Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
CS/HS precursor [lysosomal lumen]
Stable Identifier
R-ALL-2065212
Type
Chemical Compound [SimpleEntity]
Compartment
lysosomal lumen
Synonyms
GlcA-Gal-Gal-Xyl linker chain, beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates and carbohydrate derivatives (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Chondroitin sulfate/dermatan sulfate metabolism (Bos taurus)
CS/DS degradation (Bos taurus)
GUSB tetramer hydrolyses CS/HS precursor (Bos taurus)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Bos taurus)
CS/HS precursor [lysosomal lumen]
Metabolism (Caenorhabditis elegans)
Metabolism of carbohydrates and carbohydrate derivatives (Caenorhabditis elegans)
Glycosaminoglycan metabolism (Caenorhabditis elegans)
Chondroitin sulfate/dermatan sulfate metabolism (Caenorhabditis elegans)
CS/DS degradation (Caenorhabditis elegans)
GUSB tetramer hydrolyses CS/HS precursor (Caenorhabditis elegans)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Caenorhabditis elegans)
CS/HS precursor [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates and carbohydrate derivatives (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Chondroitin sulfate/dermatan sulfate metabolism (Canis familiaris)
CS/DS degradation (Canis familiaris)
GUSB tetramer hydrolyses CS/HS precursor (Canis familiaris)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Canis familiaris)
CS/HS precursor [lysosomal lumen]
Metabolism (Danio rerio)
Metabolism of carbohydrates and carbohydrate derivatives (Danio rerio)
Glycosaminoglycan metabolism (Danio rerio)
Chondroitin sulfate/dermatan sulfate metabolism (Danio rerio)
CS/DS degradation (Danio rerio)
GUSB tetramer hydrolyses CS/HS precursor (Danio rerio)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Danio rerio)
CS/HS precursor [lysosomal lumen]
Metabolism (Drosophila melanogaster)
Metabolism of carbohydrates and carbohydrate derivatives (Drosophila melanogaster)
Glycosaminoglycan metabolism (Drosophila melanogaster)
Chondroitin sulfate/dermatan sulfate metabolism (Drosophila melanogaster)
CS/DS degradation (Drosophila melanogaster)
GUSB tetramer hydrolyses CS/HS precursor (Drosophila melanogaster)
CS/HS precursor [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates and carbohydrate derivatives (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Chondroitin sulfate/dermatan sulfate metabolism (Gallus gallus)
CS/DS degradation (Gallus gallus)
GUSB tetramer hydrolyses CS/HS precursor (Gallus gallus)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Gallus gallus)
CS/HS precursor [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of carbohydrate metabolism (Homo sapiens)
Mucopolysaccharidoses (Homo sapiens)
MPS VII - Sly syndrome (CS/DS degradation) (Homo sapiens)
Defective GUSB does not hydrolyse CS/HS precursor (Homo sapiens)
CS/HS precursor [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates and carbohydrate derivatives (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
CS/DS degradation (Homo sapiens)
GUSB tetramer hydrolyses CS/HS precursor (Homo sapiens)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Homo sapiens)
CS/HS precursor [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates and carbohydrate derivatives (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Chondroitin sulfate/dermatan sulfate metabolism (Mus musculus)
CS/DS degradation (Mus musculus)
GUSB tetramer hydrolyses CS/HS precursor (Mus musculus)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Mus musculus)
CS/HS precursor [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates and carbohydrate derivatives (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Chondroitin sulfate/dermatan sulfate metabolism (Rattus norvegicus)
CS/DS degradation (Rattus norvegicus)
GUSB tetramer hydrolyses CS/HS precursor (Rattus norvegicus)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Rattus norvegicus)
CS/HS precursor [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates and carbohydrate derivatives (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Chondroitin sulfate/dermatan sulfate metabolism (Sus scrofa)
CS/DS degradation (Sus scrofa)
GUSB tetramer hydrolyses CS/HS precursor (Sus scrofa)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Sus scrofa)
CS/HS precursor [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates and carbohydrate derivatives (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Chondroitin sulfate/dermatan sulfate metabolism (Xenopus tropicalis)
CS/DS degradation (Xenopus tropicalis)
GUSB tetramer hydrolyses CS/HS precursor (Xenopus tropicalis)
CS/HS precursor [lysosomal lumen]
HYAL1-4 hydrolyze chondroitin chains (Xenopus tropicalis)
CS/HS precursor [lysosomal lumen]
External Reference Information
External Reference
beta-D-GlcpA-(1->3)-beta-D-Galp-(1->3)-beta-D-Galp-(1->4)-beta-D-Xylp(1-) [ChEBI:747385]
Participates
as an input of
Defective GUSB does not hydrolyse CS/HS precursor (Homo sapiens)
GUSB tetramer hydrolyses CS/HS precursor (Caenorhabditis elegans)
GUSB tetramer hydrolyses CS/HS precursor (Drosophila melanogaster)
GUSB tetramer hydrolyses CS/HS precursor (Gallus gallus)
GUSB tetramer hydrolyses CS/HS precursor (Xenopus tropicalis)
GUSB tetramer hydrolyses CS/HS precursor (Danio rerio)
GUSB tetramer hydrolyses CS/HS precursor (Sus scrofa)
GUSB tetramer hydrolyses CS/HS precursor (Canis familiaris)
GUSB tetramer hydrolyses CS/HS precursor (Rattus norvegicus)
GUSB tetramer hydrolyses CS/HS precursor (Mus musculus)
GUSB tetramer hydrolyses CS/HS precursor (Homo sapiens)
GUSB tetramer hydrolyses CS/HS precursor (Bos taurus)
as an output of
HYAL1-4 hydrolyze chondroitin chains (Caenorhabditis elegans)
HYAL1-4 hydrolyze chondroitin chains (Gallus gallus)
HYAL1-4 hydrolyze chondroitin chains (Xenopus tropicalis)
HYAL1-4 hydrolyze chondroitin chains (Danio rerio)
HYAL1-4 hydrolyze chondroitin chains (Sus scrofa)
HYAL1-4 hydrolyze chondroitin chains (Canis familiaris)
HYAL1-4 hydrolyze chondroitin chains (Rattus norvegicus)
HYAL1-4 hydrolyze chondroitin chains (Mus musculus)
HYAL1-4 hydrolyze chondroitin chains (Homo sapiens)
HYAL1-4 hydrolyze chondroitin chains (Bos taurus)
© 2026
Reactome
This website requires cookies and the limited processing of your personal data in order to function. By using the site you are agreeing to this as outlined in our
Privacy Notice
.
I agree, dismiss this banner
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text