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ACAA1 [peroxisomal matrix]
Stable Identifier
R-HSA-390238
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
peroxisomal matrix
Synonyms
Acetyl-Coenzyme A acyltransferase 1, 3-ketoacyl-CoA thiolase, peroxisomal
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Peroxisomal lipid metabolism (Homo sapiens)
Beta-oxidation of very long chain fatty acids (Homo sapiens)
3-ketohexacosanoyl-CoA + CoASH => tetracosanoyl-CoA + acetyl-CoA (Homo sapiens)
ACAA1 [peroxisomal matrix] (Homo sapiens)
alpha-linolenic (omega3) and linoleic (omega6) acid metabolism (Homo sapiens)
alpha-linolenic acid (ALA) metabolism (Homo sapiens)
Formation of DHA-CoA catalysed by 3-ketoacyl-CoA thiolase (Homo sapiens)
ACAA1 [peroxisomal matrix] (Homo sapiens)
Protein localization (Homo sapiens)
Peroxisomal protein import (Homo sapiens)
TYSND1 cleaves peroxisomal proteins (Homo sapiens)
TYSND1 cleaves ACAA1 (Homo sapiens)
ACAA1 [peroxisomal matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:P09110 ACAA1
Gene Names
ACAA1, ACAA, PTHIO
Chain
transit peptide:1-26, chain:27-424
Reference Genes
BioGPS Gene:30 ACAA1
COSMIC (genes):ACAA1 ACAA1
CTD Gene:30 ACAA1
dbSNP Gene:30 ACAA1
ENSEMBL:ENSG00000060971 ACAA1
ENSEMBL:ENSG00000060971.19 ACAA1
HGNC:82 ACAA1
KEGG Gene (Homo sapiens):30 ACAA1
Monarch:30 ACAA1
NCBI Gene:30 ACAA1
OMIM:604054 ACAA1
UCSC:P09110 ACAA1
Reference Transcript
RefSeq:NM_001607.3 ACAA1
RefSeq:NM_001130410.1 ACAA1
Other Identifiers
11720921_s_at
11730542_x_at
11745824_x_at
11746655_a_at
11746656_x_at
16952244
202025_PM_x_at
202025_x_at
214274_PM_s_at
214274_s_at
2669536
2669537
2669538
2669542
2669543
2669545
2669547
2669549
2669551
2669553
2669554
2669557
2669559
2669561
2669562
2669563
30
36417_s_at
40415_at
8086201
A_23_P69339
GE58258
GO:0000038
GO:0003824
GO:0003985
GO:0003988
GO:0005515
GO:0005576
GO:0005777
GO:0005782
GO:0005829
GO:0006629
GO:0006631
GO:0006635
GO:0008206
GO:0008775
GO:0010124
GO:0016020
GO:0016401
GO:0016491
GO:0016740
GO:0016746
GO:0016747
GO:0031410
GO:0033540
GO:0035580
GO:0036109
GO:0043226
GO:0050633
HMNXSV003012662
HMNXSV003016276
Hs.200188.5.A1_3p_s_at
ILMN_1738921
PH_hs_0010007
TC03002862.hg
X14813_at
g6598316_3p_s_at
Participates
as an output of
TYSND1 cleaves ACAA1 (Homo sapiens)
Other forms of this molecule
ACAA1(1-26) [peroxisomal matrix]
ACAA1(1-424) [peroxisomal matrix]
ACAA1(1-424) [cytosol]
ACAA1 [extracellular region]
ACAA1 [specific granule lumen]
Inferred To
zgc:92385 [peroxisomal matrix]
(Danio rerio)
ACAA1 [peroxisomal matrix]
(Bos taurus)
ACAA1 [peroxisomal matrix]
(Canis familiaris)
ACAA1 [peroxisomal matrix]
(Dictyostelium discoideum)
ACAA1 [peroxisomal matrix]
(Gallus gallus)
ACAA1 [peroxisomal matrix]
(Mus musculus)
ACAA1 [peroxisomal matrix]
(Rattus norvegicus)
ACAA1 [peroxisomal matrix]
(Sus scrofa)
POT1 [peroxisomal matrix]
(Saccharomyces cerevisiae)
acaa1 [peroxisomal matrix]
(Xenopus tropicalis)
Cross References
RefSeq
NP_001598.1
,
NP_001123882.1
OpenTargets
ENSG00000060971
IntEnz
2.3.1.9
GeneCards
P09110
HPA
ENSG00000060971-ACAA1
Ensembl
ENST00000333167
,
ENSG00000060971
,
ENSP00000301810
,
ENSP00000333664
,
ENST00000301810
PRO
P09110
Pharos - Targets
P09110
Orphanet
24322
PDB
2IIK
HMDB Protein
HMDBP00045
Interactors (3)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q12800 TFCP2
0.556
3
UniProt:Q9BSK4 FEM1A
1
FEM1A [cytosol]
(R-HSA-8863141)
0.556
3
UniProt:Q9NSY1 BMP2K
0.488
2
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