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Schema
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Reaction
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Entries
UROD decarboxylates URO1 to COPRO1
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authored
[InstanceEdit:191749] Jassal, B, D'Eustachio, P, 2007-01-24 10:19:49
catalystActivity
[CatalystActivity:189412] carbon-carbon lyase activity of 2xUROD [cytosol]
category
transition
compartment
[Compartment:70101] cytosol
created
[InstanceEdit:190162] Jassal, B, 2006-12-18 09:12:35
crossReference
[DatabaseIdentifier:12668033] RHEA:31240
dbId
190182
displayName
UROD decarboxylates URO1 to COPRO1
edited
[InstanceEdit:191749] Jassal, B, D'Eustachio, P, 2007-01-24 10:19:49
eventOf
[Pathway:R-HSA-189451] Heme biosynthesis - Homo sapiens
input
4 ×
[SimpleEntity:R-ALL-70106] H+ [cytosol]
[SimpleEntity:R-ALL-190157] URO1 [cytosol]
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:190134] Purification and properties of uroporphyrinogen decarboxylase from human erythrocytes. A single enzyme catalyzing the four sequential decarboxylations of uroporphyrinogens I and III.
[LiteratureReference:190137] Uroporphyrinogen decarboxylase: complete human gene sequence and molecular study of three families with hepatoerythropoietic porphyria
maxDepth
1
modified
[InstanceEdit:11108703] Weiser, Joel, 2026-03-16
name
UROD decarboxylates URO1 to COPRO1
4 H(+) + uroporphyrinogen I => 4 CO2 + coproporphyrinogen I
Uroporphyrinogen I is decarboxylated to form coproporphyrinogen I
orthologousEvent
[Reaction:R-GGA-421459] uroporphyrinogen I => coproporphyrinogen I + 4 CO2 - Gallus gallus
[Reaction:R-RNO-190182] UROD decarboxylates URO1 to COPRO1 - Rattus norvegicus
[Reaction:R-PFA-190182] UROD decarboxylates URO1 to COPRO1 - Plasmodium falciparum
[Reaction:R-SCE-190182] UROD decarboxylates URO1 to COPRO1 - Saccharomyces cerevisiae
[Reaction:R-SPO-190182] UROD decarboxylates URO1 to COPRO1 - Schizosaccharomyces pombe
[Reaction:R-DDI-190182] UROD decarboxylates URO1 to COPRO1 - Dictyostelium discoideum
[Reaction:R-DME-190182] UROD decarboxylates URO1 to COPRO1 - Drosophila melanogaster
[Reaction:R-GGA-190182] UROD decarboxylates URO1 to COPRO1 - Gallus gallus
[Reaction:R-XTR-190182] UROD decarboxylates URO1 to COPRO1 - Xenopus tropicalis
[Reaction:R-DRE-190182] UROD decarboxylates URO1 to COPRO1 - Danio rerio
[Reaction:R-SSC-190182] UROD decarboxylates URO1 to COPRO1 - Sus scrofa
[Reaction:R-BTA-190182] UROD decarboxylates URO1 to COPRO1 - Bos taurus
[Reaction:R-CFA-190182] UROD decarboxylates URO1 to COPRO1 - Canis familiaris
[Reaction:R-MMU-190182] UROD decarboxylates URO1 to COPRO1 - Mus musculus
output
4 ×
[SimpleEntity:R-ALL-113528] CO2 [cytosol]
[SimpleEntity:R-ALL-190128] COPRO1 [cytosol]
precedingEvent
[Reaction:R-HSA-190168] HMBL spontaneously transforms to URO1 - Homo sapiens
previousReviewStatus
[ReviewStatus:9821384] two stars
releaseDate
2007-02-20
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:191750] Sassa, S, 2007-01-24 10:18:36
[InstanceEdit:9861359] Hill, David P, 2024-02-16
revised
[InstanceEdit:421639] D'Eustachio, P, 2009-05-19 13:25:07
[InstanceEdit:9854168] D'Eustachio, Peter, 2023-11-22
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-190182
summation
[Summation:190153] Cytosolic uroporphyrinogen decarboxylase (UROD) catalyzes th...
updateTrackers
[UpdateTracker:9864044] Update Tracker - [Reaction:190182] UROD decarboxylates URO1 to COPRO1 - v88:[addInput]
[UpdateTracker:9787756] Update Tracker - [Reaction:190182] UROD decarboxylates URO1 to COPRO1 - v44:[modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9864044] Update Tracker - [Reaction:190182] UROD decarboxylates URO1 to COPRO1 - v88:[addInput]
[UpdateTracker:9787756] Update Tracker - [Reaction:190182] UROD decarboxylates URO1 to COPRO1 - v44:[modifyText]
(hasEvent)
[Pathway:R-HSA-189451] Heme biosynthesis
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