Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
FDX2 [mitochondrial matrix]
Stable Identifier
R-HSA-2395506
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
FDX1L, Adrenodoxin-like protein, mitochondrial, ADXL_HUMAN
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Metabolic disorders of biological oxidation enzymes (Homo sapiens)
Defective CYP11A1 causes AICSR (Homo sapiens)
Defective CYP11A1 does not cleave 20a,22b-DHCHOL (Homo sapiens)
CYP11A1 mutants:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
Metabolism (Homo sapiens)
Biological oxidations (Homo sapiens)
Phase I - Functionalization of compounds (Homo sapiens)
Cytochrome P450 - arranged by substrate type (Homo sapiens)
Endogenous sterols (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (ox.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Metabolism of steroids (Homo sapiens)
Metabolism of steroid hormones (Homo sapiens)
Pregnenolone biosynthesis (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (ox.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
Mitochondrial iron-sulfur cluster biogenesis (Homo sapiens)
Electron transport from NADPH to Ferredoxin (Homo sapiens)
FDXR transfers electrons to FDX1,2 (FDX1L) (Homo sapiens)
FDX1,FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Homo sapiens)
FDX1,FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q6P4F2 FDX2
Gene Names
FDX2, FDX1L
Chain
transit peptide:1-52, chain:53-183
Reference Genes
BioGPS Gene:112812 FDX2
COSMIC (genes):FDX2 FDX2
CTD Gene:112812 FDX2
dbSNP Gene:112812 FDX2
ENSEMBL:ENSG00000267673 FDX2
HGNC:30546 FDX2
Monarch:112812 FDX2
NCBI Gene:112812 FDX2
OMIM:614585 FDX2
UCSC:Q6P4F2 FDX2
Reference Transcript
RefSeq:NM_001031734.3 FDX2
Other Identifiers
112812
11720366_at
16868638
16868654
226451_PM_at
226451_at
3850203
3850204
3850205
3850206
3850207
3850208
3850209
3850210
3850211
3850212
3850213
3850214
3850215
3850216
3850217
3850218
3850219
3850220
3850221
3850222
3850223
3850224
3850225
3850226
3850229
3850233
54158_at
8033960
A_24_P416656
A_24_P416660
A_33_P3320748
GO:0005515
GO:0005739
GO:0005759
GO:0006091
GO:0009055
GO:0016226
GO:0022900
GO:0043226
GO:0044571
GO:0044572
GO:0046872
GO:0051536
GO:0051537
GO:0140647
GO:1990229
HMNXSV003014423
HMNXSV003042961
Hs.72169.0.A1_3p_at
ILMN_1744628
PH_hs_0012029
PH_hs_0016555
TC19001161.hg
Participates
as a component of
FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
Inferred To
Fdx2 [mitochondrial matrix]
(Rattus norvegicus)
fdx2 [mitochondrial matrix]
(Xenopus tropicalis)
FDX2 [mitochondrial matrix]
(Bos taurus)
FDX2 [mitochondrial matrix]
(Caenorhabditis elegans)
FDX2 [mitochondrial matrix]
(Canis familiaris)
FDX2 [mitochondrial matrix]
(Danio rerio)
FDX2 [mitochondrial matrix]
(Dictyostelium discoideum)
FDX2 [mitochondrial matrix]
(Drosophila melanogaster)
FDX2 [mitochondrial matrix]
(Mus musculus)
FDX2 [mitochondrial matrix]
(Plasmodium falciparum)
FDX2 [mitochondrial matrix]
(Saccharomyces cerevisiae)
FDX2 [mitochondrial matrix]
(Sus scrofa)
Cross References
RefSeq
NP_001026904.2
ENSEMBL
ENSP00000377311
,
ENST00000393708
OpenTargets
ENSG00000267673
HPA
ENSG00000267673-FDX2
PRO
Q6P4F2
Pharos - Targets
Q6P4F2
PDB
2Y5C
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text