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C3 beta chain [extracellular region]
Stable Identifier
R-HSA-166821
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
extracellular region
Synonyms
C3(23-667)
Icon
Locations in the PathwayBrowser
Expand all
Immune System (Homo sapiens)
Innate Immune System (Homo sapiens)
Complement cascade (Homo sapiens)
Activation of C3 and C5 (Homo sapiens)
Activation of C5 (Homo sapiens)
C5 convertases [plasma membrane] (Homo sapiens)
C3b:Bb:C3b:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C4b:C2a:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cleavage of C3 by C3 convertases (Homo sapiens)
C3 convertases [plasma membrane] (Homo sapiens)
C3(H2O):Bb [extracellular region] (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C4b:C2a:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Complement factor 3 [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Formation of classic pathway C5 convertase (Homo sapiens)
C4b:C2a:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Initial triggering of complement (Homo sapiens)
Alternative complement activation (Homo sapiens)
C3(H2O):Factor Bb cleaves C3 to C3b and C3a (Homo sapiens)
C3(H2O):Bb [extracellular region] (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Complement factor 3 [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C3b binds to cell surface (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor B binds to C3(H2O) (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C3(H2O):CFB [extracellular region] (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor B binds to surface-associated C3b (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:CFB [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor D cleaves C3(H2O)-bound Factor B (Homo sapiens)
C3(H2O):Bb [extracellular region] (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C3(H2O):CFB [extracellular region] (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor D cleaves C3b-bound Factor B (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:CFB [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Formation of alternative pathway C5 convertase (Homo sapiens)
C3b:Bb:C3b:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Complement factor 3 [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Properdin stabilizes C3b:Bb bound to cell surfaces (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Spontaneous hydrolysis of C3 thioester (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Complement factor 3 [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Regulation of Complement cascade (Homo sapiens)
C3 convertases spontaneously dissociate (Homo sapiens)
C3 convertases [plasma membrane] (Homo sapiens)
C3(H2O):Bb [extracellular region] (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C4b:C2a:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:Bb:Properdin [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CD46 binds C3b (Homo sapiens)
CD46:Cell surface:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CD55 (DAF) binds C3bBb, C4bC2a (Homo sapiens)
C4bC2a, C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CD55:C3 convertase complexes [plasma membrane] (Homo sapiens)
CD55:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CD55 (DAF) promotes C3bBb/C4bC2a dissociation (Homo sapiens)
CD55:C3 convertase complexes [plasma membrane] (Homo sapiens)
CD55:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CD55:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CFHR dimers bind C3b (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:C3b:CFHR dimers [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CR1 binds C3bBb/C4bC2a (Homo sapiens)
