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Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Stable Identifier
R-ALL-2105007
Type
Chemical Compound [SimpleEntity]
Compartment
lysosomal lumen
Synonyms
beta-D-Galp6S-(1->4)-beta-D-GlcpNAc6S-(1->3)-beta-D-Galp-(1->4)-beta-D-GlcpNAc6S-(1->3)-D-Galp
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Canis familiaris
Danio rerio
Gallus gallus
Mus musculus
Rattus norvegicus
Schizosaccharomyces pombe
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates and carbohydrate derivatives (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Keratan sulfate/keratin metabolism (Bos taurus)
Keratan sulfate degradation (Bos taurus)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Bos taurus)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates and carbohydrate derivatives (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Keratan sulfate/keratin metabolism (Canis familiaris)
Keratan sulfate degradation (Canis familiaris)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Canis familiaris)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Metabolism (Danio rerio)
Metabolism of carbohydrates and carbohydrate derivatives (Danio rerio)
Glycosaminoglycan metabolism (Danio rerio)
Keratan sulfate/keratin metabolism (Danio rerio)
Keratan sulfate degradation (Danio rerio)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Danio rerio)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates and carbohydrate derivatives (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Keratan sulfate/keratin metabolism (Gallus gallus)
Keratan sulfate degradation (Gallus gallus)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Gallus gallus)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of carbohydrate metabolism (Homo sapiens)
Mucopolysaccharidoses (Homo sapiens)
MPS IV - Morquio syndrome A (Homo sapiens)
Defective GALNS does not hydrolyse sulfate from Gal6S in keratan sulfate (Homo sapiens)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates and carbohydrate derivatives (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Keratan sulfate/keratin metabolism (Homo sapiens)
Keratan sulfate degradation (Homo sapiens)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Homo sapiens)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Unknown endo-β-galactosidase cleaves keratan chain (Homo sapiens)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates and carbohydrate derivatives (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Keratan sulfate/keratin metabolism (Mus musculus)
Keratan sulfate degradation (Mus musculus)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Mus musculus)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates and carbohydrate derivatives (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Keratan sulfate/keratin metabolism (Rattus norvegicus)
Keratan sulfate degradation (Rattus norvegicus)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Rattus norvegicus)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Metabolism (Schizosaccharomyces pombe)
Metabolism of carbohydrates and carbohydrate derivatives (Schizosaccharomyces pombe)
Glycosaminoglycan metabolism (Schizosaccharomyces pombe)
Keratan sulfate/keratin metabolism (Schizosaccharomyces pombe)
Keratan sulfate degradation (Schizosaccharomyces pombe)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Schizosaccharomyces pombe)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates and carbohydrate derivatives (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Keratan sulfate/keratin metabolism (Sus scrofa)
Keratan sulfate degradation (Sus scrofa)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Sus scrofa)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates and carbohydrate derivatives (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Keratan sulfate/keratin metabolism (Xenopus tropicalis)
Keratan sulfate degradation (Xenopus tropicalis)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Xenopus tropicalis)
Gal(S)-GlcNAc(S)-Gal-GlcNAc(S)-Gal [lysosomal lumen]
External Reference Information
External Reference
beta-D-Galp6S-(1->4)-beta-D-GlcpNAc6S-(1->3)-beta-D-Galp-(1->4)-beta-D-GlcpNAc6S-(1->3)-D-Galp [ChEBI:63846]
Participates
as an input of
Defective GALNS does not hydrolyse sulfate from Gal6S in keratan sulfate (Homo sapiens)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Schizosaccharomyces pombe)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Gallus gallus)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Xenopus tropicalis)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Danio rerio)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Sus scrofa)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Bos taurus)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Canis familiaris)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Rattus norvegicus)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Mus musculus)
GALNS oligomer hydrolyses sulfate from Gal6S in keratan sulfate (Homo sapiens)
as an output of
Unknown endo-β-galactosidase cleaves keratan chain (Homo sapiens)
Cross References
KEGG Glycan
G13031
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