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Schema
>
Reaction
>
Entries
leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1]
Show undefined attributes
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catalystActivity
[CatalystActivity:70700] branched-chain-amino-acid transaminase activity of BCAT1 dimer [cytosol]
catalystActivityReference
[CatalystActivityReference:9643740] branched-chain-amino-acid transaminase activity of BCAT1 dimer [cytosol] Structural determinants for branched-chain aminotransferase isozyme-specific inhibition by the anticonvulsant drug gabapentin
category
transition
compartment
[Compartment:70101] cytosol
crossReference
[DatabaseIdentifier:9917060] RHEA:18322
[DatabaseIdentifier:9917056] RHEA:24802
[DatabaseIdentifier:9917057] RHEA:24814
dbId
70723
deleted
[Deleted:513019] Deletion of instance: 70702
[Deleted:508194] Deletion of instance: 70847
displayName
leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1]
eventOf
[Pathway:R-HSA-70895] Branched-chain amino acid catabolism - Homo sapiens
followingEvent
[Reaction:R-HSA-9859148] BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV - Homo sapiens
[Reaction:R-HSA-210444] L-Glutamate loading of synaptic vesicle - Homo sapiens
input
[SimpleEntity:R-ALL-29406] 2OG [cytosol]
[DefinedSet:R-ALL-508182] Leu, Ile, Val [cytosol]
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:508185] Structural determinants for branched-chain aminotransferase isozyme-specific inhibition by the anticonvulsant drug gabapentin
maxDepth
1
modified
[InstanceEdit:11080360] Weiser, Joel, 2026-03-16
name
leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1]
2-oxoglutarate + L-leucine => 4-methyl-2-oxopentanoate + L-glutamate
2-oxoglutarate + L-isoleucine => (S)-3-methyl-2-oxopentanoate + L-glutamate
2-oxoglutarate + L-valine => 3-methyl-2-oxobutanoate + L-glutamate
negativePrecedingEvent
[NegativePrecedingEvent:9908871] Futile Cycle: a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate <=> leu, ile, or val + alpha-ketoglutarate [BCAT1]
orthologousEvent
[Reaction:R-SCE-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Saccharomyces cerevisiae
[Reaction:R-SPO-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Schizosaccharomyces pombe
[Reaction:R-DDI-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Dictyostelium discoideum
[Reaction:R-CEL-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Caenorhabditis elegans
[Reaction:R-DME-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Drosophila melanogaster
[Reaction:R-GGA-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Gallus gallus
[Reaction:R-XTR-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Xenopus tropicalis
[Reaction:R-DRE-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Danio rerio
[Reaction:R-SSC-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Sus scrofa
[Reaction:R-BTA-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Bos taurus
[Reaction:R-CFA-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Canis familiaris
[Reaction:R-RNO-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Rattus norvegicus
[Reaction:R-MMU-70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - Mus musculus
output
[DefinedSet:R-ALL-508187] KIC,KMVA,KIV [cytosol]
[SimpleEntity:R-ALL-29404] L-Glu [cytosol]
releaseDate
2004-07-06
reviewStatus
[ReviewStatus:9821382] five stars
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-70723
summation
[Summation:178919] Cytosolic branched-chain-amino-acid aminotransferase (BCAT1)...
updateTrackers
[UpdateTracker:9791000] Update Tracker - [Reaction:70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - v32:[add_removeInput, add_removeLiteratureReference, add_removeOutput, modifyText]
[UpdateTracker:9777342] Update Tracker - [Reaction:70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - v72:[modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9791000] Update Tracker - [Reaction:70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - v32:[add_removeInput, add_removeLiteratureReference, add_removeOutput, modifyText]
[UpdateTracker:9777342] Update Tracker - [Reaction:70723] leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1] - v72:[modifyText]
(replacementInstances)
[Deleted:513019] Deletion of instance: 70702
[Deleted:508194] Deletion of instance: 70847
(precedingEvent)
[Reaction:R-HSA-210444] L-Glutamate loading of synaptic vesicle
[Reaction:R-HSA-9859148] BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV
[NegativePrecedingEvent:9908872] Futile Cycle: leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT1]
(hasEvent)
[Pathway:R-HSA-70895] Branched-chain amino acid catabolism
(reverseReaction)
[Reaction:R-HSA-508189] a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate <=> leu, ile, or val + alpha-ketoglutarate [BCAT1]
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