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CAR [mitochondrial matrix]
Stable Identifier
R-ALL-201023
Type
Chemical Compound [SimpleEntity]
Compartment
mitochondrial matrix
Synonyms
(R)-carnitine, gamma-Trimethyl-hydroxybutyrobetaine, carnitine, 3-Hydroxy-4-trimethylammoniobutanoate
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Saccharomyces cerevisiae
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of amino acids and derivatives (Bos taurus)
Branched-chain amino acid catabolism (Bos taurus)
CRAT transfers ISB to CAR (Bos taurus)
CAR [mitochondrial matrix]
Metabolism of lipids (Bos taurus)
Fatty acid metabolism (Bos taurus)
Carnitine shuttle (Bos taurus)
CPT2 converts acylcarnitine to acyl-CoA (Bos taurus)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Bos taurus)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Bos taurus)
CAR [mitochondrial matrix]
Metabolism (Caenorhabditis elegans)
Metabolism of amino acids and derivatives (Caenorhabditis elegans)
Branched-chain amino acid catabolism (Caenorhabditis elegans)
CRAT transfers ISB to CAR (Caenorhabditis elegans)
CAR [mitochondrial matrix]
Metabolism of lipids (Caenorhabditis elegans)
Fatty acid metabolism (Caenorhabditis elegans)
Carnitine shuttle (Caenorhabditis elegans)
CPT2 converts acylcarnitine to acyl-CoA (Caenorhabditis elegans)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Caenorhabditis elegans)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Caenorhabditis elegans)
CAR [mitochondrial matrix]
Metabolism (Canis familiaris)
Metabolism of amino acids and derivatives (Canis familiaris)
Branched-chain amino acid catabolism (Canis familiaris)
CRAT transfers ISB to CAR (Canis familiaris)
CAR [mitochondrial matrix]
Metabolism of lipids (Canis familiaris)
Fatty acid metabolism (Canis familiaris)
Carnitine shuttle (Canis familiaris)
CPT2 converts acylcarnitine to acyl-CoA (Canis familiaris)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Canis familiaris)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Canis familiaris)
CAR [mitochondrial matrix]
Metabolism (Danio rerio)
Metabolism of amino acids and derivatives (Danio rerio)
Branched-chain amino acid catabolism (Danio rerio)
CRAT transfers ISB to CAR (Danio rerio)
CAR [mitochondrial matrix]
Metabolism of lipids (Danio rerio)
Fatty acid metabolism (Danio rerio)
Carnitine shuttle (Danio rerio)
CPT2 converts acylcarnitine to acyl-CoA (Danio rerio)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Danio rerio)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Danio rerio)
CAR [mitochondrial matrix]
Metabolism (Drosophila melanogaster)
Metabolism of amino acids and derivatives (Drosophila melanogaster)
Branched-chain amino acid catabolism (Drosophila melanogaster)
CRAT transfers ISB to CAR (Drosophila melanogaster)
CAR [mitochondrial matrix]
Metabolism of lipids (Drosophila melanogaster)
Fatty acid metabolism (Drosophila melanogaster)
Carnitine shuttle (Drosophila melanogaster)
CPT2 converts acylcarnitine to acyl-CoA (Drosophila melanogaster)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Drosophila melanogaster)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Drosophila melanogaster)
CAR [mitochondrial matrix]
Metabolism (Gallus gallus)
Metabolism of amino acids and derivatives (Gallus gallus)
Branched-chain amino acid catabolism (Gallus gallus)
CRAT transfers ISB to CAR (Gallus gallus)
CAR [mitochondrial matrix]
Metabolism of lipids (Gallus gallus)
Fatty acid metabolism (Gallus gallus)
Carnitine shuttle (Gallus gallus)
CPT2 converts acylcarnitine to acyl-CoA (Gallus gallus)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Gallus gallus)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Gallus gallus)
CAR [mitochondrial matrix]
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Branched-chain amino acid catabolism (Homo sapiens)
CRAT transfers ISB to CAR (Homo sapiens)
CAR [mitochondrial matrix]
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Carnitine shuttle (Homo sapiens)
CPT2 converts acylcarnitine to acyl-CoA (Homo sapiens)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Homo sapiens)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Homo sapiens)
CAR [mitochondrial matrix]
Metabolism (Mus musculus)
Metabolism of amino acids and derivatives (Mus musculus)
Branched-chain amino acid catabolism (Mus musculus)
CRAT transfers ISB to CAR (Mus musculus)
CAR [mitochondrial matrix]
Metabolism of lipids (Mus musculus)
Fatty acid metabolism (Mus musculus)
Carnitine shuttle (Mus musculus)
CPT2 converts acylcarnitine to acyl-CoA (Mus musculus)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Mus musculus)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Mus musculus)
CAR [mitochondrial matrix]
Metabolism (Rattus norvegicus)
Metabolism of amino acids and derivatives (Rattus norvegicus)
Branched-chain amino acid catabolism (Rattus norvegicus)
CRAT transfers ISB to CAR (Rattus norvegicus)
CAR [mitochondrial matrix]
Metabolism of lipids (Rattus norvegicus)
Fatty acid metabolism (Rattus norvegicus)
