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Schema
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Reaction
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Entries
MMADHC targets transport of cytosolic cob(II)alamin to mitochondria
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authored
[InstanceEdit:196747] Jassal, B, 2007-04-24 08:38:46
catalystActivity
[CatalystActivity:9908939] molecular carrier activity of MMACHC:MMADHC:cob(II)alamin [cytosol]
category
transition
compartment
[Compartment:70101] cytosol
[Compartment:5460] mitochondrial matrix
created
[InstanceEdit:3149561] Jassal, Bijay, 2013-02-18
dbId
3149563
displayName
MMADHC targets transport of cytosolic cob(II)alamin to mitochondria
edited
[InstanceEdit:3149561] Jassal, Bijay, 2013-02-18
eventOf
[Pathway:R-HSA-9759218] Cobalamin (Cbl) metabolism - Homo sapiens
followingEvent
[Reaction:R-HSA-3159253] MMAB adenosylates cob(I)alamin - Homo sapiens
input
[Complex:R-HSA-3149533] MMACHC:MMADHC:cob(II)alamin [cytosol]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:9758714] Redox-Linked Coordination Chemistry Directs Vitamin B
12
Trafficking
[LiteratureReference:3149550] Gene identification for the cblD defect of vitamin B12 metabolism
[LiteratureReference:3245902] Molecular mechanisms leading to three different phenotypes in the cblD defect of intracellular cobalamin metabolism
maxDepth
1
modified
[InstanceEdit:10996769] Weiser, Joel, 2026-03-16
name
MMADHC targets transport of cytosolic cob(II)alamin to mitochondria
MMADHC targets cytosolic cob(II)alamin for entry to mitochondria
orthologousEvent
[Reaction:R-DDI-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Dictyostelium discoideum
[Reaction:R-CEL-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Caenorhabditis elegans
[Reaction:R-GGA-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Gallus gallus
[Reaction:R-XTR-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Xenopus tropicalis
[Reaction:R-DRE-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Danio rerio
[Reaction:R-SSC-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Sus scrofa
[Reaction:R-BTA-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Bos taurus
[Reaction:R-CFA-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Canis familiaris
[Reaction:R-RNO-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Rattus norvegicus
[Reaction:R-MMU-3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - Mus musculus
output
[SimpleEntity:R-ALL-3149564] cob(II)alamin [mitochondrial matrix]
[EntityWithAccessionedSequence:R-HSA-2980949] MMACHC [cytosol]
[EntityWithAccessionedSequence:R-HSA-3149529] MMADHC [cytosol]
precedingEvent
[Reaction:R-HSA-3149494] MMACHC:cob(II)alamin binds MMADHC - Homo sapiens
previousReviewStatus
[ReviewStatus:9821385] four stars
releaseDate
2013-06-11
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:3288227] D'Eustachio, P, 2013-04-15
[InstanceEdit:9917333] Hill, David P, 2024-08-02
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-3149563
summation
[Summation:3149562] MMADHC (Methylmalonic aciduria and homocystinuria type D pro...
updateTrackers
[UpdateTracker:9911090] Update Tracker - [Reaction:3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - v89:[addCatalystActivity, modifyText]
[UpdateTracker:9786296] Update Tracker - [BlackBoxEvent:3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - v50:[modifyText]
[UpdateTracker:9774998] Update Tracker - [BlackBoxEvent:3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - v80:[addLiteratureReference, add_removeOutput, modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9911090] Update Tracker - [Reaction:3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - v89:[addCatalystActivity, modifyText]
[UpdateTracker:9786296] Update Tracker - [BlackBoxEvent:3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - v50:[modifyText]
[UpdateTracker:9774998] Update Tracker - [BlackBoxEvent:3149563] MMADHC targets transport of cytosolic cob(II)alamin to mitochondria - v80:[addLiteratureReference, add_removeOutput, modifyText]
(hasEvent)
[Pathway:R-HSA-9759218] Cobalamin (Cbl) metabolism
(precedingEvent)
[Reaction:R-HSA-3159253] MMAB adenosylates cob(I)alamin
[NegativePrecedingEvent:9764887] Incorrect Order: MMADHC targets transport of cytosolic cob(II)alamin to mitochondria
[NegativePrecedingEvent:9764879] Incorrect Order: MMADHC targets transport of cytosolic cob(II)alamin to mitochondria
[NegativePrecedingEvent:9764885] Incorrect Order: MMADHC targets transport of cytosolic cob(II)alamin to mitochondria
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