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Schema
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Reaction
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Entries
Fibrillin-1 degradation by MMP3, CTSK, CTSL2
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authored
[InstanceEdit:2426629] Jupe, S, 2012-08-08
catalystActivity
[CatalystActivity:1604695] serine-type endopeptidase activity of MMP3, CTSK, CTSL2 [extracellular region]
category
transition
compartment
[Compartment:984] extracellular region
created
[InstanceEdit:2514810] Jupe, S, 2012-10-10
dbId
2514772
displayName
Fibrillin-1 degradation by MMP3, CTSK, CTSL2
edited
[InstanceEdit:4090280] Jupe, S, 2013-08-13
eventOf
[Pathway:R-HSA-1474228] Degradation of the extracellular matrix - Homo sapiens
input
[Polymer:R-HSA-2159874] Fibrillin-1 [extracellular region]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:2485133] Fibrillin degradation by matrix metalloproteinases: implications for connective tissue remodelling
[LiteratureReference:2514804] Classical and neonatal Marfan syndrome mutations in fibrillin-1 cause differential protease susceptibilities and protein function
maxDepth
1
modified
[InstanceEdit:10996769] Weiser, Joel, 2026-03-16
name
Fibrillin-1 degradation by MMP3, CTSK, CTSL2
orthologousEvent
[Reaction:R-DDI-2514772] Fibrillin-1 degradation by MMP3, CTSK, CTSL2 - Dictyostelium discoideum
[Reaction:R-CEL-2514772] Fibrillin-1 degradation by MMP3, CTSK, CTSL2 - Caenorhabditis elegans
[Reaction:R-GGA-2514772] Fibrillin-1 degradation by MMP3, CTSK, CTSL2 - Gallus gallus
[Reaction:R-DRE-2514772] Fibrillin-1 degradation by MMP3, CTSK, CTSL2 - Danio rerio
[Reaction:R-BTA-2514772] Fibrillin-1 degradation by MMP3, CTSK, CTSL2 - Bos taurus
[Reaction:R-CFA-2514772] Fibrillin-1 degradation by MMP3, CTSK, CTSL2 - Canis familiaris
[Reaction:R-RNO-2514772] Fibrillin-1 degradation by MMP3, CTSK, CTSL2 - Rattus norvegicus
[Reaction:R-MMU-2514772] Fibrillin-1 degradation by MMP3, CTSK, CTSL2 - Mus musculus
output
[Polymer:R-HSA-2514812] Cleaved fibrillin-1 [extracellular region]
releaseDate
2013-09-18
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:4088447] Ricard-Blum, Sylvie, 2013-08-13
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-2514772
summation
[Summation:2514780] Fibrillin-1 can be degraded by MMP3 (Ashworth et al. 1999) a...
Referrals
(hasEvent)
[Pathway:R-HSA-1474228] Degradation of the extracellular matrix
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