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NDUFB9 [mitochondrial inner membrane]
Stable Identifier
R-HSA-60176
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase B22 subunit , Complex I-B22, CI-B22
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB9 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9Y6M9 NDUFB9
Gene Names
NDUFB9, LYRM3, UQOR22
Chain
initiator methionine:, chain:2-179
Reference Genes
BioGPS Gene:4715 NDUFB9
COSMIC (genes):NDUFB9 NDUFB9
CTD Gene:4715 NDUFB9
dbSNP Gene:4715 NDUFB9
ENSEMBL:ENSG00000147684 NDUFB9
HGNC:7704 NDUFB9
KEGG:hsa:4715 NDUFB9
Monarch:4715 NDUFB9
NCBI Gene:4715 NDUFB9
OMIM:601445 NDUFB9
UCSC:Q9Y6M9 NDUFB9
Reference Transcript
RefSeq:NM_001311168.1 NDUFB9
RefSeq:NM_005005.2 NDUFB9
Other Identifiers
11716029_a_at
11716030_x_at
11761015_at
11763101_x_at
17072506
222992_PM_s_at
222992_s_at
3073166
3114650
3114651
3114653
3114654
3114655
3114656
3114657
3114658
3114659
3114660
3114661
3114662
3114663
3114664
3114665
3114666
3114667
3114668
3114669
3114670
3114671
3114672
3114673
3114675
3114677
44711_at
4715
80935_at
8148270
86212_at
A_14_P133978
A_23_P157669
A_24_P154006
GE61237
GO:0003824
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0006091
GO:0006120
GO:0007605
GO:0008137
GO:0009060
GO:0016491
GO:0032981
GO:0042776
GO:0043226
GO:0045271
GO:0050877
GO:0055085
GO:0055086
GO:0065003
GO:1901135
GO:1902600
HMNXSV003016306
PH_hs_0001471
TC08000726.hg
g9802311_3p_s_at
Participates
as a component of
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
Inferred To
ndufb9 [mitochondrial inner membrane]
(Danio rerio)
ndufb9 [mitochondrial inner membrane]
(Xenopus tropicalis)
ND-B22 [mitochondrial inner membrane]
(Drosophila melanogaster)
Ghost homologue of NDUFB9 [mitochondrial inner membrane]
(Rattus norvegicus)
Ndufb9 [mitochondrial inner membrane]
(Mus musculus)
NDUFB9 [mitochondrial inner membrane]
(Bos taurus)
NDUFB9 [mitochondrial inner membrane]
(Caenorhabditis elegans)
NDUFB9 [mitochondrial inner membrane]
(Canis familiaris)
NDUFB9 [mitochondrial inner membrane]
(Gallus gallus)
NDUFB9 [mitochondrial inner membrane]
(Sus scrofa)
Cross References
ENSEMBL
ENST00000276689
,
ENSP00000276689
,
ENST00000677021
,
ENSP00000504235
OpenTargets
ENSG00000147684
HPA
ENSG00000147684-NDUFB9
PRO
Q9Y6M9
Pharos - Targets
Q9Y6M9
GlyGen
Q9Y6M9
Orphanet
NDUFB9
HMDB Protein
HMDBP00187
PDB
5XTC
,
5XTD
,
5XTI
,
5XTH
Interactors (6)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P42858 HTT
1
HTT [nucleoplasm]
(R-HSA-9023590)
0.666
10
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.643
6
UniProt:Q6UWR7 ENPP6
1
ENPP6 [plasma membrane]
(R-HSA-6814799)
0.527
2
UniProt:Q9UI09 NDUFA12
1
NDUFA12 [mitochondrial inner membrane]
(R-HSA-59864)
0.527
2
UniProt:O75380 NDUFS6
1
NDUFS6 [mitochondrial inner membrane]
(R-HSA-163922)
0.527
4
UniProt:O43920 NDUFS5
1
NDUFS5 [mitochondrial inner membrane]
(R-HSA-60226)
0.527
3
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