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Gal-Gal-Xyl-proteins [Golgi lumen]
Stable Identifier
R-HSA-2064214
Type
Set [DefinedSet]
Species
Homo sapiens
Compartment
Golgi lumen
Synonyms
(Gal)2 (Xyl)1 (Ser)1
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with glycosaminoglycan metabolism (Homo sapiens)
Defective B3GAT3 causes JDSSDHD (Homo sapiens)
Defective B3GAT3 does not transfer GlcA to tetrasaccharide linker (Homo sapiens)
Gal-Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
A tetrasaccharide linker sequence is required for GAG synthesis (Homo sapiens)
B3GALT6 transfers Gal to the tetrasaccharide linker (Homo sapiens)
Gal-Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
B3GAT dimers transfer GlcA to tetrasaccharide linker (Homo sapiens)
Gal-Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
B3GAT3 dimer transfers GlcA to tetrasaccharide linker (Homo sapiens)
Gal-Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
Heparan sulfate/heparin (HS-GAG) metabolism (Homo sapiens)
A tetrasaccharide linker sequence is required for GAG synthesis (Homo sapiens)
B3GALT6 transfers Gal to the tetrasaccharide linker (Homo sapiens)
Gal-Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
B3GAT dimers transfer GlcA to tetrasaccharide linker (Homo sapiens)
Gal-Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
B3GAT3 dimer transfers GlcA to tetrasaccharide linker (Homo sapiens)
Gal-Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
Participants
members
Gal-Gal-Xyl-AGRN [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-GPC1 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-GPC2 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-GPC3 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-GPC4 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-GPC5 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-GPC6 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-HSPG2 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-SDC1 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-SDC2 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-SDC3 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-SDC4 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-BCAN [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-BGN [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-CSPG4 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-CSPG5 [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-DCN [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-NCAN [Golgi lumen]
(Homo sapiens)
Gal-Gal-Xyl-VCAN [Golgi lumen]
(Homo sapiens)
Participates
as an input of
Defective B3GAT3 does not transfer GlcA to tetrasaccharide linker (Homo sapiens)
B3GAT3 dimer transfers GlcA to tetrasaccharide linker (Homo sapiens)
B3GAT dimers transfer GlcA to tetrasaccharide linker (Homo sapiens)
as an output of
B3GALT6 transfers Gal to the tetrasaccharide linker (Homo sapiens)
Inferred To
Gal-Gal-Xyl-proteins [Golgi lumen]
(Bos taurus)
Gal-Gal-Xyl-proteins [Golgi lumen]
(Caenorhabditis elegans)
Gal-Gal-Xyl-proteins [Golgi lumen]
(Canis familiaris)
Gal-Gal-Xyl-proteins [Golgi lumen]
(Danio rerio)
Gal-Gal-Xyl-proteins [Golgi lumen]
(Drosophila melanogaster)
Gal-Gal-Xyl-proteins [Golgi lumen]
(Gallus gallus)
Gal-Gal-Xyl-proteins [Golgi lumen]
(Mus musculus)
Gal-Gal-Xyl-proteins [Golgi lumen]
(Rattus norvegicus)
Gal-Gal-Xyl-proteins [Golgi lumen]
(Sus scrofa)
Gal-Gal-Xyl-proteins [Golgi lumen]
(Xenopus tropicalis)
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