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C3b alpha' [extracellular region]
Stable Identifier
R-HSA-166830
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
extracellular region
Synonyms
C3(749-1663)
Icon
Locations in the PathwayBrowser
Expand all
Immune System (Homo sapiens)
Innate Immune System (Homo sapiens)
Complement cascade (Homo sapiens)
Activation of C3 and C5 (Homo sapiens)
Activation of C5 (Homo sapiens)
C5 convertases [plasma membrane] (Homo sapiens)
C3b:Bb:C3b:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
C4b:C2a:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cleavage of C3 by C3 convertases (Homo sapiens)
C3 convertases [plasma membrane] (Homo sapiens)
C4b:C2a:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Formation of classic pathway C5 convertase (Homo sapiens)
C4b:C2a:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Initial triggering of complement (Homo sapiens)
Alternative complement activation (Homo sapiens)
C3(H2O):Factor Bb cleaves C3 to C3b and C3a (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
C3b binds to cell surface (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Factor B binds to surface-associated C3b (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:CFB [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Factor D cleaves C3b-bound Factor B (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:CFB [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Formation of alternative pathway C5 convertase (Homo sapiens)
C3b:Bb:C3b:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Properdin stabilizes C3b:Bb bound to cell surfaces (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Regulation of Complement cascade (Homo sapiens)
C3 convertases spontaneously dissociate (Homo sapiens)
C3 convertases [plasma membrane] (Homo sapiens)
C4b:C2a:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CD46 binds C3b (Homo sapiens)
CD46:Cell surface:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CD55 (DAF) binds C3bBb, C4bC2a (Homo sapiens)
C4bC2a, C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CD55:C3 convertase complexes [plasma membrane] (Homo sapiens)
CD55:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CD55 (DAF) promotes C3bBb/C4bC2a dissociation (Homo sapiens)
CD55:C3 convertase complexes [plasma membrane] (Homo sapiens)
CD55:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CD55:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CFHR dimers bind C3b (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:C3b:CFHR dimers [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CR1 binds C3bBb/C4bC2a (Homo sapiens)
C4bC2a, C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CR1:C3bBb, C4bC2a complexes [plasma membrane] (Homo sapiens)
CR1:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Complement factor I binds to MCP, CR1:C4b, C3b (Homo sapiens)
CD46, CR1:C4b:C3b complexes [plasma membrane] (Homo sapiens)
CD46:Cell surface:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CR1:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CFI:CD46, CR1:C4b, C3b complexes [plasma membrane] (Homo sapiens)
CD46, CR1:C4b:C3b complexes [plasma membrane] (Homo sapiens)
CD46:Cell surface:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CR1:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Complement factor I binds to extracellular Factor H:C3b (Homo sapiens)
CFH:C3b [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CFI:CFH:C3b [extracellular region] (Homo sapiens)
CFH:C3b [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Complement factor I binds to membrane-associated Factor H:C3b (Homo sapiens)
