Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
AFG3L2 [mitochondrial inner membrane]
Stable Identifier
R-CFA-8949650
Type
Protein [EntityWithAccessionedSequence]
Species
Canis familiaris
Compartment
mitochondrial inner membrane
Synonyms
AFG3L2, A0A8I3MPX0
Locations in the PathwayBrowser
Expand all
Metabolism of proteins (Canis familiaris)
Mitochondrial protein degradation (Canis familiaris)
AFG3L2 binds mitochondrial inner membrane proteins (Canis familiaris)
AFG3L2:Zn2+ hexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:substrate protein (mitochondrial inner membrane) [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ hexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 binds mitochondrial matrix proteins (Canis familiaris)
AFG3L2:Zn2+ hexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:substrate protein (mitochondrial matrix) [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ hexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 degrades mitochondrial inner membrane proteins (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ hexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:substrate protein (mitochondrial inner membrane) [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ hexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 degrades mitochondrial matrix proteins (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ hexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:substrate protein (mitochondrial matrix) [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ hexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:SPG7 binds SMDT1 (EMRE) (Canis familiaris)
AFG3L2:SPG7:SMDT1 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+:SPG7:Zn2+ heterohexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+:SPG7:Zn2+ heterohexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:SPG7 degrades SMDT1 (EMRE) (Canis familiaris)
AFG3L2:SPG7:SMDT1 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+:SPG7:Zn2+ heterohexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+:SPG7:Zn2+ heterohexamer [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
Transport of small molecules (Canis familiaris)
Mitochondrial calcium ion transport (Canis familiaris)
Processing of SMDT1 (Canis familiaris)
AFG3L2 (m-AAA protease) degrades SMDT1 that is not assembled in MCU (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
C2orf47:AFG3L2:SPG7:PHB:PHB2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
C2orf47:AFG3L2 binds the transit peptide of SMDT1 (Canis familiaris)
C2orf47:AFG3L2:SPG7:PHB:PHB2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
proSMDT1:C2orf47:AFG3L2:SPG7:PHB:PHB2 [mitochondrial inner membrane] (Canis familiaris)
C2orf47:AFG3L2:SPG7:PHB:PHB2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
PMPCA:PMPCB cleaves the transit peptide of proSMDT1 (proEMRE) (Canis familiaris)
C2orf47:AFG3L2:SPG7:PHB:PHB2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
proSMDT1:C2orf47:AFG3L2:SPG7:PHB:PHB2 [mitochondrial inner membrane] (Canis familiaris)
C2orf47:AFG3L2:SPG7:PHB:PHB2 [mitochondrial inner membrane] (Canis familiaris)
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
AFG3L2 [mitochondrial inner membrane] (Canis familiaris)
External Reference Information
External Reference
UniProt:A0A8I3MPX0
Gene Names
AFG3L2
Reference Genes
BioGPS Gene:490560 AFG3L2
ENSEMBL:ENSCAFG00845005029.1
Monarch:490560 AFG3L2
NCBI Gene:490560 AFG3L2
UCSC:A0A8I3MPX0 AFG3L2
Reference Transcript
RefSeq:XM_038543908.1 AFG3L2
RefSeq:XM_038672708.1 AFG3L2
RefSeq:XM_547682.7 AFG3L2
Other Identifiers
490560
Cfa.19965.1.S1_s_at
CfaAffx.28741.1.S1_at
GO:0000166
GO:0004176
GO:0004222
GO:0005524
GO:0005739
GO:0005743
GO:0005745
GO:0006508
GO:0007005
GO:0007409
GO:0007528
GO:0008053
GO:0008233
GO:0008237
GO:0008270
GO:0016020
GO:0016485
GO:0016540
GO:0016787
GO:0016887
GO:0021675
GO:0030163
GO:0033619
GO:0034330
GO:0034982
GO:0036444
GO:0040014
GO:0042407
GO:0042552
GO:0046872
GO:0048856
GO:0051560
GO:0051604
GO:0055001
GO:0055085
GO:0060013
GO:0072753
GO:0110097
GO:0140657
GO:0141164
GO:0160007
Participates
as a component of
AFG3L2:Zn2+ [mitochondrial inner membrane] (Canis familiaris)
Inferred From
AFG3L2 [mitochondrial inner membrane]
(Homo sapiens)
Cross References
RefSeq
XP_038528636.1
,
XP_038399836.1
,
XP_547682.2
ENSEMBL
ENSCAFP00845007117
,
ENSCAFT00845009027
,
ENSCAFG00845005029
© 2026
Reactome
This website requires cookies and the limited processing of your personal data in order to function. By using the site you are agreeing to this as outlined in our
Privacy Notice
.
I agree, dismiss this banner
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text