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Entries
Mitochondrial protein import
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authored
[InstanceEdit:1258402] May, B, 2011-05-03
compartment
[Compartment:70101] cytosol
[Compartment:70616] mitochondrial inner membrane
[Compartment:17927] mitochondrial intermembrane space
[Compartment:5460] mitochondrial matrix
[Compartment:17906] mitochondrial outer membrane
created
[InstanceEdit:1268021] May, B, 2011-05-09
dbId
1268020
displayName
Mitochondrial protein import
edited
[InstanceEdit:1258402] May, B, 2011-05-03
eventOf
[TopLevelPathway:R-HSA-9609507] Protein localization - Homo sapiens
figure
[Figure:2463866] /figures/Pathway_Illustrations/MPI_72_oicr.png
goBiologicalProcess
[GO_BiologicalProcess:18877] protein targeting to mitochondrion
hasDiagram
true
hasEHLD
false
hasEvent
[Reaction:R-HSA-1268022] TOMM40 complex translocates proteins from the cytosol to the mitochondrial intermembrane space - Homo sapiens
[Reaction:R-HSA-1307802] MIA40:ERV1 (CHCHD4:GFER) oxidizes cysteine residues to cystine disulfide bonds - Homo sapiens
[Reaction:R-HSA-1299484] TIMM8:TIMM13 chaperones hydrophobic proteins - Homo sapiens
[Reaction:R-HSA-1299481] TIMM9:TIMM10 binds hydrophobic proteins - Homo sapiens
[Reaction:R-HSA-1955380] TIMM9:TIMM10 transfers proteins to TIMM22 - Homo sapiens
[Reaction:R-HSA-1268025] SAM50 complex inserts proteins into mitochondrial outer membrane - Homo sapiens
[Reaction:R-HSA-1307803] TIMM22 inserts proteins into inner membrane - Homo sapiens
[Reaction:R-HSA-1299487] Precursor proteins enter TIMM23 SORT - Homo sapiens
[Reaction:R-HSA-1299476] MPP cleaves targeting peptide (presequence) of inner membrane precursors - Homo sapiens
[Reaction:R-HSA-1299482] TIMM23 SORT inserts proteins into inner membrane - Homo sapiens
[Reaction:R-HSA-1299480] Precursor proteins enter TIMM23 PAM - Homo sapiens
[Reaction:R-HSA-1299478] MPP cleaves targeting peptide (presequence) of matrix precursors - Homo sapiens
[Reaction:R-HSA-1299475] TIMM23 PAM translocates proteins from the mitochondrial intermembrane space to the mitochondrial matrix - Homo sapiens
[BlackBoxEvent:R-HSA-8986181] PITRM1 proteolyzes mitochondrial targeting peptides (presequences) - Homo sapiens
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:1307738] Multiple pathways for mitochondrial protein traffic
[LiteratureReference:1307772] Diverse mechanisms and machineries for import of mitochondrial proteins
[LiteratureReference:1307732] Oxidative protein folding in the mitochondrial intermembrane space
[LiteratureReference:1307751] Disulphide bond formation in the intermembrane space of mitochondria
[LiteratureReference:1307775] On the mechanism of preprotein import by the mitochondrial presequence translocase
[LiteratureReference:1307739] Multiple pathways for sorting mitochondrial precursor proteins
[LiteratureReference:1307740] Cooperation of translocase complexes in mitochondrial protein import
[LiteratureReference:1307763] The MIA system for protein import into the mitochondrial intermembrane space
[LiteratureReference:1252288] Roles of Tom70 in import of presequence-containing mitochondrial proteins
[LiteratureReference:9609511] Mitochondrial protein transport in health and disease
[LiteratureReference:9609509] Mitochondrial Machineries for Protein Import and Assembly
modified
[InstanceEdit:10931649] Wright, Adam, 2024-03-08
name
Mitochondrial protein import
orthologousEvent
[Pathway:R-MMU-1268020] Mitochondrial protein import - Mus musculus
[Pathway:R-RNO-1268020] Mitochondrial protein import - Rattus norvegicus
[Pathway:R-CFA-1268020] Mitochondrial protein import - Canis familiaris
[Pathway:R-BTA-1268020] Mitochondrial protein import - Bos taurus
[Pathway:R-SSC-1268020] Mitochondrial protein import - Sus scrofa
[Pathway:R-DRE-1268020] Mitochondrial protein import - Danio rerio
[Pathway:R-XTR-1268020] Mitochondrial protein import - Xenopus tropicalis
[Pathway:R-GGA-1268020] Mitochondrial protein import - Gallus gallus
[Pathway:R-DME-1268020] Mitochondrial protein import - Drosophila melanogaster
[Pathway:R-CEL-1268020] Mitochondrial protein import - Caenorhabditis elegans
[Pathway:R-DDI-1268020] Mitochondrial protein import - Dictyostelium discoideum
[Pathway:R-SPO-1268020] Mitochondrial protein import - Schizosaccharomyces pombe
[Pathway:R-SCE-1268020] Mitochondrial protein import - Saccharomyces cerevisiae
[Pathway:R-PFA-1268020] Mitochondrial protein import - Plasmodium falciparum
releaseDate
2012-03-13
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:1914221] D'Eustachio, P, 2011-11-01
[InstanceEdit:2108993] Endo, T, 2012-02-12
schemaClass
Pathway
species
[Species:48887] Homo sapiens
stId
R-HSA-1268020
summation
[Summation:1307730] A human mitochondrion contains about 1500 proteins, more tha...
Referrals
(hasEvent)
[TopLevelPathway:R-HSA-9609507] Protein localization
(hasEncapsulatedEvent)
[Pathway:R-HSA-1592230] Mitochondrial biogenesis
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