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BRCC3 [nucleoplasm]
Stable Identifier
R-HSA-5682577
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
nucleoplasm
Synonyms
Lys-63-specific deubiquitinase BRCC36, BRCC36
Locations in the PathwayBrowser
Expand all
Cell Cycle (Homo sapiens)
Cell Cycle Checkpoints (Homo sapiens)
G2/M Checkpoints (Homo sapiens)
G2/M DNA damage checkpoint (Homo sapiens)
CHEK2 is recruited to DNA DSBs (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex:CHEK2 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
Phosphorylation and activation of CHEK2 by ATM (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex:CHEK2 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA Repair (Homo sapiens)
DNA Double-Strand Break Repair (Homo sapiens)
DNA Double Strand Break Response (Homo sapiens)
Recruitment and ATM-mediated phosphorylation of repair and signaling proteins at DNA double strand breaks (Homo sapiens)
CHEK2 is recruited to DNA DSBs (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex:CHEK2 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
CHEK2 phosphorylates BRCA1 (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-5S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-5S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
Formation of BRCA1-A complex at DNA DSBs (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:BRCA1-A complex [nucleoplasm] (Homo sapiens)
BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
Phosphorylation and activation of CHEK2 by ATM (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex:CHEK2 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
Phosphorylation of BRCA1-A complex at multiple sites by ATM (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:BRCA1-A complex [nucleoplasm] (Homo sapiens)
BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-4S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
Homology Directed Repair (Homo sapiens)
HDR through Homologous Recombination (HRR) or Single Strand Annealing (SSA) (Homo sapiens)
Processing of DNA double-strand break ends (Homo sapiens)
PIAS4 SUMOylates MDC1 (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:SUMO2:K1840,p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-5S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-5S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-5S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-5S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
RNF4 ubiquitinates MDC1 (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:SUMO2:K1840,p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-5S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-5S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
Nonhomologous End-Joining (NHEJ) (Homo sapiens)
RIF1 and PAX1IP bind TP53BP1 at DNA DSBs (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
DNA DNA DSBs:p-MRN:p-S1981,Ac-K3016-ATM:KAT5:K63PolyUb-K14,K16,p-S139-H2AFX,Me2K21-HIST1H4A-Nucleosome:p-5T-MDC1:p-S102-WHSC1:RNF8:Zn2+:SUMO1:p-T4827-HERC2:UBE2N:UBE2V2:RNF168:PIAS4:p-S25,S1778-TP53BP1:p-5S,2T-BRCA1-A complex [nucleoplasm] (Homo sapiens)
p-5S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Deubiquitination (Homo sapiens)
Metalloprotease DUBs (Homo sapiens)
BRCA1-A complex deubiquitinates K63polyUb-histone H2A (Homo sapiens)
BRCA1-A Complex:Histone H2A [nucleoplasm] (Homo sapiens)
BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
BRCA1-A Complex:K63polyUb-histone H2A [nucleoplasm] (Homo sapiens)
BRCA1-A Complex [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
BRISC complex deubiquitinates NLRP3 (Homo sapiens)
BRCC3 [nucleoplasm] (Homo sapiens)
External Reference Information
External Reference
UniProt:P46736 BRCC3
Gene Names
BRCC3, BRCC36, C6.1A, CXorf53
Chain
initiator methionine:1, chain:2-316
Reference Genes
BioGPS Gene:79184 BRCC3
COSMIC (genes):BRCC3 BRCC3
CTD Gene:79184 BRCC3
dbSNP Gene:79184 BRCC3
