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ECI1 [mitochondrial matrix]
Stable Identifier
R-HSA-53376
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
3,2-trans-enoyl-CoA isomerase, mitochondrial precursor , Dodecenoyl-CoA delta-isomerase, DCI
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Homo sapiens)
Isomerization of 3-trans-decenoyl-CoA to form trans-dec-2-enoyl-CoA (Homo sapiens)
DCI dimer [mitochondrial matrix] (Homo sapiens)
ECI1 [mitochondrial matrix] (Homo sapiens)
Isomerization of cis,cis-3,6-Dodecadienoyl-CoA to form trans,cis-Lauro-2,6-dienoyl-CoA (Homo sapiens)
DCI dimer [mitochondrial matrix] (Homo sapiens)
ECI1 [mitochondrial matrix] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
CLPXP binds mitochondrial matrix proteins (Homo sapiens)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Homo sapiens)
ECI1 [mitochondrial matrix] (Homo sapiens)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Homo sapiens)
ECI1 [mitochondrial matrix] (Homo sapiens)
CLPXP degrades mitochondrial matrix proteins (Homo sapiens)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Homo sapiens)
ECI1 [mitochondrial matrix] (Homo sapiens)
LONP1 binds mitochondrial matrix proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
ECI1 [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
ECI1 [mitochondrial matrix] (Homo sapiens)
LONP1 degrades mitochondrial matrix proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
ECI1 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:P42126 ECI1
Gene Names
ECI1, DCI
Chain
transit peptide:1-41, chain:42-302
Reference Genes
BioGPS Gene:1632 ECI1
COSMIC (genes):ECI1 ECI1
CTD Gene:1632 ECI1
dbSNP Gene:1632 ECI1
ENSEMBL:ENSG00000167969 ECI1
HGNC:2703 ECI1
KEGG:hsa:1632 ECI1
Monarch:1632 ECI1
NCBI Gene:1632 ECI1
OMIM:600305 ECI1
UCSC:P42126 ECI1
Reference Transcript
RefSeq:NM_001178029.1 ECI1
RefSeq:NM_001919.3 ECI1
Other Identifiers
11732220_a_at
1632
16823087
209759_PM_s_at
209759_s_at
3676650
3676651
3676652
3676653
3676654
3676655
3676656
3676657
3676658
3676659
3676660
3676662
3676664
3676665
3676666
3676667
3676668
37982_at
7998762
A_23_P163647
GE60379
GE83890
GE85002
GE85003
GO:0003824
GO:0004165
GO:0005739
GO:0005759
GO:0006629
GO:0006631
GO:0006635
GO:0016853
GO:0016863
GO:0043226
HMNXSV003040817
ILMN_2049303
L24774_s_at
PH_hs_0019128
TC16000781.hg
g12803812_3p_s_at
Participates
as a member of
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Homo sapiens)
as a component of
DCI dimer [mitochondrial matrix] (Homo sapiens)
Inferred To
ECI1 [mitochondrial matrix]
(Bos taurus)
ECI1 [mitochondrial matrix]
(Canis familiaris)
ECI1 [mitochondrial matrix]
(Gallus gallus)
ECI1 [mitochondrial matrix]
(Mus musculus)
ECI1 [mitochondrial matrix]
(Rattus norvegicus)
ECI1 [mitochondrial matrix]
(Sus scrofa)
eci1 [mitochondrial matrix]
(Xenopus tropicalis)
Dmel\CG4598 [mitochondrial matrix]
(Drosophila melanogaster)
Cross References
ENSEMBL
ENSG00000167969
,
ENSP00000301729
,
ENST00000301729
,
ENST00000562238
,
ENSP00000456319
OpenTargets
ENSG00000167969
GeneCards
ECI1
HPA
ENSG00000167969-ECI1
PRO
P42126
Pharos - Targets
P42126
GlyGen
P42126
HMDB Protein
HMDBP03314
PDB
1SG4
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