C4bC2a, C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CR1:C3bBb, C4bC2a complexes [plasma membrane] (Homo sapiens)
CR1:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Complement factor I binds to MCP, CR1:C4b, C3b (Homo sapiens)
CD46, CR1:C4b:C3b complexes [plasma membrane] (Homo sapiens)
CD46:Cell surface:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CR1:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CFI:CD46, CR1:C4b, C3b complexes [plasma membrane] (Homo sapiens)
CD46, CR1:C4b:C3b complexes [plasma membrane] (Homo sapiens)
CD46:Cell surface:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CR1:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Complement factor I binds to extracellular Factor H:C3b (Homo sapiens)
CFH:C3b [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CFI:CFH:C3b [extracellular region] (Homo sapiens)
CFH:C3b [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Complement factor I binds to membrane-associated Factor H:C3b (Homo sapiens)
CFI:CFH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Displacement of C2a/Bb by CR1 (Homo sapiens)
CR1:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CR1:C3bBb, C4bC2a complexes [plasma membrane] (Homo sapiens)
CR1:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor H binds to C3b (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CFH:C3b [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor H binds to C3bBb (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:CFH, CFHR3:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor H binds to membrane-associated C3b (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor H displaces Bb (Homo sapiens)
Cell surface:CFH, CFHR3:C3bBb [plasma membrane] (Homo sapiens)
Cell surface:C3b:Bb [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor I cleaves iC3b (Homo sapiens)
C3c [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor I inactivates Factor H-boundC3b (Homo sapiens)
CFI:CFH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:FH,FHR3:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor I inactivates MCP/CR1-bound C4b/C3b (Homo sapiens)
CFI:CD46, CR1:C4b, C3b complexes [plasma membrane] (Homo sapiens)
CD46, CR1:C4b:C3b complexes [plasma membrane] (Homo sapiens)
CD46:Cell surface:C3b [plasma membrane] (Homo sapiens)
Cell surface:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
CR1:C3b [plasma membrane] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Factor I inactivates plasma Factor H-bound C3b (Homo sapiens)
CFI:CFH:C3b [extracellular region] (Homo sapiens)
CFH:C3b [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
iC3b [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Neutrophil degranulation (Homo sapiens)
Exocytosis of azurophil granule lumen proteins (Homo sapiens)
Azurophil granule lumen proteins [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
Exocytosis of secretory granule lumen proteins (Homo sapiens)
Secretory granule lumen proteins [extracellular region] (Homo sapiens)
C3 beta chain [extracellular region] (Homo sapiens)
External Reference Information
External Reference
UniProt:P01024 C3
Gene Names
C3, CPAMD1
Chain
signal peptide:1-22, chain:23-1663, chain:23-667, chain:569-667, chain:672-1663, chain:672-748, chain:672-747, chain:749-1663, chain:749-954, chain:955-1303, chain:955-1001, chain:1002-1303, peptide:1304-1320, chain:1321-1663
Reference Genes
BioGPS Gene:718 C3
COSMIC (genes):C3 C3
CTD Gene:718 C3
dbSNP Gene:718 C3
ENSEMBL:ENSG00000125730 C3
HGNC:1318 C3
KEGG:hsa:718 C3
Monarch:718 C3
NCBI Gene:718 C3
OMIM:120700 C3
UCSC:P01024 C3
Reference Transcript
RefSeq:NM_000064.3 C3
Participates
as a member of
