Reactome | bHIB-CoA [mitochondrial matrix]

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bHIB-CoA [mitochondrial matrix] Show undefined attributes

compartment	[Compartment:5460] mitochondrial matrix
consumedByEvent	[FailedReaction:R-HSA-9916727] HIBCH mutants don't synthesize beta-hydroxyisobutyrate - Homo sapiens [Reaction:R-PFA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Plasmodium falciparum [Reaction:R-SCE-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Saccharomyces cerevisiae [Reaction:R-SPO-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Schizosaccharomyces pombe [Reaction:R-DDI-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Dictyostelium discoideum [Reaction:R-CEL-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Caenorhabditis elegans [Reaction:R-DME-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Drosophila melanogaster [Reaction:R-GGA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Gallus gallus [Reaction:R-DRE-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Danio rerio [Reaction:R-SSC-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Sus scrofa [Reaction:R-BTA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Bos taurus [Reaction:R-CFA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Canis familiaris [Reaction:R-RNO-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Rattus norvegicus [Reaction:R-MMU-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Mus musculus [Reaction:R-HSA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA - Homo sapiens
crossReference	[DatabaseIdentifier:38144] COMPOUND:C06000
dbId	71847
displayName	bHIB-CoA [mitochondrial matrix]
inDisease	false
maxDepth	1
modified	[InstanceEdit:9917131] Stephan, Ralf, 2024-07-30
name	bHIB-CoA beta-hydroxyisobutyryl-CoA (S)-3-hydroxyisobutyryl-CoA 3-hydroxyisobutyryl-CoA
producedByEvent	[Reaction:R-DDI-70870] ECHS1 hydrates methacrylyl-CoA - Dictyostelium discoideum [Reaction:R-CEL-70870] ECHS1 hydrates methacrylyl-CoA - Caenorhabditis elegans [Reaction:R-DME-70870] ECHS1 hydrates methacrylyl-CoA - Drosophila melanogaster [Reaction:R-GGA-70870] ECHS1 hydrates methacrylyl-CoA - Gallus gallus [Reaction:R-XTR-70870] ECHS1 hydrates methacrylyl-CoA - Xenopus tropicalis [Reaction:R-DRE-70870] ECHS1 hydrates methacrylyl-CoA - Danio rerio [Reaction:R-SSC-70870] ECHS1 hydrates methacrylyl-CoA - Sus scrofa [Reaction:R-BTA-70870] ECHS1 hydrates methacrylyl-CoA - Bos taurus [Reaction:R-CFA-70870] ECHS1 hydrates methacrylyl-CoA - Canis familiaris [Reaction:R-RNO-70870] ECHS1 hydrates methacrylyl-CoA - Rattus norvegicus [Reaction:R-MMU-70870] ECHS1 hydrates methacrylyl-CoA - Mus musculus [Reaction:R-HSA-70870] ECHS1 hydrates methacrylyl-CoA - Homo sapiens
referenceEntity	[ReferenceMolecule:chebi:62611] (S)-3-hydroxyisobutyryl-CoA(4-) [ChEBI:62611]
referenceType	ReferenceMolecule
schemaClass	SimpleEntity
stId	R-ALL-71847
updateTrackers	[UpdateTracker:9919635] Update Tracker - [SimpleEntity:71847] bHIB-CoA [mitochondrial matrix] - v90:[add_removeReferenceEntity] [UpdateTracker:9874165] Update Tracker - [SimpleEntity:71847] bHIB-CoA [mitochondrial matrix] - v43:[addName] [UpdateTracker:9891877] Update Tracker - [SimpleEntity:71847] bHIB-CoA [mitochondrial matrix] - v52:[addName]

Referrals

(updatedInstance)	[UpdateTracker:9919635] Update Tracker - [SimpleEntity:71847] bHIB-CoA [mitochondrial matrix] - v90:[add_removeReferenceEntity] [UpdateTracker:9874165] Update Tracker - [SimpleEntity:71847] bHIB-CoA [mitochondrial matrix] - v43:[addName] [UpdateTracker:9891877] Update Tracker - [SimpleEntity:71847] bHIB-CoA [mitochondrial matrix] - v52:[addName]
(input)	[FailedReaction:R-HSA-9916727] HIBCH mutants don't synthesize beta-hydroxyisobutyrate [Reaction:R-PFA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-SCE-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-SPO-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-DDI-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-CEL-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-DME-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-GGA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-DRE-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-SSC-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-BTA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-CFA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-RNO-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-MMU-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA [Reaction:R-HSA-70881] beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA
(output)	[Reaction:R-DDI-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-CEL-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-DME-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-GGA-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-XTR-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-DRE-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-SSC-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-BTA-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-CFA-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-RNO-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-MMU-70870] ECHS1 hydrates methacrylyl-CoA [Reaction:R-HSA-70870] ECHS1 hydrates methacrylyl-CoA

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