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Schema
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Entries
B3GAT dimers transfer GlcA to tetrasaccharide linker
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authored
[InstanceEdit:1889961] Jassal, B, 2011-11-01
catalystActivity
[CatalystActivity:1889977] galactosylgalactosylxylosylprotein 3-beta-glucuronosyltransferase activity of B3GAT dimers [Golgi membrane]
category
transition
compartment
[Compartment:20699] Golgi membrane
[Compartment:17963] Golgi lumen
created
[InstanceEdit:1889961] Jassal, B, 2011-11-01
crossReference
[DatabaseIdentifier:9941337] RHEA:24169
dbId
1889955
deleted
[Deleted:9953307] Deletion of instance: 9638064
[Deleted:9953107] Deletion of instance: 9638064
diseaseReaction
[FailedReaction:R-HSA-3560802] Defective B3GAT3 does not transfer GlcA to tetrasaccharide linker - Homo sapiens
displayName
B3GAT dimers transfer GlcA to tetrasaccharide linker
edited
[InstanceEdit:1889961] Jassal, B, 2011-11-01
eventOf
[Pathway:R-HSA-1971475] Glycosaminoglycan-protein linkage region biosynthesis - Homo sapiens
followingEvent
[Reaction:R-HSA-1971482] CSGALNACTs transfer GalNAc to CS linker glycan - Homo sapiens
[Reaction:R-HSA-9941039] FAM20B phosphorylates Xyl moiety - Homo sapiens
[Reaction:R-HSA-9953259] EXTL3 dimer transfers GlcNAc to the GAG linker - Homo sapiens
input
[DefinedSet:R-HSA-2064214] Gal-Gal-Xyl-proteins [Golgi lumen]
[SimpleEntity:R-ALL-1889970] UDP-GlcA [Golgi lumen]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:1889979] Structural basis for acceptor substrate recognition of a human glucuronyltransferase, GlcAT-P, an enzyme critical in the biosynthesis of the carbohydrate epitope HNK-1
[LiteratureReference:1889974] Molecular cloning and expression of glucuronyltransferase I involved in the biosynthesis of the glycosaminoglycan-protein linkage region of proteoglycans
[LiteratureReference:1889986] Structure/function of the human Ga1beta1,3-glucuronosyltransferase. Dimerization and functional activity are mediated by two crucial cysteine residues
[LiteratureReference:1889985] Cloning, characterization, and chromosome mapping of the human GlcAT-S gene
maxDepth
1
modified
[InstanceEdit:10914110] Weiser, Joel, 2026-03-16
name
B3GAT dimers transfer GlcA to tetrasaccharide linker
A glucuronate moiety is the fourth addition to the tetrasaccharide linker
orthologousEvent
[Reaction:R-BTA-1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - Bos taurus
[Reaction:R-CEL-1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - Caenorhabditis elegans
[Reaction:R-DME-1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - Drosophila melanogaster
[Reaction:R-GGA-1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - Gallus gallus
[Reaction:R-XTR-1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - Xenopus tropicalis
[Reaction:R-DRE-1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - Danio rerio
[Reaction:R-SSC-1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - Sus scrofa
[Reaction:R-CFA-1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - Canis familiaris
[Reaction:R-MMU-1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - Mus musculus
output
[DefinedSet:R-HSA-2064225] GlcA-Gal-Gal-Xyl-proteins [Golgi lumen]
[SimpleEntity:R-ALL-425969] H+ [Golgi lumen]
[SimpleEntity:R-ALL-205687] UDP [Golgi lumen]
precedingEvent
[Reaction:R-HSA-1889978] B3GALT6 transfers Gal to the tetrasaccharide linker - Homo sapiens
previousReviewStatus
[ReviewStatus:9821385] four stars
releaseDate
2012-06-12
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:2172129] D'Eustachio, P, 2012-03-28
[InstanceEdit:9941989] D'Eustachio, Peter, 2025-03-12
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-1889955
summation
[Summation:1889959] Galactosylgalactosylxylosylprotein 3-beta-glucuronosyltransf...
updateTrackers
[UpdateTracker:9953561] Update Tracker - [Reaction:1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - v93:[modifyText, removeOutput]
[UpdateTracker:9785950] Update Tracker - [Reaction:1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - v50:[modifyText]
[UpdateTracker:9778508] Update Tracker - [Reaction:1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - v68:[modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9953561] Update Tracker - [Reaction:1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - v93:[modifyText, removeOutput]
[UpdateTracker:9785950] Update Tracker - [Reaction:1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - v50:[modifyText]
[UpdateTracker:9778508] Update Tracker - [Reaction:1889955] B3GAT dimers transfer GlcA to tetrasaccharide linker - v68:[modifyText]
(replacementInstances)
[Deleted:9953307] Deletion of instance: 9638064
[Deleted:9953107] Deletion of instance: 9638064
(normalReaction)
[FailedReaction:R-HSA-3560802] Defective B3GAT3 does not transfer GlcA to tetrasaccharide linker
(hasEvent)
[Pathway:R-HSA-1971475] Glycosaminoglycan-protein linkage region biosynthesis
(precedingEvent)
[Reaction:R-HSA-1971482] CSGALNACTs transfer GalNAc to CS linker glycan
[Reaction:R-HSA-9941039] FAM20B phosphorylates Xyl moiety
[Reaction:R-HSA-9953259] EXTL3 dimer transfers GlcNAc to the GAG linker
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