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ACADSB(52-432) [mitochondrial matrix]
Stable Identifier
R-HSA-70796
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
2-methyl branched chain acyl-CoA dehydrogenase, ACADSB, acyl-CoA dehydrogenase, short/branched chain specific, 2-methylbutyryl-CoA dehydrogenase, Acyl-CoA dehydrogenase, short/branched chain specific, mitochondrial precursor (EC 1.3.99.-) (SBCAD) (2-methyl branched chain acyl-CoA dehydrogenase) (2-MEBCAD) (2-methylbutyryl-coenzyme A dehydrogenase) (2-methylbutyryl-CoA dehydrogenase), Acyl-CoA dehydrogenase, short/branched chain specific, mitochondrial precursor , SBCAD, 2-MEBCAD, 2-methylbutyryl-coenzyme A dehydrogenase
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Branched-chain amino acid catabolism (Homo sapiens)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Homo sapiens)
ACADSB tetramer [mitochondrial matrix] (Homo sapiens)
ACADSB(52-432) [mitochondrial matrix] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
LONP1 binds mitochondrial matrix proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
ACADSB(52-432) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
ACADSB(52-432) [mitochondrial matrix] (Homo sapiens)
LONP1 degrades mitochondrial matrix proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
ACADSB(52-432) [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:P45954 ACADSB
Gene Names
ACADSB
Chain
transit peptide:1-33, chain:34-432
Reference Genes
BioGPS Gene:36 ACADSB
COSMIC (genes):ACADSB ACADSB
CTD Gene:36 ACADSB
dbSNP Gene:36 ACADSB
ENSEMBL:ENSG00000196177 ACADSB
HGNC:91 ACADSB
KEGG:hsa:36 ACADSB
Monarch:36 ACADSB
NCBI Gene:36 ACADSB
OMIM:600301 ACADSB
UCSC:P45954 ACADSB
Reference Transcript
RefSeq:NM_001609.3 ACADSB
RefSeq:NM_001330174.1 ACADSB
Other Identifiers
11718312_at
11748196_a_at
16710245
205355_PM_at
205355_at
226030_PM_at
226030_at
3268589
3268598
3268602
3268603
3268604
3268606
3268607
3268608
3268609
3268612
3268613
3268615
3268616
3268617
3268618
3268619
3268620
3268621
3268622
3268623
3268642
3268643
36
40673_at
48447_at
56518_at
7931168
A_14_P136584
A_23_P158570
A_24_P189516
A_32_P31945
A_32_P61313
A_33_P3248992
GE58935
GO:0003824
GO:0003853
GO:0003995
GO:0005739
GO:0005759
GO:0006520
GO:0006550
GO:0006629
GO:0006631
GO:0016491
GO:0016627
GO:0016937
GO:0042802
GO:0043226
GO:0050660
HMNXSV003034502
Hs.11805.0.A1_3p_at
ILMN_1740920
ILMN_1850115
PH_hs_0004682
PH_hs_0008375
TC10000896.hg
U12778_at
Participates
as a member of
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
as a component of
ACADSB tetramer [mitochondrial matrix] (Homo sapiens)
Inferred To
ACADSB [mitochondrial matrix]
(Canis familiaris)
ACADSB [mitochondrial matrix]
(Sus scrofa)
ACADSB(52-432) [mitochondrial matrix]
(Bos taurus)
ACADSB(52-432) [mitochondrial matrix]
(Dictyostelium discoideum)
ACADSB(52-432) [mitochondrial matrix]
(Gallus gallus)
ACADSB(52-432) [mitochondrial matrix]
(Mus musculus)
ACADSB(52-432) [mitochondrial matrix]
(Rattus norvegicus)
acadsb [mitochondrial matrix]
(Xenopus tropicalis)
acdh-3 [mitochondrial matrix]
(Caenorhabditis elegans)
GH07925p [mitochondrial matrix]
(Drosophila melanogaster)
Cross References
RefSeq
NP_001317103.1
,
NP_001600.1
ENSEMBL
ENSP00000357862
,
ENSP00000357873
,
ENST00000368869
,
ENST00000358776
OpenTargets
ENSG00000196177
HPA
ENSG00000196177-ACADSB
PRO
P45954
Pharos - Targets
P45954
Orphanet
ACADSB
HMDB Protein
HMDBP01613
PDB
2JIF
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