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Schema
>
Reaction
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Entries
POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1
Show undefined attributes
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authored
[InstanceEdit:5617054] Jassal, Bijay, 2014-07-30
catalystActivity
[CatalystActivity:5617108] acetylglucosaminyltransferase activity of POMGNT1:Mn2+ [Golgi membrane]
category
transition
compartment
[Compartment:17963] Golgi lumen
[Compartment:20699] Golgi membrane
created
[InstanceEdit:5617054] Jassal, Bijay, 2014-07-30
crossReference
[DatabaseIdentifier:9942324] RHEA:54129
dbId
5617037
diseaseReaction
[FailedReaction:R-HSA-5617096] Defective POMGNT1 does not transfer GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - Homo sapiens
displayName
POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1
edited
[InstanceEdit:5617054] Jassal, Bijay, 2014-07-30
eventOf
[Pathway:R-HSA-8932506] DAG1 core M1 glycosylations - Homo sapiens
followingEvent
[Reaction:R-HSA-8932427] MGAT5B transfers GlcNAc from UDP-GlcNAc to GlcNAc-Man-DAG1 - Homo sapiens
input
[EntityWithAccessionedSequence:R-HSA-9940750] Core M3-DAG1 [Golgi lumen]
2 ×
[SimpleEntity:R-ALL-914003] UDP-GlcNAc [Golgi lumen]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:5617077] Muscular dystrophy and neuronal migration disorder caused by mutations in a glycosyltransferase, POMGnT1
maxDepth
1
modified
[InstanceEdit:10732209] Weiser, Joel, 2026-03-16
name
POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1
orthologousEvent
[Reaction:R-GGA-5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - Gallus gallus
[Reaction:R-XTR-5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - Xenopus tropicalis
[Reaction:R-DRE-5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - Danio rerio
[Reaction:R-SSC-5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - Sus scrofa
[Reaction:R-BTA-5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - Bos taurus
[Reaction:R-CFA-5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - Canis familiaris
[Reaction:R-RNO-5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - Rattus norvegicus
[Reaction:R-MMU-5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - Mus musculus
output
[EntityWithAccessionedSequence:R-HSA-5617087] Core M1,3-DAG1 [Golgi lumen]
2 ×
[SimpleEntity:R-ALL-425969] H+ [Golgi lumen]
2 ×
[SimpleEntity:R-ALL-205687] UDP [Golgi lumen]
precedingEvent
[BlackBoxEvent:R-HSA-9940714] Glycosylated alpha-DAG1 localizes to Golgi - Homo sapiens
previousReviewStatus
[ReviewStatus:9821384] two stars
releaseDate
2016-03-23
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:8849944] Hansen, Lars, Joshi, Hiren, 2015-12-18
[InstanceEdit:9944933] D'Eustachio, Peter, 2025-04-08
[InstanceEdit:9947107] Zaru, Rossana, 2025-05-01
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-5617037
summation
[Summation:5617083] Golgi membrane resident protein O-linked-mannose beta-1,2-N-...
updateTrackers
[UpdateTracker:9953744] Update Tracker - [Reaction:5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - v93:[add_removeInput, removeOutput]
[UpdateTracker:9782772] Update Tracker - [Reaction:5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - v58:[add_removeInput, add_removeOutput, modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9953744] Update Tracker - [Reaction:5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - v93:[add_removeInput, removeOutput]
[UpdateTracker:9782772] Update Tracker - [Reaction:5617037] POMGNT1 transfers GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1 - v58:[add_removeInput, add_removeOutput, modifyText]
(normalReaction)
[FailedReaction:R-HSA-5617096] Defective POMGNT1 does not transfer GlcNAc from UDP-GlcNAc to Man-O-Ser-DAG1
(hasEvent)
[Pathway:R-HSA-8932506] DAG1 core M1 glycosylations
[Pathway:R-HSA-8932504] DAG1 core M2 glycosylations
(precedingEvent)
[Reaction:R-HSA-8932427] MGAT5B transfers GlcNAc from UDP-GlcNAc to GlcNAc-Man-DAG1
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