ENSEMBL:ENSG00000185515 BRCC3
HGNC:24185 BRCC3
KEGG Gene (Homo sapiens):79184 BRCC3
Monarch:79184 BRCC3
NCBI Gene:79184 BRCC3
OMIM:300617 BRCC3
UCSC:P46736 BRCC3
Reference Transcript
RefSeq:XM_017029838.1 BRCC3
RefSeq:NM_001018055.2 BRCC3
RefSeq:NM_001242640.1 BRCC3
RefSeq:NM_024332.3 BRCC3
Other Identifiers
0104050102
11726529_s_at
11726530_x_at
11726531_x_at
11733210_x_at
11733211_x_at
11750003_s_at
17108546
216521_PM_s_at
216521_s_at
221196_PM_x_at
221196_x_at
229436_PM_x_at
229436_x_at
231913_PM_s_at
231913_s_at
2842475
2842476
2842477
2842478
2842481
3996756
3996757
3996759
3996760
3996761
3996764
3996766
3996767
3996768
3996777
3996778
3996780
3996783
3996785
79184
8171006
A_23_P217659
A_33_P3303940
A_33_P3385461
GE59908
GO:0000151
GO:0000152
GO:0000278
GO:0000922
GO:0003674
GO:0004843
GO:0005515
GO:0005575
GO:0005622
GO:0005634
GO:0005654
GO:0005737
GO:0005829
GO:0005856
GO:0006259
GO:0006281
GO:0006282
GO:0006302
GO:0006325
GO:0006464
GO:0006508
GO:0006950
GO:0006974
GO:0007049
GO:0007095
GO:0007165
GO:0008150
GO:0008233
GO:0008237
GO:0010165
GO:0010212
GO:0016579
GO:0016787
GO:0030234
GO:0031593
GO:0032991
GO:0034641
GO:0035518
GO:0043167
GO:0043226
GO:0044818
GO:0045739
GO:0046872
GO:0050790
GO:0051276
GO:0051301
GO:0051865
GO:0061578
GO:0070122
GO:0070531
GO:0070536
GO:0070537
GO:0070552
GO:0071479
GO:0140492
GO:2000001
HMNXSV003007440
HMNXSV003018106
Hs.301927.1.A1_3p_a_at
Hs.301927.2.S1_3p_a_at
ILMN_1697546
ILMN_1700026
ILMN_1744613
PH_hs_0027362
TC0X000783.hg
TC0X001943.hg
X64643_at
Participates
as an output of
RIF1 and PAX1IP bind TP53BP1 at DNA DSBs (Homo sapiens)
RNF4 ubiquitinates MDC1 (Homo sapiens)
as an input of
Formation of BRCA1-A complex at DNA DSBs (Homo sapiens)
as a component of
BRCA1-A Complex [nucleoplasm] (Homo sapiens)
p-4S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
p-5S,2T-BRCA1-A Complex [nucleoplasm] (Homo sapiens)
Other forms of this molecule
BRCC3 [cytosol]
Inferred To
BRCC3 [nucleoplasm]
(Bos taurus)
BRCC3 [nucleoplasm]
(Canis familiaris)
BRCC3 [nucleoplasm]
(Gallus gallus)
BRCC3 [nucleoplasm]
(Sus scrofa)
brcc3 [nucleoplasm]
(Danio rerio)
brcc3 [nucleoplasm]
(Xenopus tropicalis)
Brcc3 [nucleoplasm]
(Mus musculus)
Brcc3 [nucleoplasm]
(Rattus norvegicus)
Cross References
RefSeq
NP_001018065.1
,
NP_001229569.1
,
XP_016885327.1
,
NP_077308.1
OpenTargets
ENSG00000185515
HPA
ENSG00000185515-BRCC3
GeneCards
P46736
Ensembl
ENSP00000358474
,
ENSP00000328641
,
ENSP00000344103
,
ENST00000340647
,
ENST00000330045
,
ENST00000369462
,
ENSG00000185515
,
ENSP00000358471
,
ENST00000369459
PRO
P46736
Pharos - Targets
P46736
Orphanet
20200
PDB
6R8F
,
6H3C
HMDB Protein
HMDBP13773
Interactors (5)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q96RL1-1 UIMC1
0.688
4
UniProt:Q6UWZ7 ABRAXAS1
1
p-S406-FAM175A [nucleoplasm]
(R-HSA-5682575)
0.656
4
UniProt:Q9NXR7 BABAM2
2
BRE [nucleoplasm]
(R-HSA-5682579)
BRE [cytosol]
(R-HSA-5691413)
0.589
3
UniProt:X5D778 X5D778
0.556
3
UniProt:P38398 BRCA1
20
polySUMO2,3-BRCA1 [nucleoplasm]
(R-HSA-2997624)
monoSUMO1-K109-BRCA1 [nucleoplasm]
(R-HSA-2997644)
BRCA1 M1411T [nucleoplasm]
(R-HSA-9702140)
BRCA1 M1400V [nucleoplasm]
(R-HSA-9701202)
BRCA1 L1407P [nucleoplasm]
(R-HSA-9702135)
BRCA1 Y777* [nucleoplasm]
(R-HSA-9702765)
BRCA1 S1009* [nucleoplasm]
(R-HSA-9702755)
BRCA1 P724Lfs*12 [nucleoplasm]
(R-HSA-9703778)
BRCA1 S451* [nucleoplasm]
(R-HSA-9702754)
BRCA1 S864* [nucleoplasm]
(R-HSA-9702752)
BRCA1 P897Kfs*5 [nucleoplasm]
(R-HSA-9703782)
BRCA1 N555Kfs*17 [nucleoplasm]
(R-HSA-9703781)
BRCA1 Y1127Sfs*6 [nucleoplasm]
(R-HSA-9703780)
BRCA1 S886Cfs*16 [nucleoplasm]
(R-HSA-9703802)
BRCA1 V83Cfs*2 [nucleoplasm]
(R-HSA-9703800)
BRCA1 T464Pfs*11 [nucleoplasm]
(R-HSA-9703807)
BRCA1 G813Dfs*2 [nucleoplasm]
(R-HSA-9703549)
BRCA1 V340Gfs*6 [nucleoplasm]
(R-HSA-9703804)
BRCA1 Y655* [nucleoplasm]
(R-HSA-9702769)
BRCA1 W372* [nucleoplasm]
(R-HSA-9702768)
0.483
2
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