The tetrameric lysosomal enzyme beta-glucuronidase hydrolyses glucuronate from heparan or the linker chain (Oshima et al. 1987). L-aspartic acid is an inhibitor of enzyme activity (Kreamer et al. 2001).
Kyle, JW, Gravel, RA, Powell, PP, Tropak, M, Sly, WS, Miller, RD, Grubb, JH, Oshima, A, Guise, KS, Hoffmann, JW
Siegel, FL, Kreamer, BL, Gourley, GR
beta-glucuronidase activity of GUSB tetramer [lysosomal lumen]
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