Carnitine shuttle (Rattus norvegicus)
CPT2 converts acylcarnitine to acyl-CoA (Rattus norvegicus)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Rattus norvegicus)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Rattus norvegicus)
CAR [mitochondrial matrix]
Metabolism (Saccharomyces cerevisiae)
Metabolism of amino acids and derivatives (Saccharomyces cerevisiae)
Branched-chain amino acid catabolism (Saccharomyces cerevisiae)
CRAT transfers ISB to CAR (Saccharomyces cerevisiae)
CAR [mitochondrial matrix]
Metabolism of lipids (Saccharomyces cerevisiae)
Fatty acid metabolism (Saccharomyces cerevisiae)
Carnitine shuttle (Saccharomyces cerevisiae)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Saccharomyces cerevisiae)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Saccharomyces cerevisiae)
CAR [mitochondrial matrix]
Metabolism (Sus scrofa)
Metabolism of amino acids and derivatives (Sus scrofa)
Branched-chain amino acid catabolism (Sus scrofa)
CRAT transfers ISB to CAR (Sus scrofa)
CAR [mitochondrial matrix]
Metabolism of lipids (Sus scrofa)
Fatty acid metabolism (Sus scrofa)
Carnitine shuttle (Sus scrofa)
CPT2 converts acylcarnitine to acyl-CoA (Sus scrofa)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Sus scrofa)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Sus scrofa)
CAR [mitochondrial matrix]
Metabolism (Xenopus tropicalis)
Metabolism of amino acids and derivatives (Xenopus tropicalis)
Branched-chain amino acid catabolism (Xenopus tropicalis)
CRAT transfers ISB to CAR (Xenopus tropicalis)
CAR [mitochondrial matrix]
Metabolism of lipids (Xenopus tropicalis)
Fatty acid metabolism (Xenopus tropicalis)
Carnitine shuttle (Xenopus tropicalis)
CPT2 converts acylcarnitine to acyl-CoA (Xenopus tropicalis)
CAR [mitochondrial matrix]
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Xenopus tropicalis)
CAR [mitochondrial matrix]
SLC25A20 exports excess acyl-CAR (Xenopus tropicalis)
CAR [mitochondrial matrix]
External Reference Information
External Reference
(R)-carnitine [ChEBI:16347]
Participates
as an input of
CRAT transfers ISB to CAR (Danio rerio)
CRAT transfers ISB to CAR (Homo sapiens)
CRAT transfers ISB to CAR (Mus musculus)
CRAT transfers ISB to CAR (Rattus norvegicus)
CRAT transfers ISB to CAR (Canis familiaris)
CRAT transfers ISB to CAR (Bos taurus)
CRAT transfers ISB to CAR (Sus scrofa)
CRAT transfers ISB to CAR (Xenopus tropicalis)
CRAT transfers ISB to CAR (Gallus gallus)
CRAT transfers ISB to CAR (Drosophila melanogaster)
CRAT transfers ISB to CAR (Caenorhabditis elegans)
CRAT transfers ISB to CAR (Saccharomyces cerevisiae)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Canis familiaris)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Homo sapiens)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Mus musculus)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Rattus norvegicus)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Bos taurus)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Sus scrofa)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Danio rerio)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Xenopus tropicalis)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Gallus gallus)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Drosophila melanogaster)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Caenorhabditis elegans)
Exchange of acylcarnitine and carnitine across the inner mitochondrial membrane (Saccharomyces cerevisiae)
as an output of
SLC25A20 exports excess acyl-CAR (Saccharomyces cerevisiae)
SLC25A20 exports excess acyl-CAR (Caenorhabditis elegans)
CPT2 converts acylcarnitine to acyl-CoA (Canis familiaris)
CPT2 converts acylcarnitine to acyl-CoA (Homo sapiens)
CPT2 converts acylcarnitine to acyl-CoA (Mus musculus)
CPT2 converts acylcarnitine to acyl-CoA (Rattus norvegicus)
CPT2 converts acylcarnitine to acyl-CoA (Bos taurus)
CPT2 converts acylcarnitine to acyl-CoA (Sus scrofa)
CPT2 converts acylcarnitine to acyl-CoA (Danio rerio)
CPT2 converts acylcarnitine to acyl-CoA (Xenopus tropicalis)
CPT2 converts acylcarnitine to acyl-CoA (Gallus gallus)
CPT2 converts acylcarnitine to acyl-CoA (Drosophila melanogaster)
CPT2 converts acylcarnitine to acyl-CoA (Caenorhabditis elegans)
SLC25A20 exports excess acyl-CAR (Homo sapiens)
SLC25A20 exports excess acyl-CAR (Mus musculus)
SLC25A20 exports excess acyl-CAR (Rattus norvegicus)
SLC25A20 exports excess acyl-CAR (Canis familiaris)
SLC25A20 exports excess acyl-CAR (Bos taurus)
SLC25A20 exports excess acyl-CAR (Sus scrofa)
SLC25A20 exports excess acyl-CAR (Danio rerio)
SLC25A20 exports excess acyl-CAR (Xenopus tropicalis)
SLC25A20 exports excess acyl-CAR (Gallus gallus)
SLC25A20 exports excess acyl-CAR (Drosophila melanogaster)
Other forms of this molecule
CAR [extracellular region]
CAR [cytosol]
CAR [mitochondrial intermembrane space]
CAR [peroxisomal matrix]
Cross References
Guide to Pharmacology - Ligands
4780
COMPOUND
C00487
,
C00318
HMDB Metabolite
HMDB0000062
ZINC
ZINC000003079340
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