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(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment]
Stable Identifier
R-ALL-912298
Type
Chemical Compound [SimpleEntity]
Compartment
endoplasmic reticulum quality control compartment
Synonyms
N(4)-{alpha-D-Man-(1->2)-alpha-D-Man-(1->3)-[alpha-D-Man-(1->2)-alpha-D-Man-(1->3)-[alpha-D-Man-(1->2)-alpha-D-Man-(1->6)]-alpha-D-Man-(1->6)]-beta-D-Man-(1->4)-beta-D-GlaNAc-(1->4)-beta-D-GlcNAc}-Asn residue, N(4)-{alpha-D-Man-(1->2)-alpha-D-Man-(1->3)-[alpha-D-Man-(1->2)-alpha-D-Man-(1->3)-[alpha-D-Man-(1->2)-alpha-D-Man-(1->6)]-alpha-D-Man-(1->6)]-beta-D-Man-(1->4)-beta-D-GlcNAc-(1->4)-beta-D-GlcNAc}-Asn residue
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with N-glycosylation of proteins (Homo sapiens)
Defective MAN1B1 causes MRT15 (Homo sapiens)
Defective MAN1B1 does not hydrolyse a second 1,2-linked mannose (a branch) (Homo sapiens)
unfolded protein:(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment] (Homo sapiens)
(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment]
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Asparagine N-linked glycosylation (Homo sapiens)
N-glycan trimming in the ER and Calnexin/Calreticulin cycle (Homo sapiens)
Calnexin/calreticulin cycle (Homo sapiens)
ER Quality Control Compartment (ERQC) (Homo sapiens)
MAN1B1 hydrolyses 1,2-linked mannose (a branch) (Homo sapiens)
unfolded protein:(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment] (Homo sapiens)
(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment]
MAN1B1 hydrolyses a second 1,2-linked mannose (a branch) (Homo sapiens)
unfolded protein:(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment] (Homo sapiens)
(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment]
OS9:SEL1:ERAD E3 ligase:DERL2 ubiquitinates unfolded protein:(GlcNAc)2 (Man)9-5 (Homo sapiens)
Ub-unfolded protein:(GlcNAc)2 (Man)9-5 [endoplasmic reticulum quality control compartment] (Homo sapiens)
unfolded protein:(GlcNAc)2 (Man)9-5 [endoplasmic reticulum quality control compartment] (Homo sapiens)
unfolded protein:(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment] (Homo sapiens)
(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment]
unfolded protein:(GlcNAc)2 (Man)9-5 [endoplasmic reticulum quality control compartment] (Homo sapiens)
unfolded protein:(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment] (Homo sapiens)
(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment]
Ub-unfolded protein:(GlcNAc)2 (Man)9-5 translocates from ERQC to cytosol (Homo sapiens)
Ub-unfolded protein:(GlcNAc)2 (Man)9-5 [endoplasmic reticulum quality control compartment] (Homo sapiens)
unfolded protein:(GlcNAc)2 (Man)9-5 [endoplasmic reticulum quality control compartment] (Homo sapiens)
unfolded protein:(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment] (Homo sapiens)
(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment]
Transport to the Golgi and subsequent modification (Homo sapiens)
Transport of glycoproteins with Man8 (or Man9) N-glycans to the Golgi (Homo sapiens)
Glycoproteins with Man8 N-glycans [endoplasmic reticulum quality control compartment] (Homo sapiens)
unfolded protein:(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment] (Homo sapiens)
(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment]
External Reference Information
External Reference
N(4)-{alpha-D-Man-(1->2)-alpha-D-Man-(1->3)-[alpha-D-Man-(1->2)-alpha-D-Man-(1->3)-[alpha-D-Man-(1->2)-alpha-D-Man-(1->6)]-alpha-D-Man-(1->6)]-beta-D-Man-(1->4)-beta-D-GlcNAc-(1->4)-beta-D-GlcNAc}-Asn residue [ChEBI:60627]
Participates
as a component of
unfolded protein:(GlcNAc)2 (Man)8a [endoplasmic reticulum quality control compartment] (Homo sapiens)
Other forms of this molecule
(GlcNAc)2 (Man)8a [Golgi lumen]
(GlcNAc)2 (Man)8a [COPII-coated ER to Golgi transport vesicle]
(GlcNAc)2 (Man)8a [endoplasmic reticulum lumen]
(GlcNAc)2 (Man)8a [endoplasmic reticulum-Golgi intermediate compartment membrane]
(GlcNAc)2 (Man)8a [cytosol]
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