CFI:CFH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Displacement of C2a/Bb by CR1 (Homo sapiens)
CR1:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CR1:C3bBb, C4bC2a complexes [plasma membrane] (Homo sapiens)
CR1:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Factor H binds to C3b (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CFH:C3b [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Factor H binds to C3bBb (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:CFH, CFHR3:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Factor H binds to membrane-associated C3b (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Factor H displaces Bb (Homo sapiens)
Cell surface:CFH, CFHR3:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Factor I inactivates Factor H-boundC3b (Homo sapiens)
CFI:CFH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Factor I inactivates MCP/CR1-bound C4b/C3b (Homo sapiens)
CFI:CD46, CR1:C4b, C3b complexes [plasma membrane] (Homo sapiens)
CD46, CR1:C4b:C3b complexes [plasma membrane] (Homo sapiens)
CD46:Cell surface:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
CR1:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
Factor I inactivates plasma Factor H-bound C3b (Homo sapiens)
CFI:CFH:C3b [extracellular region] (Homo sapiens)
CFH:C3b [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3b alpha' [extracellular region] (Homo sapiens)
External Reference Information
External Reference
UniProt:P01024 C3
Gene Names
C3, CPAMD1
Chain
signal peptide:1-22, chain:23-1663, chain:23-667, chain:569-667, chain:672-1663, chain:672-748, chain:672-747, chain:749-1663, chain:749-954, chain:955-1303, chain:955-1001, chain:1002-1303, peptide:1304-1320, chain:1321-1663
Reference Genes
BioGPS Gene:718 C3
COSMIC (genes):C3 C3
CTD Gene:718 C3
dbSNP Gene:718 C3
ENSEMBL:ENSG00000125730 C3
ENSEMBL_homo_sapiens_GENE:ENSG00000125730 C3
HGNC:1318 C3
KEGG Gene (Homo sapiens):718 C3
Monarch:718 C3
NCBI Gene:718 C3
OMIM:120700 C3
Reference Transcript
RefSeq:NM_000064.3 C3
Other Identifiers
0006650731
11715393_a_at
16867784
1C3D
1GHQ
1W2S
20432
217767_at
2A73
2A74
2I07
2ICE
2ICF
2NOJ
2QKI
2WII
2WIN
2WY7
2WY8
2XQW
2XWB
2XWJ
3563
3848040
3848041
3848043
3848044
3848045
3848047
3848049
3848051
3848052
3848055
3848057
3848059
3848061
3848065
3848066
3848068
3848072
3848074
3848075
3848076
3848077
3848078
3848080
3848082
3848083
3848084
3848085
3848088
3848089
3848090
3848092
3848093
3848095
3848096
3848097
3848098
3848099
3848100
3848101
3848102
3848104
3848105
3848106
3848107
3848108
3D5R
3D5S
3G6J
3L3O
3L5N
3NMS
3OED
3OHX
3OXU
3RJ3
3T4A
4209
4HW5
4HWJ
4I6O
4M76
4ONT
4ZH1
5FO7
5FO8
5FO9
5FOA
5FOB
5M6W
5NBQ
5O32
5O35
6EHG
718
8033257
A_23_P101407
A_33_P3347869
AAA85332
AAI50180
AAI50201
AAR89906
ACJ13656
AY513239
BC150179
BC150200
C3
C3-201
CAB004209
CCDS32883
CH471139
EAW69071
ENSG00000125730
ENSP00000245907
ENST00000245907
EntrezGene:718
EU794602
g4557384_3p_at
GE61301
GO:0001798
GO:0001934
GO:0001970
GO:0002376
GO:0003674
GO:0004252
GO:0004866
GO:0005102
GO:0005515
GO:0005575
GO:0005576
GO:0005615
GO:0005622
GO:0005623
GO:0005737
GO:0005764
GO:0005773
GO:0005783
GO:0005788
GO:0005886
GO:0006464
GO:0006508
GO:0006629
GO:0006631
GO:0006810
GO:0006911
GO:0006950
GO:0006954
GO:0006955
GO:0006956
GO:0006957
GO:0006958
GO:0007165
GO:0007186
GO:0007267
GO:0008150
GO:0008233
GO:0009058
GO:0009617
GO:0010575
GO:0010828
GO:0010866
GO:0010884
GO:0010951
GO:0016192
GO:0030234
GO:0030449
GO:0031410
GO:0031715
GO:0032991
GO:0034774
GO:0035578
GO:0043226
GO:0043312
GO:0043687
GO:0044267
GO:0044281
GO:0045087
GO:0045745
GO:0045766
GO:0048646
GO:0048856
GO:0050766
GO:0050776
GO:0051604
GO:0055085
GO:0060100
GO:0061024
GO:0070062
GO:0072562
GO:0097242
GO:1905114
