BBOX1:AscH-:Fe2+ dimer dioxygenates TEABT and 2OG to form CAR and SUCCA

catalystActivity
catalystActivityReference [CatalystActivityReference:9644024] gamma-butyrobetaine dioxygenase activity of BBOX1:AscH-:Fe2+ dimer [cytosol] Crystal structure of human gamma-butyrobetaine hydroxylase
category transition
compartment
dbId 71261
displayName BBOX1:AscH-:Fe2+ dimer dioxygenates TEABT and 2OG to form CAR and SUCCA
eventOf
followingEvent
input
isInDisease false
isInferred false
literatureReference
maxDepth 1
modified [InstanceEdit:11080360] Weiser, Joel, 2026-03-16
name
  • BBOX1:AscH-:Fe2+ dimer dioxygenates TEABT and 2OG to form CAR and SUCCA
  • 2-oxoglutarate + 4-(trimethylamino)butanoate + O2 => carnitine + CO2 + succinate
  • gamma-butyrobetaine + alpha-ketoglutarate + O2 => carnitine + succinate + CO2
orthologousEvent
output
precedingEvent
releaseDate 2004-07-06
reviewStatus [ReviewStatus:9821382] five stars
revised
schemaClass Reaction
species
stId R-HSA-71261
summation
updateTrackers
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