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C6S-BGN
Stable Identifier
R-HSA-2064017
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
extracellular region
Synonyms
_BGN, Biglycan, PGS1_HUMAN, BGN
Locations in the PathwayBrowser
Expand all
Extracellular matrix organization (Homo sapiens)
ECM proteoglycans (Homo sapiens)
BGN binds Collagen types I, VI, (IX) (Homo sapiens)
BGN [extracellular region] (Homo sapiens)
C6S-BGN [extracellular region] (Homo sapiens)
BGN:Collagen types I, VI, (IX) [extracellular region] (Homo sapiens)
BGN [extracellular region] (Homo sapiens)
C6S-BGN [extracellular region] (Homo sapiens)
BGN binds Collagen types II, III (Homo sapiens)
BGN [extracellular region] (Homo sapiens)
C6S-BGN [extracellular region] (Homo sapiens)
BGN:Collagen types II, III [extracellular region] (Homo sapiens)
BGN [extracellular region] (Homo sapiens)
C6S-BGN [extracellular region] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
CS/DS degradation (Homo sapiens)
DSPG and CSPG translocate to the lysosome for degradation (Homo sapiens)
CSPGs [extracellular region] (Homo sapiens)
C6S-PGs [extracellular region] (Homo sapiens)
C6S-BGN [extracellular region] (Homo sapiens)
Chondroitin sulfate biosynthesis (Homo sapiens)
CSPG is secreted (Homo sapiens)
CSPGs [extracellular region] (Homo sapiens)
C6S-PGs [extracellular region] (Homo sapiens)
C6S-BGN [extracellular region] (Homo sapiens)
External Reference Information
External Reference
UniProt:P21810 BGN
Gene Names
BGN, SLRR1A
Chain
signal peptide:1-16, propeptide:17-37, chain:38-368
Reference Genes
BioGPS Gene:633 BGN
COSMIC (genes):BGN BGN
CTD Gene:633 BGN
dbSNP Gene:633 BGN
ENSEMBL:ENSG00000182492 BGN
HGNC:1044 BGN
KEGG Gene (Homo sapiens):hsa:633 BGN
Monarch:633 BGN
NCBI Gene:633 BGN
OMIM:301870 BGN
UCSC:P21810 BGN
Reference Transcript
RefSeq:NM_001711.5 BGN
RefSeq:XM_017029724.1 BGN
Other Identifiers
0002030280
11721244_a_at
11721245_s_at
11721246_x_at
11749066_s_at
11751483_s_at
11751484_x_at
11752779_x_at
17108003
201261_x_at
201262_s_at
213905_x_at
3157
3678
38126_at
3995635
3995641
3995642
3995643
3995644
3995650
3995651
3995654
3995655
3995657
3995658
3995659
3995660
3995661
3995662
3995663
3995664
633
74989_at
8170648
89603_at
A_23_P34126
BGN
BGN-201
CAB003678
CCDS14721
ENSG00000182492
ENSP00000327336
ENST00000331595
EntrezGene:633
g12803216_3p_a_at
g4502402_3p_a_at
g4502402_3p_x_at
GE57511
GO:0001974
GO:0004860
GO:0005201
GO:0005539
GO:0005576
GO:0005578
GO:0005615
GO:0005622
GO:0005737
GO:0005796
GO:0006469
GO:0008150
GO:0009986
GO:0019221
GO:0019800
GO:0030133
GO:0030198
GO:0030203
GO:0030206
GO:0030207
GO:0030208
GO:0031012
GO:0042383
GO:0043202
GO:0046426
GO:0050840
GO:0070062
HGNC:1044
HPA003157
Hs.821
Hs.821.1.A1_3p_a_at
ILMN_1709139
ILMN_2206746
J04599_at
MIM:300106
MIM:300989
MIM:301870
NM_001711
NP_001702
PF01462
PF13855
PH_hs_0000098
SM00013
SM00369
TC0X000750.hg
uc004fhr.3
UPI000003BDBA
XM_017029724
XP_016885213
Participant Of
hasMember
BGN [extracellular region]
C6S-PGs [extracellular region]
Other forms of this molecule
BGN [extracellular region]
D2,4,4(S)3-BGN [lysosomal lumen]
D2,4(S)2-BGN [lysosomal lumen]
D4S-BGN [lysosomal lumen]
BGN [lysosomal lumen]
CSE-BGN [lysosomal lumen]
C6S-BGN [lysosomal lumen]
C4S-BGN [lysosomal lumen]
CSE-BGN [extracellular region]
C4S-BGN [extracellular region]
CSE-BGN [Golgi lumen]
C6S-BGN [Golgi lumen]
XylS-BGN [Golgi lumen]
Gal-Xyl-BGN [Golgi lumen]
BGN [Golgi lumen]
Gal-Gal-Xyl-BGN [Golgi lumen]
GlcA-Gal-Gal-Xyl-BGN [Golgi lumen]
D2,4(S)2-BGN [Golgi lumen]
dermatan-BGN [Golgi lumen]
D4S-BGN [Golgi lumen]
D2,4,4(S)3-BGN [Golgi lumen]
chondroitin(3)-BGN [Golgi lumen]
C4S-BGN [Golgi lumen]
chondroitin(2)-BGN [Golgi lumen]
chondroitin(1)-BGN [Golgi lumen]
D2,4,4(S)3-BGN [extracellular region]
D2,4(S)2-BGN [extracellular region]
D4S-BGN [extracellular region]
Inferred To
C6S-BGN [extracellular region] (Bos taurus)
C6S-BGN [extracellular region] (Canis familiaris)
C6S-BGN [extracellular region] (Danio rerio)
C6S-BGN [extracellular region] (Mus musculus)
C6S-BGN [extracellular region] (Rattus norvegicus)
C6S-BGN [extracellular region] (Sus scrofa)
C6S-BGN [extracellular region] (Xenopus tropicalis)
Homologues of C6S-BGN [extracellular region] (Danio rerio)
Homologues of C6S-BGN [extracellular region] (Sus scrofa)
Homologues of C6S-BGN [extracellular region] (Xenopus tropicalis)
Modified Residues
Name
O-xylosyl-L-serine (ChEBI:63512) at unknown position
Modification
beta-D-GalNAc-(1->4)-beta-D-GlcA-(1->3)-beta-D-GalNAc6S-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
PsiMod Name
O-xylosyl-L-serine
PsiMod Definition
A protein modification that effectively converts an L-serine residue to O3-xylosylserine.
Cross References
RefSeq
NP_001702.1
,
XP_016885213.1
GeneCards
P21810
PRO
P21810
Orphanet
23903
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