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L-MM-CoA [mitochondrial matrix]
Stable Identifier
R-ALL-71009
Type
Chemical Compound [SimpleEntity]
Compartment
mitochondrial matrix
Synonyms
L-methylmalonyl-CoA, (R)-methylmalonyl-CoA, (R)-2-methyl-3-oxopropanoyl-CoA
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of lipids (Bos taurus)
Fatty acid metabolism (Bos taurus)
Mitochondrial Fatty Acid Beta-Oxidation (Bos taurus)
Propionyl-CoA catabolism (Bos taurus)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Bos taurus)
L-MM-CoA [mitochondrial matrix]
MUT isomerises L-MM-CoA to SUCC-CoA (Bos taurus)
L-MM-CoA [mitochondrial matrix]
Metabolism (Caenorhabditis elegans)
Metabolism of lipids (Caenorhabditis elegans)
Fatty acid metabolism (Caenorhabditis elegans)
Mitochondrial Fatty Acid Beta-Oxidation (Caenorhabditis elegans)
Propionyl-CoA catabolism (Caenorhabditis elegans)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Caenorhabditis elegans)
L-MM-CoA [mitochondrial matrix]
MUT isomerises L-MM-CoA to SUCC-CoA (Caenorhabditis elegans)
L-MM-CoA [mitochondrial matrix]
Metabolism (Canis familiaris)
Metabolism of lipids (Canis familiaris)
Fatty acid metabolism (Canis familiaris)
Mitochondrial Fatty Acid Beta-Oxidation (Canis familiaris)
Propionyl-CoA catabolism (Canis familiaris)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Canis familiaris)
L-MM-CoA [mitochondrial matrix]
MUT isomerises L-MM-CoA to SUCC-CoA (Canis familiaris)
L-MM-CoA [mitochondrial matrix]
Metabolism (Danio rerio)
Metabolism of lipids (Danio rerio)
Fatty acid metabolism (Danio rerio)
Mitochondrial Fatty Acid Beta-Oxidation (Danio rerio)
Propionyl-CoA catabolism (Danio rerio)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Danio rerio)
L-MM-CoA [mitochondrial matrix]
MUT isomerises L-MM-CoA to SUCC-CoA (Danio rerio)
L-MM-CoA [mitochondrial matrix]
Metabolism (Dictyostelium discoideum)
Metabolism of lipids (Dictyostelium discoideum)
Fatty acid metabolism (Dictyostelium discoideum)
Mitochondrial Fatty Acid Beta-Oxidation (Dictyostelium discoideum)
Propionyl-CoA catabolism (Dictyostelium discoideum)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Dictyostelium discoideum)
L-MM-CoA [mitochondrial matrix]
Metabolism (Gallus gallus)
Metabolism of lipids (Gallus gallus)
Fatty acid metabolism (Gallus gallus)
Mitochondrial Fatty Acid Beta-Oxidation (Gallus gallus)
Propionyl-CoA catabolism (Gallus gallus)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Gallus gallus)
L-MM-CoA [mitochondrial matrix]
MUT isomerises L-MM-CoA to SUCC-CoA (Gallus gallus)
L-MM-CoA [mitochondrial matrix]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of mitochondrial beta oxidation (Homo sapiens)
Diseases of propionyl-CoA catabolism (Homo sapiens)
Defective MUT causes MMAM (Homo sapiens)
Defective MUT does not isomerise L-MM-CoA to SUCC-CoA (Homo sapiens)
L-MM-CoA [mitochondrial matrix]
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
Propionyl-CoA catabolism (Homo sapiens)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Homo sapiens)
L-MM-CoA [mitochondrial matrix]
MUT isomerises L-MM-CoA to SUCC-CoA (Homo sapiens)
L-MM-CoA [mitochondrial matrix]
Metabolism (Mus musculus)
Metabolism of lipids (Mus musculus)
Fatty acid metabolism (Mus musculus)
Mitochondrial Fatty Acid Beta-Oxidation (Mus musculus)
Propionyl-CoA catabolism (Mus musculus)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Mus musculus)
L-MM-CoA [mitochondrial matrix]
MUT isomerises L-MM-CoA to SUCC-CoA (Mus musculus)
L-MM-CoA [mitochondrial matrix]
Metabolism (Rattus norvegicus)
Metabolism of lipids (Rattus norvegicus)
Fatty acid metabolism (Rattus norvegicus)
Mitochondrial Fatty Acid Beta-Oxidation (Rattus norvegicus)
Propionyl-CoA catabolism (Rattus norvegicus)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Rattus norvegicus)
L-MM-CoA [mitochondrial matrix]
MUT isomerises L-MM-CoA to SUCC-CoA (Rattus norvegicus)
L-MM-CoA [mitochondrial matrix]
Metabolism (Sus scrofa)
Metabolism of lipids (Sus scrofa)
Fatty acid metabolism (Sus scrofa)
Mitochondrial Fatty Acid Beta-Oxidation (Sus scrofa)
Propionyl-CoA catabolism (Sus scrofa)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Sus scrofa)
L-MM-CoA [mitochondrial matrix]
MUT isomerises L-MM-CoA to SUCC-CoA (Sus scrofa)
L-MM-CoA [mitochondrial matrix]
Metabolism (Xenopus tropicalis)
Metabolism of lipids (Xenopus tropicalis)
Fatty acid metabolism (Xenopus tropicalis)
Mitochondrial Fatty Acid Beta-Oxidation (Xenopus tropicalis)
Propionyl-CoA catabolism (Xenopus tropicalis)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Xenopus tropicalis)
L-MM-CoA [mitochondrial matrix]
External Reference Information
External Reference
(R)-methylmalonyl-CoA [ChEBI:15465]
Participates
as an input of
Defective MUT does not isomerise L-MM-CoA to SUCC-CoA (Homo sapiens)
MUT isomerises L-MM-CoA to SUCC-CoA (Caenorhabditis elegans)
MUT isomerises L-MM-CoA to SUCC-CoA (Gallus gallus)
MUT isomerises L-MM-CoA to SUCC-CoA (Danio rerio)
MUT isomerises L-MM-CoA to SUCC-CoA (Sus scrofa)
MUT isomerises L-MM-CoA to SUCC-CoA (Bos taurus)
MUT isomerises L-MM-CoA to SUCC-CoA (Canis familiaris)
MUT isomerises L-MM-CoA to SUCC-CoA (Rattus norvegicus)
MUT isomerises L-MM-CoA to SUCC-CoA (Mus musculus)
MUT isomerises L-MM-CoA to SUCC-CoA (Homo sapiens)
as an output of
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Dictyostelium discoideum)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Caenorhabditis elegans)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Gallus gallus)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Xenopus tropicalis)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Danio rerio)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Sus scrofa)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Bos taurus)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Canis familiaris)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Rattus norvegicus)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Mus musculus)
D-methylmalonyl-CoA <=> L-methylmalonyl-CoA (Homo sapiens)
Cross References
COMPOUND
C01213
PubChem Substance
8143340
ZINC
ZINC000008551337
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