Reactome | BCKDHA:BCKDHB tetramer [mitochondrial matrix]

Schema > Complex > Entries

BCKDHA:BCKDHB tetramer [mitochondrial matrix] Show undefined attributes

compartment	[Compartment:5460] mitochondrial matrix
componentOf	[Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens [Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] - Homo sapiens
dbId	70016
deleted	[Deleted:508265] Deletion of instances: 70052, 70044, 70031
displayName	BCKDHA:BCKDHB tetramer [mitochondrial matrix]
hasComponent	2 × [EntityWithAccessionedSequence:R-HSA-70014] BCKDHA [mitochondrial matrix] 2 × [EntityWithAccessionedSequence:R-HSA-70015] BCKDHB [mitochondrial matrix] 4 × [SimpleEntity:R-ALL-9859159] K+ [mitochondrial matrix] 2 × [SimpleEntity:R-ALL-113547] TDP [mitochondrial matrix]
inDisease	false
inferredTo	[Complex:R-MMU-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Mus musculus [Complex:R-RNO-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Rattus norvegicus [Complex:R-CFA-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Canis familiaris [Complex:R-BTA-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Bos taurus [Complex:R-SSC-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Sus scrofa [Complex:R-DRE-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Danio rerio [Complex:R-XTR-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Xenopus tropicalis [Complex:R-GGA-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Gallus gallus [Complex:R-DME-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Drosophila melanogaster [Complex:R-CEL-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Caenorhabditis elegans [Complex:R-DDI-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Dictyostelium discoideum [Complex:R-PFA-70016] BCKDHA:BCKDHB tetramer [mitochondrial matrix] - Plasmodium falciparum
maxDepth	2
modified	[InstanceEdit:9859160] Stephan, Ralf, 2024-01-16
name	BCKDHA:BCKDHB tetramer 2xBCKDHA:2xBCKDHB:2xTDP branched-chain alpha-ketoacid dehydrogenase E1 complex
schemaClass	Complex
species	[Species:48887] Homo sapiens
stId	R-HSA-70016

Referrals

(replacementInstances)	[Deleted:508265] Deletion of instances: 70052, 70044, 70031
(hasComponent)	[Complex:R-HSA-9865106] DBT mutant-BCKDH [mitochondrial matrix] [Complex:R-HSA-9907590] DLD mutant-BCKDH [mitochondrial matrix] [Complex:R-HSA-70019] BCKDH [mitochondrial matrix]
(activeUnit)	[CatalystActivity:9859137] oxidoreductase activity, acting on the aldehyde or oxo group of donors, disulfide as acceptor of BCKDH [mitochondrial matrix]

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