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Peroxisomal lipid metabolism
Stable Identifier
R-HSA-390918
DOI
10.3180/REACT_16880.1
Type
Pathway
Species
Homo sapiens
ReviewStatus
5/5
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Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Peroxisomal lipid metabolism (Homo sapiens)
General
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In humans, the catabolism of phytanate, pristanate, and very long chain fatty acids as well as the first four steps of the biosynthesis of plasmalogens are catalyzed by peroxisomal enzymes. Defects in any of these enzymes or in the assembly of peroxisomes are associated with severe developmental disorders (Wanders and Watherham 2006).
Literature References
PubMed ID
Title
Journal
Year
16756494
Biochemistry of mammalian peroxisomes revisited
Wanders, RJA
,
Waterham, HR
Annu Rev Biochem
2006
Participants
Events
HAO2 tetramer oxidises 2OH-PALM
(Homo sapiens)
Alpha-oxidation of phytanate
(Homo sapiens)
Beta-oxidation of pristanoyl-CoA
(Homo sapiens)
Beta-oxidation of very long chain fatty acids
(Homo sapiens)
ACBD4,5 bind MCFA-CoA and LCFA-CoA
(Homo sapiens)
NUDT7 hydrolyses CoA-SH to 3',5'-ADP and PPANT
(Homo sapiens)
NUDT19 hydrolyses acyl-CoA to 3',5'-ADP and acyl-PPANT
(Homo sapiens)
Participates
as an event of
Fatty acid metabolism (Homo sapiens)
Event Information
Go Biological Process
fatty acid catabolic process (0009062)
Orthologous Events
Peroxisomal lipid metabolism (Bos taurus)
Peroxisomal lipid metabolism (Caenorhabditis elegans)
Peroxisomal lipid metabolism (Canis familiaris)
Peroxisomal lipid metabolism (Danio rerio)
Peroxisomal lipid metabolism (Dictyostelium discoideum)
Peroxisomal lipid metabolism (Drosophila melanogaster)
Peroxisomal lipid metabolism (Gallus gallus)
Peroxisomal lipid metabolism (Mus musculus)
Peroxisomal lipid metabolism (Plasmodium falciparum)
Peroxisomal lipid metabolism (Rattus norvegicus)
Peroxisomal lipid metabolism (Saccharomyces cerevisiae)
Peroxisomal lipid metabolism (Schizosaccharomyces pombe)
Peroxisomal lipid metabolism (Sus scrofa)
Peroxisomal lipid metabolism (Xenopus tropicalis)
Authored
D'Eustachio, P (2009-02-11)
Reviewed
Jassal, B (2009-02-27)
Created
D'Eustachio, P (2009-02-11)
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