conversion of 3-Ureidoiosbutyrate to 3-Aminoisobutyrate

authored
catalystActivity
catalystActivityReference [CatalystActivityReference:9643299] beta-ureidopropionase activity of UPB1:Zn2+ [cytosol] beta-Ureidopropionase deficiency: an inborn error of pyrimidine degradation associated with neurological abnormalities
category transition
compartment
created [InstanceEdit:73446] Jassal, B, 2003-06-17 09:00:25
crossReference
dbId 73620
displayName conversion of 3-Ureidoiosbutyrate to 3-Aminoisobutyrate
edited
eventOf
followingEvent
input
isInDisease false
isInferred false
literatureReference
maxDepth 1
modified [InstanceEdit:10996769] Weiser, Joel, 2026-03-16
name
  • conversion of 3-Ureidoiosbutyrate to 3-Aminoisobutyrate
  • 3-(carbamoylamino)-2-methylpropanoate + H2O + 2 H(+) => (R)-3-amino-2-methylpropanoate + NH4(+) + CO2
orthologousEvent
output
precedingEvent
releaseDate 2004-07-06
reviewStatus [ReviewStatus:9821382] five stars
revised
schemaClass Reaction
species
stId R-HSA-73620
summation
updateTrackers
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