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MT-ND2 [mitochondrial inner membrane]
Stable Identifier
R-HSA-60553
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase chain 2 (EC 1.6.5.3)
Icon
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
ND2, ND3, ND6, NDUFB6 bind the MCIA complex to form a 370kDa subcomplex (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex (-MCIA complex) [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex (-MCIA complex) [mitochondrial inner membrane] (Homo sapiens)
MT-ND2 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:P03891 MT-ND2
Gene Names
MT-ND2, MTND2, NADH2, ND2
Chain
chain:1-347
Reference Genes
BioGPS Gene:4536 MT-ND2
COSMIC (genes):MT-ND2 MT-ND2
CTD Gene:4536 MT-ND2
dbSNP Gene:4536 MT-ND2
ENSEMBL:ENSG00000198763 MT-ND2
HGNC:7456 MT-ND2
KEGG Gene (Homo sapiens):4536 MT-ND2
Monarch:4536 MT-ND2
NCBI Gene:4536 MT-ND2
OMIM:516001 MT-ND2
Reference Transcript
RefSeq:NC_012920.1 MT-ND2
Other Identifiers
0004920075
1553551_3p_s_at
1553551_s_at
17100649
17100651
17100653
17100655
17100657
2315227
2315305
2315306
2315307
2315308
2315309
2315310
3560048
4037603
4037605
4037607
4037609
4037610
4037611
4037612
4037614
4037616
4037618
4037620
4037622
4037624
4037625
4536
7896746
7896748
8165656
8165658
ADDON000548.hg
ADDON001198.hg
A_23_P431853
GO:0003674
GO:0005575
GO:0005622
GO:0005737
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0007005
GO:0008137
GO:0008150
GO:0014069
GO:0016020
GO:0016021
GO:0016491
GO:0019899
GO:0019901
GO:0022607
GO:0032981
GO:0032991
GO:0035255
GO:0043226
GO:0055114
GO:0065003
GO:0070469
GO:0072593
Hs2Affx.1.29.S1_3p_s_at
TC01004109.hg
TC0M000004.hg
Participant Of
input
ND2, ND3, ND6, NDUFB6 bind the MCIA complex to form a 370kDa subcomplex
hasComponent
370 kDa subcomplex (-MCIA complex) [mitochondrial inner membrane]
370 kDa subcomplex [mitochondrial inner membrane]
Inferred To
nd2 [mitochondrial inner membrane] (Xenopus tropicalis)
mt-nd2 [mitochondrial inner membrane] (Danio rerio)
Mtnd2 [mitochondrial inner membrane] (Mus musculus)
Mtnd2 [mitochondrial inner membrane] (Rattus norvegicus)
Ghost homologue of MT-ND2 [mitochondrial inner membrane] (Bos taurus)
Ghost homologue of MT-ND2 [mitochondrial inner membrane] (Sus scrofa)
MT-ND2 [mitochondrial inner membrane] (Canis familiaris)
MT-ND2 [mitochondrial inner membrane] (Gallus gallus)
mt:ND2 [mitochondrial inner membrane] (Drosophila melanogaster)
Cross References
RefSeq
YP_003024027.1
OpenTargets
ENSG00000198763
GeneCards
P03891
HPA
ENSG00000198763-MT-ND2
Ensembl
ENSP00000355046
,
ENSG00000198763
,
ENST00000361453
PRO
P03891
Orphanet
16479
PDB
5XTD
,
5XTH
,
5XTI
,
5XTC
HMDB Protein
HMDBP00154
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