FH tetramer hydrates fumarate to L-malate

catalystActivity
catalystActivityReference [CatalystActivityReference:9643531] fumarate hydratase activity of FH tetramer [mitochondrial matrix] Mutation of the fumarase gene in two siblings with progressive encephalopathy and fumarase deficiency
category transition
compartment
crossReference
dbId 70982
displayName FH tetramer hydrates fumarate to L-malate
eventOf
followingEvent
input
isInDisease false
isInferred false
literatureReference
maxDepth 1
modified [InstanceEdit:11080360] Weiser, Joel, 2026-03-16
name
  • FH tetramer hydrates fumarate to L-malate
  • fumarate + H2O => (S)-malate
orthologousEvent
output
precedingEvent
releaseDate 2004-07-06
reviewStatus [ReviewStatus:9821382] five stars
reviewed
revised
schemaClass Reaction
species
stId R-HSA-70982
summation
updateTrackers
Cite Us!