UVSSA stabilizes ERCC6 (CSB) during transcription-coupled nu...

created [InstanceEdit:6782070] Orlic-Milacic, Marija, 2015-06-04
dbId 6782067
displayName UVSSA stabilizes ERCC6 (CSB) during transcription-coupled nu...
modified [InstanceEdit:6783893] Orlic-Milacic, Marija, 2015-06-17
schemaClass Summation
text UVSSA stabilizes ERCC6 (CSB) during transcription-coupled nucleotide excision repair (TC-NER) by targeting ubiquitin protease USP7 to ubiquitinated ERCC6, thus preventing proteasome-mediated degradation of ERCC6. Mutations in UVSSA cause UV-sensitive syndrome (Nakazawa et al. 2012, Schwertman et al. 2012, Zhang et al. 2012, Fei and Chen 2012).
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