GO:2000427
HGNC:1318
HPA003563
HPA020432
ILMN_1662523
ILMN_1713182
ILMN_1762260
ILMN_1804151
IPR000020
IPR001134
IPR001599
IPR001840
IPR002890
IPR008930
IPR008993
IPR009048
IPR011625
IPR011626
IPR013783
IPR018081
IPR018933
IPR019565
IPR019742
IPR035711
IPR035815
IPR036595
K02765
K02765_at
LRG_27
M0QYC8
M0R0Q9
M0R1Q1
MIM:120700
MIM:611378
MIM:612925
MIM:613779
NM_000064
NP_000055
PF00207
PF01759
PF01821
PF01835
PF07677
PF07678
PF07703
PF10569
PH_hs_0014742
PR00004
SM00104
SM00643
SM01359
SM01360
SM01361
TC19001103.hg
uc002mfm.4
UPI000013EC9B
V9HWA9
Participant Of
hasComponent
C3b [extracellular region]
Other forms of this molecule
C3d fragment [extracellular region]
p-C3 [endoplasmic reticulum lumen]
C3 [endoplasmic reticulum lumen]
C3c alpha' chain fragment 1 precursor [extracellular region]
C3c alpha' chain fragment 2 [extracellular region]
C3c alpha' chain fragment 1 [extracellular region]
C3a-desArg [extracellular region]
C3dg [plasma membrane]
C3d [plasma membrane]
C3f [extracellular region]
C3 beta chain [plasma membrane]
C3c alpha' chain fragment 1 precursor [plasma membrane]
C3c alpha' chain fragment 2 [plasma membrane]
C3 alpha chain [secretory granule lumen]
C3 beta chain [secretory granule lumen]
C3 alpha chain [azurophil granule lumen]
C3 beta chain [azurophil granule lumen]
dNQ-C3(672-1663) [extracellular region]
C3 alpha chain [extracellular region]
C3 beta chain [extracellular region]
C3a [extracellular region]
Inferred To
Homologues of C3b alpha' [extracellular region] (Canis familiaris)
Homologues of C3b alpha' [extracellular region] (Danio rerio)
Homologues of C3b alpha' [extracellular region] (Drosophila melanogaster)
Homologues of C3b alpha' [extracellular region] (Gallus gallus)
Homologues of C3b alpha' [extracellular region] (Rattus norvegicus)
Homologues of C3b alpha' [extracellular region] (Sus scrofa)
Homologues of C3b alpha' [extracellular region] (Xenopus tropicalis)
C3b alpha' [extracellular region] (Bos taurus)
C3b alpha' [extracellular region] (Canis familiaris)
C3b alpha' [extracellular region] (Danio rerio)
C3b alpha' [extracellular region] (Drosophila melanogaster)
C3b alpha' [extracellular region] (Gallus gallus)
C3b alpha' [extracellular region] (Mus musculus)
C3b alpha' [extracellular region] (Rattus norvegicus)
C3b alpha' [extracellular region] (Sus scrofa)
C3b alpha' [extracellular region] (Xenopus tropicalis)
Cross References
RefSeq
NP_000055.2
OpenTargets
ENSG00000125730
GeneCards
P01024
DOCK Blaster
3L3O
,
3T4A
,
5FOA
,
2ICF
,
2ICE
,
4M76
,
3L5N
,
2GOX
,
3OED
,
2NOJ
,
3NMS
,
2WY7
,
4ONT
,
4ZH1
,
2I07
,
2XQW
,
3OXU
,
3D5R
,
5M6W
,
2WY8
,
2A73
,
2A74
,
3D5S
,
1GHQ
,
5FO8
,
5FO9
,
4I6O
,
2XWB
,
2WIN
,
5FO7
,
2XWJ
,
3OHX
,
4HWJ
,
2WII
,
3RJ3
,
4HW5
,
1C3D
,
3G6J
,
2QKI
,
5FOB
ZINC target
P01024
PRO
P01024
BRENDA (Homo sapiens)
3.4.21.47
Orphanet
17446
PDB
4ONT
,
4I6O
,
5O35
,
2I07
,
5FOA
,
2A73
,
2QKI
,
3NMS
,
1GHQ
,
2WY8
,
2A74
,
3OED
,
2WY7
,
5FOB
,
3OHX
,
2XQW
,
4HWJ
,
1W2S
,
2NOJ
,
3D5S
,
2XWJ
,
3OXU
,
2ICF
,
3D5R
,
5NBQ
,
2ICE
,
3RJ3
,
1C3D
,
2GOX
,
5FO7
,
5M6W
,
4HW5
,
2XWB
,
5FO8
,
2WIN
,
4ZH1
,
4M76
,
5O32
,
6EHG
,
5FO9
,
2WII
,
3G6J
,
3T4A
,
3L3O
,
3L5N
Interactors (9)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P08603 CFH
1
CFH [extracellular region]
(R-HSA-976788)
0.655
5
UniProt:Q9Y279-1 VSIG4
0.591
5
UniProt:Q9Y279-2 VSIG4
0.524
2
UniProt:O95967 EFEMP2
1
EFEMP2 [extracellular region]
(R-HSA-2161231)
0.488
2
UniProt:A6NEM1 GG6L9
0.488
2
UniProt:P60410 KRTAP10-8
1
KRTAP10-8 [cytosol]
(R-HSA-6810301)
0.488
2
UniProt:Q15323 KRT31
1
KRT31 [cytosol]
(R-HSA-6809616)
0.488
2
UniProt:Q9H8W4 PKHF2
0.488
2
UniProt:O95994 AGR2
0.488
2
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