Cytosolic gamma-butyrobetaine hydroxylase dimer (BBOX1), a dioxygenase, catalyzes the reaction of oxygen, 4-trimethylammoniobutanoate (TEABT), and 2-oxoglutarate (2OG)to form CO2, succinate (SUCCA), and carnitine (CAR) (Lindstedt and Nordin 1984; Tars et al. 2010; Vaz et al. 1998).
Nordin, I, Lindstedt, S
Kuka, J, Kotelovica, S, Rumnieks, J, Viksna, A, Tars, K, Kazaks, A, Zeltins, A, Dambrova, M, Leonciks, A, Sharipo, J, Liepinsh, E
Vaz, FM, Ijlst, L, van Gool, S, Ofman, R
gamma-butyrobetaine dioxygenase activity of BBOX1:AscH-:Fe2+ dimer [cytosol]
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