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Entries
Branched-chain amino acid catabolism
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authored
[InstanceEdit:73677] D'Eustachio, P, 2003-06-24 00:00:00
dbId
70895
displayName
Branched-chain amino acid catabolism
doi
10.3180/REACT_197.2
edited
[InstanceEdit:165080] D'Eustachio, P, 0000-00-00 00:00:00
eventOf
[Pathway:R-HSA-71291] Metabolism of amino acids and derivatives - Homo sapiens
goBiologicalProcess
[GO_BiologicalProcess:19354] branched-chain amino acid catabolic process
hasDiagram
true
hasEHLD
false
hasEvent
[Reaction:R-HSA-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Homo sapiens
[Reaction:R-HSA-508189] a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate <=> leu, ile, or val + alpha-ketoglutarate [BCAT1] - Homo sapiens
[Reaction:R-HSA-9672770] SLC25A44 transports Leu, Ile and Val from cytosol to mitochondrial matrix - Homo sapiens
[Reaction:R-HSA-70724] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT2] - Homo sapiens
[Reaction:R-HSA-508179] a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate <=> leu, ile, or val + alpha-ketoglutarate [BCAT2] - Homo sapiens
[Reaction:R-HSA-70713] BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV - Homo sapiens
[Reaction:R-HSA-5693148] BCKDK phosphorylates BCKDH - Homo sapiens
[Reaction:R-HSA-5693153] PPM1K dephosphorylates p-BCKDH - Homo sapiens
[Reaction:R-HSA-70745] isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 - Homo sapiens
[Reaction:R-HSA-70773] beta-methylcrotonyl-CoA + ATP + CO2 <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O [MCCA] - Homo sapiens
[Reaction:R-HSA-508308] beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O <=> beta-methylcrotonyl-CoA + ATP + CO2 [MCCA] - Homo sapiens
[Reaction:R-HSA-70785] beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA - Homo sapiens
[Reaction:R-HSA-70800] alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 - Homo sapiens
[Reaction:R-HSA-70830] tiglyl-CoA + H2O <=> alpha-methyl-beta-hydroxybutyryl-CoA - Homo sapiens
[Reaction:R-HSA-70837] alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ - Homo sapiens
[Reaction:R-HSA-508369] alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ - Homo sapiens
[Reaction:R-HSA-70844] alpha-methyl-acetoacetyl-CoA + CoA => propionyl-CoA + acetyl-CoA - Homo sapiens
[Reaction:R-HSA-70859] isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 - Homo sapiens
[Reaction:R-HSA-70870] ECHS1 hydrates methacrylyl-CoA - Homo sapiens
[Reaction:R-HSA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Homo sapiens
[Reaction:R-HSA-70885] beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ - Homo sapiens
[Reaction:R-HSA-508473] methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ - Homo sapiens
[Reaction:R-HSA-70893] methylmalonate semialdehyde + NAD+ + CoA => propionyl-CoA + CO2 + NADH + H+ - Homo sapiens
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:9672787] Branched Chain Amino Acids
modified
[InstanceEdit:10931649] Wright, Adam, 2024-03-08
name
Branched-chain amino acid catabolism
orthologousEvent
[Pathway:R-BTA-70895] Branched-chain amino acid catabolism - Bos taurus
[Pathway:R-PFA-70895] Branched-chain amino acid catabolism - Plasmodium falciparum
[Pathway:R-SCE-70895] Branched-chain amino acid catabolism - Saccharomyces cerevisiae
[Pathway:R-SPO-70895] Branched-chain amino acid catabolism - Schizosaccharomyces pombe
[Pathway:R-DDI-70895] Branched-chain amino acid catabolism - Dictyostelium discoideum
[Pathway:R-CEL-70895] Branched-chain amino acid catabolism - Caenorhabditis elegans
[Pathway:R-DME-70895] Branched-chain amino acid catabolism - Drosophila melanogaster
[Pathway:R-GGA-70895] Branched-chain amino acid catabolism - Gallus gallus
[Pathway:R-XTR-70895] Branched-chain amino acid catabolism - Xenopus tropicalis
[Pathway:R-DRE-70895] Branched-chain amino acid catabolism - Danio rerio
[Pathway:R-SSC-70895] Branched-chain amino acid catabolism - Sus scrofa
[Pathway:R-CFA-70895] Branched-chain amino acid catabolism - Canis familiaris
[Pathway:R-RNO-70895] Branched-chain amino acid catabolism - Rattus norvegicus
[Pathway:R-MMU-70895] Branched-chain amino acid catabolism - Mus musculus
releaseDate
2003-05-04
reviewStatus
[ReviewStatus:9821382] five stars
revised
[InstanceEdit:517475] D'Eustachio, P, 2010-02-18
[InstanceEdit:9672919] D'Eustachio, Peter, 2020-01-03
schemaClass
Pathway
species
[Species:48887] Homo sapiens
stId
R-HSA-70895
summation
[Summation:70896] The branched-chain amino acids, leucine, isoleucine, and val...
Referrals
(hasEvent)
[Pathway:R-HSA-71291] Metabolism of amino acids and derivatives
(hasEncapsulatedEvent)
[Pathway:R-HSA-9857492] Protein lipoylation
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