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Schema
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Pathway
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Entries
Mitochondrial Fatty Acid Beta-Oxidation
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authored
[InstanceEdit:77247] Gillespie, ME, 2003-09-19 00:00:00
compartment
[Compartment:5460] mitochondrial matrix
created
[InstanceEdit:77247] Gillespie, ME, 2003-09-19 00:00:00
dbId
77289
displayName
Mitochondrial Fatty Acid Beta-Oxidation
doi
10.3180/REACT_1473.1
edited
[InstanceEdit:165085] Gillespie, ME, 0000-00-00 00:00:00
eventOf
[Pathway:R-HSA-8978868] Fatty acid metabolism - Homo sapiens
goBiologicalProcess
[GO_BiologicalProcess:20426] fatty acid beta-oxidation
hasDiagram
true
hasEHLD
false
hasEvent
[Pathway:R-HSA-77286] mitochondrial fatty acid beta-oxidation of saturated fatty acids - Homo sapiens
[Pathway:R-HSA-77288] mitochondrial fatty acid beta-oxidation of unsaturated fatty acids - Homo sapiens
[Reaction:R-HSA-5695980] ACAD10 dehydrogenates S-2MPDA-CoA - Homo sapiens
[Reaction:R-HSA-5695989] ACAD11 dehydrogenates BH-CoA - Homo sapiens
[Pathway:R-HSA-71032] Propionyl-CoA catabolism - Homo sapiens
[Reaction:R-HSA-8874745] ACAA2 tetramer transfers acyl group from Ac-CoA to acyl-CoA forming 3OA-CoA and CoA-SH - Homo sapiens
[Reaction:R-HSA-8933547] MCAT transfers Mal from Mal-CoA to NDUFAB1 - Homo sapiens
[Reaction:R-HSA-5696004] ACSF2 ligates CoA-SH to MCFA - Homo sapiens
[Reaction:R-HSA-5690066] ACOT2,9,THEM4,5 hydrolyse MCFA-CoA, LCFA-CoA - Homo sapiens
[Reaction:R-HSA-5690043] Cytosolic ACOTs hydrolyse MCFA-CoA, LCFA-CoA - Homo sapiens
[Reaction:R-HSA-8848250] ACBD6 binds LCFA-CoA - Homo sapiens
[Reaction:R-HSA-8848246] DBI, ACBD7 bind MCFA-CoA and LCFA-CoA - Homo sapiens
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:77290] Recent developments in the investigation of inherited metabolic disorders using cultured human cells.
[LiteratureReference:77292] Fatty acid oxidation disorders.
[LiteratureReference:77294] Molecular basis of mitochondrial fatty acid oxidation defects.
[LiteratureReference:77296] Genetic disorders of mitochondrial fatty acid oxidation.
[Book:77402] The Metabolic and Molecular Bases of Inherited Disease, 8th ed Scriver, CR Mitochondrial fatty acid oxidation disorders 0079130356
modified
[InstanceEdit:10931649] Wright, Adam, 2024-03-08
name
Mitochondrial Fatty Acid Beta-Oxidation
orthologousEvent
[Pathway:R-MMU-77289] Mitochondrial Fatty Acid Beta-Oxidation - Mus musculus
[Pathway:R-PFA-77289] Mitochondrial Fatty Acid Beta-Oxidation - Plasmodium falciparum
[Pathway:R-SCE-77289] Mitochondrial Fatty Acid Beta-Oxidation - Saccharomyces cerevisiae
[Pathway:R-SPO-77289] Mitochondrial Fatty Acid Beta-Oxidation - Schizosaccharomyces pombe
[Pathway:R-DDI-77289] Mitochondrial Fatty Acid Beta-Oxidation - Dictyostelium discoideum
[Pathway:R-CEL-77289] Mitochondrial Fatty Acid Beta-Oxidation - Caenorhabditis elegans
[Pathway:R-DME-77289] Mitochondrial Fatty Acid Beta-Oxidation - Drosophila melanogaster
[Pathway:R-GGA-77289] Mitochondrial Fatty Acid Beta-Oxidation - Gallus gallus
[Pathway:R-XTR-77289] Mitochondrial Fatty Acid Beta-Oxidation - Xenopus tropicalis
[Pathway:R-DRE-77289] Mitochondrial Fatty Acid Beta-Oxidation - Danio rerio
[Pathway:R-SSC-77289] Mitochondrial Fatty Acid Beta-Oxidation - Sus scrofa
[Pathway:R-CFA-77289] Mitochondrial Fatty Acid Beta-Oxidation - Canis familiaris
[Pathway:R-RNO-77289] Mitochondrial Fatty Acid Beta-Oxidation - Rattus norvegicus
[Pathway:R-BTA-77289] Mitochondrial Fatty Acid Beta-Oxidation - Bos taurus
releaseDate
2004-07-06
reviewStatus
[ReviewStatus:9821382] five stars
schemaClass
Pathway
species
[Species:48887] Homo sapiens
stId
R-HSA-77289
summation
[Summation:77298] Beta-oxidation begins once fatty acids have been imported in...
Referrals
(hasEvent)
[Pathway:R-HSA-8978868] Fatty acid metabolism
(normalPathway)
[Pathway:R-HSA-9759774] Diseases of mitochondrial beta oxidation
(hasEncapsulatedEvent)
[Pathway:R-HSA-196849] Metabolism of water-soluble vitamins and cofactors
[Pathway:R-HSA-163200] Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins.
[Pathway:R-HSA-9857492] Protein lipoylation
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