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chondroitin(2)-core proteins [Golgi lumen]
Stable Identifier
R-HSA-2064050
Type
Set [DefinedSet]
Species
Homo sapiens
Compartment
Golgi lumen
Synonyms
(GlcA)1 (GalNAc)1 (GlcA)1 (Gal)2 (Xyl)1 (Ser)1
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with glycosaminoglycan metabolism (Homo sapiens)
Defective CHSY1 causes TPBS (Homo sapiens)
Defective CHSY1 does not transfer GalNAc to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
Chondroitin sulfate biosynthesis (Homo sapiens)
CHPF,CHPF2,CHSY3 transfer GlcA to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
CHPF,CHSY3 transfer GalNAc to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
CHSY1 transfers GalNAc to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
CHSY1 transfers GlcA to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
Participants
members
chondroitin(2)-BCAN [Golgi lumen] (Homo sapiens)
chondroitin(2)-BGN [Golgi lumen] (Homo sapiens)
chondroitin(2)-CSPG4 [Golgi lumen] (Homo sapiens)
chondroitin(2)-CSPG5 [Golgi lumen] (Homo sapiens)
chondroitin(2)-DCN [Golgi lumen] (Homo sapiens)
chondroitin(2)-NCAN [Golgi lumen] (Homo sapiens)
chondroitin(2)-VCAN [Golgi lumen] (Homo sapiens)
Participant Of
input
CHPF,CHSY3 transfer GalNAc to chondroitin
CHSY1 transfers GalNAc to chondroitin
Defective CHSY1 does not transfer GalNAc to chondroitin
output
CHPF,CHPF2,CHSY3 transfer GlcA to chondroitin
CHSY1 transfers GlcA to chondroitin
Inferred To
chondroitin(2)-core proteins [Golgi lumen] (Bos taurus)
chondroitin(2)-core proteins [Golgi lumen] (Canis familiaris)
chondroitin(2)-core proteins [Golgi lumen] (Danio rerio)
chondroitin(2)-core proteins [Golgi lumen] (Drosophila melanogaster)
chondroitin(2)-core proteins [Golgi lumen] (Gallus gallus)
chondroitin(2)-core proteins [Golgi lumen] (Mus musculus)
chondroitin(2)-core proteins [Golgi lumen] (Rattus norvegicus)
chondroitin(2)-core proteins [Golgi lumen] (Sus scrofa)
chondroitin(2)-core proteins [Golgi lumen] (Xenopus tropicalis)
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