Reactome | D-methylmalonyl-CoA <=> L-methylmalonyl-CoA

D-methylmalonyl-CoA <=> L-methylmalonyl-CoA

Stable Identifier

R-HSA-71020

Type

Reaction

Species

Homo sapiens

Compartment

mitochondrial matrix

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D-methylmalonyl-CoA <=> L-methylmalonyl-CoA

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The layout of this reaction may differ from that in the pathway view due to the constraints in pathway layout

At the beginning of this reaction, 1 molecule of 'D-methylmalonyl-CoA' is present. At the end of this reaction, 1 molecule of 'L-methylmalonyl-CoA' is present.

This reaction takes place in the 'mitochondrial matrix' and is mediated by the 'methylmalonyl-CoA epimerase activity' of 'methylmalonyl-CoA epimerase'.

Literature References

PubMed ID	Title	Journal	Year
	The Metabolic and Molecular Bases of Inherited Disease, 8th ed Beaudet, AL, Scriver, CR, Sly, WS, Valle, D		2001
11481338	Identification of the human methylmalonyl-CoA racemase gene based on the analysis of prokaryotic gene arrangements. Implications for decoding the human genome. Bobik, TA, Rasche, ME	J Biol Chem	2001
13934211	Metabolism of propionic acid in animal tissues. IX. Methylmalonyl coenzyme A racemase Sasakawa, T, Ochoa, S, Mazumder, R, Kaziro, Y	J Biol Chem	1962