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RPUSD3 [mitochondrial matrix]
Stable Identifier
R-HSA-9936258
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Mitochondrial mRNA pseudouridine synthase RPUSD3 ecNumber evidence="5"5.4.99.-, RUSD3_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism of RNA (Homo sapiens)
Mitochondrial mRNA modification (Homo sapiens)
RPUSD3,TRUB2 pseudouridylates MT-CO1,MT-CO3 mRNA (Homo sapiens)
RPUSD3,TRUB2 [mitochondrial matrix] (Homo sapiens)
RPUSD3 [mitochondrial matrix] (Homo sapiens)
mitochondrial pseudouridylation module [mitochondrial matrix] (Homo sapiens)
RPUSD3 [mitochondrial matrix] (Homo sapiens)
rRNA processing (Homo sapiens)
rRNA processing in the mitochondrion (Homo sapiens)
rRNA modification in the mitochondrion (Homo sapiens)
RPUSD4 in the mitochondrial pseudouridylation module transforms uridine-1397 to pseudouridine-1397 in mitochondrial 16S rRNA (Homo sapiens)
mitochondrial pseudouridylation module [mitochondrial matrix] (Homo sapiens)
RPUSD3 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q6P087 RPUSD3
Gene Names
RPUSD3
Chain
transit peptide:1-25, chain:26-351
Reference Genes
BioGPS Gene:285367 RPUSD3
COSMIC - genes:RPUSD3 RPUSD3
CTD Gene:285367 RPUSD3
dbSNP Gene:285367 RPUSD3
ENSEMBL:ENSG00000156990 RPUSD3
HGNC:28437 RPUSD3
KEGG:hsa:285367 RPUSD3
Monarch:285367 RPUSD3
NCBI Gene:285367 RPUSD3
OMIM:617759 RPUSD3
UCSC:Q6P087 RPUSD3
Reference Transcript
RefSeq:NM_173659.5 RPUSD3
RefSeq:NM_001142547.3 RPUSD3
Other Identifiers
11731230_a_at
1555916_PM_at
1555916_at
1561329_PM_s_at
1561329_s_at
1566603_PM_s_at
1566603_s_at
16950584
225743_PM_at
225743_at
2662398
2662399
2662402
2662403
2662404
2662405
2662406
2662407
2662408
2662409
2662410
2662411
2662412
2662413
2662414
2662415
2662416
2662417
2662418
2662419
2662420
2662421
2662422
2662423
2662424
2662425
2662426
285367
61708_at
8085233
88671_at
A_23_P255916
GE476991
GO:0001522
GO:0003723
GO:0005515
GO:0005739
GO:0005759
GO:0006397
GO:0009451
GO:0009982
GO:0016071
GO:0016853
GO:0035770
GO:0043226
GO:0070131
GO:1990481
HMNXSV003009093
Hs.33719.0.A1_3p_at
Hs2.378102.1.S1_3p_at
Hs2.435412.1.S1_3p_s_at
Hs2.435412.2.S1_3p_s_at
ILMN_1795383
PH_hs_0002806
PH_hs_0038949
TC03001151.hg
Participates
as a component of
mitochondrial pseudouridylation module [mitochondrial matrix] (Homo sapiens)
as a member of
RPUSD3,TRUB2 [mitochondrial matrix] (Homo sapiens)
Cross References
RefSeq
NP_775930.3
,
NP_001136019.2
ENSEMBL
ENST00000433972
,
ENST00000433535
,
ENSP00000395446
,
ENST00000383820
,
ENSP00000398921
,
ENSG00000156990
,
ENSP00000373331
OpenTargets
ENSG00000156990
GeneCards
RPUSD3
HPA
ENSG00000156990-RPUSD3
PRO
Q6P087
Pharos - Targets
Q6P087
HMDB Protein
HMDBP09200
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P10809 HSPD1
6
HSPD1(1-26) [mitochondrial matrix]
(R-HSA-8986171)
HSPD1(1-573) [mitochondrial inner membrane]
(R-HSA-1299442)
HSPD1 [mitochondrial inner membrane]
(R-HSA-1299455)
HSPD1(1-573) [mitochondrial intermembrane space]
(R-HSA-1267963)
HSPD1(1-573) [cytosol]
(R-HSA-1267989)
HSPD1 [mitochondrial matrix]
(R-HSA-1299448)
0.527
4
UniProt:P84103 SRSF3
1
SRSF3 [nucleoplasm]
(R-HSA-72035)
0.527
2
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