + ADP [TK2] [Reaction:R-DDI-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-GGA-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-XTR-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-DRE-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-SSC-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-BTA-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-CFA-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-RNO-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-HSA-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-MMU-74207] dA, dG, or dI + ATP => dAMP, dGMP, or dIMP + ADP (DGUOK) [Reaction:R-SCE-1252253] TIM23 PAM complex translocates proteins from the mitochondrial intermembrane space to the mitochondrial matrix [Reaction:R-HSA-1299475] TIMM23 PAM translocates proteins from the mitochondrial intermembrane space to the mitochondrial matrix [Reaction:R-PFA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-SCE-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-SPO-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-DDI-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-CEL-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-DME-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-GGA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-XTR-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-DRE-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-SSC-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-BTA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-CFA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-MMU-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-HSA-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-RNO-163215] SLC25A5,6 dimers exchange ATP for ADP across the mitochondrial inner membrane [Reaction:R-PFA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-SCE-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-SPO-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-DDI-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-CEL-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-DME-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-GGA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-XTR-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-DRE-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-SSC-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-BTA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-CFA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-MMU-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-HSA-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-RNO-6806967] CARKD dehydrates S-NAD(P)HX to NADPH [Reaction:R-SCE-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-SPO-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-DDI-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-CEL-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-DME-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-GGA-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-DRE-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-SSC-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-BTA-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-CFA-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-MMU-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-HSA-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-RNO-200474] NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD [Reaction:R-PFA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-CEL-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-DME-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-GGA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-XTR-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-SSC-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-BTA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-CFA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-MMU-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-HSA-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-RNO-8955030] NADK2 dimer phosphorylates NAD+ to NADP+ [Reaction:R-CEL-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-DME-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-GGA-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-XTR-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-DRE-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-SSC-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-BTA-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-RNO-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-MMU-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-HSA-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-CFA-5696004] ACSF2 ligates CoA-SH to MCFA [Reaction:R-DDI-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-CEL-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-DME-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-GGA-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-XTR-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-SSC-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-BTA-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-CFA-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-RNO-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-MMU-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-HSA-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-DRE-70773] beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) [Reaction:R-CEL-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-DME-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-SCE-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-SPO-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-RNO-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-GGA-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-XTR-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-SSC-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-BTA-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-CFA-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-SCE-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-SPO-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-GGA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-XTR-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-SSC-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-BTA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-CFA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-RNO-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-MMU-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-HSA-70555] 2 ATP + NH4+ + HCO3- => 2 ADP + orthophosphate + carbamoyl phosphate [mitochondrial] [Reaction:R-MMU-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-HSA-508040] glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] [Reaction:R-SPO-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-GGA-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-SCE-70501] PC carboxylates PYR to OA [Reaction:R-SPO-70501] PC carboxylates PYR to OA [Reaction:R-CEL-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-CEL-70501] PC carboxylates PYR to OA [Reaction:R-DME-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-DME-70501] PC carboxylates PYR to OA [Reaction:R-XTR-70501] PC carboxylates PYR to OA [Reaction:R-XTR-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-BTA-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-CFA-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-RNO-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-MMU-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-SSC-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-SSC-70501] PC carboxylates PYR to OA [Reaction:R-HSA-70501] PC carboxylates PYR to OA [Reaction:R-HSA-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-DRE-203946] PDK isozymes phosphorylate PDHC subunit E1 [Reaction:R-DRE-70501] PC carboxylates PYR to OA [Reaction:R-HSA-8875013] ACSM3,ACSM6 ligate CoA to BUT [Reaction:R-MMU-8875039] Acsm3 ligates CoA to BUT [Reaction:R-MMU-70501] PC carboxylates PYR to OA [Reaction:R-HSA-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-MMU-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-RNO-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-CFA-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-BTA-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-SSC-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-DRE-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-XTR-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-GGA-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-CEL-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-DDI-3159253] MMAB adenosylates cob(I)alamin [Reaction:R-HSA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-HSA-5693148] BCKDK phosphorylates BCKDH [Reaction:R-MMU-5693148] BCKDK phosphorylates BCKDH [Reaction:R-RNO-5693148] BCKDK phosphorylates BCKDH [Reaction:R-CFA-5693148] BCKDK phosphorylates BCKDH [Reaction:R-BTA-5693148] BCKDK phosphorylates BCKDH [Reaction:R-SSC-5693148] BCKDK phosphorylates BCKDH [Reaction:R-DRE-5693148] BCKDK phosphorylates BCKDH [Reaction:R-XTR-5693148] BCKDK phosphorylates BCKDH [Reaction:R-GGA-5693148] BCKDK phosphorylates BCKDH [Reaction:R-MMU-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-RNO-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-CFA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-BTA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-DRE-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-XTR-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-GGA-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-CEL-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-DDI-71031] propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate [Reaction:R-RNO-70501] PC carboxylates PYR to OA [Reaction:R-CFA-70501] PC carboxylates PYR to OA [Reaction:R-BTA-70501] PC carboxylates PYR to OA
(output)	[Reaction:R-GGA-372977] succinylCoA + ADP + Pi <=> succinate + CoASH + ATP [Reaction:R-PFA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-SCE-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-SPO-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-DDI-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-CEL-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-DME-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-GGA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-XTR-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-DRE-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-SSC-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-BTA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-CFA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-RNO-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-MMU-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-HSA-6801456] MTHFD1L transforms 10-formyl-THF to HCOOH and THF [Reaction:R-PFA-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-SCE-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-SPO-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-DDI-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-CEL-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-DME-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-XTR-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-DRE-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-SSC-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-BTA-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-CFA-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-MMU-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-HSA-482812] (d)NTP + ADP <=> (d)NDP + ATP (NME4) [Reaction:R-CEL-164834] Enzyme-bound ATP is released [Reaction:R-DME-164834] Enzyme-bound ATP is released [Reaction:R-GGA-164834] Enzyme-bound ATP is released [Reaction:R-DRE-164834] Enzyme-bound ATP is released [Reaction:R-SSC-164834] Enzyme-bound ATP is released [Reaction:R-BTA-164834] Enzyme-bound ATP is released [Reaction:R-CFA-164834] Enzyme-bound ATP is released [Reaction:R-MMU-164834] Enzyme-bound ATP is released [Reaction:R-HSA-164834] Enzyme-bound ATP is released [Reaction:R-RNO-164834] Enzyme-bound ATP is released [Reaction:R-DDI-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-CEL-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-DME-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-GGA-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-XTR-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-DRE-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-SSC-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-BTA-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-CFA-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-RNO-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-MMU-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-HSA-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) [Reaction:R-PFA-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-XTR-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-SSC-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-BTA-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-DDI-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-SCE-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-SPO-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-CEL-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-GGA-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-DME-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-MMU-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-HSA-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-RNO-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-CFA-70997] SUCLG1/A2 cleaves succinyl-CoA [Reaction:R-DRE-70997] SUCLG1/A2 cleaves succinyl-CoA
(regulator)	[NegativeRegulation:R-HSA-9012284] Negative regulation by 'ATP [mitochondrial matrix]' [PositiveRegulation:9987148] Positive regulation by 'ATP [mitochondrial matrix]' [PositiveRegulation:9853679] Positive regulation by 'ATP [mitochondrial matrix]' [NegativeRegulation:9853611] Negative regulation by 'ATP [mitochondrial matrix]'
(replacementInstances)	[Deleted:9655303] Deletion of instance: 8938081
(updatedInstance)	[UpdateTracker:9900714] Update Tracker - [SimpleEntity:113593] ATP [mitochondrial matrix] - v70:[addName, add_removeReferenceEntity]

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