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Schema
>
Reaction
>
Entries
IDUA hydrolyses Heparan sulfate chain(1)
Show undefined attributes
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authored
[InstanceEdit:1678699] Jassal, B, 2011-10-19
catalystActivity
[CatalystActivity:1678683] L-iduronidase activity of IDUA [lysosomal lumen]
category
transition
compartment
[Compartment:161320] lysosomal lumen
created
[InstanceEdit:1678699] Jassal, B, 2011-10-19
dbId
1678716
displayName
IDUA hydrolyses Heparan sulfate chain(1)
edited
[InstanceEdit:1678699] Jassal, B, 2011-10-19
eventOf
[Pathway:R-HSA-2024096] HS-GAG degradation - Homo sapiens
followingEvent
[Reaction:R-HSA-1678708] SGSH hydrolyses Heparan sulfate chain(2) - Homo sapiens
input
[SimpleEntity:R-ALL-1605715] H2O [lysosomal lumen]
[SimpleEntity:R-ALL-2090033] Heparan sulfate chain(1) [lysosomal lumen]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:1678628] Human alpha-L-iduronidase: cDNA isolation and expression
[LiteratureReference:1678646] Mucopolysaccharidosis type I: characterization of novel mutations affecting alpha-L-iduronidase activity
modified
[InstanceEdit:10818988] Wright, Adam, 2024-03-08
name
IDUA hydrolyses Heparan sulfate chain(1)
orthologousEvent
[Reaction:R-DDI-1678716] IDUA hydrolyses Heparan sulfate chain(1) - Dictyostelium discoideum
[Reaction:R-DME-1678716] IDUA hydrolyses Heparan sulfate chain(1) - Drosophila melanogaster
[Reaction:R-GGA-1678716] IDUA hydrolyses Heparan sulfate chain(1) - Gallus gallus
[Reaction:R-XTR-1678716] IDUA hydrolyses Heparan sulfate chain(1) - Xenopus tropicalis
[Reaction:R-SSC-1678716] IDUA hydrolyses Heparan sulfate chain(1) - Sus scrofa
[Reaction:R-BTA-1678716] IDUA hydrolyses Heparan sulfate chain(1) - Bos taurus
[Reaction:R-CFA-1678716] IDUA hydrolyses Heparan sulfate chain(1) - Canis familiaris
[Reaction:R-RNO-1678716] IDUA hydrolyses Heparan sulfate chain(1) - Rattus norvegicus
[Reaction:R-MMU-1678716] IDUA hydrolyses Heparan sulfate chain(1) - Mus musculus
output
[SimpleEntity:R-ALL-1678617] aldehydo-L-iduronic acid [lysosomal lumen]
[SimpleEntity:R-ALL-2090072] Heparan sulfate chain(2) [lysosomal lumen]
precedingEvent
[Reaction:R-HSA-1667005] Heparanase (HPSE) cleaves heparan sulfate from its proteoglycan (lysosome) - Homo sapiens
releaseDate
2012-06-12
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:2172129] D'Eustachio, P, 2012-03-28
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-1678716
summation
[Summation:1678630] An L-iduronic acid residue can be cleaved from either hepara...
Referrals
(normalReaction)
[FailedReaction:R-HSA-9036037] Defective IDUA does not hydrolyse Heparan sulfate chain(1)
(hasEvent)
[Pathway:R-HSA-2024096] HS-GAG degradation
(precedingEvent)
[Reaction:R-HSA-1678708] SGSH hydrolyses Heparan sulfate chain(2)
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