lipo-BCKDH [mitochondrial matrix]

Stable Identifier
R-HSA-70019
Type
Complex
Species
Homo sapiens
Compartment
Synonyms
lipoylated branched-chain alpha-ketoacid dehydrogenase complex
Locations in the PathwayBrowser
Literature References
PubMed ID Title Journal Year
10745006 Crystal structure of human branched-chain alpha-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease.

Hol, WG, Turley, S, Chuang, DT, Chuang, JL, Wynn, RM, Aevarsson, A

Structure Fold Des 2000
2188967 Structure-function relationships in dihydrolipoamide acyltransferases.

Reed, LJ, Hackert, ML

J Biol Chem 1990
  The Metabolic and Molecular Bases of Inherited Disease, 8th ed

Beaudet, AL, Scriver, CR, Sly, WS, Valle, D

  2001
Participants
Participates
Inferred To
Cross References
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