Reactome | D-methylmalonyl-CoA <=> L-methylmalonyl-CoA

D-methylmalonyl-CoA <=> L-methylmalonyl-CoA

Stable Identifier

R-HSA-71020

Type

Reaction [transition]

Species

Homo sapiens

Compartment

mitochondrial matrix

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D-methylmalonyl-CoA <=> L-methylmalonyl-CoA

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The layout of this reaction may differ from that in the pathway view due to the constraints in pathway layout

At the beginning of this reaction, 1 molecule of 'D-methylmalonyl-CoA' is present. At the end of this reaction, 1 molecule of 'L-methylmalonyl-CoA' is present.

This reaction takes place in the 'mitochondrial matrix' and is mediated by the 'methylmalonyl-CoA epimerase activity' of 'methylmalonyl-CoA epimerase'.

Literature References

PubMed ID	Title	Journal	Year
11481338	Identification of the human methylmalonyl-CoA racemase gene based on the analysis of prokaryotic gene arrangements. Implications for decoding the human genome. Bobik, TA, Rasche, ME	J Biol Chem	2001
	The Metabolic and Molecular Bases of Inherited Disease, 8th ed Scriver, CR, Beaudet, AL, Valle, D, Sly, WS		2001
13934211	Metabolism of propionic acid in animal tissues. IX. Methylmalonyl coenzyme A racemase Mazumder, R, Sasakawa, T, Kaziro, Y, Ochoa, S	J Biol Chem	1962