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GlcA-Gal-Gal-Xyl-CSPG4
Stable Identifier
R-HSA-2064190
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
Golgi lumen
Synonyms
CSPG4, Chondroitin sulfate proteoglycan 4, CSPG4_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
A tetrasaccharide linker sequence is required for GAG synthesis (Homo sapiens)
B3GATs transfer GlcA to tetrasaccharide linker (Homo sapiens)
GlcA-Gal-Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Homo sapiens)
Chondroitin sulfate biosynthesis (Homo sapiens)
The addition of GalNAc to the terminal glucuronate residue forms chondroitin (Homo sapiens)
GlcA-Gal-Gal-Xyl-CS proteins [Golgi lumen] (Homo sapiens)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Homo sapiens)
Heparan sulfate/heparin (HS-GAG) metabolism (Homo sapiens)
A tetrasaccharide linker sequence is required for GAG synthesis (Homo sapiens)
B3GATs transfer GlcA to tetrasaccharide linker (Homo sapiens)
GlcA-Gal-Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q6UVK1 CSPG4
Gene Names
CSPG4, MCSP
Chain
signal peptide:1-29, chain:30-2322
Reference Genes
BioGPS Gene:1464 CSPG4
COSMIC (genes):CSPG4 CSPG4
CTD Gene:1464 CSPG4
dbSNP Gene:1464 CSPG4
ENSEMBL:ENSG00000173546 CSPG4
HGNC:2466 CSPG4
KEGG Gene (Homo sapiens):hsa:1464 CSPG4
Monarch:1464 CSPG4
NCBI Gene:1464 CSPG4
OMIM:601172 CSPG4
UCSC:Q6UVK1 CSPG4
Reference Transcript
RefSeq:NM_001897.4 CSPG4
Other Identifiers
0000130435
110_at
11739547_at
11739548_at
1464
16189
16811858
17121214
17121220
204736_s_at
214297_at
2951
3603037
3603038
3603045
3603046
3603052
3603053
3603058
3603081
3604691
3604754
3604759
3604841
3604889
3605115
3606195
3633579
3633580
3633582
3633584
3633585
3633586
3633591
3633593
3633594
3633595
3633596
3633598
3633607
3633608
3636033
3636789
38004_at
4038921
4039468
42785
50008
7990545
A_23_P21976
CAB016189
CCDS10284
CSPG4
CSPG4-201
ENSG00000173546
ENSP00000312506
ENST00000308508
EntrezGene:1464
g4503098_3p_a_at
GE60186
GO:0000187
GO:0001525
GO:0004871
GO:0005576
GO:0005796
GO:0005886
GO:0005887
GO:0005925
GO:0007165
GO:0007169
GO:0007275
GO:0008283
GO:0008347
GO:0009986
GO:0016020
GO:0016021
GO:0016324
GO:0019901
GO:0030154
GO:0030203
GO:0030206
GO:0030207
GO:0030208
GO:0031012
GO:0031258
GO:0035556
GO:0042995
GO:0043202
GO:0048771
GO:0050731
GO:0070062
HGNC:2466
HPA002951
HPA042785
HPA050008
Hs.513044
Hs.9004.1.S1_3p_at
ILMN_1666894
MIM:601172
NM_001897
NP_001888
PF00054
PF02210
PF16184
PH_hs_0025491
SM00282
TC15001670.hg
uc002baw.3
UPI00001AEEB6
X96753_at
Participant Of
hasMember
GlcA-Gal-Gal-Xyl-CS proteins [Golgi lumen]
GlcA-Gal-Gal-Xyl-proteins [Golgi lumen]
Other forms of this molecule
D2,4,4(S)3-CSPG4 [lysosomal lumen]
D2,4(S)2-CSPG4 [lysosomal lumen]
D4S-CSPG4 [lysosomal lumen]
CSPG4 [lysosomal lumen]
CSE-CSPG4 [lysosomal lumen]
C6S-CSPG4 [lysosomal lumen]
C4S-CSPG4 [lysosomal lumen]
CSE-CSPG4 [extracellular region]
C6S-CSPG4 [extracellular region]
C4S-CSPG4 [extracellular region]
CSE-CSPG4 [Golgi lumen]
XylS-CSPG4 [Golgi lumen]
Gal-Xyl-CSPG4 [Golgi lumen]
CSPG4 [Golgi lumen]
Gal-Gal-Xyl-CSPG4 [Golgi lumen]
D2,4(S)2-CSPG4 [Golgi lumen]
dermatan-CSPG4 [Golgi lumen]
D4S-CSPG4 [Golgi lumen]
D2,4,4(S)3-CSPG4 [Golgi lumen]
chondroitin(3)-CSPG4 [Golgi lumen]
C4S-CSPG4 [Golgi lumen]
chondroitin(2)-CSPG4 [Golgi lumen]
chondroitin(1)-CSPG4 [Golgi lumen]
D2,4,4(S)3-CSPG4 [extracellular region]
D2,4(S)2-CSPG4 [extracellular region]
D4S-CSPG4 [extracellular region]
C6S-CSPG4 [Golgi lumen]
Inferred To
Homologues of GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Canis familiaris)
Homologues of GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Drosophila melanogaster)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Bos taurus)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Canis familiaris)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Danio rerio)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Drosophila melanogaster)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Gallus gallus)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Mus musculus)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Rattus norvegicus)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Sus scrofa)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Taeniopygia guttata)
GlcA-Gal-Gal-Xyl-CSPG4 [Golgi lumen] (Xenopus tropicalis)
Modified Residues
Name
O-xylosyl-L-serine (ChEBI:63505) at unknown position
Modification
beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
PsiMod Name
O-xylosyl-L-serine
PsiMod Definition
A protein modification that effectively converts an L-serine residue to O3-xylosylserine.
Cross References
RefSeq
NP_001888.2
GeneCards
Q6UVK1
PRO
Q6UVK1
HMDB Protein
HMDBP10791
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