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chondroitin(3)-core proteins [Golgi lumen]
Stable Identifier
R-HSA-2064075
Type
Set [DefinedSet]
Species
Homo sapiens
Compartment
Golgi lumen
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with glycosaminoglycan metabolism (Homo sapiens)
Defective CHST3 causes SEDCJD (Homo sapiens)
Defective CHST3 does not transfer SO4(2-) to chondroitin (Homo sapiens)
chondroitin(3)-core proteins [Golgi lumen] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
Chondroitin sulfate biosynthesis (Homo sapiens)
CHPF,CHSY3 transfer GalNAc to chondroitin (Homo sapiens)
chondroitin(3)-core proteins [Golgi lumen] (Homo sapiens)
CHST3,7 transfer SO4(2-) to position 6 of GalNAc on chondroitin chains (Homo sapiens)
chondroitin(3)-core proteins [Golgi lumen] (Homo sapiens)
CHSY1 transfers GalNAc to chondroitin (Homo sapiens)
chondroitin(3)-core proteins [Golgi lumen] (Homo sapiens)
Chondroitin can be sulfated on position 4 of GalNAc by CHST9, 11, 12 and 13 (Homo sapiens)
chondroitin(3)-core proteins [Golgi lumen] (Homo sapiens)
Dermatan sulfate biosynthesis (Homo sapiens)
Dermatan-sulfate epimerase (DSE) converts chondroitin sulfate (CS) to dermatan sulfate (DS) (Homo sapiens)
DSE,DSEL substrates [Golgi lumen] (Homo sapiens)
chondroitin(3)-core proteins [Golgi lumen] (Homo sapiens)
Participants
members
chondroitin(3)-BCAN [Golgi lumen]
(Homo sapiens)
chondroitin(3)-BGN [Golgi lumen]
(Homo sapiens)
chondroitin(3)-CSPG4 [Golgi lumen]
(Homo sapiens)
chondroitin(3)-CSPG5 [Golgi lumen]
(Homo sapiens)
chondroitin(3)-DCN [Golgi lumen]
(Homo sapiens)
chondroitin(3)-NCAN [Golgi lumen]
(Homo sapiens)
chondroitin(3)-VCAN [Golgi lumen]
(Homo sapiens)
Participates
as an input of
Defective CHST3 does not transfer SO4(2-) to chondroitin (Homo sapiens)
CHST3,7 transfer SO4(2-) to position 6 of GalNAc on chondroitin chains (Homo sapiens)
Chondroitin can be sulfated on position 4 of GalNAc by CHST9, 11, 12 and 13 (Homo sapiens)
as an output of
CHSY1 transfers GalNAc to chondroitin (Homo sapiens)
CHPF,CHSY3 transfer GalNAc to chondroitin (Homo sapiens)
as a member of
DSE,DSEL substrates [Golgi lumen] (Homo sapiens)
Inferred To
chondroitin(3)-core proteins [Golgi lumen]
(Bos taurus)
chondroitin(3)-core proteins [Golgi lumen]
(Canis familiaris)
chondroitin(3)-core proteins [Golgi lumen]
(Danio rerio)
chondroitin(3)-core proteins [Golgi lumen]
(Drosophila melanogaster)
chondroitin(3)-core proteins [Golgi lumen]
(Gallus gallus)
chondroitin(3)-core proteins [Golgi lumen]
(Mus musculus)
chondroitin(3)-core proteins [Golgi lumen]
(Rattus norvegicus)
chondroitin(3)-core proteins [Golgi lumen]
(Sus scrofa)
chondroitin(3)-core proteins [Golgi lumen]
(Xenopus tropicalis)
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