Reactome | Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix]

Schema > DefinedSet > Entries

Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] Show undefined attributes

compartment	[Compartment:70616] mitochondrial inner membrane [Compartment:5460] mitochondrial matrix
componentOf	[Complex:R-MMU-9837986] LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] - Mus musculus
consumedByEvent	[Reaction:R-MMU-9838093] LONP1 binds mitochondrial matrix proteins - Mus musculus
created	[InstanceEdit:9984900] Weiser, Joel, 2026-03-16
dbId	10094308
displayName	Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix]
hasMember	[EntityWithAccessionedSequence:R-MMU-70855] ACAD8 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-70796] ACADSB(52-432) [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-70838] ACAT1(35-427) [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-70968] ACO2 [mitochondrial matrix] - Mus musculus [DefinedSet:R-MMU-5690045-5] Homologues of ACOT2 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-5696097] ALDH1B1 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-71718] ALDH2 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-452025] ARG2 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-164575] ATP5F1A [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-164576] ATP5F1B [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-164577] Atp5f1c [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-70972] CS [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-6792584] DBT [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-9838037] ECH1 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-53376] ECI1 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-189441] FECH [mitochondrial inner membrane] - Mus musculus [EntityWithAccessionedSequence:R-MMU-70980] FH [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-70582] GLUD1 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-71051] HADH [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-56573] HMGCS2 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-70831] HSD17B10 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-8878802] HSPA9 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-1299448] HSPD1 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-379571] IARS2 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-70977] MDH2 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-9012080] ME2 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-9839674] Mrpl12 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-9839664] MRPL32 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-9839682] Mrps2 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-9839687] Mrps10 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-8933311] Nadk2 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-6788513] NDUFS1 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-69981] OGDH [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-74317] Oxct1 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-8933301] Oxsm [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-3323190] Pccb [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-69967] PDHB [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-1592222] TWNK [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-203944] PDK1 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-1299450] Pmpca [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-1592217] Ssbp1 [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-9838092] Star [mitochondrial matrix] - Mus musculus [EntityWithAccessionedSequence:R-MMU-9838277] phospho-Tfam [mitochondrial matrix] - Mus musculus
inDisease	false
inferredFrom	[DefinedSet:R-HSA-9837979] Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] - Homo sapiens
maxDepth	3
name	Substrate of LONP1 (mitochondrial matrix)
schemaClass	DefinedSet
species	[Species:48892] Mus musculus
stId	R-MMU-9837979

Referrals

(input)	[Reaction:R-MMU-9838093] LONP1 binds mitochondrial matrix proteins
(hasComponent)	[Complex:R-MMU-9837986] LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix]
(inferredTo)	[DefinedSet:R-HSA-9837979] Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix]

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