Reactome | Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix]

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Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] Show undefined attributes

compartment	[Compartment:70616] mitochondrial inner membrane [Compartment:5460] mitochondrial matrix
componentOf	[Complex:R-RNO-9837986] LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] - Rattus norvegicus
consumedByEvent	[Reaction:R-RNO-9838093] LONP1 binds mitochondrial matrix proteins - Rattus norvegicus
created	[InstanceEdit:10102717] Weiser, Joel, 2026-03-16
dbId	10217462
displayName	Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix]
hasMember	[EntityWithAccessionedSequence:R-RNO-70855] Acad8 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-70796] ACADSB(52-432) [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-70838] ACAT1(35-427) [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-70968] ACO2 [mitochondrial matrix] - Rattus norvegicus [DefinedSet:R-RNO-5690045-5] Homologues of ACOT2 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-5696097] ALDH1B1 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-71718] ALDH2 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-452025] ARG2 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-164575] ATP5F1A [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-164576] ATP5F1B [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-164577] Atp5f1c [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-70972] CS [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-6792584] Dbt [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-9838037] ECH1 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-53376] ECI1 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-189441] Fech [mitochondrial inner membrane] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-70980] FH [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-70582] GLUD1 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-71051] HADH [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-56573] HMGCS2 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-70831] HSD17B10 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-8878802] HSPA9 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-1299448] HSPD1 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-379571] Iars2 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-70977] MDH2 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-9012080] ME2 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-9839674] Mrpl12 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-9839664] Mrpl32 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-9839682] Mrps2 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-9839687] Mrps10 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-8933311] Nadk2 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-6788513] NDUFS1 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-69981] OGDH [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-74317] Oxct1 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-8933301] Oxsm [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-3323190] Pccb [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-69967] PDHB [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-1592222] Twnk [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-203944] PDK1 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-1299450] Pmpca [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-1592217] Ssbp1 [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-9838092] Star [mitochondrial matrix] - Rattus norvegicus [EntityWithAccessionedSequence:R-RNO-9838277] phospho-Tfam [mitochondrial matrix] - Rattus norvegicus
inDisease	false
inferredFrom	[DefinedSet:R-HSA-9837979] Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] - Homo sapiens
maxDepth	3
name	Substrate of LONP1 (mitochondrial matrix)
schemaClass	DefinedSet
species	[Species:48895] Rattus norvegicus
stId	R-RNO-9837979

Referrals

(input)	[Reaction:R-RNO-9838093] LONP1 binds mitochondrial matrix proteins
(hasComponent)	[Complex:R-RNO-9837986] LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix]
(inferredTo)	[DefinedSet:R-HSA-9837979] Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix]

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