Azurophil granule lumen proteins [extracellular region] (Homo sapiens)
Secretory granule lumen proteins [extracellular region] (Homo sapiens)
as a component of
iC3b [extracellular region] (Homo sapiens)
C3c [extracellular region] (Homo sapiens)
Complement factor 3 [extracellular region] (Homo sapiens)
C3b [extracellular region] (Homo sapiens)
C3(H2O) [extracellular region] (Homo sapiens)
Other forms of this molecule
C3a [extracellular region]
dNQ-C3(672-1663) [extracellular region]
C3b alpha' [extracellular region]
C3 alpha chain [extracellular region]
C3c alpha' chain fragment 2 [plasma membrane]
C3c alpha' chain fragment 1 precursor [plasma membrane]
C3 beta chain [plasma membrane]
C3f [extracellular region]
C3d [plasma membrane]
C3dg [plasma membrane]
C3a-desArg [extracellular region]
C3c alpha' chain fragment 1 [extracellular region]
C3c alpha' chain fragment 2 [extracellular region]
C3c alpha' chain fragment 1 precursor [extracellular region]
C3 [endoplasmic reticulum lumen]
p-C3 [endoplasmic reticulum lumen]
C3 beta chain [secretory granule lumen]
C3 alpha chain [secretory granule lumen]
C3 beta chain [azurophil granule lumen]
C3 alpha chain [azurophil granule lumen]
C3d fragment [extracellular region]
Inferred To
LOC100491968 [extracellular region]
(Xenopus tropicalis)
C3 [extracellular region]
(Bos taurus)
C3 [extracellular region]
(Canis familiaris)
C3 [extracellular region]
(Mus musculus)
C3 [extracellular region]
(Rattus norvegicus)
C3 [extracellular region]
(Sus scrofa)
C3 beta chain [extracellular region]
(Gallus gallus)
Homologues of C3 beta chain [extracellular region]
(Xenopus tropicalis)
c3a.2 [extracellular region]
(Danio rerio)
LOC100170611 [extracellular region]
(Xenopus tropicalis)
Cross References
RefSeq
NP_000055.2
OpenTargets
ENSG00000125730
ENSEMBL
ENST00000245907
,
ENSP00000245907
,
ENSG00000125730
GeneCards
C3
HPA
ENSG00000125730-C3
ZINC - Substances
CO3_HUMAN
ZINC target
P01024
PRO
P01024
Pharos - Targets
P01024
GlyGen
P01024
Orphanet
C3
PDB
4ZH1
,
5O32
,
2XQW
,
3NMS
,
6RMT
,
8I9L
,
4HWJ
,
3D5R
,
6RUR
,
2I07
,
5FO9
,
5O35
,
3RJ3
,
2A74
,
8UH2
,
2WII
,
2QKI
,
8HK2
,
2ICF
,
6RUV
,
5NBQ
,
5FOA
,
7AKK
,
4HW5
,
7QIV
,
4M76
,
4I6O
,
2WY7
,
8EOK
,
7NOZ
,
3L3O
,
2XWJ
,
6EHG
,
3OHX
,
8ENU
,
1GHQ
,
7TV9
,
3OED
,
8OVB
,
6RMU
,
7UE9
,
3L5N
,
3OXU
,
3D5S
,
2A73
,
6YO6
,
3T4A
,
2WIN
,
2GOX
,
2ICE
,
8OQ3
,
3G6J
,
1C3D
,
5FOB
,
7BAG
,
7PI6
,
7ZGK
,
2WY8
,
5FO7
,
8UIN
,
6S0B
,
5FO8
,
1W2S
,
4ONT
,
2NOJ
,
2XWB
Interactors (19)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
IntAct:EBI-12735745 C3B
0.801
12
UniProt:P08603 CFH
1
CFH [extracellular region]
(R-HSA-976788)
0.743
6
UniProt:P20023 CR2
1
CR2 [plasma membrane]
(R-HSA-197936)
0.719
4
UniProt:P15529 CD46
1
CD46 [plasma membrane]
(R-HSA-977362)
0.623
2
UniProt:O60741 HCN1
1
HCN1 [plasma membrane]
(R-HSA-977503)
0.623
7
UniProt:Q92496-1 CFHR4
0.609
5
UniProt:Q9Y279-1 VSIG4
0.591
5
ChEBI:28304 HEPARIN
0.589
2
UniProt:Q15323 KRT31
1
KRT31 [cytosol]
(R-HSA-6809616)
0.556
3
UniProt:A6NEM1 GG6L9
0.556
3
UniProt:O95967 EFEMP2
1
EFEMP2 [extracellular region]
(R-HSA-2161231)
0.556
3
UniProt:O95994 AGR2
0.556
3
UniProt:Q9H8W4 PKHF2
0.556
3
UniProt:P60410 KRTAP10-8
1
KRTAP10-8 [cytosol]
(R-HSA-6810301)
0.556
3
UniProt:Q16659 MAPK6 gene
6
p-3S,T MAPK6 [nucleoplasm]
(R-HSA-5692665)
MAPK6 [nucleoplasm]
(R-HSA-5692686)
p-S189 MAPK6 [nucleoplasm]
(R-HSA-5687015)
p-S189 MAPK6 [cytosol]
(R-HSA-5687019)
MAPK6 [cytosol]
(R-HSA-5686979)
ub-MAPK6 [cytosol]
(R-HSA-5687000)
0.527
2
UniProt:Q9H8H2 DDX31
0.527
2
UniProt:P35219 CAH8
0.527
2
UniProt:Q9Y279-2 VSIG4
0.524
2
UniProt:Q13936 CACNA1C
1
CACNA1C [plasma membrane]
(R-HSA-265551)
0.499
2
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