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NDUFA10 [mitochondrial inner membrane]
Stable Identifier
R-HSA-163937
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase 42 kDa subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
NDUFA10 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O95299 NDUFA10
Gene Names
NDUFA10
Chain
transit peptide:1-35, chain:36-355
Reference Genes
BioGPS Gene:4705 NDUFA10
COSMIC (genes):NDUFA10 NDUFA10
CTD Gene:4705 NDUFA10
dbSNP Gene:4705 NDUFA10
ENSEMBL:ENSG00000130414.13 NDUFA10
HGNC:7684 NDUFA10
KEGG Gene (Homo sapiens):4705 NDUFA10
Monarch:4705 NDUFA10
NCBI Gene:4705 NDUFA10
OMIM:603835 NDUFA10
UCSC:O95299 NDUFA10
Reference Transcript
RefSeq:NM_004544.3 NDUFA10
Other Identifiers
0002850239
0103940048
11748707_a_at
11753028_a_at
11754964_a_at
1555548_PM_at
1555548_at
16910081
217860_PM_at
217860_at
227206_PM_at
227206_at
2606584
2606585
2606586
2606587
2606588
2606589
2606603
2606604
2606606
2606607
2606609
2606612
2606613
2606614
2606617
2606618
2606619
2606620
2606621
2606622
4705
50715_at
65759_at
8060063
A_24_P396881
A_24_P396889
A_33_P3351914
GE638692
GE79581
GE87261
GO:0005215
GO:0005622
GO:0005737
GO:0005739
GO:0005743
GO:0005747
GO:0005759
GO:0006091
GO:0006120
GO:0007005
GO:0008137
GO:0009060
GO:0016491
GO:0032981
GO:0032991
GO:0042776
GO:0043226
GO:0055086
GO:0065003
GO:0070469
GO:1901135
HMNXSV003022199
HMNXSV003042638
Hs.108593.0.S1_3p_at
Hs2.198271.2.S1_3p_a_at
Hs2.198271.3.S1_3p_at
ILMN_1758640
ILMN_1791119
PH_hs_0011678
g4758767_3p_at
Participates
as a component of
NDUFA10:FAD [mitochondrial inner membrane] (Homo sapiens)
Inferred To
NDUFA10 [mitochondrial inner membrane]
(Bos taurus)
NDUFA10 [mitochondrial inner membrane]
(Canis familiaris)
NDUFA10 [mitochondrial inner membrane]
(Danio rerio)
NDUFA10 [mitochondrial inner membrane]
(Gallus gallus)
NDUFA10 [mitochondrial inner membrane]
(Sus scrofa)
nuo-4 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Ghost homologue of NDUFA10 [mitochondrial inner membrane]
(Xenopus tropicalis)
ND-42 [mitochondrial inner membrane]
(Drosophila melanogaster)
Ndufa10 [mitochondrial inner membrane]
(Mus musculus)
Ndufa10 [mitochondrial inner membrane]
(Rattus norvegicus)
Cross References
RefSeq
NP_004535.1
OpenTargets
ENSG00000130414
HPA
ENSG00000130414-NDUFA10
GeneCards
O95299
Ensembl
ENST00000307300
,
ENSG00000130414
,
ENSP00000302321
,
ENSP00000504765
,
ENSP00000252711
,
ENST00000676929
,
ENST00000678158
,
ENSP00000503956
,
ENST00000252711
PRO
O95299
Pharos - Targets
O95299
Orphanet
20138
HMDB Protein
HMDBP00144
PDB
5XTH
,
5XTD
,
5XTI
,
5XTC
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