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MTRR:FMN:FAD [cytosol]
Stable Identifier
R-HSA-3149530
Type
Complex
Species
Homo sapiens
Compartment
cytosol
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Defects in vitamin and cofactor metabolism (Homo sapiens)
Defects in cobalamin (B12) metabolism (Homo sapiens)
Defective MTR causes methylmalonic aciduria and homocystinuria type cblG (Homo sapiens)
Defective MTR does not transfer CH3 group from MTHF to cob(I)alamin (Homo sapiens)
MTRR:mutant MTR(cob(I)alamin) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
Defective MTR does not transfer CH3 group from MeCbl to HCYS (Homo sapiens)
MTRR:mutant MTR(MeCbl) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
Metabolism (Homo sapiens)
Biological oxidations (Homo sapiens)
Phase II - Conjugation of compounds (Homo sapiens)
Methylation (Homo sapiens)
MTR transfers CH3 from MeCbl to HCYS (Homo sapiens)
MTRR:MTR(MeCbl) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
MTRR:MTR(cob(I)alamin) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Sulfur amino acid metabolism (Homo sapiens)
MTR transfers CH3 from MeCbl to HCYS (Homo sapiens)
MTRR:MTR(MeCbl) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
MTRR:MTR(cob(I)alamin) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of water-soluble vitamins and cofactors (Homo sapiens)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Homo sapiens)
MTR transfers CH3 from MeCbl to HCYS (Homo sapiens)
MTRR:MTR(MeCbl) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
MTRR:MTR(cob(I)alamin) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
MTR transfers CH3 group from MTHF to cob(I)alamin (Homo sapiens)
MTRR:MTR(MeCbl) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
MTRR:MTR(cob(I)alamin) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
MTRR reduces cob(II)alamin to meCbl (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
MTRR:MTR(MeCbl) [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
MTRR:MTR(cob(II)alamin) [cytosol] (Homo sapiens)
MTRR:MTR [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
cob(II)alamin binds to MTRR:MTR (Homo sapiens)
MTRR:MTR [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
MTRR:MTR(cob(II)alamin) [cytosol] (Homo sapiens)
MTRR:MTR [cytosol] (Homo sapiens)
MTRR:FMN:FAD [cytosol] (Homo sapiens)
Participants
components
FAD [cytosol]
FMN [cytosol]
MTRR [cytosol] (Homo sapiens)
Participant Of
hasComponent
MTRR:MTR [cytosol]
MTRR:MTR(cob(I)alamin) [cytosol]
MTRR:MTR(MeCbl) [cytosol]
MTRR:mutant MTR(cob(I)alamin) [cytosol]
MTRR:mutant MTR(MeCbl) [cytosol]
Inferred To
MTRR:FMN:FAD [cytosol] (Caenorhabditis elegans)
MTRR:FMN:FAD [cytosol] (Canis familiaris)
MTRR:FMN:FAD [cytosol] (Danio rerio)
MTRR:FMN:FAD [cytosol] (Dictyostelium discoideum)
MTRR:FMN:FAD [cytosol] (Gallus gallus)
MTRR:FMN:FAD [cytosol] (Mus musculus)
MTRR:FMN:FAD [cytosol] (Rattus norvegicus)
MTRR:FMN:FAD [cytosol] (Sus scrofa)
MTRR:FMN:FAD [cytosol] (Xenopus tropicalis)
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