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FDX1L (red.) [mitochondrial matrix]
Stable Identifier
R-HSA-2395503
Type
Complex
Species
Homo sapiens
Compartment
mitochondrial matrix
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Metabolic disorders of biological oxidation enzymes (Homo sapiens)
Defective CYP11A1 causes Adrenal insufficiency, congenital, with 46,XY sex reversal (AICSR) (Homo sapiens)
Defective CYP11A1 does not cleave 20a,22b-DHCHOL (Homo sapiens)
CYP11A1 mutants:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
Metabolism (Homo sapiens)
Biological oxidations (Homo sapiens)
Phase I - Functionalization of compounds (Homo sapiens)
Cytochrome P450 - arranged by substrate type (Homo sapiens)
Endogenous sterols (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Metabolism of steroids (Homo sapiens)
Metabolism of steroid hormones (Homo sapiens)
Pregnenolone biosynthesis (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
Mitochondrial iron-sulfur cluster biogenesis (Homo sapiens)
Electron transport from NADPH to Ferredoxin (Homo sapiens)
FDXR transfers electrons to FDX1/1L (Homo sapiens)
FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Homo sapiens)
FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
Participants
components
(2Fe-2S)(1+) [mitochondrial matrix]
FDX1L [mitochondrial matrix] (Homo sapiens)
Participant Of
hasMember
FDX1,FDX1L (red.) [mitochondrial matrix]
Inferred To
FDX1L (red.) [mitochondrial matrix] (Arabidopsis thaliana)
FDX1L (red.) [mitochondrial matrix] (Bos taurus)
FDX1L (red.) [mitochondrial matrix] (Caenorhabditis elegans)
FDX1L (red.) [mitochondrial matrix] (Canis familiaris)
FDX1L (red.) [mitochondrial matrix] (Danio rerio)
FDX1L (red.) [mitochondrial matrix] (Drosophila melanogaster)
FDX1L (red.) [mitochondrial matrix] (Gallus gallus)
FDX1L (red.) [mitochondrial matrix] (Mus musculus)
FDX1L (red.) [mitochondrial matrix] (Oryza sativa)
FDX1L (red.) [mitochondrial matrix] (Plasmodium falciparum)
FDX1L (red.) [mitochondrial matrix] (Rattus norvegicus)
FDX1L (red.) [mitochondrial matrix] (Saccharomyces cerevisiae)
FDX1L (red.) [mitochondrial matrix] (Xenopus tropicalis)
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